The American Journal of Human Genetics - 2004

329 articles | Last updated: 2025-12-03 14:12:57
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T A T A T A T A
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Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
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This Month in the<i>Journal</i>
Announcements11.Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please e-mail announcements to [email protected]. Submission must be received at l
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Employment Opportunities; Conference
This Month in the Journal
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Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please e-mail announcements to [email protected]. Submission must be received at
Announcements
This Month in the Journal
Contents of Volume 74
Employment Opportunities; Conference; Call for Patients
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
Contents of Volume 75
This Month in the Journal
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
This Month in the<i>Journal</i>
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
This Month in the Journal
This Month in the Journal
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
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Editorial Reviewers for 2004
This Month in the Journal
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Chronic and Recurrent Otitis Media: A Genome Scan for Susceptibility Loci
Mutations in the AHI1 Gene, Encoding Jouberin, Cause Joubert Syndrome with Cortical Polymicrogyria
Attention-Deficit/Hyperactivity Disorder in a Population Isolate: Linkage to Loci at 4q13.2, 5q33.3, 11q22, and 17p11
Comparison of Microsatellites Versus Single-Nucleotide Polymorphisms in a Genome Linkage Screen for Prostate Cancer–Susceptibility Loci
The Genetic or Mythical Ancestry of Descent Groups: Lessons from the Y Chromosome
Ignoring Linkage Disequilibrium among Tightly Linked Markers Induces False-Positive Evidence of Linkage for Affected Sib Pair Analysis
Complex Genetics of Amyotrophic Lateral Sclerosis
Contractions of D4Z4 on 4qB Subtelomeres Do Not Cause Facioscapulohumeral Muscular Dystrophy
A Common Mutation Is Associated with a Mild, Potentially Asymptomatic Phenotype in Patients with Isovaleric Acidemia Diagnosed by Newborn Screening
CYP3A Variation and the Evolution of Salt-Sensitivity Variants
A Second-Generation Genomic Screen for Multiple Sclerosis
Mutations in the X-Linked Cyclin-Dependent Kinase–Like 5 (CDKL5/STK9) Gene Are Associated with Severe Neurodevelopmental Retardation
Phylogeny of Mitochondrial DNA Macrohaplogroup N in India, Based on Complete Sequencing: Implications for the Peopling of South Asia
Errata
CHEK2 Is a Multiorgan Cancer Susceptibility Gene
A 77-Kilobase Region of Chromosome 6p22.2 Is Associated with Dyslexia in Families From the United Kingdom and From the United States
A Combined Linkage-Physical Map of the Human Genome
Polymorphisms in the Sclerosteosis/van Buchem Disease Gene (SOST) Region Are Associated with Bone-Mineral Density in Elderly Whites
Genetic Inheritance of Gene Expression in Human Cell Lines
Mutations of CDKL5 Cause a Severe Neurodevelopmental Disorder with Infantile Spasms and Mental Retardation
Errata
Evidence for Sex-Specific Risk Alleles in Autism Spectrum Disorder
A Genomewide Search Using an Original Pairwise Sampling Approach for Large Genealogies Identifies a New Locus for Total and Low-Density Lipoprotein Cholesterol in Two Genetically Differentiated Isolat
Etruscan Artifacts: Much Ado about Nothing
Autosomal Recessive Familial Exudative Vitreoretinopathy Is Associated with Mutations in LRP5
Erratum
Isolated 3-Methylcrotonyl-CoA Carboxylase Deficiency: Evidence for an Allele-Specific Dominant Negative Effect and Responsiveness to Biotin Therapy
Genetic Variation in Radiation-Induced Expression Phenotypes
ADAMTS10 Mutations in Autosomal Recessive Weill-Marchesani Syndrome
Identification of a KCNE2 Gain-of-Function Mutation in Patients with Familial Atrial Fibrillation
A Powerful and Robust New Linkage Statistic for Discordant Sibling Pairs
Disrupted in Schizophrenia 1 (DISC1): Association with Schizophrenia, Schizoaffective Disorder, and Bipolar Disorder
Finding Haplotype Tagging SNPs by Use of Principal Components Analysis
The Molecular Dissection of mtDNA Haplogroup H Confirms That the Franco-Cantabrian Glacial Refuge Was a Major Source for the European Gene Pool European gene pool
Ethiopian Mitochondrial DNA Heritage: Tracking Gene Flow Across and Around the Gate of Tears
Etruscan Artifacts
On the Etruscan Mitochondrial DNA Contribution to Modern Humans
Association of the DTNBP1 Locus with Schizophrenia in a U.S. Population
Statistical Tests for Admixture Mapping with Case-Control and Cases-Only Data
A Mutation in the Vesicle-Trafficking Protein VAPB Causes Late-Onset Spinal Muscular Atrophy and Amyotrophic Lateral Sclerosis
Association of the Gene Encoding Wingless-Type Mammary Tumor Virus Integration-Site Family Member 5B (WNT5B) with Type 2 Diabetes
GDD1 Is Identical to TMEM16E, a Member of the TMEM16 Family
Response to Katoh and Katoh
Family-Based Association Study of Synapsin II and Schizophrenia
Functional Analysis of Genetic Variation in Catechol-O-Methyltransferase (COMT): Effects on mRNA, Protein, and Enzyme Activity in Postmortem Human Brain
The Genetics of Sun Sensitivity in Humans
Microdeletion of LIT1 in Familial Beckwith-Wiedemann Syndrome
Chromosomal Instability at Common Fragile Sites in Seckel Syndrome
Attention Deficit Hyperactivity Disorder: Fine Mapping Supports Linkage to 5p13, 6q12, 16p13, and 17p11
Integrated Evaluation of DNA Sequence Variants of Unknown Clinical Significance: Application to BRCA1 and BRCA2
Indications of Linkage and Association of Gilles de la Tourette Syndrome in Two Independent Family Samples: 17q25 Is a Putative Susceptibility Region
A Powerful Strategy to Account for Multiple Testing in the Context of Haplotype Analysis
Genetics of Mitochondrial Diseases
Linkage Disequilibrium and Association of MAPT H1 in Parkinson Disease
Mutants: On Genetic Variety and the Human Body
Erratum
Transmission-Ratio Distortion and Allele Sharing in Affected Sib Pairs: A New Linkage Statistic with Reduced Bias, with Application to Chromosome 6q25.3
Germline PHOX2B Mutation in Hereditary Neuroblastoma
The Interleukin 1 Gene Cluster Contains a Major Susceptibility Locus for Ankylosing Spondylitis
Guidelines for Genotyping in Genomewide Linkage Studies: Single-Nucleotide–Polymorphism Maps Versus Microsatellite Maps
The Longue Durée of Genetic Ancestry: Multiple Genetic Marker Systems and Celtic Origins on the Atlantic Facade of Europe
NIPBL Mutational Analysis in 120 Individuals with Cornelia de Lange Syndrome and Evaluation of Genotype-Phenotype Correlations
No “Bias” Toward the Null Hypothesis in Most Conventional Multipoint Nonparametric Linkage Analyses
Conventional Multipoint Nonparametric Linkage Analysis Is Not Necessarily Inherently Biased
“Bias toward the Null” Means Reduced Power
No Bias in Linkage Analysis
Got Bias? The Authors Reply
Mutation History of the Roma/Gypsies
Mutations in the Slow Skeletal Muscle Fiber Myosin Heavy Chain Gene (MYH7) Cause Laing Early-Onset Distal Myopathy (MPD1)
The G/G Genotype of a Resistin Single-Nucleotide Polymorphism at −420 Increases Type 2 Diabetes Mellitus Susceptibility by Inducing Promoter Activity through Specific Binding of Sp1/3
Comparative Frequency of Fragile-X (FMR1) and Creatine Transporter (SLC6A8) Mutations in X-Linked Mental Retardation
Reply to Mandel
The IL12B Gene Is Associated with Asthma
Polymorphisms in the Trace Amine Receptor 4 (TRAR4) Gene on Chromosome 6q23.2 Are Associated with Susceptibility to Schizophrenia
Sequence-Based Linkage Analysis
Retinal Dehydrogenase 12 (RDH12) Mutations in Leber Congenital Amaurosis
Signatures of Selection and Gene Conversion Associated with Human Color Vision Variation
Microarray Analysis of Cell-Free Fetal DNA in Amniotic Fluid: a Prenatal Molecular Karyotype
Trisomy Recurrence: A Reconsideration Based on North American Data
Evidence for a Novel Late-Onset Alzheimer Disease Locus on Chromosome 19p13.2
Are Sequence Family Variants Useful for Identifying Deletions in the Human Y Chromosome?
Reply to Repping et al.
Genomewide Scan for Gout in Taiwanese Aborigines Reveals Linkage to Chromosome 4q25
Estimating the Rate of Gene Conversion on Human Chromosome 21
Problematic Use of Greenberg's Linguistic Classification of the Americas in Studies of Native American Genetic Variation
Erratum
Paternal Germline Origin and Sex-Ratio Distortion in Transmission of PTPN11 Mutations in Noonan Syndrome
High Frequency of Mosaicism among Patients with Neurofibromatosis Type 1 (NF1) with Microdeletions Caused by Somatic Recombination of the JJAZ1 Gene
Efficient Computation of Significance Levels for Multiple Associations in Large Studies of Correlated Data, Including Genomewide Association Studies
Human Genome Epidemiology
Genomewide Linkage Scan for Myopia Susceptibility Loci among Ashkenazi Jewish Families Shows Evidence of Linkage on Chromosome 22q12 Ashkenazi Jewish Families
Genetic Association of the R620W Polymorphism of Protein Tyrosine Phosphatase PTPN22 with Human SLE
Genetics and the Logic of Evolution
The Phylogeography of Mitochondrial DNA Haplogroup L3g in Africa and the Atlantic Slave Trade
Reply to Bortolini et al.
A Major Lung Cancer Susceptibility Locus Maps to Chromosome 6q23–25
Replication Study Supports Evidence for Linkage to 9p24 in Obsessive-Compulsive Disorder
A Genomewide Scan for Early-Onset Coronary Artery Disease in 438 Families: The GENECARD Study
The Future of Association Studies: Gene-Based Analysis and Replication
Beckwith-Wiedemann Syndrome and IVF: A Case-Control Study
Comparative Genomic Analysis Identifies an ADP-Ribosylation Factor–like Gene as the Cause of Bardet-Biedl Syndrome (BBS3)
Age-Related Maculopathy: A Genomewide Scan with Continued Evidence of Susceptibility Loci within the 1q31, 10q26, and 17q25 Regions
Mutations in the FTSJ1 Gene Coding for a Novel S-Adenosylmethionine–Binding Protein Cause Nonsyndromic X-Linked Mental Retardation
Common Variants in the 5′ Region of the Leptin Gene Are Associated with Body Mass Index in Men from the National Heart, Lung, and Blood Institute Family Heart Study
Mutations in the DLG3 Gene Cause Nonsyndromic X-Linked Mental Retardation
Intergenerational Instability of the Expanded CTG Repeat in the DMPK Gene: Studies in Human Gametes and Preimplantation Embryos
Mutations in the Gene Encoding Gap Junction Protein α12 (Connexin 46.6) Cause Pelizaeus-Merzbacher–Like Disease
Authenticity of Ancient-DNA Results: A Statistical Approach
A Missense Single-Nucleotide Polymorphism in a Gene Encoding a Protein Tyrosine Phosphatase (PTPN22) Is Associated with Rheumatoid Arthritis
High-Resolution Molecular Characterization of 15q11-q13 Rearrangements by Array Comparative Genomic Hybridization (Array CGH) with Detection of Gene Dosage
Mutations in Microcephalin Cause Aberrant Regulation of Chromosome Condensation
A Population-Genetic Test of Founder Effects and Implications for Ashkenazi Jewish Diseases
A Susceptibility Locus for Myopia in the Normal Population Is Linked to the PAX6 Gene Region on Chromosome 11: A Genomewide Scan of Dizygotic Twins
Jane M. Olson (December 6, 1952–May 2, 2004)
SLEN2 (2q34–35) and SLEN1 (10q22.3) Replication in Systemic Lupus Erythematosus Stratified by Nephritis
Genomewide Linkage Scan for Bipolar-Disorder Susceptibility Loci among Ashkenazi Jewish Families Ashkenazi Jewish
Meta-Analysis of 13 Genome Scans Reveals Multiple Cleft Lip/Palate Genes with Novel Loci on 9q21 and 2q32-35
The Hereditary Basis of Allergic Disease
Genotype-Phenotype Correlations for Nervous System Tumors in Neurofibromatosis 2: A Population-Based Study
Autosomal Dominant Avascular Necrosis of Femoral Head in Two Taiwanese Pedigrees and Linkage to Chromosome 12q13
Erratum
Large-Scale Single-Nucleotide Polymorphism (SNP) and Haplotype Analyses, Using Dense SNP Maps, of 199 Drug-Related Genes in 752 Subjects: the Analysis of the Association between Uncommon SNPs within H
A Predominantly Neolithic Origin for Y-Chromosomal DNA Variation in North Africa
The NPHP1 Gene Deletion Associated with Juvenile Nephronophthisis Is Present in a Subset of Individuals with Joubert Syndrome
Mutations in the Transmembrane Natriuretic Peptide Receptor NPR-B Impair Skeletal Growth and Cause Acromesomelic Dysplasia, Type Maroteaux
Uncommon Deletions of the Smith-Magenis Syndrome Region Can Be Recurrent When Alternate Low-Copy Repeats Act as Homologous Recombination Substrates
High Prevalence of SLC6A8 Deficiency in X-Linked Mental Retardation
Hypergonadotropic Ovarian Failure Associated with an Inherited Mutation of Human Bone Morphogenetic Protein-15 (BMP15) Gene
Linkage Disequilibrium Mapping via Cladistic Analysis of Single-Nucleotide Polymorphism Haplotypes
On the Significance of Linkage Studies of Complex Traits: Reply to Newton-Cheh et al.
Identification and Functional Analysis of a Defect in the Human ALG9 Gene: Definition of Congenital Disorder of Glycosylation Type IL
Theodore Reich, M.D. (1938–2003)
Theoretical and Empirical Power of Regression and Maximum-Likelihood Methods to Map Quantitative Trait Loci in General Pedigrees
Spinocerebellar Ataxia Type 8: Molecular Genetic Comparisonsand Haplotype Analysis of 37 Families with Ataxia
A HOX Gene Mutation in a Family with Isolated Congenital Vertical Talus and Charcot-Marie-Tooth Disease
Mechanism and Timing of Mitotic Rearrangements in the Subtelomeric D4Z4 Repeat Involved in Facioscapulohumeral Muscular Dystrophy
Whole-Genome Scan, in a Complex Disease, Using 11,245 Single-Nucleotide Polymorphisms: Comparison with Microsatellites
Phylogeography of Y-Chromosome Haplogroup I Reveals Distinct Domains of Prehistoric Gene Flow in Europe
On the Significance of Linkage Studies of Complex Traits
Erratum
A Common Haplotype of the Nicotine Acetylcholine Receptor α4 Subunit Gene Is Associated with Vulnerability to Nicotine Addiction in Men
Delineation of Cohen Syndrome Following a Large-Scale Genotype-Phenotype Screen
Allelic Heterogeneity in the COH1 Gene Explains Clinical Variabilityin Cohen Syndrome
Long-Term Safety and Efficacy of Enzyme Replacement Therapyfor Fabry Disease
Modes of Action of HLA-DR Susceptibility Specificities in Multiple Sclerosis
Nuclear Factor TDP-43 Binds to the Polymorphic TG Repeats in CFTR Intron 8 and Causes Skipping of Exon 9: A Functional Link with Disease Penetrance
Relevance of Connexin Deafness (DFNB1) to Human Evolution **This article represents the opinions of the authors and has not been peer-reviewed.
The T Allele of a Single-Nucleotide Polymorphism 13.9 kb Upstream of the Lactase Gene (LCT) (C−13.9kbT) Does Not Predict or Cause the Lactase-Persistence Phenotype in Africans
Genetic Signatures of Strong Recent Positive Selection at the Lactase Gene
Fibroblast Growth Factor 20 Polymorphisms and Haplotypes Strongly Influence Risk of Parkinson Disease
Mutated MESP2 Causes Spondylocostal Dysostosis in Humans
DNA/RNA Helicase Gene Mutations in a Form of Juvenile Amyotrophic Lateral Sclerosis (ALS4)
Graphical Modeling of the Joint Distribution of Alleles at Associated Loci
Comparative Genomic Hybridization–Array Analysis Enhances the Detection of Aneuploidies and Submicroscopic Imbalances in Spontaneous Miscarriages
CHEK2*1100delC and Susceptibility to Breast Cancer: A Collaborative Analysis Involving 10,860 Breast Cancer Cases and 9,065 Controls from 10 Studies
Linkage Analysis of a Complex Disease through Use of Admixed Populations
Extended Linkage Disequilibrium Surrounding the Hemoglobin E Variant Due to Malarial Selection
Mutations in the Human TBX4 Gene Cause Small Patella Syndrome
Penetrance and Expressivity of MSH6 Germline Mutations in Seven Kindreds Not Ascertained by Family History
Genomewide Significant Linkage to Recurrent, Early-Onset Major Depressive Disorder on Chromosome 15q
Offspring Gender Ratio and the Rate of Recurrent Spontaneous Miscarriages in Jewish Women at High Risk for Breast/Ovarian Cancer
Disruption of Contactin 4 (CNTN4) Results in Developmental Delay and Other Features of 3p Deletion Syndrome
Lost Paradises and the Ethics of Research and Publication.
Somatic and Germline Instability of the ATTCT Repeat in Spinocerebellar Ataxia Type 10
The Novel Gene Encoding a Putative Transmembrane Protein Is Mutated in Gnathodiaphyseal Dysplasia (GDD)
Insulin Receptor Splicing Alteration in Myotonic Dystrophy Type 2
Highly Significant Linkage to the SLI1 Locus in an Expanded Sample of Individuals Affected by Specific Language Impairment
Missense Mutation in Pseudouridine Synthase 1 (PUS1) Causes Mitochondrial Myopathy and Sideroblastic Anemia (MLASA)
A Comprehensive Survey of Human Y-Chromosomal Microsatellites
Mutations of the Ephrin-B1 Gene Cause Craniofrontonasal Syndrome
Chromosomal Abnormalities among Offspring of Childhood-Cancer Survivors in Denmark: A Population-Based Study
AICA-Ribosiduria: A Novel, Neurologically Devastating Inborn Error of Purine Biosynthesis Caused by Mutation of ATIC
Bias toward the Null Hypothesis in Model-Free Linkage Analysis Is Highly Dependent on the Test Statistic Used
A Genomewide Scan Identifies Novel Early-Onset Primary Open-Angle Glaucoma Loci on 9q22 and 20p12
Bietti Crystalline Corneoretinal Dystrophy Is Caused by Mutations in the Novel Gene CYP4V2
MSH2 c.1452–1455delAATG Is a Founder Mutation and an Important Cause of Hereditary Nonpolyposis Colorectal Cancer in the Southern Chinese Population Southern Chinese Population
Origin, Diffusion, and Differentiation of Y-Chromosome Haplogroups E and J: Inferences on the Neolithization of Europe and Later Migratory Events in the Mediterranean Area Neolithization of Europe; Europe; Mediterranean area
Erratum
Fragile-X–Associated Tremor/Ataxia Syndrome (FXTAS) in Females with the FMR1 Premutation
Little Loss of Information Due to Unknown Phase for Fine-Scale Linkage-Disequilibrium Mapping with Single-Nucleotide–Polymorphism Genotype Data
Rare Autosomal Recessive Cardiac Valvular Form of Ehlers-Danlos Syndrome Results from Mutations in the COL1A2 Gene That Activate the Nonsense-Mediated RNA Decay Pathway
Design and Analysis of Admixture Mapping Studies
Ching Chun Li (1912–2003):A Personal Remembrance of a Hero of Genetics
Methods for High-Density Admixture Mapping of Disease Genes
Where West Meets East: The Complex mtDNA Landscape of the Southwest and Central Asian Corridor
Positional Cloning by Linkage Disequilibrium
Myotonic Dystrophy: RNA Pathogenesis Comes into Focus
Linkage Disequilibrium Mapping of Schizophrenia Susceptibility to the CAPON Region of Chromosome 1q22
Genomewide Linkage Analysis of Bipolar Disorder by Use of a High-Density Single-Nucleotide–Polymorphism (SNP) Genotyping Assay: A Comparison with Microsatellite Marker Assays and Finding of Significan
Natural Selection and Population History in the Human Angiotensinogen Gene (AGT): 736 Complete AGT Sequences in Chromosomes from Around the World
Identification of a Novel Gene (HSN2) Causing Hereditary Sensory and Autonomic Neuropathy Type II through the Study of Canadian Genetic Isolates
Novel PMS2 Pseudogenes Can Conceal Recessive Mutations Causing a Distinctive Childhood Cancer Syndrome
The Genetic Architecture of Selection at the Human Dopamine Receptor D4 (DRD4) Gene Locus
A High-Density Admixture Map for Disease Gene Discovery in African Americans
Inferring Phylogenies.
Analyses of Genetic Structure of Tibeto-Burman Populations Reveals Sex-Biased Admixture in Southern Tibeto-Burmans
Mutations in AXIN2 Cause Familial Tooth Agenesis and Predispose to Colorectal Cancer
Phylogeographic Analysis of Haplogroup E3b (E-M215) Y Chromosomes Reveals Multiple Migratory Events Within and Out Of Africa
The Fragile-X Premutation: A Maturing Perspective
Polymorphisms in the Low-Density Lipoprotein Receptor–Related Protein 5 (LRP5) Gene Are Associated with Variation in Vertebral Bone Mass, Vertebral Bone Size, and Stature in Whites
Genomewide Linkage Scan Identifies a Novel Susceptibility Locus for Restless Legs Syndrome on Chromosome 9p
Haplotype Diversity across 100 Candidate Genes for Inflammation, Lipid Metabolism, and Blood Pressure Regulation in Two Populations
Huntington’s Disease
Entwined Lives: Twins and What They Tell Us about Human Behavior
A Dual Phenotype of Periventricular Nodular Heterotopia and Frontometaphyseal Dysplasia in One Patient Caused by a Single FLNA Mutation Leading to Two Functionally Different Aberrant Transcripts
Novel Analytical Methods Applied to Type 1 Diabetes Genome-Scan Data
Mutations in LRP5 or FZD4 Underlie the Common Familial Exudative Vitreoretinopathy Locus on Chromosome 11q
Novel Truncating Mutations in the Polyglutamine Tract Binding Protein 1 Gene (PQBP1) Cause Renpenning Syndrome and X-Linked Mental Retardation in Another Family with Microcephaly
A Simple Correction for Multiple Testing for Single-Nucleotide Polymorphisms in Linkage Disequilibrium with Each Other
High Proportion of Mutant Osteoblasts Is Compatible with Normal Skeletal Function in Mosaic Carriers of Osteogenesis Imperfecta**Presented as a platform presentation at the National Meeting of the Ame
Power for Genetic Association Studies with Random Allele Frequencies and Genotype Distributions
The Etruscans: A Population-Genetic Study
Nonmuscle Myosin Heavy-Chain Gene MYH14 Is Expressed in Cochlea and Mutated in Patients Affected by Autosomal Dominant Hearing Impairment (DFNA4)
Crohn Disease: Frequency and Nature of CARD15 Mutations in Ashkenazi and Sephardi/Oriental Jewish Families Ashkenazi and Sephardi/Oriental Jewish families
Errata
Epigenetics and Assisted Reproductive Technology: A Call for Investigation
Natural Selection and Molecular Evolution in PTC, a Bitter-Taste Receptor Gene
Paradoxical NSD1 Mutations in Beckwith-Wiedemann Syndrome and 11p15 Anomalies in Sotos Syndrome
Identification of 51 Novel Exons of the Usher Syndrome Type 2A (USH2A) Gene That Encode Multiple Conserved Functional Domains and That Are Mutated in Patients with Usher Syndrome Type II
The Western and Eastern Roots of the Saami—the Story of Genetic “Outliers” Told by Mitochondrial DNA and Y Chromosomes
Ribose-5-Phosphate Isomerase Deficiency: New Inborn Error in the Pentose Phosphate Pathway Associated with a Slowly Progressive Leukoencephalopathy
Germline Mutations of the Paired–Like Homeobox 2B (PHOX2B) Gene in Neuroblastoma
Variations in GABRA2, Encoding the α2 Subunit of the GABAA Receptor, Are Associated with Alcohol Dependence and with Brain Oscillations
Errata
Increasing the Power and Efficiency of Disease-Marker Case-Control Association Studies through Use of Allele-Sharing Information
Genomewide Scan in Families with Schizophrenia from the Founder Population of Afrikaners Reveals Evidence for Linkage and Uniparental Disomy on Chromosome 1
Introductory Speech for Joan Marks**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November 8, 2003.
Introductory Speech for Sir David Weatherall**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November 7, 2003.
The African Diaspora: Mitochondrial DNA and the Atlantic Slave Trade
Errata
X-Chromosome Inactivation Patterns Are Unbalanced and Affect the Phenotypic Outcome in a Mouse Model of Rett Syndrome
Impact of Genotyping Errors on Type I Error Rate of the Haplotype-Sharing Transmission/Disequilibrium Test (HS-TDT)
Errata
Melanocortin-4 Receptor Gene Variant I103 Is Negatively Associated with Obesity
On Low Expectations Exceeded; or, The Genomic Salvation of the Y Chromosome**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November 8, 2003.
Age-Related Macular Degeneration: A High-Resolution Genome Scan for Susceptibility Loci in a Population Enriched for Late-Stage Disease
Genetics, Individuality, and Medicine in the 21st Century**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November 5, 2003.
The Thalassemias: The Role of Molecular Genetics in an Evolving Global Health Problem**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November
Assessing Whether an Allele Can Account in Part for a Linkage Signal: The Genotype-IBD Sharing Test (GIST)
Introductory Speech for David Page**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November 8, 2003.
2003 Cotterman Award Winners
Multiple Comparisons in Studies of Gene × Gene and Gene × Environment Interaction
Revisiting the Clinical Validity of Multiplex Genetic Testing in Complex Diseases
Reply to Kraft
Revisiting the Clinical Validity of Multiplex Genetic Testing in Complex Diseases: Reply to Janssens et al.
Errata
Linkage Analysis of Extremely Discordant and Concordant Sibling Pairs Identifies Quantitative Trait Loci Influencing Variation in Human Menopausal Age
X-Linked Mental Retardation and Autism Are Associated with a Mutation in the NLGN4 Gene, a Member of the Neuroligin Family
Human Male Recombination Maps for Individual Chromosomes
Homozygous WNT3 Mutation Causes Tetra-Amelia in a Large Consanguineous Family
Incorporating Genotyping Uncertainty in Haplotype Inference for Single-Nucleotide Polymorphisms
Intracranial Aneurysms in Finnish Families: Confirmation of Linkage and Refinement of the Interval to Chromosome 19q13.3 Finnish families
The Levant versus the Horn of Africa: Evidence for Bidirectional Corridors of Human Migrations
Reply to Knapp and Becker
Deficiency of GDP-Man:GlcNAc2-PP-Dolichol Mannosyltransferase Causes Congenital Disorder of Glycosylation Type Ik
Congenital Disorder of Glycosylation Type Ik (CDG-Ik): A Defect of Mannosyltransferase I
The Importance of Genetic Counseling**Previously presented at the annual meeting of The American Society of Human Genetics, in Los Angeles, on November 8, 2003.
Oculocutaneous Albinism Type 4 Is One of the Most Common Types of Albinism in Japan
Both Rare and Common Polymorphisms Contribute Functional Variation at CHGA, a Regulator of Catecholamine Physiology
Are Variants in the CAPN10 Gene Related to Risk of Type 2 Diabetes? A Quantitative Assessment of Population and Family-Based Association Studies
Confirmation of Linkage to Chromosome 1q for Peak Vertebral Bone Mineral Density in Premenopausal White Women
Erratum
Comparative Genomics and the Evolution of Human Mitochondrial DNA: Assessing the Effects of Selection
Pathogenic Mutations Associated with Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy Differently Affect Jagged1 Binding and Notch3 Activity via the RBP/JK Si
Genomewide Linkage Analysis for Internal Carotid Artery Intimal Medial Thickness: Evidence for Linkage to Chromosome 12
Premature Myocardial Infarction Novel Susceptibility Locus on Chromosome 1P34-36 Identified by Genomewide Linkage Analysis
Joint Analysis of the DRD5 Marker Concludes Association with Attention-Deficit/Hyperactivity Disorder Confined to the Predominantly Inattentive and Combined Subtypes
Pleiotropic Effects of a Chromosome 3 Locus on Speech-Sound Disorder and Reading
PBAT: Tools for Family-Based Association Studies
Ethylmalonic Encephalopathy Is Caused by Mutations in ETHE1, a Gene Encoding a Mitochondrial Matrix Protein
Mutations in the VLGR1 Gene Implicate G-Protein Signaling in the Pathogenesis of Usher Syndrome Type II
Inherent Bias toward the Null Hypothesis in Conventional Multipoint Nonparametric Linkage Analysis
Null Leukemia Inhibitory Factor Receptor (LIFR) Mutations in Stüve-Wiedemann/Schwartz-Jampel Type 2 Syndrome
Matching Strategies for Genetic Association Studies in Structured Populations
Evidence of a Novel Quantitative-Trait Locus for Obesity on Chromosome 4p in Mexican Americans
Mutations within the MGC4607 Gene Cause Cerebral Cavernous Malformations
The Breakpoint Region of the Most Common Isochromosome, i(17q), in Human Neoplasia Is Characterized by a Complex Genomic Architecture with Large, Palindromic, Low-Copy Repeats
Hormones, Genes, and Cancer
Dissection of Genomewide-Scan Data in Extended Families Reveals a Major Locus and Oligogenic Susceptibility for Age-Related Macular Degeneration
Linkage at 12q24 with Systemic Lupus Erythematosus (SLE) Is Established and Confirmed in Hispanic and European American Families European American; Hispanic
A Novel Syndrome Combining Thyroid and Neurological Abnormalities Is Associated with Mutations in a Monocarboxylate Transporter Gene
Selecting a Maximally Informative Set of Single-Nucleotide Polymorphisms for Association Analyses Using Linkage Disequilibrium
Antisense-Induced Multiexon Skipping for Duchenne Muscular Dystrophy Makes More Sense
Population-Genetic Basis of Haplotype Blocks in the 5q31 Region
The Burden of Genetic Disease on Inpatient Care in a Children’s Hospital
Early-Onset Renal Cell Carcinoma as a Novel Extraparaganglial Component of SDHB-Associated Heritable Paraganglioma
Evidence for Extensive Transmission Distortion in the Human Genome
A Large AZFc Deletion Removes DAZ3/DAZ4 and Nearby Genes from Men in Y Haplogroup N
Maternally Inherited Aminoglycoside-Induced and Nonsyndromic Deafness Is Associated with the Novel C1494T Mutation in the Mitochondrial 12S rRNA Gene in a Large Chinese Family
The PARK8 Locus in Autosomal Dominant Parkinsonism: Confirmation of Linkage and Further Delineation of the Disease-Containing Interval
The Effective Mutation Rate at Y Chromosome Short Tandem Repeats, with Application to Human Population-Divergence Time
Mapping Multiple Sclerosis Susceptibility to the HLA-DR Locus in African Americans
Identification and Functional Analysis of ZIC3 Mutations in Heterotaxy and Related Congenital Heart Defects
Variation in a Repeat Sequence Determines Whether a Common Variant of the Cystic Fibrosis Transmembrane Conductance Regulator Gene Is Pathogenic or Benign
Mutation of CERKL, a Novel Human Ceramide Kinase Gene, Causes Autosomal Recessive Retinitis Pigmentosa (RP26)
Novel Vitiligo Susceptibility Loci on Chromosomes 7 (AIS2) and 8 (AIS3), Confirmation of SLEV1 on Chromosome 17, and Their Roles in an Autoimmune Diathesis