The American Journal of Human Genetics - 2009

225 articles | Last updated: 2025-12-03 14:12:57
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T A T A T A T A
mtDNA Data Mining in GenBank Needs Surveying
Response to Li et al.
The Biological Coherence of Human Phenome Databases
A Truncating Mutation of TRAPPC9 Is Associated with Autosomal-Recessive Intellectual Disability and Postnatal Microcephaly
Meta-Analysis of Genome-wide Association Studies with Overlapping Subjects
Homozygous Inactivating Mutations in the NKX3-2 Gene Result in Spondylo-Megaepiphyseal-Metaphyseal Dysplasia
Response to Falush: A Role for cis-Element Polymorphisms in HD
Combination of Linkage Mapping and Microarray-Expression Analysis Identifies NF-κB Signaling Defect as a Cause of Autosomal-Recessive Mental Retardation
Dosage-Dependent Severity of the Phenotype in Patients with Mental Retardation Due to a Recurrent Copy-Number Gain at Xq28 Mediated by an Unusual Recombination
Genetic Landscape of Eurasia and “Admixture” in Uyghurs
Haplotype Background, Repeat Length Evolution, and Huntington's Disease
Identification of Mutations in TRAPPC9, which Encodes the NIK- and IKK-β-Binding Protein, in Nonsyndromic Autosomal-Recessive Mental Retardation
Loss of Dermatan-4-Sulfotransferase 1 Function Results in Adducted Thumb-Clubfoot Syndrome
Remarkably Little Variation in Proteins Encoded by the Y Chromosome's Single-Copy Genes, Implying Effective Purifying Selection
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Response to Yao et al.
A Cytogenetic Abnormality and Rare Coding Variants Identify ABCA13 as a Candidate Gene in Schizophrenia, Bipolar Disorder, and Depression
Genomic Dissection of Population Substructure of Han Chinese and Its Implication in Association Studies
Deletions and Point Mutations of LRRC50 Cause Primary Ciliary Dyskinesia Due to Dynein Arm Defects
Genetic Structure of the Han Chinese Population Revealed by Genome-wide SNP Variation
Short Telomeres are Sufficient to Cause the Degenerative Defects Associated with Aging
Loss-of-Function Mutations in the Human Ortholog of Chlamydomonas reinhardtii ODA7 Disrupt Dynein Arm Assembly and Cause Primary Ciliary Dyskinesia
Using Lifetime Risk Estimates in Personal Genomic Profiles: Estimation of Uncertainty
Simultaneous Genotype Calling and Haplotype Phasing Improves Genotype Accuracy and Reduces False-Positive Associations for Genome-wide Association Studies
ATRIUM: Testing Untyped SNPs in Case-Control Association Studies with Related Individuals
FREM1 Mutations Cause Bifid Nose, Renal Agenesis, and Anorectal Malformations Syndrome
Gene-centric Association Signals for Lipids and Apolipoproteins Identified via the HumanCVD BeadChip
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Common Variants in the Trichohyalin Gene Are Associated with Straight Hair in Europeans Europeans
CNTNAP2 and NRXN1 Are Mutated in Autosomal-Recessive Pitt-Hopkins-like Mental Retardation and Determine the Level of a Common Synaptic Protein in Drosophila
Mutation of the Variant α-Tubulin TUBA8 Results in Polymicrogyria with Optic Nerve Hypoplasia
Mutations in TRPM1 Are a Common Cause of Complete Congenital Stationary Night Blindness
TRPM1 Is Mutated in Patients with Autosomal-Recessive Complete Congenital Stationary Night Blindness
Autosomal-Dominant Retinitis Pigmentosa Caused by a Mutation in SNRNP200, a Gene Required for Unwinding of U4/U6 snRNAs
Recessive Mutations of the Gene TRPM1 Abrogate ON Bipolar Cell Function and Cause Complete Congenital Stationary Night Blindness in Humans
Spinocerebellar Ataxia Type 31 Is Associated with “Inserted” Penta-Nucleotide Repeats Containing (TGGAA)n
Public Opinion about the Importance of Privacy in Biobank Research
The Relationship between Imputation Error and Statistical Power in Genetic Association Studies in Diverse Populations
Sequence Variants in Three Loci Influence Monocyte Counts and Erythrocyte Volume
Mutations in the Beta Propeller WDR72 Cause Autosomal-Recessive Hypomaturation Amelogenesis Imperfecta
Use of a Modified α-N-Acetylgalactosaminidase in the Development of Enzyme Replacement Therapy for Fabry Disease
A Distinct DNA-Methylation Boundary in the 5′- Upstream Sequence of the FMR1 Promoter Binds Nuclear Proteins and Is Lost in Fragile X Syndrome
Identification of CANT1 Mutations in Desbuquois Dysplasia
Missense Mutations in a Retinal Pigment Epithelium Protein, Bestrophin-1, Cause Retinitis Pigmentosa
Homozygous Mutations in ADAMTS10 and ADAMTS17 Cause Lenticular Myopia, Ectopia Lentis, Glaucoma, Spherophakia, and Short Stature
A Genome-wide Association Study of Lung Cancer Identifies a Region of Chromosome 5p15 Associated with Risk for Adenocarcinoma
Mutations in LTBP4 Cause a Syndrome of Impaired Pulmonary, Gastrointestinal, Genitourinary, Musculoskeletal, and Dermal Development
Ethics and Newborn Genetic Screening: New Technologies, New Challenges
A Common Variation in EDAR Is a Genetic Determinant of Shovel-Shaped Incisors
Familial Hemophagocytic Lymphohistiocytosis Type 5 (FHL-5) Is Caused by Mutations in Munc18-2 and Impaired Binding to Syntaxin 11
Incidence of Fragile X Syndrome by Newborn Screening for Methylated FMR1 DNA
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Identification of an Agrin Mutation that Causes Congenital Myasthenia and Affects Synapse Function
Genomic and Genic Deletions of the FOX Gene Cluster on 16q24.1 and Inactivating Mutations of FOXF1 Cause Alveolar Capillary Dysplasia and Other Malformations
OFD1 Is Mutated in X-Linked Joubert Syndrome and Interacts with LCA5-Encoded Lebercilin
Clinical Diagnostics in Human Genetics with Semantic Similarity Searches in Ontologies
Integration of Genomic and Genetic Approaches Implicates IREB2 as a COPD Susceptibility Gene
Rare, Evolutionarily Unlikely Missense Substitutions in ATM Confer Increased Risk of Breast Cancer
PPIB Mutations Cause Severe Osteogenesis Imperfecta
A Homozygous Nonsense Mutation in the Human Desmocollin-3 (DSC3) Gene Underlies Hereditary Hypotrichosis and Recurrent Skin Vesicles
Heterozygous NTF4 Mutations Impairing Neurotrophin-4 Signaling in Patients with Primary Open-Angle Glaucoma
Complex Segmental Duplications Mediate a Recurrent dup(X)(p11.22-p11.23) Associated with Mental Retardation, Speech Delay, and EEG Anomalies in Males and Females
Genetic Rounds: A Doctor's Encounters in the Field that Revolutionized Medicine
Epistasis and Its Implications for Personal Genetics
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Mutations in MMP9 and MMP13 Determine the Mode of Inheritance and the Clinical Spectrum of Metaphyseal Anadysplasia
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The Editors' Recollections on the Occasion of the 60th Anniversary of The American Journal of Human Genetics
A Generalized Family-Based Association Test for Dichotomous Traits
Acute Infantile Liver Failure Due to Mutations in the TRMU Gene
Allele-Specific Chromatin Remodeling in the ZPBP2/GSDMB/ORMDL3 Locus Associated with the Risk of Asthma and Autoimmune Disease
Mutations in LOXHD1, an Evolutionarily Conserved Stereociliary Protein, Disrupt Hair Cell Function in Mice and Cause Progressive Hearing Loss in Humans
FREM1 Mutations Cause Bifid Nose, Renal Agenesis, and Anorectal Malformations Syndrome
Folate Receptor Alpha Defect Causes Cerebral Folate Transport Deficiency: A Treatable Neurodegenerative Disorder Associated with Disturbed Myelin Metabolism
A Positive Modifier of Spinal Muscular Atrophy in the SMN2 Gene
Mutations of the FHL1 Gene Cause Emery-Dreifuss Muscular Dystrophy
Complex Segmental Duplications Mediate a Recurrent dup(X)(p11.22-p11.23) Associated with Mental Retardation, Speech Delay, and EEG Anomalies in Males and Females
The Ethics of Protocells—Moral and Social Implications of Creating Life in the Laboratory
Massively Parallel Sequencing: The Next Big Thing in Genetic Medicine
PRKCA: A Positional Candidate Gene for Body Mass Index and Asthma
X Chromosomal Variation Is Associated with Slow Progression to AIDS in HIV-1-Infected Women
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IDS Crossing of the Blood-Brain Barrier Corrects CNS Defects in MPSII Mice
A Heterozygous Truncating Mutation in RRM2B Causes Autosomal-Dominant Progressive External Ophthalmoplegia with Multiple mtDNA Deletions
Genome-wide Association Study Reveals Multiple Nasopharyngeal Carcinoma-Associated Loci within the HLA Region at Chromosome 6p21.3
Dominant Renin Gene Mutations Associated with Early-Onset Hyperuricemia, Anemia, and Chronic Kidney Failure
A Genome-wide In Vitro Bacterial-Infection Screen Reveals Human Variation in the Host Response Associated with Inflammatory Disease
CMIP and ATP2C2 Modulate Phonological Short-Term Memory in Language Impairment
Molecular Basis of DFNB73: Mutations of BSND Can Cause Nonsyndromic Deafness or Bartter Syndrome
Skewed X Chromosome Inactivation and Trisomic Spontaneous Abortion: No Association
Spinal Muscular Atrophy with Pontocerebellar Hypoplasia Is Caused by a Mutation in the VRK1 Gene
Mutations in the Fatty Acid Transport Protein 4 Gene Cause the Ichthyosis Prematurity Syndrome
Identification of an Agrin Mutation that Causes Congenital Myasthenia and Affects Synapse Function
RIN2 Deficiency Results in Macrocephaly, Alopecia, Cutis Laxa, and Scoliosis: MACS Syndrome
Mutations in MMP9 and MMP13 Determine the Mode of Inheritance and the Clinical Spectrum of Metaphyseal Anadysplasia
Homozygosity Mapping Reveals PDE6C Mutations in Patients with Early-Onset Cone Photoreceptor Disorders
Multiple Synostoses Syndrome Is Due to a Missense Mutation in Exon 2 of FGF9 Gene
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Diverse Evolutionary Histories for β-adrenoreceptor Genes in Humans
Gene Conversion between the X Chromosome and the Male-Specific Region of the Y Chromosome at a Translocation Hotspot
Noncoding Mutations of HGF Are Associated with Nonsyndromic Hearing Loss, DFNB39
Deficiency of Dol-P-Man Synthase Subunit DPM3 Bridges the Congenital Disorders of Glycosylation with the Dystroglycanopathies
Mutation in Pyrroline-5-Carboxylate Reductase 1 Gene in Families with Cutis Laxa Type 2
Genome-wide Study of Families with Absolute Pitch Reveals Linkage to 8q24.21 and Locus Heterogeneity
PRKCA: A Positional Candidate Gene for Body Mass Index and Asthma
Loss-of-Function Mutation in the Dioxygenase-Encoding FTO Gene Causes Severe Growth Retardation and Multiple Malformations
Mutation in the AP4M1 Gene Provides a Model for Neuroaxonal Injury in Cerebral Palsy
Closing the Gap: Inverting the Genetics Curriculum to Ensure an Informed Public
WNT10A Mutations Are a Frequent Cause of a Broad Spectrum of Ectodermal Dysplasias with Sex-Biased Manifestation Pattern in Heterozygotes
Gene Ontology Analysis of GWA Study Data Sets Provides Insights into the Biology of Bipolar Disorder
Mutations in a BTB-Kelch Protein, KLHL7, Cause Autosomal-Dominant Retinitis Pigmentosa
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Fixing Sex: Intersex, Medical Authority, and Lived Experience
A Multiplex Human Syndrome Implicates a Key Role for Intestinal Cell Kinase in Development of Central Nervous, Skeletal, and Endocrine Systems
The Primordial Growth Disorder 3-M Syndrome Connects Ubiquitination to the Cytoskeletal Adaptor OBSL1
X Chromosome Inactivation Is Initiated in Human Preimplantation Embryos
Mutations in the Heparan-Sulfate Proteoglycan Glypican 6 (GPC6) Impair Endochondral Ossification and Cause Recessive Omodysplasia
Mitochondrial Haplogroup U5b3: A Distant Echo of the Epipaleolithic in Italy and the Legacy of the Early Sardinians
Genomic and Genic Deletions of the FOX Gene Cluster on 16q24.1 and Inactivating Mutations of FOXF1 Cause Alveolar Capillary Dysplasia and Other Malformations
Correcting for Purifying Selection: An Improved Human Mitochondrial Molecular Clock
Copy-Number Mutations on Chromosome 17q24.2-q24.3 in Congenital Generalized Hypertrichosis Terminalis with or without Gingival Hyperplasia
Mutation of a Gene Essential for Ribosome Biogenesis, EMG1, Causes Bowen-Conradi Syndrome
Mutations in NDUFAF3 (C3ORF60), Encoding an NDUFAF4 (C6ORF66)-Interacting Complex I Assembly Protein, Cause Fatal Neonatal Mitochondrial Disease
Genome-wide Association Analysis Identifies PDE4D as an Asthma-Susceptibility Gene
Mutations of KCNJ10 Together with Mutations of SLC26A4 Cause Digenic Nonsyndromic Hearing Loss Associated with Enlarged Vestibular Aqueduct Syndrome
The Diversity Present in 5140 Human Mitochondrial Genomes
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Genome-wide Association Study of Vitamin B6, Vitamin B12, Folate, and Homocysteine Blood Concentrations
Genetic Effects on Environmental Vulnerability to Disease
Genome-wide Insights into the Patterns and Determinants of Fine-Scale Population Structure in Humans
DYNC2H1 Mutations Cause Asphyxiating Thoracic Dystrophy and Short Rib-Polydactyly Syndrome, Type III
Human RAD50 Deficiency in a Nijmegen Breakage Syndrome-like Disorder
Mutations in Smooth Muscle Alpha-Actin (ACTA2) Cause Coronary Artery Disease, Stroke, and Moyamoya Disease, Along with Thoracic Aortic Disease
The Mitochondrial Disulfide Relay System Protein GFER Is Mutated in Autosomal-Recessive Myopathy with Cataract and Combined Respiratory-Chain Deficiency
IFRD1 Is a Candidate Gene for SMNA on Chromosome 7q22-q23
Frontorhiny, a Distinctive Presentation of Frontonasal Dysplasia Caused by Recessive Mutations in the ALX3 Homeobox Gene
Loss of the Metalloprotease ADAM9 Leads to Cone-Rod Dystrophy in Humans and Retinal Degeneration in Mice
Multilocus Bayesian Meta-Analysis of Gene-Disease Associations
Significant Linkage Evidence for a Predisposition Gene for Pelvic Floor Disorders on Chromosome 9q21
Gain-of-Function Mutation of KIT Ligand on Melanin Synthesis Causes Familial Progressive Hyperpigmentation
A Nonsense Mutation in COQ9 Causes Autosomal-Recessive Neonatal-Onset Primary Coenzyme Q10 Deficiency: A Potentially Treatable Form of Mitochondrial Disease
Revisiting Race in a Genomic Age
Genetic Control of Human Brain Transcript Expression in Alzheimer Disease
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IFAP Syndrome Is Caused by Deficiency in MBTPS2, an Intramembrane Zinc Metalloprotease Essential for Cholesterol Homeostasis and ER Stress Response
Ciliary Abnormalities Due to Defects in the Retrograde Transport Protein DYNC2H1 in Short-Rib Polydactyly Syndrome
Ovaries and Female Phenotype in a Girl with 46,XY Karyotype and Mutations in the CBX2 Gene
Null Mutations in LTBP2 Cause Primary Congenital Glaucoma
Population Analysis of Large Copy Number Variants and Hotspots of Human Genetic Disease
Winter Temperature and UV Are Tightly Linked to Genetic Changes in the p53 Tumor Suppressor Pathway in Eastern Asia
Human Male Infertility Caused by Mutations in the CATSPER1 Channel Protein
Oligodontia Is Caused by Mutation in LTBP3, the Gene Encoding Latent TGF-β Binding Protein 3
DECIPHER: Database of Chromosomal Imbalance and Phenotype in Humans Using Ensembl Resources
Association Test for X-Linked QTL in Family-Based Designs
Autosomal-Dominant Distal Myopathy Associated with a Recurrent Missense Mutation in the Gene Encoding the Nuclear Matrix Protein, Matrin 3
Duplications Involving a Conserved Regulatory Element Downstream of BMP2 Are Associated with Brachydactyly Type A2
TMEM126A, Encoding a Mitochondrial Protein, Is Mutated in Autosomal-Recessive Nonsyndromic Optic Atrophy
Genome-wide Linkage Screen in Familial Parkinson Disease Identifies Loci on Chromosomes 3 and 18
Genome-wide Association Study of Vitamin B6, Vitamin B12, Folate, and Homocysteine Blood Concentrations
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Haplotype-Sharing Analysis Implicates Chromosome 7q36 Harboring DPP6 in Familial Idiopathic Ventricular Fibrillation
Exocrine Pancreatic Insufficiency, Dyserythropoeitic Anemia, and Calvarial Hyperostosis Are Caused by a Mutation in the COX4I2 Gene
Mutations in SPATA7 Cause Leber Congenital Amaurosis and Juvenile Retinitis Pigmentosa
Genome-wide Association Study of Smoking Initiation and Current Smoking
Genome-wide Association and Replication Studies Identified TRHR as an Important Gene for Lean Body Mass
Genome-wide Association and Follow-Up Replication Studies Identified ADAMTS18 and TGFBR3 as Bone Mass Candidate Genes in Different Ethnic Groups
Mutations in BMP4 Are Associated with Subepithelial, Microform, and Overt Cleft Lip
Diverse Genome-wide Association Studies Associate the IL12/IL23 Pathway with Crohn Disease
CAG Expansion in the Huntington Disease Gene Is Associated with a Specific and Targetable Predisposing Haplogroup
Signatures of Purifying and Local Positive Selection in Human miRNAs
A Genome-wide Analysis Identifies Genetic Variants in the RELN Gene Associated with Otosclerosis
Mutations in the Gene Encoding the Calcium-Permeable Ion Channel TRPV4 Produce Spondylometaphyseal Dysplasia, Kozlowski Type and Metatropic Dysplasia
Replication Stress Induces Genome-wide Copy Number Changes in Human Cells that Resemble Polymorphic and Pathogenic Variants
Genotype-Imputation Accuracy across Worldwide Human Populations
Mutations in STIL, Encoding a Pericentriolar and Centrosomal Protein, Cause Primary Microcephaly
Awards and Addresses Summary
A Unified Approach to Genotype Imputation and Haplotype-Phase Inference for Large Data Sets of Trios and Unrelated Individuals
A Homozygous Mutation in ADAMTSL4 Causes Autosomal-Recessive Isolated Ectopia Lentis
Response to Zang et al. and Han et al.
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TFAP2A Mutations Result in Branchio-Oculo-Facial Syndrome
William Allan Award Introduction: Haig H. Kazazian, Jr.
A Testing Framework for Identifying Susceptibility Genes in the Presence of Epistasis
A Whole-Genome Scan and Fine-Mapping Linkage Study of Auditory-Visual Synesthesia Reveals Evidence of Linkage to Chromosomes 2q24, 5q33, 6p12, and 12p12
Is the Tail-Strength Measure More Powerful in Tests of Genetic Association?
A Missense Mutation in CASK Causes FG Syndrome in an Italian Family Italian (family)
Allan Award Lecture: On Jumping Fields and “Jumping Genes”
Mutations in CNNM4 Cause Recessive Cone-Rod Dystrophy with Amelogenesis Imperfecta
A Genome-wide Survey of the Prevalence and Evolutionary Forces Acting on Human Nonsense SNPs
Mutations in CNNM4 Cause Jalili Syndrome, Consisting of Autosomal-Recessive Cone-Rod Dystrophy and Amelogenesis Imperfecta
Mutations in Radial Spoke Head Protein Genes RSPH9 and RSPH4A Cause Primary Ciliary Dyskinesia with Central-Microtubular-Pair Abnormalities
Tail Strength to Combine Two p Values: Their Correlation Cannot Be Ignored
Inferential Genotyping of Y Chromosomes in Latter-Day Saints Founders and Comparison to Utah Samples in the HapMap Project
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Searching for Genotype-Phenotype Structure: Using Hierarchical Log-Linear Models in Crohn Disease
Common Variation in the β-Carotene 15,15′-Monooxygenase 1 Gene Affects Circulating Levels of Carotenoids: A Genome-wide Association Study
Mutations in SPINT2 Cause a Syndromic Form of Congenital Sodium Diarrhea
A Multiplex Human Syndrome Implicates a Key Role for Intestinal Cell Kinase in Development of Central Nervous, Skeletal, and Endocrine Systems
Population Analysis of Large Copy Number Variants and Hotspots of Human Genetic Disease
Genome-wide Linkage Scan Reveals Three Putative Breast-Cancer-Susceptibility Loci
Mutations in LPIN1 Cause Recurrent Acute Myoglobinuria in Childhood
Fine Mapping on Chromosome 10q22-q23 Implicates Neuregulin 3 in Schizophrenia
Low Allele Frequency of ADH1B∗47His in West China and Different ADH1B Haplotypes in Western and Eastern Asia
Distribution of the Alcohol Dehydrogenase ADH1B∗47His Allele in Eurasia
Genome-wide Association Study Implicates a Chromosome 12 Risk Locus for Late-Onset Alzheimer Disease
Infection-Triggered Familial or Recurrent Cases of Acute Necrotizing Encephalopathy Caused by Mutations in a Component of the Nuclear Pore, RANBP2
Deleterious Variants of FIG4, a Phosphoinositide Phosphatase, in Patients with ALS
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A Genome-wide Association Study Identifies Three Loci Associated with Mean Platelet Volume
A Recessive Skeletal Dysplasia, SEMD Aggrecan Type, Results from a Missense Mutation Affecting the C-Type Lectin Domain of Aggrecan
Mutations of the SYCP3 Gene in Women with Recurrent Pregnancy Loss
Mutations in DDR2 Gene Cause SMED with Short Limbs and Abnormal Calcifications
Genetic Defects in Surfactant Protein A2 Are Associated with Pulmonary Fibrosis and Lung Cancer
Variants in TF and HFE Explain ∼40% of Genetic Variation in Serum-Transferrin Levels
Association of Genetic Variants at 3q22 with Nephropathy in Patients with Type 1 Diabetes Mellitus