The American Journal of Human Genetics - 2003

385 articles | Last updated: 2025-12-03 14:12:57
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T A T A T A T A
Announcements11.Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
Notice of Policy
This Month in the Journal
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
This Month in the Journal
Announcements
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Editorial Reviewers for 2003
This Month in the Journal
Erratum
This Month in the Journal
This Month in the Journal
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
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Employment Opportunites; Training Programs
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
Employment Opportunities; Course; Meeting; Conference
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Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Contents of Volume 72
Employment Opportunities; Resources for Human Genetic Research; ABMG Diplomates
Employment Opportunities; Call for Patients; Course
Editorial Reviewers for 2003
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Contents of Volume 73
Announcements1
Allelic Heterogeneity in LINE-1 Retrotransposition Activity
Further Evidence of IBD5/CARD15 (NOD2) Epistasis in the Susceptibility to Ulcerative Colitis
Dominant Intermediate Charcot-Marie-Tooth Type C Maps to Chromosome 1p34-p35
Capillary Malformation–Arteriovenous Malformation, a New Clinical and Genetic Disorder Caused by RASA1 Mutations
Genetic Anthropology of the Colorectal Cancer–Susceptibility Allele APC I1307K: Evidence of Genetic Drift within the Ashkenazim Ashkenazim
MDR1 Ala893 Polymorphism Is Associated with Inflammatory Bowel Disease
The DTNBP1 (Dysbindin) Gene Contributes to Schizophrenia, Depending on Family History of the Disease
Erratum
Erratum
Array-Based Comparative Genomic Hybridization for the Genomewide Detection of Submicroscopic Chromosomal Abnormalities
Predisposition Locus for Major Depression at Chromosome 12q22-12q23.2
Reciprocal Crossovers and a Positional Preference for Strand Exchange in Recombination Events Resulting in Deletion or Duplication of Chromosome 17p11.2
Prevalence and Evolutionary Origins of the del(GJB6-D13S1830) Mutation in the DFNB1 Locus in Hearing-Impaired Subjects: a Multicenter Study
A Systematic Genomewide Linkage Study in 353 Sib Pairs with Schizophrenia
SVA Elements Are Nonautonomous Retrotransposons that Cause Disease in Humans
Mutations in the ZNF41 Gene Are Associated with Cognitive Deficits: Identification of a New Candidate for X-Linked Mental Retardation
Reports of the Death of the Epistasis Model Are Greatly Exaggerated
Comparative Linkage-Disequilibrium Analysis of the β-Globin Hotspot in Primates
Affected-Sib-Pair Data Can Be Used to Distinguish Two-Locus Heterogeneity from Two-Locus Epistasis
Reply to Cordell and Farrall
Cockayne Syndrome Group B Cellular and Biochemical Functions
Fine-Scale Mapping of Disease Genes with Multiple Mutations via Spatial Clustering Techniques
Informativeness of Genetic Markers for Inference of Ancestry*
A Novel Claudin 16 Mutation Associated with Childhood Hypercalciuria Abolishes Binding to ZO-1 and Results in Lysosomal Mistargeting
Inference on Haplotype Effects in Case-Control Studies Using Unphased Genotype Data
Mutations in a Gene Encoding a Novel Protein Containing a Phosphotyrosine-Binding Domain Cause Type 2 Cerebral Cavernous Malformations
Search for Haplotype Interactions That Influence Susceptibility to Type 1 Diabetes, through Use of Unphased Genotype Data
Missense Mutations in hMLH1 and hMSH2 Are Associated with Exonic Splicing Enhancers
Genomewide Distribution of High-Frequency, Completely Mismatching SNP Haplotype Pairs Observed To Be Common across Human Populations
David M. Danks, M.D., A.O. (June 4, 1931–July 8, 2003):Founder, Murdoch Childrens Research Institute
Sequence Analysis in a Nutshell: A Guide to Common Tools and Databases
Maspardin Is Mutated in Mast Syndrome, a Complicated Form of Hereditary Spastic Paraplegia Associated with Dementia
Accounting for Linkage in Family-Based Tests of Association with Missing Parental Genotypes
Protein-Truncating Mutations in ASPM Cause Variable Reduction in Brain Size
Mutations in the γ-Actin Gene (ACTG1) Are Associated with Dominant Progressive Deafness (DFNA20/26)
A Comparison of Bayesian Methods for Haplotype Reconstruction from Population Genotype Data
RP2 and RPGR Mutations and Clinical Correlations in Patients with X-Linked Retinitis Pigmentosa
Localization of a Gene for Migraine without Aura to Chromosome 4q21
A Major Susceptibility Locus on Chromosome 22q12 Plays a Critical Role in the Control of Kala-Azar
Origin and Diffusion of mtDNA Haplogroup X
Mutations in a Novel Gene, NHS, Cause the Pleiotropic Effects of Nance-Horan Syndrome, Including Severe Congenital Cataract, Dental Anomalies, and Mental Retardation
Microduplication 22q11.2, an Emerging Syndrome: Clinical, Cytogenetic, and Molecular Analysis of Thirteen Patients
Ordered-Subsets Linkage Analysis Detects Novel Alzheimer Disease Loci on Chromosomes 2q34 and 15q22
Meta-Analysis and a Large Association Study Confirm a Role for Calpain-10 Variation in Type 2 Diabetes Susceptibility
Haplotypes in the Dystrophin DNA Segment Point to a Mosaic Origin of Modern Human Diversity
Germline Inactivation of PTEN and Dysregulation of the Phosphoinositol-3-Kinase/Akt Pathway Cause Human Lhermitte-Duclos Disease in Adults
Replication Inhibitors Modulate Instability of an Expanded Trinucleotide Repeat at the Myotonic Dystrophy Type 1 Disease Locus in Human Cells
eIF2B-Related Disorders: Antenatal Onset and Involvement of Multiple Organs
Molecular and Fluorescence In Situ Hybridization Characterization of the Breakpoints in 46 Large Supernumerary Marker 15 Chromosomes Reveals an Unexpected Level of Complexity
Mutations in a Gene Encoding a Novel SH3/TPR Domain Protein Cause Autosomal Recessive Charcot-Marie-Tooth Type 4C Neuropathy
Mutations in the Gene Encoding Capillary Morphogenesis Protein 2 Cause Juvenile Hyaline Fibromatosis and Infantile Systemic Hyalinosis
Multiple Origins of Ashkenazi Levites: Y Chromosome Evidence for Both Near Eastern and European Ancestries European Ancestries
Genomic Imprinting and Linkage Test for Quantitative-Trait Loci in Extended Pedigrees
Genomewide Linkage and Linkage Disequilibrium Analyses Identify COL6A1, on Chromosome 21, as the Locus for Ossification of the Posterior Longitudinal Ligament of the Spine
Myotonic Dystrophy Type 2: Human Founder Haplotype and Evolutionary Conservation of the Repeat Tract
Mutations in Capillary Morphogenesis Gene-2 Result in the Allelic Disorders Juvenile Hyaline Fibromatosis and Infantile Systemic Hyalinosis
Erratum
HLA-DRB1*1101: A Significant Risk Factor for Sarcoidosis in Blacks and Whites Blacks and Whites
Slowed Conduction and Thin Myelination of Peripheral Nerves Associated with Mutant Rho Guanine-Nucleotide Exchange Factor 10
The Paternal-Age Effect in Apert Syndrome Is Due, in Part, to the Increased Frequency of Mutations in Sperm
A Genomewide Scan for Age-Related Macular Degeneration Provides Evidence for Linkage to Several Chromosomal Regions
Pooled Analysis of Loss of Heterozygosity in Breast Cancer: a Genome Scan Provides Comparative Evidence for Multiple Tumor Suppressors and Identifies Novel Candidate Regions
SCA8 Repeat Expansion Coexists with SCA1—Not Only with SCA6
Confirmation of the Type 2 Myotonic Dystrophy (CCTG) Expansion Mutation in Patients with Proximal Myotonic Myopathy/Proximal Myotonic Dystrophy of Different European Origins: A Single Shared Haplotype Different European Origins
Common and Unique Susceptibility Loci in Graves and Hashimoto Diseases: Results of Whole-Genome Screening in a Data Set of 102 Multiplex Families
Recent Advances in Human Quantitative-Trait–Locus Mapping: Comparison of Methods for Selected Sibling Pairs
Recent Advances in Human Quantitative-Trait–Locus Mapping: Comparison of Methods for Discordant Sibling Pairs
Using the Noninformative Families in Family-Based Association Tests: A Powerful New Testing Strategy
An Alu Transposition Model for the Origin and Expansion of Human Segmental Duplications
Loss of CpG Methylation Is Strongly Correlated with Loss of Histone H3 Lysine 9 Methylation at DMR-LIT1 in Patients with Beckwith-Wiedemann Syndrome
A Genomewide Screen of 345 Families for Autism-Susceptibility Loci
Erroneous Claims about the Impact of Mitochondrial DNA Sequence Database Errors
Identification of Four Highly Conserved Genes between Breakpoint Hotspots BP1 and BP2 of the Prader-Willi/Angelman Syndromes Deletion Region That Have Undergone Evolutionary Transposition Mediated by
NIPA1 Gene Mutations Cause Autosomal Dominant Hereditary Spastic Paraplegia (SPG6)
“Are We There Yet?”: Deciding When One Has Demonstrated Specific Genetic Causation in Complex Diseases and Quantitative Traits
This Month in the Journal
Genetic Disorders of the Skeleton: A Developmental Approach
ACTN3 Genotype Is Associated with Human Elite Athletic Performance
A Locus for Hereditary Sensory Neuropathy with Cough and Gastroesophageal Reflux on Chromosome 3p22-p24
Age-Related Macular Degeneration—a Genome Scan in Extended Families
Phylogeny of East Asian Mitochondrial DNA Lineages Inferred from Complete Sequences
CARD15: a Pleiotropic Autoimmune Gene That Confers Susceptibility to Psoriatic Arthritis
Assessing the Performance of the Haplotype Block Model of Linkage Disequilibrium
A Full-Likelihood Method for the Evaluation of Causality of Sequence Variants from Family Data
Natural Selection on the Olfactory Receptor Gene Family in Humans and Chimpanzees
A Genome Scan for Modifiers of Age at Onset in Huntington Disease: The HD MAPS Study
Extensive Normal Copy Number Variation of a β-Defensin Antimicrobial-Gene Cluster
Genomewide Linkage Scan for Schizophrenia Susceptibility Loci among Ashkenazi Jewish Families Shows Evidence of Linkage on Chromosome 10q22 Ashkenazi Jewish
Reflections of Our Past: How Human History Is Revealed in Our Genes
Linkage Analysis in Families with Joubert Syndrome Plus Oculo-Renal Involvement Identifies the CORS2 Locus on Chromosome 11p12-q13.3
Novel Case-Control Test in a Founder Population Identifies P-Selectin as an Atopy-Susceptibility Locus
Description, Nomenclature, and Mapping of a Novel Cerebello-Renal Syndrome with the Molar Tooth Malformation
This Month in the Journal
MC1R Mutations Modify the Classic Phenotype of Oculocutaneous Albinism Type 2 (OCA2)
Y-Chromosome Evidence for Differing Ancient Demographic Histories in the Americas
A Novel Y-Chromosome Variant Puts an Upper Limit on the Timing of First Entry into the Americas
ERRATUM
Effects of Electron-Beam Irradiation on Buccal-Cell DNA
Miller-Dieker Syndrome: Analysis of a Human Contiguous Gene Syndrome in the Mouse
Selection and Evaluation of Tagging SNPs in the Neuronal-Sodium-Channel Gene SCN1A: Implications for Linkage-Disequilibrium Gene Mapping
An Integrated Haplotype Map of the Human Major Histocompatibility Complex
Dependence of Mutational Asymmetry on Gene-Expression Levels in the Human Genome
ERRATUM
Transmission/Disequilibrium Test Based on Haplotype Sharing for Tightly Linked Markers
Estimation of the Inbreeding Coefficient through Use of Genomic Data
Mutations of the RNA-Specific Adenosine Deaminase Gene (DSRAD) Are Involved in Dyschromatosis Symmetrica Hereditaria
Association of Specific Language Impairment (SLI) to the Region of 7q31
Ovarian Failure Related to Eukaryotic Initiation Factor 2B Mutations
Familial and Ovarian Cancer: Genetics, Screening and Management
Errors, Phantom and Otherwise, in Human mtDNA Sequences
South Asia, the Andamanese, and the Genetic Evidence for an “Early” Human Dispersal out of Africa
Reply to Cordaux and Stoneking
A Genomewide Screen for Generalized Vitiligo: Confirmation of AIS1 on Chromosome 1p31 and Evidence for Additional Susceptibility Loci
A Locus for Autosomal Dominant Mitral Valve Prolapse on Chromosome 11p15.4
A Populationwide Coalescent Analysis of Icelandic Matrilineal and Patrilineal Genealogies: Evidence for a Faster Evolutionary Rate of mtDNA Lineages than Y Chromosomes
Cohen Syndrome Is Caused by Mutations in a Novel Gene, COH1, Encoding a Transmembrane Protein with a Presumed Role in Vesicle-Mediated Sorting and Intracellular Protein Transport
The Structure of Linkage Disequilibrium at the DBH Locus Strongly Influences the Magnitude of Association between Diallelic Markers and Plasma Dopamine β-Hydroxylase Activity
A Whole-Genome Screen of a Quantitative Trait of Age-Related Maculopathy in Sibships from the Beaver Dam Eye Study
Variation in the HLA-G Promoter Region Influences Miscarriage Rates
Sequence Analysis of the Mitochondrial Genomes from Dutch Pedigrees with Leber Hereditary Optic Neuropathy
Disruption of the Serine/Threonine Kinase 9 Gene Causes Severe X-Linked Infantile Spasms and Mental Retardation
Mutations of the PAX6 Gene Detected in Patients with a Variety of Optic-Nerve Malformations
Genomewide Scan for Hand Osteoarthritis: A Novel Mutation in Matrilin-3
Essentials of Medical Genomics
Control of Confounding of Genetic Associations in Stratified Populations
Mutations in the Transcription Factor Gene SOX18 Underlie Recessive and Dominant Forms of Hypotrichosis-Lymphedema-Telangiectasia
Reply to Bunce et al.
Single-Nucleotide Polymorphisms and Glaucoma Severity
Identification of a Novel Gene and a Common Variant Associated with Uric Acid Nephrolithiasis in a Sardinian Genetic Isolate Sardinian genetic isolate
Two Modes of Germline Instability at Human Minisatellite MS1 (Locus D1S7): Complex Rearrangements and Paradoxical Hyperdeletion
Multiple Mutations ofMYO1A, a Cochlear-Expressed Gene, in Sensorineural Hearing Loss
Association and Interaction of the IL4R, IL4, and IL13 Loci with Type 1 Diabetes among Filipinos
A Novel Class of Tests for the Detection of Mitochondrial DNA–Mutation Involvement in Diseases
A Neutral Explanation for the Correlation of Diversity with Recombination Rates in Humans
Definition of a Critical Region on Chromosome 18 for Congenital Aural Atresia by ArrayCGH
Babyface: A Story of Heart and Bones
DNA Microarrays: A Molecular Cloning Manual
Ehlers-Danlos Syndrome with Severe Early-Onset Periodontal Disease (EDS-VIII) Is a Distinct, Heterogeneous Disorder with One Predisposition Gene at Chromosome 12p13
IBD5 is a General Risk Factor for Inflammatory Bowel Disease: Replication of Association with Crohn Disease and Identification of a Novel Association with Ulcerative Colitis
Mutations in TNNT3 Cause Multiple Congenital Contractures: A Second Locus for Distal Arthrogryposis Type 2B
Hot and Cold Spots of Recombination in the Human Genome: the Reason We Should Find Them and How This Can Be Achieved
Mutations in the Fumarate Hydratase Gene Cause Hereditary Leiomyomatosis and Renal Cell Cancer in Families in North America
Expressivity of Holt-Oram Syndrome Is Not Predicted by TBX5 Genotype
Haplotype Block Partition with Limited Resources and Applications to Human Chromosome 21 Haplotype Data
Minimum Description Length Block Finder, a Method to Identify Haplotype Blocks and to Compare the Strength of Block Boundaries
Genome Scan Meta-Analysis of Schizophrenia and Bipolar Disorder, Part III: Bipolar Disorder
Genome Scan Meta-Analysis of Schizophrenia and Bipolar Disorder, Part I: Methods and Power Analysis
Genome Scan Meta-Analysis of Schizophrenia and Bipolar Disorder, Part II: Schizophrenia
Selection of Genetic Markers for Association Analyses, Using Linkage Disequilibrium and Haplotypes
Genomewide Linkage Analyses of Bipolar Disorder: A New Sample of 250 Pedigrees from the National Institute of Mental Health Genetics Initiative
Two-Locus Heterogeneity Cannot Be Distinguished from Two-Locus Epistasis on the Basis of Affected-Sib-Pair Data
Haploinsufficiency of TNXB Is Associated with Hypermobility Type of Ehlers-Danlos Syndrome
Mutational Mechanisms of Williams-Beuren Syndrome Deletions
A Haplotype Implicated in Schizophrenia Susceptibility Is Associated with Reduced COMT Expression in Human Brain
Fabry Disease: Novel α-Galactosidase A 3′-Terminal Mutations Result in Multiple Transcripts Due to Aberrant 3′-End Formation
Loss of Kindlin-1, a Human Homolog of the Caenorhabditis elegans Actin–Extracellular-Matrix Linker Protein UNC-112, Causes Kindler Syndrome
Crossover Interference in Humans
Sheldon C. Reed, Ph.D. (November 7, 1910–February 1, 2003): Genetic Counseling, Behavioral Genetics
Erratum
Sequence Variants of the Brain-Derived Neurotrophic Factor (BDNF) Gene Are Strongly Associated with Obsessive-Compulsive Disorder
Mutations in Novel Peroxin Gene PEX26 That Cause Peroxisome-Biogenesis Disorders of Complementation Group 8 Provide a Genotype-Phenotype Correlation
Nuclear and Mitochondrial DNA Analysis of a 2,000-Year-Old Necropolis in the Egyin Gol Valley of Mongolia
BRD2 (RING3) Is a Probable Major Susceptibility Gene for Common Juvenile Myoclonic Epilepsy
A Gene Locus Responsible for Dyschromatosis Symmetrica Hereditaria (DSH) Maps to Chromosome 6q24.2-q25.2
The Possibility of a Selection Process in the Ashkenazi Jewish Population
Selection in the Ashkenazi Jewish Population Unlikely—Reply to Zlotogora and Bach
Finding Haplotype Block Boundaries by Using the Minimum-Description-Length Principle
New Molecular Mechanism for Ullrich Congenital Muscular Dystrophy: A Heterozygous In-Frame Deletion in the COL6A1 Gene Causes a Severe Phenotype
Mutations of von Hippel-Lindau Tumor-Suppressor Gene and Congenital Polycythemia
Germline PTEN Promoter Mutations and Deletions in Cowden/Bannayan-Riley-Ruvalcaba Syndrome Result in Aberrant PTEN Protein and Dysregulation of the Phosphoinositol-3-Kinase/Akt Pathway
Erratum
Discordance between Genetic and Epigenetic Defects in Pseudohypoparathyroidism Type 1b Revealed by Inconsistent Loss of Maternal Imprinting at GNAS1
A 3.9-Centimorgan-Resolution Human Single-Nucleotide Polymorphism Linkage Map and Screening Set
Linkage Disequilibrium and Inference of Ancestral Recombination in 538 Single-Nucleotide Polymorphism Clusters across the Human Genome
Localization of a Susceptibility Gene for Type 2 Diabetes to Chromosome 5q34–q35.2
Localization of a Novel Melanoma Susceptibility Locus to 1p22
A New Familial Amyotrophic Lateral Sclerosis Locus on Chromosome 16q12.1-16q12.2
Two Families with Familial Amyotrophic Lateral Sclerosis Are Linked to a Novel Locus on Chromosome 16q
Identification of Two Novel Loci for Dominantly Inherited Familial Amyotrophic Lateral Sclerosis
The International Psoriasis Genetics Study: Assessing Linkage to 14 Candidate Susceptibility Loci in a Cohort of 942 Affected Sib Pairs
African American Hypertensive Nephropathy Maps to a New Locus on Chromosome 9q31-q32
Notice of Retraction
This Month in the Journal
Genetic Evidence for Interaction of the 5q31 Cytokine Locus and the CARD15 Gene in Crohn Disease
This Month in the Journal
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
Richard H. Ward, Ph.D. (June 7, 1943–February 14, 2003): Wild Ride of the Valkyries
Cleft Lip and Palate: From Origin to Treatment.
Overgrowth Syndromes.
Epimutations in Prader-Willi and Angelman Syndromes: A Molecular Study of 136 Patients with an Imprinting Defect
Erratum
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Erratum
PowerTrim: An Automated Decision Support Algorithm for Preprocessing Family-Based Genetic Data
The Emperor’s New Methods
An Ancestral Ashkenazi Haplotype at the HMPS/CRAC1 Locus on 15q13–q14 Is Associated with Hereditary Mixed Polyposis Syndrome Ancestral Ashkenazi
Erratum
Connective Tissue and Its Heritable Disorders: Molecular, Genetic, and Medical Aspects
Identification of IκBL as the Second Major Histocompatibility Complex–Linked Susceptibility Locus for Rheumatoid Arthritis
Mice Lacking Zfhx1b, the Gene That Codes for Smad-Interacting Protein-1, Reveal a Role for Multiple Neural Crest Cell Defects in the Etiology of Hirschsprung Disease–Mental Retardation Syndrome
Hierarchical Modeling of Linkage Disequilibrum: Genetic Structure and Spatial Relations
Education: A Joint Effort**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 19, 2002.
2002 Cotterman Award Winners
Confirmatory Evidence for Linkage of Relative Hand Skill to 2p12-q11
A Novel NOD2/CARD15 Haplotype Conferring Risk for Crohn Disease in Ashkenazi Jews
Reciprocal and Nonreciprocal Recombination at the Glucocerebrosidase Gene Region: Implications for Complexity in Gaucher Disease
Human Population Genetic Structure and Inference of Group Membership
Mutations in Two Nonhomologous Genes in a Head-to-Head Configuration Cause Ellis-van Creveld Syndrome
Undetected Genotyping Errors Cause Apparent Overtransmission of Common Alleles in the Transmission/Disequilibrium Test
Tissue-Specific Reduction in Splicing Efficiency of IKBKAP Due to the Major Mutation Associated with Familial Dysautonomia
The Pedigree Rate of Sequence Divergence in the Human Mitochondrial Genome: There Is a Difference Between Phylogenetic and Pedigree Rates
Informative Missingness in Genetic Association Studies: Case-Parent Designs
Rapid Direct Sequence Analysis of the Dystrophin Gene
Combined Analysis of Genome Scans of Dutch and Finnish Families Reveals a Susceptibility Locus for High-Density Lipoprotein Cholesterol on Chromosome 16q
Refinement of a 400-kb Critical Region Allows Genotypic Differentiation between Isolated Lissencephaly, Miller-Dieker Syndrome, and Other Phenotypes Secondary to Deletions of 17p13.3
Lodewijk A. Sandkuijl, M.D. (July 31, 1953–December 4, 2002)
Estimation and Testing of Parent-of-Origin Effects for Quantitative Traits
In Vitro Fertilization May Increase the Risk of Beckwith-Wiedemann Syndrome Related to the Abnormal Imprinting of the KCNQ1OT Gene
Down Syndrome: Visions for the 21st Century
KLOTHO Allele Status and the Risk of Early-Onset Occult Coronary Artery Disease
The CHEK2 1100delC Mutation Identifies Families with a Hereditary Breast and Colorectal Cancer Phenotype
A Genomewide Scan for Attention-Deficit/Hyperactivity Disorder in an Extended Sample: Suggestive Linkage on 17p11
Molecular Cytogenetics: Protocols and Applications
FOXL2 and BPES: Mutational Hotspots, Phenotypic Variability, and Revision of the Genotype-Phenotype Correlation
Introductory Speech for Albert de la Chapelle**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 18, 2002.
Introductory Speech for James R. Lupski**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 19, 2002.
Obligate Short-Arm Exchange in De Novo Robertsonian Translocation Formation Influences Placement of Crossovers in Chromosome 21 Nondisjunction
Expansion of the Fragile X CGG Repeat in Females with Premutation or Intermediate Alleles
The Genetic Legacy of the Mongols
Mutations in the Small GTP-ase Late Endosomal Protein RAB7 Cause Charcot-Marie-Tooth Type 2B Neuropathy
A Tobit Variance-Component Method for Linkage Analysis of Censored Trait Data
Extensive Linkage Disequilibrium, a Common 16.7-Kilobase Deletion, and Evidence of Balancing Selection in the Human Protocadherin α Cluster
Genes and Mechanisms in Vertebrate Sex Determination, The Genetics and Biology of Sex Determination.
Mutations in Genes Encoding Fast-Twitch Contractile Proteins Cause Distal Arthrogryposis Syndromes
Mitochondrial Polymorphisms Significantly Reduce the Risk of Parkinson Disease
Genetic Heterogeneity of Cutis Laxa: A Heterozygous Tandem Duplication within the Fibulin-5 (FBLN5) Gene
Variants in CHEK2 Other than 1100delC Do Not Make a Major Contribution to Breast Cancer Susceptibility
Genome Architecture Catalyzes Nonrecurrent Chromosomal Rearrangements
Conditional JAG1 Mutation Shows the Developing Heart Is More Sensitive Than Developing Liver to JAG1 Dosage
Germline p53 Mutations in a Cohort with Childhood Sarcoma: Sex Differences in Cancer Risk
Missense Mutations in the Homeodomain of HOXD13 Are Associated with Brachydactyly Types D and E
Reply to Silva et al.
A Method for the Assessment of Disease Associations with Single-Nucleotide Polymorphism Haplotypes and Environmental Variables in Case-Control Studies
Preferential Paternal Origin of Microdeletions Caused by Prezygotic Chromosome or Chromatid Rearrangements in Sotos Syndrome
A Family-Based Test for Correlation between Gene Expression and Trait Values
Genetic Interaction of BBS1 Mutations with Alleles at Other BBS Loci Can Result in Non-Mendelian Bardet-Biedl Syndrome
A Whole-Genome Scan for Obstructive Sleep Apnea and Obesity
Identification of PEX7 as the Second Gene Involved in Refsum Disease
Studying Parents and Grandparents to Assess Genetic Contributions to Early-Onset Disease
Evaluation of Complex Inheritance Involving the Most Common Bardet-Biedl Syndrome Locus (BBS1)
Simulation-Based P Values: Response to North et al.
The Complexity of Complex Diseases**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 16, 2002.
Failure to Find DUP25 in Patients with Anxiety Disorders, in Control Individuals, or in Previously Reported Positive Control Cell Lines
Fine Mapping of Autistic Disorder to Chromosome 15q11-q13 by Use of Phenotypic Subtypes
Accumulation of Mitochondrial DNA Mutations in Human Immunodeficiency Virus–Infected Patients Treated with Nucleoside-Analogue Reverse-Transcriptase Inhibitors
Identification of a Novel Bardet-Biedl Syndrome Protein, BBS7, That Shares Structural Features with BBS1 and BBS2
Large Differences between LINE-1 Amplification Rates in the Human and Chimpanzee Lineages
Six Novel Missense Mutations in the LDL Receptor-Related Protein 5 (LRP5) Gene in Different Conditions with an Increased Bone Density
Mutations in PRKCSH Cause Isolated Autosomal Dominant Polycystic Liver Disease
ATLAS: A System to Selectively Identify Human-Specific L1 Insertions
Molecular Analysis of Hereditary Nonpolyposis Colorectal Cancer in the United States: High Mutation Detection Rate among Clinically Selected Families and Characterization of an American Founder Genomi
Evidence for a Gene Influencing Serum Bilirubin on Chromosome 2q Telomere: A Genomewide Scan in the Framingham Study
Genome Association Studies of Complex Diseases by Case-Control Designs
Linkage Analysis of Extremely Discordant and Concordant Sibling Pairs Identifies Quantitative-Trait Loci That Influence Variation in the Human Personality Trait Neuroticism
Unraveling Monogenic Channelopathies and Their Implications for Complex Polygenic Disease
Fragile X Premutation Tremor/Ataxia Syndrome: Molecular, Clinical, and Neuroimaging Correlates
Significant Linkage of Parkinson Disease to Chromosome 2q36-37
Analysis of GNAS1 and Overlapping Transcripts Identifies the Parental Origin of Mutations in Patients with Sporadic Albright Hereditary Osteodystrophy and Reveals a Model System in Which to Observe th
Native American Y Chromosomes in Polynesia: The Genetic Impact of the Polynesian Slave Trade
Mutations in MTMR13, a New Pseudophosphatase Homologue of MTMR2 and Sbf1, in Two Families with an Autosomal Recessive Demyelinating Form of Charcot-Marie-Tooth Disease Associated with Early-Onset Glau
Glycyl tRNA Synthetase Mutations in Charcot-Marie-Tooth Disease Type 2D and Distal Spinal Muscular Atrophy Type V
Correction: Mitochondrial DNA Variation in Amerindians
Mutations of MYO6 Are Associated with Recessive Deafness, DFNB37
Anxiety with Panic Disorder Linked to Chromosome 9q in Iceland
A Whole-Genome Scan in 164 Dutch Sib Pairs with Attention-Deficit/Hyperactivity Disorder: Suggestive Evidence for Linkage on Chromosomes 7p and 15q
Cost-Effective Designs for Linkage Disequilibrium Mapping of Complex Traits
Physical Map of 1p36, Placement of Breakpoints in Monosomy 1p36, and Clinical Characterization of the Syndrome
Sensitive and Efficient Detection of RB1 Gene Mutations Enhances Care for Families with Retinoblastoma
Reduced Y-Chromosome, but Not Mitochondrial DNA, Diversity in Human Populations from West New Guinea
Cold-Induced Sweating Syndrome Is Caused by Mutations in the CRLF1 Gene
On Estimating P Values by Monte Carlo Methods
Introductory Speech for Kurt Hirschhorn**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 19, 2002.
HLA-DR2 Dose Effect on Susceptibility to Multiple Sclerosis and Influence on Disease Course
Mapping the Wolf-Hirschhorn Syndrome Phenotype Outside the Currently Accepted WHS Critical Region and Defining a New Critical Region, WHSCR-2
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Use of Multivariate Linkage Analysis for Dissection of a Complex Cognitive Trait
Erratum
Confirmation of Linkage of Prostate Cancer Aggressiveness with Chromosome 19q
Mitochondrial DNA Haplogroups Do Not Play a Role in the Variable Phenotypic Presentation of the A3243G Mutation
Deletion of the Telomerase Reverse Transcriptase Gene and Haploinsufficiency of Telomere Maintenance in Cri du Chat Syndrome
Polymorphisms at the G72/G30 Gene Locus, on 13q33, Are Associated with Bipolar Disorder in Two Independent Pedigree Series*
Past Exposure to Densely Ionizing Radiation Leaves a Unique Permanent Signature in the Genome
A Multicolor FISH Assay Does Not Detect DUP25 in Control Individuals or in Reported Positive Control Cells
The Epidemiology of Leber Hereditary Optic Neuropathy in the North East of England
Estimation of Haplotype Frequencies, Linkage-Disequilibrium Measures, and Combination of Haplotype Copies in Each Pool by Use of Pooled DNA Data
Mental Retardation and Abnormal Skeletal Development (Dyggve-Melchior-Clausen Dysplasia) Due to Mutations in a Novel, Evolutionarily Conserved Gene
Inherited Human Diseases: Victories, Challenges, Disappointments**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 18, 2002.
Missense Mutations in the Regulatory Domain of PKCγ: A New Mechanism for Dominant Nonepisodic Cerebellar Ataxia
This Month in the Journal
Genetic Linkage Analysis of a Dichotomous Trait Incorporating a Tightly Linked Quantitative Trait in Affected Sib Pairs
2-Methyl-3-Hydroxybutyryl-CoA Dehydrogenase Deficiency Is Caused by Mutations in the HADH2 Gene
To Trust or Not to Trust an Idiosyncratic Mitochondrial Data Set
This Month in the Journal
The Genetic Heritage of the Earliest Settlers Persists Both in Indian Tribal and Caste Populations
Connexin 43 (GJA1) Mutations Cause the Pleiotropic Phenotype of Oculodentodigital Dysplasia
CD36 Polymorphism Is Associated with Protection from Cerebral Malaria
Mutations in CHEK2 Associated with Prostate Cancer Risk
A Note on the Calculation of Empirical P Values from Monte Carlo Procedures
Genomic Disorders: Recombination-Based Disease Resulting from Genome Architecture**Previously presented at the annual meeting of The American Society of Human Genetics, in Baltimore, on October 19, 20
Genomewide Linkage Analysis Identifies Polymorphism in the Human Interferon-γ Receptor Affecting Helicobacter pylori Infection
SCA8 Repeat Expansion: Large CTA/CTG Repeat Alleles Are More Common in Ataxic Patients, Including Those with SCA6
Improving the Prediction of Complex Diseases by Testing for Multiple Disease-Susceptibility Genes
The Constitutional t(17;22): Another Translocation Mediated by Palindromic AT-Rich Repeats
Splitting p63
On the Identification of Disease Mutations by the Analysis of Haplotype Similarity and Goodness of Fit
Autosomal Recessive HEM/Greenberg Skeletal Dysplasia Is Caused by 3β-Hydroxysterol Δ14-Reductase Deficiency Due to Mutations in the Lamin B Receptor Gene
Missense Mutations in CRELD1 Are Associated with Cardiac Atrioventricular Septal Defects
Extensive Female-Mediated Gene Flow from Sub-Saharan Africa into Near Eastern Arab Populations
Features of Evolution and Expansion of Modern Humans, Inferred from Genomewide Microsatellite Markers
Skewed X-Chromosome Inactivation Is Associated with Trisomy in Women Ascertained on the Basis of Recurrent Spontaneous Abortion or Chromosomally Abnormal Pregnancies
Resolving ATM Haplotypes in Whites
Geographic Distribution of Disease Mutations in the Ashkenazi Jewish Population Supports Genetic Drift over Selection
Homozygous Mutations in IHH Cause Acrocapitofemoral Dysplasia, an Autosomal Recessive Disorder with Cone-Shaped Epiphyses in Hands and Hips
Elevated Risk for MPNST in NF1 Microdeletion Patients
Average Risks of Breast and Ovarian Cancer Associated with BRCA1 or BRCA2 Mutations Detected in Case Series Unselected for Family History: A Combined Analysis of 22 Studies
Distribution Patterns of Postmortem Damage in Human Mitochondrial DNA
Support for Association of Schizophrenia with Genetic Variation in the 6p22.3 Gene, Dysbindin, in Sib-Pair Families with Linkage and in an Additional Sample of Triad Families
Pharmacogenomics.
Early-Onset Brain Tumor and Lymphoma in MSH2-Deficient Children
A Locus for Migraine without Aura Maps on Chromosome 14q21.2-q22.3
Recombinant Enzyme Therapy for Fabry Disease: Absence of Editing of Human α-Galactosidase A mRNA
Characterization of Genetic Miscoding Lesions Caused by Postmortem Damage
A 122.5-Kilobase Deletion of the P Gene Underlies the High Prevalence of Oculocutaneous Albinism Type 2 in the Navajo Population
A Founding Locus within the RET Proto-Oncogene May Account for a Large Proportion of Apparently Sporadic Hirschsprung Disease and a Subset of Cases of Sporadic Medullary Thyroid Carcinoma
The Genetic Origins of the Andaman Islanders
A Mutation in the Fibroblast Growth Factor 14 Gene Is Associated with Autosomal Dominant Cerebral Ataxia
Mutations in COX15 Produce a Defect in the Mitochondrial Heme Biosynthetic Pathway, Causing Early-Onset Fatal Hypertrophic Cardiomyopathy
A Susceptibility Gene for Psoriatic Arthritis Maps to Chromosome 16q: Evidence for Imprinting
Comparison of Genome Screens for Two Independent Cohorts Provides Replication of Suggestive Linkage of Bone Mineral Density to 3p21 and 1p36
Another Case of Imprinting Defect in a Girl with Angelman Syndrome Who Was Conceived by Intracytoplasmic Sperm Injection
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The Molecule Hunt.
Hereditary p16-Leiden Mutation in a Patient with Multiple Head and Neck Tumors
Identification of CRYM as a Candidate Responsible for Nonsyndromic Deafness, through cDNA Microarray Analysis of Human Cochlear and Vestibular Tissues**Nucleotide sequence data reported herein are ava
NSD1 Mutations Are the Major Cause of Sotos Syndrome and Occur in Some Cases of Weaver Syndrome but Are Rare in Other Overgrowth Phenotypes
Association of In Vitro Fertilization with Beckwith-Wiedemann Syndrome and Epigenetic Alterations of LIT1 and H19
This Month in the Journal
Two Percent of Men with Early-Onset Prostate Cancer Harbor Germline Mutations in the BRCA2 Gene
Susceptibility Loci for Preeclampsia on Chromosomes 2p25 and 9p13 in Finnish Families
Association between the Severity of Angiographic Coronary Artery Disease and Paraoxonase Gene Polymorphisms in the National Heart, Lung, and Blood Institute–Sponsored Women’s Ischemia Syndrome Evaluat
Association of Neuregulin 1 with Schizophrenia Confirmed in a Scottish Population
Interacting Genetic Loci on Chromosomes 20 and 10 Influence Extreme Human Obesity
Erratum
Significant Linkage on Chromosome 10p in Families with Bulimia Nervosa
Common Sequence Variants of the Macrophage Scavenger Receptor 1 Gene Are Associated with Prostate Cancer Risk