The American Journal of Human Genetics - 1999

528 articles | Last updated: 2025-12-03 14:12:57
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T A T A T A T A
Erratum
Subject Index for Volume 64
Author Index for Volume 60
Contents of Volume 64
Relationship Estimation by Markov-Process Models in a Sib-Pair Linkage Study
Errata
Editorial Reviewers for 1999
Erratum
Erratum
Errata
Errata
Errata
Errata
Errata
Subject Index for Volume 65
Author Index for Volume 64
Subject Index for Volume 64
Author Index for Volume 65
Gene Localization for Aculeiform Cataract, on Chromosome 2q33‐35
Errata
Errata
Contents of Volume 65
Contents of Volume 64
On the Assessment of Statistical Significance in Disease-Gene Discovery
This Month in the Journal
The 2588G→C Mutation in the ABCR Gene Is a Mild Frequent Founder Mutation in the Western European Population and Allows the Classification of ABCR Mutations in Patients with Stargardt Disease Western European Population
Identification of Novel pro-α2(IX) Collagen Gene Mutations in Two Families with Distinctive Oligo-Epiphyseal Forms of Multiple Epiphyseal Dysplasia
The γ-Crystallins and Human Cataracts: A Puzzle Made Clearer
Combined Linkage and Association Sib-Pair Analysis for Quantitative Traits
Williams Syndrome: Use of Chromosomal Microdeletions as a Tool to Dissect Cognitive and Physical Phenotypes
Myotonic Dystrophy: The Role of RNA CUG Triplet Repeats
mtDNA Analysis of Nile River Valley Populations: A Genetic Corridor or a Barrier to Migration?
Unlinking Tumor Necrosis Factor Biology from the Major Histocompatibility Complex: Lessons from Human Genetics and Animal Models
The Bare Lymphocyte Syndrome: Molecular Clues to the Transcriptional Regulation of Major Histocompatibility Complex Class II Genes
Localization of a Gene for Benign Adult Familial Myoclonic Epilepsy to Chromosome 8q23.3-q24.1
Functional and Structural Brain Abnormalities Associated with a Genetic Disorder of Speech and Language
The Role of Community Review in Evaluating the Risks of Human Genetic Variation Research
Monoamine Oxidase in Neuropsychiatry and Behavior
A Novel Skeletal Dysplasia with Developmental Delay and Acanthosis Nigricans Is Caused by a Lys650Met Mutation in the Fibroblast Growth Factor Receptor 3 Gene
Severe Hepatic Fibrosis in Schistosoma mansoni Infection Is Controlled by a Major Locus That Is Closely Linked to the Interferon-γ Receptor Gene
Cyclic Ichthyosis with Epidermolytic Hyperkeratosis: A Phenotype Conferred by Mutations in the 2B Domain of Keratin K1
Low-Copy Repeats Mediate the Common 3-Mb Deletion in Patients with Velo-cardio-facial Syndrome
Genetic Linkage of Hyper-IgE Syndrome to Chromosome 4
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
An HFE Intronic Variant Promotes Misdiagnosis of Hereditary Hemochromatosis
A Founder Effect in the Newfoundland Population Reduces the Bardet-Biedl Syndrome I (BBS1) Interval to 1 cM
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please send announcement text by E-mail to [email protected] or by fax to
Ancestral Origins and Worldwide Distribution of the PRNP 200K Mutation Causing Familial Creutzfeldt-Jakob Disease
Juvenile Hemochromatosis Locus Maps to Chromosome 1q
Connexin46 Mutations in Autosomal Dominant Congenital Cataract
This Month in the Journal
Diaphragmatic Spinal Muscular Atrophy with Respiratory Distress Is Heterogeneous, and One Form Is Linked to Chromosome 11q13-q21
Y-Chromosome Evidence for a Northward Migration of Modern Humans into Eastern Asia during the Last Ice Age
Mice and the Role of Unequal Recombination in Gene-Family Evolution
Evidence for Effective Suppression of Recombination in the Chromosome 17q21 Segment Spanning RNU2–BRCA1
Refinement of the Chromosome 5p Locus for Familial Calcium Pyrophosphate Dihydrate Deposition Disease
An mtDNA Mutation in the Initiation Codon of the Cytochrome C Oxidase Subunit II Gene Results in Lower Levels of the Protein and a Mitochondrial Encephalomyopathy
Identifying Families with Likely Genetic Protective Factors against Alzheimer Disease
Errata
Editorial Reviewers for 1999
Mosaicism and Sporadic Familial Adenomatous Polyposis
Eugenics and the Misuse of Genetic Information to Restrict Reproductive Freedom
Molecular and Clinical Study of 18 Families with ADCA Type II: Evidence for Genetic Heterogeneity and De Novo Mutation
Splicing Defects in the Ataxia-Telangiectasia Gene, ATM: Underlying Mutations and Consequences
The Size Distribution of Homozygous Segments in the Human Genome
Exclusion of Chromosome 7 for Kartagener Syndrome but Suggestion of Linkage in Families with Other Forms of Primary Ciliary Dyskinesia
Function and Dysfunction of the Presenilins
Transcription Factors and Human Disease.
Specificity in Transforming Growth Factor–β Signaling Pathways
This Month in the Journal
Poly(ADP-Ribose) Polymerase in the Cellular Response to DNA Damage, Apoptosis, and Disease
X-Linked Late-Onset Sensorineural Deafness Caused by a Deletion Involving OA1 and a Novel Gene Containing WD-40 Repeats
Mutational Analysis of the Defective Protease in Classic Late-Infantile Neuronal Ceroid Lipofuscinosis, a Neurodegenerative Lysosomal Storage Disorder
Cysteine Substitutions in Epidermal Growth Factor–Like Domains of Fibrillin-1: Distinct Effects on Biochemical and Clinical Phenotypes
Reply to Niermeijer
Organelle Diseases
A Loss-of-Function Mutation in the Endothelin-Converting Enzyme 1 (ECE-1) Associated with Hirschsprung Disease, Cardiac Defects, and Autonomic Dysfunction
A Genomewide Analysis Provides Evidence for Novel Linkages in Inflammatory Bowel Disease in a Large European Cohort European cohort
An mtDNA Analysis in Ancient Basque Populations: Implications for Haplogroup V as a Marker for a Major Paleolithic Expansion from Southwestern Europe Southwestern Europe
On a Randomization Procedure in Linkage Analysis
Mapping of a Familial Moyamoya Disease Gene to Chromosome 3p24.2-p26
Down-Weighting of Multiple Affected Sib Pairs Leads to Biased Likelihood-Ratio Tests, under the Assumption of No Linkage
Human Pedigree-Based Quantitative-Trait–Locus Mapping: Localization of Two Genes Influencing HDL-Cholesterol Metabolism
Autoimmune Lymphoproliferative Syndrome with Defective Fas: Genotype Influences Penetrance
Allowing for Missing Parents in Genetic Studies of Case-Parent Triads
Errata
Genes, Demography, and Life Span: The Contribution of Demographic Data in Genetic Studies on Aging and Longevity
A Generalization of the Transmission/Disequilibrium Test for Uncertain-Haplotype Transmission
A Genome Scan for Familial Combined Hyperlipidemia Reveals Evidence of Linkage with a Locus on Chromosome 11
Naturally Occurring Mutations of the Luteinizing-Hormone Receptor: Lessons Learned about Reproductive Physiology and G Protein–Coupled Receptors
The Spectrum of Mutations in TBX3: Genotype/Phenotype Relationship in Ulnar-Mammary Syndrome
Peroxisomal Bifunctional Protein Deficiency Revisited: Resolution of Its True Enzymatic and Molecular Basis
Characterization of a Germline Mosaicism in Families with Lowe Syndrome, and Identification of Seven Novel Mutations in the OCRL1 Gene
Congenital Insensitivity to Pain with Anhidrosis: Novel Mutations in the TRKA (NTRK1) Gene Encoding A High-Affinity Receptor for Nerve Growth Factor
Genetics of Angelman Syndrome
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
COL9A3: A Third Locus for Multiple Epiphyseal Dysplasia
Delineation of the Critical Deletion Region for Congenital Heart Defects, on Chromosome 8p23.1
Joint Multipoint Linkage Analysis of Multivariate Qualitative and Quantitative Traits. II. Alcoholism and Event-Related Potentials
A Gene for X-Linked Idiopathic Congenital Nystagmus (NYS1) Maps to Chromosome Xp11.4-p11.3
Biology of Aging: Observations and Principles, 2d ed.
Primary Autosomal Recessive Microcephaly: Homozygosity Mapping of MCPH4 to Chromosome 15
Genetic Linkage of Autosomal-Dominant Alport Syndrome with Leukocyte Inclusions and Macrothrombocytopenia (Fechtner Syndrome) to Chromosome 22q11-13
Identification of a Genetic Defect in the Hairless Gene in Atrichia with Papular Lesions: Evidence for Phenotypic Heterogeneity among Inherited Atrichias
Campomelic Dysplasia Translocation Breakpoints Are Scattered over 1 Mb Proximal to SOX9: Evidence for an Extended Control Region
Loss-of-Function Mutations in a Human Gene Related to Chlamydomonas reinhardtii Dynein IC78 Result in Primary Ciliary Dyskinesia
A Simulation Study of the Effects of Assignment of Prior Identity-by-Descent Probabilities to Unselected Sib Pairs, in Covariance-Structure Modeling of a Quantitative-Trait Locus
Molecular Genetic Analysis of Remains of a 2,000-Year-Old Human Population in China—and Its Relevance for the Origin of the Modern Japanese Population
A Gene for Autosomal Recessive Symmetrical Spastic Cerebral Palsy Maps to Chromosome 2q24-25
Brachydactyly Type B: Linkage to Chromosome 9q22 and Evidence for Genetic Heterogeneity
A Novel Syndrome of Episodic Muscle Weakness Maps to Xp22.3
Direct Power Comparisons between Simple LOD Scores and NPL Scores for Linkage Analysis in Complex Diseases
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
The Emerging Tree of West Eurasian mtDNAs: A Synthesis of Control-Region Sequences and RFLPs West Eurasian
Evidence for Linkage of Adolescent-Onset Idiopathic Generalized Epilepsies to Chromosome 8—and Genetic Heterogeneity
Mapping of a New SGBS Locus to Chromosome Xp22 in a Family with a Severe Form of Simpson-Golabi-Behmel Syndrome
A Second Locus for Familial Generalized Epilepsy with Febrile Seizures Plus Maps to Chromosome 2q21-q33
Evidence for Interaction between Psoriasis-Susceptibility Loci on Chromosomes 6p21 and 1q21
Are There Low-Penetrance TP53 Alleles? Evidence from Childhood Adrenocortical Tumors
Mutations in the RP2 Gene Cause Disease in 10% of Families with Familial X-Linked Retinitis Pigmentosa Assessed in This Study
A Chromosomal Duplication Map of Malformations: Regions of Suspected Haplo- and Triplolethality—and Tolerance of Segmental Aneuploidy—in Humans
Diaphyseal Medullary Stenosis with Malignant Fibrous Histiocytoma: a Hereditary Bone Dysplasia/Cancer Syndrome Maps to 9p21-22
The X Chromosome and Recurrent Spontaneous Abortion: The Significance of Transmanifesting Carriers
A Locus for Isolated Cleft Palate, Located on Human Chromosome 2q32
Temperature-Sensitive RB Mutations Linked to Incomplete Penetrance of Familial Retinoblastoma in 12 Families
Identification and Characterization of a Mutation, in the Human UDP-Galactose-4-Epimerase Gene, Associated with Generalized Epimerase-Deficiency Galactosemia
A Gene for Inherited Cutaneous Venous Anomalies (“Glomangiomas”) Localizes to Chromosome 1p21-22
Human Ehlers-Danlos Syndrome Type VII C and Bovine Dermatosparaxis Are Caused by Mutations in the Procollagen I N-Proteinase Gene
Mutations in NPC1 Highlight a Conserved NPC1-Specific Cysteine-Rich Domain
p53 Variants Predisposing to Cancer Are Present in Healthy Centenarians
Maternally Inherited Cardiomyopathy: An Atypical Presentation of the mtDNA 12S rRNA Gene A1555G Mutation
Localization of the Gene for Sclerosteosis to the van Buchem Disease–Gene Region on Chromosome 17q12–q21
Peopling of Sahul: mtDNA Variation in Aboriginal Australian and Papua New Guinean Populations
Location Score and Haplotype Analyses of the Locus for Autosomal Recessive Spastic Ataxia of Charlevoix-Saguenay, in Chromosome Region 13q11
A Fifth Locus for Bardet-Biedl Syndrome Maps to Chromosome 2q31
Transmission of a Fully Functional Human Neocentromere through Three Generations
Repair of mtDNA in Vertebrates
Homozygosity Mapping of the Achromatopsia Locus in the Pingelapese
Methods for Detection of Parent-of-Origin Effects in Genetic Studies of Case-Parents Triads
Monodactylous Limbs and Abnormal Genitalia Are Associated with Hemizygosity for the Human 2q31 Region That Includes the HOXD Cluster
Autosomal Dominant (Beukes) Premature Degenerative Osteoarthropathy of the Hip Joint Maps to an 11-cM Region on Chromosome 4q35
Extremely Skewed X-Chromosome Inactivation Is Increased in Women with Recurrent Spontaneous Abortion
Professor Ching Chun Li, Courageous Scholar and Educator
Erratum
Both Recessive and Dominant Forms of Anhidrotic/Hypohidrotic Ectodermal Dysplasia Map to Chromosome 2q11-q13
Complete Inactivation of the TSC2 Gene Leads to Formation of Hamartomas
Mutation Analysis of Core Binding Factor A1 in Patients with Cleidocranial Dysplasia
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Erratum
Immunoglobulin Class Switch Recombination: Will Genetics Provide New Clues to Mechanism?
A Gene for Autosomal Recessive Spondylocostal Dysostosis Maps to 19q13.1-q13.3
Penetrances of BRCA1 1675delA and 1135insA with Respect to Breast Cancer and Ovarian Cancer
A Founder Mutation in the GK1 Gene Is Responsible for Galactokinase Deficiency in Roma (Gypsies) Roma (Gypsies)
Mutation Rates in Humans. I. Overall and Sex-Specific Rates Obtained from a Population Study of Hemophilia B
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
Biological Implications of the DNA Structures Associated with Disease-Causing Triplet Repeats
Protein-Truncation Mutations in the RP2 Gene in a North American Cohort of Families with X-Linked Retinitis Pigmentosa
Gaucher Disease: The N370S Mutation in Ashkenazi Jewish and Spanish Patients has a Common Origin and Arose Several Thousand Years Ago Ashkenazi Jewish; Spanish
Response to the Letters from Hopper and Jenkins and Foulkes et al.
This Month in the Journal
Evidence for the Genetic Heterogeneity of Nephropathic Phenotypes Associated with Denys-Drash and Frasier Syndromes
A Unique Point Mutation in the PMP22 Gene Is Associated with Charcot-Marie-Tooth Disease and Deafness
Missense Mutation in the Alternative Splice Region of the PAX6 Gene in Eye Anomalies
EXT-Mutation Analysis and Loss of Heterozygosity in Sporadic and Hereditary Osteochondromas and Secondary Chondrosarcomas
Hyperparathyroidism–Jaw Tumor Syndrome: The HRPT2 Locus Is within a 0.7-cM Region on Chromosome 1q
Human Molybdopterin Synthase Gene: Genomic Structure and Mutations in Molybdenum Cofactor Deficiency Type B
The Fanconi Anemia Group E Gene, FANCE, Maps to Chromosome 6p
Mitochondrial Genetic Analyses Suggest Selection against Maternal Lineages in Bipolar Affective Disorder
STAT5 Signaling in Sexually Dimorphic Gene Expression and Growth Patterns
Precise Genetic Mapping and Haplotype Analysis of the Familial Dysautonomia Gene on Human Chromosome 9q31
New Editor of The American Journal of Human Genetics
The Contribution of Germline BRCA1 and BRCA2 Mutations to Familial Ovarian Cancer: No Evidence for Other Ovarian Cancer–Susceptibility Genes
DNA Rearrangements on Both Homologues of Chromosome 17 in a Mildly Delayed Individual with a Family History of Autosomal Dominant Carpal Tunnel Syndrome
Der(22) Syndrome and Velo-Cardio-Facial Syndrome/DiGeorge Syndrome Share a 1.5-Mb Region of Overlap on Chromosome 22q11
Identification of Mutations in the Repeated Part of the Autosomal Dominant Polycystic Kidney Disease Type 1 Gene, PKD1, by Long-Range PCR
A Gene for Lymphedema-Distichiasis Maps to 16q24.3
The A1555G Mutation in the 12S rRNA Gene of Human mtDNA: Recurrent Origins and Founder Events in Families Affected by Sensorineural Deafness
Imprinting-Mutation Mechanisms in Prader-Willi Syndrome
Different Functional Outcome of RetGC1 and RPE65 Gene Mutations in Leber Congenital Amaurosis
A New Locus for Autosomal Dominant “Pure” Hereditary Spastic Paraplegia Mapping to Chromosome 12q13, and Evidence for Further Genetic Heterogeneity
Splicing Mutations of 54-bp Exons in the COL11A1 Gene Cause Marshall Syndrome, but Other Mutations Cause Overlapping Marshall/Stickler Phenotypes
Association of Hereditary Nonpolyposis Colorectal Cancer–Related Tumors Displaying Low Microsatellite Instability with MSH6 Germline Mutations
p53 Codon 72 Polymorphism and Longevity: Additional Data on Centenarians from Continental Italy and Sardinia
De Novo Alu-Element Insertions in FGFR2 Identify a Distinct Pathological Basis for Apert Syndrome
Highly Skewed X-Chromosome Inactivation Is Associated with Idiopathic Recurrent Spontaneous Abortion
Genetic Analysis of Families with Parkinson Disease that Carry the Ala53Thr Mutation in the Gene Encoding α-Synuclein
A Genomic Screen of Autism: Evidence for a Multilocus Etiology
A Complete Genome Screen in Sib Pairs Affected by Gilles de la Tourette Syndrome
Osteoarthritis-Susceptibility Locus on Chromosome 11q, Detected by Linkage
mtDNA History of the Cayapa Amerinds of Ecuador: Detection of Additional Founding Lineages for the Native American Populations
Haploinsufficiency of the HOXA Gene Cluster, in a Patient with Hand-Foot-Genital Syndrome, Velopharyngeal Insufficiency, and Persistent Patent Ductus Botalli
Learning from the Slime Mold: Dictyostelium and Human Disease
The Importance of a Family History of Breast Cancer in Predicting the Presence of a BRCA Mutation
Linkage of Familial Hemophagocytic Lymphohistiocytosis to 10q21-22 and Evidence for Heterogeneity
Relaxed Replication of mtDNA: A Model with Implications for the Expression of Disease
Mutations of the TIGR/MYOC Gene in Primary Open-Angle Glaucoma in Korea
Homozygosity Mapping in Families with Joubert Syndrome Identifies a Locus on Chromosome 9q34.3 and Evidence for Genetic Heterogeneity
Molecular Mechanism of Angelman Syndrome in Two Large Families Involves an Imprinting Mutation
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please send announcement text by E-mail to [email protected] or by fax to
New Editor of The American Journal of Human Genetics
Erratum
This Month in the Journal
Further Evidence for the Increased Power of LOD Scores Compared with Nonparametric Methods
Nitric Oxide in Endothelial Dysfunction and Vascular Remodeling: Clinical Correlates and Experimental Links
Clear Correlation of Genotype with Disease Phenotype in Very–Long-Chain Acyl-CoA Dehydrogenase Deficiency
Comprehensive Mutation Analysis of TSC1 and TSC2—and Phenotypic Correlations in 150 Families with Tuberous Sclerosis
A Missense Mutation of Cytochrome Oxidase Subunit II Causes Defective Assembly and Myopathy
Stress-Response Proteins in Cardiovascular Disease
Molecular Characterization of CTNS Deletions in Nephropathic Cystinosis: Development of a PCR-Based Detection Assay
LINE-1 Elements at the Sites of Molecular Rearrangements in Alport Syndrome–Diffuse Leiomyomatosis
Rhmod Syndrome: A Family Study of the Translation-Initiator Mutation in the Rh50 Glycoprotein Gene
Multicentric Origin of Hemochromatosis Gene (HFE) Mutations
The Mammalian Mre11-Rad50-Nbs1 Protein Complex: Integration of Functions in the Cellular DNA–Damage Response
Noninvasive Test for Fragile X Syndrome, Using Hair Root Analysis
The Gene for Leukoencephalopathy with Vanishing White Matter Is Located on Chromosome 3q27
Distribution of Two HIV-1–Resistant Polymorphisms (SDF1-3′A and CCR2-64I) in East Asian and World Populations and Its Implication in AIDS Epidemiology East Asian; World Populations
Localization of a Gene for Duane Retraction Syndrome to Chromosome 2q31
Identification of a New Autosomal Dominant Limb-Girdle Muscular Dystrophy Locus on Chromosome 7
No Evidence of Linkage for Chromosome 1q42.2-43 in Prostate Cancer
Assignment of the Locus for Hydrolethalus Syndrome to a Highly Restricted Region on 11q23-25
Quantitative Analysis of Survival Motor Neuron Copies: Identification of Subtle SMN1 Mutations in Patients with Spinal Muscular Atrophy, Genotype-Phenotype Correlation, and Implications for Genetic Co
Making Genomic Medicine a Reality
Point and Interval Estimates of Marker Location in Radiation Hybrid Mapping
Investigation of a Family with Autosomal Dominant Dilated Cardiomyopathy Defines a Novel Locus on Chromosome 2q14-q22
Chinese Geneticists Are Far from Eugenics Movement
Remarks on Receiving the ASHG Award: Science and Science Education
Transmitting Genetic Risk Information in Families: Attitudes about Disclosing the Identity of Relatives
American Board of Medical Genetics and American Board of Genetic Counseling Diplomates
Evidence That Mutations in the X-linked DDP Gene Cause Incompletely Penetrant and Variable Skewed X Inactivation
Assessing the Feasibility of Linkage Disequilibrium Methods for Mapping Complex Traits: An Initial Screen for Bipolar Disorder Loci on Chromosome 18
Digenic Junctional Epidermolysis Bullosa: Mutations in COL17A1 and LAMB3 Genes
Localization of a Gene for Bitter-Taste Perception to Human Chromosome 5p15
Periventricular Heterotopia and the Genetics of Neuronal Migration in the Cerebral Cortex
Genetic Studies of Alcoholism and Substance Dependence
The Choice to Have a Disabled Child
Mapping of a New Autosomal Dominant Spinocerebellar Ataxia to Chromosome 22 No article text provided; only title given.
The Sex Ratio in Familial Persistent Stuttering
Mutations of UFD1L Are Not Responsible for the Majority of Cases of DiGeorge Syndrome/Velocardiofacial Syndrome without Deletions within Chromosome 22q11
New Editor of The American Journal of Human Genetics
Erratum
New Editor of The American Journal of Human Genetics
High Rate of Mosaicism in Tuberous Sclerosis Complex
Genomewide Transmission/Disequilibrium Testing: A Correction
Accelerated Telomere Shortening in the Human Inactive X Chromosome
Reply to Leder and Hodge
The “Thermolabile” Variant of Methylenetetrahydrofolate Reductase and Neural Tube Defects: An Evaluation of Genetic Risk and the Relative Importance of the Genotypes of the Embryo and the Mother
The Gene for Hypotrichosis of Marie Unna Maps between D8S258 and D8S298: Exclusion of the hr Gene by cDNA and Genomic Sequencing
Multiplex-FISH for Pre- and Postnatal Diagnostic Applications
Chromosome Breakage in the Prader-Willi and Angelman Syndromes Involves Recombination between Large, Transcribed Repeats at Proximal and Distal Breakpoints
Redefinition of Exon 7 in the COL1A1 Gene of Type I Collagen by an Intron 8 Splice-Donor–Site Mutation in a Form of Osteogenesis Imperfecta: Influence of Intron Splice Order on Outcome of Splice-Site
X-Linked Dyskeratosis Congenita Is Predominantly Caused by Missense Mutations in the DKC1 Gene
Chromosome Breakage Hotspots and Delineation of the Critical Region for the 9p-Deletion Syndrome
Sperm Chromosome Analysis in a Man Heterozygous for a Paracentric Inversion of Chromosome 14 (q24.1q32.1)
IQ and Human Intelligence.
Two Novel Single–Base-Pair Substitutions Adjacent to the CAG Repeat in the Huntington Disease Gene (IT15): Implications for Diagnostic Testing
A Third Major Locus for Autosomal Dominant Hypercholesterolemia Maps to 1p34.1-p32
MEFV-Gene Analysis in Armenian Patients with Familial Mediterranean Fever: Diagnostic Value and Unfavorable Renal Prognosis of the M694V Homozygous Genotype—Genetic and Therapeutic Implications Armenian
Outrageous Fortune: The Risk of Suicide in Genetic Testing for Huntington Disease
Heritability of Cellular Radiosensitivity: A Marker of Low-Penetrance Predisposition Genes in Breast Cancer?
Psoriasis Linkage in the HLA Region
Microglia and the Immune Pathology of Alzheimer Disease
Recurrence of the T666M Calcium Channel CACNA1A Gene Mutation in Familial Hemiplegic Migraine with Progressive Cerebellar Ataxia
Linkage Disequilibrium at the ADH2 and ADH3 Loci and Risk of Alcoholism
Kallmann Syndrome and the Link between Olfactory and Reproductive Development
Double Heterozygosity for a RET Substitution Interfering with Splicing and an EDNRB Missense Mutation in Hirschsprung Disease
Sequence Diversity in 36 Candidate Genes for Cardiovascular Disorders
Genome Analysis: A Laboratory Manual (Vols. 1–4)
Refinement of the Locus for Autosomal Recessive Retinitis Pigmentosa (RP25) Linked to Chromosome 6q in a Family of Pakistani Origin Pakistani origin
Limb Mammary Syndrome: A New Genetic Disorder with Mammary Hypoplasia, Ectrodactyly, and Other Hand/Foot Anomalies Maps to Human Chromosome 3q27
A Major Quantitative-Trait Locus for Mole Density Is Linked to the Familial Melanoma Gene CDKN2A: A Maximum-Likelihood Combined Linkage and Association Analysis in Twins and Their Sibs
Errata
The Genetic Basis for Periodic Fever
Clinical and Molecular Genetic Analysis of 19 Wolfram Syndrome Kindreds Demonstrating a Wide Spectrum of Mutations in WFS1
Concerted Evolution: Molecular Mechanism and Biological Implications
Age Estimates of Two Common Mutations Causing Factor XI Deficiency: Recent Genetic Drift Is Not Necessary for Elevated Disease Incidence among Ashkenazi Jews Ashkenazi Jews
About the “Pathological” Role of the mtDNA T3308C Mutation…
Interleukin-2 Signaling and Inherited Immunodeficiency
Reply to Michie and Marteau
An Extreme-Sib-Pair Genome Scan for Genes Regulating Blood Pressure
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Departmen
Linkage Analysis in a Large Brazilian Family with van der Woude Syndrome Suggests the Existence of a Susceptibility Locus for Cleft Palate at 17p11.2-11.1
A Means to an End: The Biological Basis of Aging and Death.
Assignment of the Muscle-Eye-Brain Disease Gene to 1p32-p34 by Linkage Analysis and Homozygosity Mapping
Molecular Analysis of SALL1 Mutations in Townes-Brocks Syndrome
High Prevalence of Mutations in the Microtubule-Associated Protein Tau in a Population Study of Frontotemporal Dementia in the Netherlands
Dominant Hereditary Inclusion-Body Myopathy Gene (IBM3) Maps to Chromosome Region 17p13.1
A New Locus for Autosomal Dominant Stargardt-Like Disease Maps to Chromosome 4
Human Mitochondrial Complex I in Health and Disease
A Stop-Codon Mutation in the Human mtDNA Cytochrome c Oxidase I Gene Disrupts the Functional Structure of Complex IV
Mapping of the Mucolipidosis Type IV Gene to Chromosome 19p and Definition of Founder Haplotypes
Prader-Willi Syndrome Is Caused by Disruption of the SNRPN Gene
An Alu-Mediated 6-kb Duplication in the BRCA1 Gene: A New Founder Mutation?
Power of Association and Linkage Tests When the Disease Alleles Are Unobserved
The Transmission/Disequilibrium Test and Parental-Genotype Reconstruction: The Reconstruction-Combined Transmission/ Disequilibrium Test
Combining the Sibling Disequilibrium Test and Transmission/Disequilibrium Test for Multiallelic Markers
Linkage Detection Adaptive to Linkage Disequilibrium: The Disequilibrium Maximum-Likelihood–Binomial Test for Affected-Sibship Data
Linkage of Inflammatory Bowel Disease to Human Chromosome 6p
Germ-Cell Nondisjunction in Testes Biopsies of Men With Idiopathic Infertility
Identification of a New Locus for Medullary Cystic Disease, on Chromosome 16p12
Early-Onset Autosomal Dominant Alzheimer Disease: Prevalence, Genetic Heterogeneity, and Mutation Spectrum
This Month in the Journal
Reply to Henke and Henke
Sex-Specific Migration Patterns in Central Asian Populations, Revealed by Analysis of Y-Chromosome Short Tandem Repeats and mtDNA
The Molecular Basis of Malonyl-CoA Decarboxylase Deficiency
Paroxysmal Kinesigenic Choreoathetosis Locus Maps to Chromosome 16p11.2-q12.1
Erratum
Mutation Rate in Human Microsatellites
Stratification Analysis of an Osteoarthritis Genome Screen—Suggestive Linkage to Chromosomes 4, 6, and 16
RB1 Gene Mutations in Peripheral Blood DNA of Patients with Isolated Unilateral Retinoblastoma
Modeling the Probability That Ashkenazi Jewish Women Carry a Founder Mutation in BRCA1 or BRCA2
This Month in the Journal
Pseudoautosomal Linkage of Hodgkin Disease
Overgrowth Syndromes and the Regulation of Signaling Complexes by Proteoglycans
A Second Gene for Autosomal Dominant Möbius Syndrome Is Localized to Chromosome 10q, in a Dutch Family
A Loss-of-Function Model for Cystogenesis in Human Autosomal Dominant Polycystic Kidney Disease Type 2
De Novo BRCA1 Mutation in a Patient with Breast Cancer and an Inherited BRCA2 Mutation
A Mutation (2314delG) in the Usher Syndrome Type IIA Gene: High Prevalence and Phenotypic Variation
Gonadoblastoma, Testicular and Prostate Cancers, and the TSPY Gene
A Worldwide Assessment of the Frequency of Suicide, Suicide Attempts, or Psychiatric Hospitalization after Predictive Testing for Huntington Disease
Prevalence of Bloom Syndrome Heterozygotes among Ashkenazi Jews Ashkenazi Jews
Possible Interaction between USH1B and USH3 Gene Products as Implied by Apparent Digenic Deafness Inheritance
HPS Gene Mutations in Hermansky-Pudlak Syndrome
Genome Scan for Predisposing Loci for Distal Interphalangeal Joint Osteoarthritis: Evidence for a Locus on 2q
Transfection of BLM into Cultured Bloom Syndrome Cells Reduces the Sister-Chromatid Exchange Rate toward Normal
Analysis of Chromosome 1q42.2-43 in 152 Families with High Risk of Prostate Cancer
Retinitis Pigmentosa and Progressive Sensorineural Hearing Loss Caused by a C12258A Mutation in the Mitochondrial MTTS2 Gene
An Optimal Algorithm for Automatic Genotype Elimination
This Month in the Journal
A Parametric Copula Model for Analysis of Familial Binary Data
A Novel NTRK1 Mutation Associated with Congenital Insensitivity to Pain with Anhidrosis
Demonstration of the Recurrence of Marfan-like Skeletal and Cardiovascular Manifestations Due to Germline Mosaicism for an FBN1 Mutation
Variegate Porphyria in Western Europe: Identification of PPOX Gene Mutations in 104 Families, Extent of Allelic Heterogeneity, and Absence of Correlation between Phenotype and Type of Mutation
Further Evidence for a Susceptibility Locus on Chromosome 20q13.11 in Families with Dominant Transmission of Graves Disease
High Frequency of Large Intragenic Deletions in the Fanconi Anemia Group A Gene
A Common Breakpoint on 11q23 in Carriers of the Constitutional t(11;22) Translocation
Localization of a Gene for Familial Hemophagocytic Lymphohistiocytosis at Chromosome 9q21.3-22 by Homozygosity Mapping
Disequilibrium Mapping of a Quantitative-Trait Locus in an Expanding Population
Cancer Genetics and Insurance
Mathematical and Statistical Methods for Genetic Analysis
The Gene for Cherubism Maps to Chromosome 4p16
Genotype/Phenotype Analysis of a Photoreceptor-Specific ATP-Binding Cassette Transporter Gene, ABCR, in Stargardt Disease
The Promoters of the Survival Motor Neuron Gene (SMN) and Its Copy (SMNc) Share Common Regulatory Elements
Rett Syndrome and Beyond: Recurrent Spontaneous and Familial MECP2 Mutations at CpG Hotspots
Mutation of the XNP/ATR-X Gene in a Family with Severe Mental Retardation, Spastic Paraplegia and Skewed Pattern of X Inactivation: Demonstration that the Mutation is Involved in the Inactivation Bias
Announcements11. Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Emory Uni
Heterogeneous X Inactivation in Trophoblastic Cells of Human Full-Term Female Placentas
Erratum
Multiple ATM-Dependent Pathways: An Explanation for Pleiotropy
Common Fragile Sites: G-Band Characteristics within an R-Band
BRCA1 and BRCA2 Testing: Weighing the Demand against the Benefits
Comparison of the Power and Accuracy of Biallelic and Microsatellite Markers in Population-Based Gene-Mapping Methods
Finite-Sample Properties of Family-Based Association Tests
A Test of Transmission/Disequilibrium for Quantitative Traits in Pedigree Data, by Multiple Regression
The Challenges of Psychopharmacogenetics
Errata
Autosomal Dominant Cerebellar Ataxia Type III: Linkage in a Large British Family to a 7.6-cM Region on Chromosome 15q14-21.3
Localization of a Gene for Autosomal Recessive Distal Renal Tubular Acidosis with Normal Hearing (rdRTA2) to 7q33-34
Optimal Ascertainment Strategies to Detect Linkage to Common Disease Alleles
Novel Locus for Autosomal Dominant Hereditary Spastic Paraplegia, on Chromosome 8q
Linkage of Low-Density Lipoprotein Size to the Lipoprotein Lipase Gene in Heterozygous Lipoprotein Lipase Deficiency
Congenital Motor Nystagmus Linked to Xq26-q27
Recurrent Williams-Beuren Syndrome in a Sibship Suggestive of Maternal Germ-Line Mosaicism
The Phenotypic Spectrum of GLI3 Morphopathies Includes Autosomal Dominant Preaxial Polydactyly Type-IV and Postaxial Polydactyly Type-A/B; No Phenotype Prediction from the Position of GLI3 Mutations
A New Neurological Syndrome with Mental Retardation, Choreoathetosis, and Abnormal Behavior Maps to Chromosome Xp11
Cystic Fibrosis Mutations in Heterozygous Newborns with Hypertrypsinemia and Low Sweat Chloride
DNA Transfer to Cultured Cells
A Third Locus Predisposing to Multiple Deletions of mtDNA in Autosomal Dominant Progressive External Ophthalmoplegia
DNA Sequence Variants of p53: Cancer and Aging
The Genetic Epidemiology of Early-Onset Epithelial Ovarian Cancer: A Population-Based Study
Inherited Colorectal Polyposis and Cancer Risk of the APC I1307K Polymorphism
Germ-Line NF2 Mutations and Disease Severity in Neurofibromatosis Type 2 Patients with Retinal Abnormalities
Use of Unlinked Genetic Markers to Detect Population Stratification in Association Studies
Testing the Robustness of the Likelihood-Ratio Test in a Variance-Component Quantitative-Trait Loci–Mapping Procedure
No Mutations in the Coding Region of the PRKCG Gene in Three Families with Retinitis Pigmentosa Linked to the RP11 Locus on Chromosome 19q
Using Exact P Values to Compare the Power between the Reconstruction-Combined Transmission/Disequilibrium Test and the Sib Transmission/Disequilibrium Test
The Prevalence of Common BRCA1 and BRCA2 Mutations among Ashkenazi Jews Ashkenazi Jews
In Swedish Families with Hereditary Prostate Cancer, Linkage to the HPC1 Locus on Chromosome 1q24-25 Is Restricted to Families with Early-Onset Prostate Cancer
Variant Manifestation of Cowden Disease in Japan: Hamartomatous Polyposis of the Digestive Tract with Mutation of the PTEN Gene
The Predisposition to Type 1 Diabetes Linked to the Human Leukocyte Antigen Complex Includes at Least One Non–Class II Gene
Complete Genomic Structure and Mutational Spectrum of PHKA2 in Patients with X-Linked Liver Glycogenosis Type I and II
Methylation Imprinting of H19 and SNRPN Genes in Human Benign Ovarian Teratomas
Structure of the GM2A Gene: Identification of an Exon 2 Nonsense Mutation and a Naturally Occurring Transcript with an In-Frame Deletion of Exon 2
X Chromosome–Inactivation Patterns Confirm the Late Timing of Monoamniotic-MZ Twinning
Localization of a Gene for Familial Patella Aplasia-Hypoplasia (PTLAH) to Chromosome 17q21–22
Variation in Short Tandem Repeats Is Deeply Structured by Genetic Background on the Human Y Chromosome
Genetic Mapping to 10q23.3-q24.2, in a Large Italian Pedigree, of a New Syndrome Showing Bilateral Cataracts, Gastroesophageal Reflux, and Spastic Paraparesis with Amyotrophy Italian
Evidence for a Rare Prostate Cancer–Susceptibility Locus at Chromosome 1p36
Modification of BRCA1-Associated Breast Cancer Risk by the Polymorphic Androgen-Receptor CAG Repeat
Interindividual Variation in Mitotic Recombination
Constitutional Mutations of the hSNF5/INI1 Gene Predispose to a Variety of Cancers
A 28-kb Deletion Spanning D15S63 (PW71) in Five Families: A Rare Neutral Variant?
Founder BRCA1/2 Mutations among Male Patients with Breast Cancer in Israel
Reply to Sharpe
The Molecular Basis of Cystathionine β-Synthase Deficiency in Dutch Patients with Homocystinuria: Effect of CBS Genotype on Biochemical and Clinical Phenotype and on Response to Treatment
Genetic Linkage of IgA Deficiency to the Major Histocompatibility Complex: Evidence for Allele Segregation Distortion, Parent-of-Origin Penetrance Differences, and the Role of Anti-IgA Antibodies in D
Interaction between the Functional Polymorphisms of the Alcohol-Metabolism Genes in Protection against Alcoholism
Candidate-Gene Association Studies of Schizophrenia
Brachydactyly Type B: Clinical Description, Genetic Mapping to Chromosome 9q, and Evidence for a Shared Ancestral Mutation
Linkage of Type 2 Diabetes Mellitus and of Age at Onset to a Genetic Location on Chromosome 10q in Mexican Americans
Reply to Baron
Calpainopathy—A Survey of Mutations and Polymorphisms
Hereditary Isolated Renal Magnesium Loss Maps to Chromosome 11q23
Combined Use of Biallelic and Microsatellite Y-Chromosome Polymorphisms to Infer Affinities among African Populations
Elevated Frequency and Allelic Heterogeneity of Congenital Nephrotic Syndrome, Finnish Type, in the Old Order Mennonites
Failure to Detect Linkage of Preeclampsia to the Region of the NOS3 Locus on Chromosome 7q
This Month in the Journal
The Critical Region for Behçet Disease in the Human Major Histocompatibility Complex Is Reduced to a 46-kb Segment Centromeric of HLA-B, by Association Analysis Using Refined Microsatellite Mapping
Identification of a Mutation Cluster in Mevalonate Kinase Deficiency, Including a New Mutation in a Patient of Mennonite Ancestry Mennonite Ancestry
Genetic Linkage of the Muckle-Wells Syndrome to Chromosome 1q44
Analysis of Alkaptonuria (AKU) Mutations and Polymorphisms Reveals that the CCC Sequence Motif Is a Mutational Hot Spot in the Homogentisate 1,2 Dioxygenase Gene (HGO)
Autosomal Dominant Myopathy with Proximal Weakness and Early Respiratory Muscle Involvement Maps to Chromosome 2q
The Origins of Hypertrophic Cardiomyopathy–Causing Mutations in Two South African Subpopulations: A Unique Profile of Both Independent and Founder Events
Hypomethylation of an Expanded FMR1 Allele Is Not Associated with a Global DNA Methylation Defect
The Duty to Recontact: Attitudes of Genetics Service Providers
Recent Male-Mediated Gene Flow over a Linguistic Barrier in Iberia, Suggested by Analysis of a Y-Chromosomal DNA Polymorphism
DNA Variation in a 5-Mb Region of the X Chromosome and Estimates of Sex-Specific/Type-Specific Mutation Rates
Visuospatial Construction
The Yeast Connection to Friedreich Ataxia
Transcription-Coupled Repair of DNA Damage: Unanticipated Players, Unexpected Complexities
Genetic Counseling and Prenatal Diagnosis for the Mitochondrial DNA Mutations at Nucleotide 8993
Genes That Regulate Eosinophilic Inflammation
Polymorphic X-Chromosome Inactivation of the Human TIMP1 Gene
Identification of a Locus on Chromosome 14q for Idiopathic Basal Ganglia Calcification (Fahr Disease)
Tissue-Specific Somatic Mosaicism in Spinal and Bulbar Muscular Atrophy Is Dependent on CAG-Repeat Length and Androgen Receptor–Gene Expression Level
A Program for the Monte Carlo Evaluation of Significance of the Extended Transmission/Disequilibrium Test
This Month in the Journal
A General Conditional-Logistic Model for Affected-Relative-Pair Linkage Studies
Blocking Gibbs Sampling for Linkage Analysis in Large Pedigrees with Many Loops
Reply to Guo and to Chen et al.
Niemann-Pick C1 Disease: The I1061T Substitution Is a Frequent Mutant Allele in Patients of Western European Descent and Correlates with a Classic Juvenile Phenotype Western European Descent
New Solutions to an Ancient Riddle: Defining the Differences between Adam and Eve
Power Comparisons of the Transmission/Disequilibrium Test and Sib–Transmission/Disequilibrium-Test Statistics
Mapping of Primary Congenital Lymphedema to the 5q35.3 Region
Cultural Difference and the Eugenics Law
Deafness Locus DFNB16 Is Located on Chromosome 15q13-q21 within a 5-cM Interval Flanked by Markers D15S994 and D15S132
Assessment of Linkage Disequilibrium by the Decay of Haplotype Sharing, with Application to Fine-Scale Genetic Mapping
Replication of Linkage Studies of Complex Traits: An Examination of Variation in Location Estimates
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please send announcement text by E-mail to [email protected] or by fax to (2
Prevalence and Phenotype Consequence of FRAXA and FRAXE Alleles in a Large, Ethnically Diverse, Special Education–Needs Population
Germ-Line Mosaicism in Tuberous Sclerosis: How Common?
Linkage-Disequilibrium Mapping of Disease Genes by Reconstruction of Ancestral Haplotypes in Founder Populations
Rett Syndrome in a Boy with a 47,XXY Karyotype
The Gene for Cherubism Maps to Chromosome 4p16.3
Mutation Detection of PKD1 Identifies a Novel Mutation Common to Three Families with Aneurysms and/or Very-Early-Onset Disease
Human Genetics: Choice and Responsibility
Phyllis J. McAlpine, Ph.D., 1941–98: In Memoriam
Localization of Familial Benign Hypercalcemia, Oklahoma Variant (FBHOk), to Chromosome 19q13
The Central Siberian Origin for Native American Y Chromosomes
A Comprehensive Linkage Analysis of Chromosome 21q22 Supports Prior Evidence for a Putative Bipolar Affective Disorder Locus
A Quantitative-Trait Locus on Chromosome 6p Influences Different Aspects of Developmental Dyslexia
Quantitative-Trait Locus for Specific Language and Reading Deficits on Chromosome 6p
Comparison of Linkage-Disequilibrium Methods for Localization of Genes Influencing Quantitative Traits in Humans
Male Infertility and the Y Chromosome
A Gene for Fluctuating, Progressive Autosomal Dominant Nonsyndromic Hearing Loss, DFNA16, Maps to Chromosome 2q23-24.3
This Month in the
Heterogenous Point Mutations in the Mitochondrial tRNA Ser(UCN) Precursor Coexisting with the A1555G Mutation in Deaf Students from Mongolia
Structure of the Gene for Congenital Nephrotic Syndrome of the Finnish Type (NPHS1) and Characterization of Mutations
Human Molybdopterin Synthase Gene: Identification of a Bicistronic Transcript with Overlapping Reading Frames
Identification of a New Locus for Generalized Epilepsy with Febrile Seizures Plus (GEFS+) on Chromosome 2q24-q33
Ancestral Asian Source(s) of New World Y-Chromosome Founder Haplotypes
A 22q11.2 Deletion That Excludes UFD1L and CDC45L in a Patient with Conotruncal and Craniofacial Defects
Mutation Rates in Humans. II. Sporadic Mutation-Specific Rates and Rate of Detrimental Human Mutations Inferred from Hemophilia B
Delineation of the Critical Interval of Bardet-Biedl Syndrome 1 (BBS1) to a Small Region of 11q13, through Linkage and Haplotype Analysis of 91 Pedigrees
When Less Is More: Gene Loss as an Engine of Evolutionary Change
Proteolipoprotein Gene Analysis in 82 Patients with Sporadic Pelizaeus-Merzbacher Disease: Duplications, the Major Cause of the Disease, Originate More Frequently in Male Germ Cells, but Point Mutatio
A Look Back
Evidence for a BRCA1 Founder Mutation in Families of West African Ancestry West African Ancestry
Spectrum of Mutations in α-Mannosidosis
Genome Scan for Human Obesity and Linkage to Markers in 20q13
The Jewish Ashkenazi Founder Mutations in the BRCA1/BRCA2 Genes Are Not Found at an Increased Frequency in Ashkenazi Patients with Prostate Cancer Ashkenazi, Jewish
A Locus for an Axonal Form of Autosomal Recessive Charcot-Marie-Tooth Disease Maps to Chromosome 1q21.2-q21.3
A New Locus for Nonsyndromic Hereditary Hearing Impairment, DFNA17, Maps to Chromosome 22 and Represents a Gene for Cochleosaccular Degeneration
Fragile Sites—Cytogenetic Similarity with Molecular Diversity
Mapping of a First Locus for Autosomal Dominant Myxomatous Mitral-Valve Prolapse to Chromosome 16p11.2-p12.1
The Glu318Gly Substitution in Presenilin 1 Is Not Causally Related to Alzheimer Disease
Absolute Pitch: Prevalence, Ethnic Variation, and Estimation of the Genetic Component
The Molecular Basis of Sjögren-Larsson Syndrome: Mutation Analysis of the Fatty Aldehyde Dehydrogenase Gene
Genomewide Scan for Familial Combined Hyperlipidemia Genes in Finnish Families, Suggesting Multiple Susceptibility Loci Influencing Triglyceride, Cholesterol, and Apolipoprotein B Levels
From the ER to the Golgi: Insights from the Study of Combined Factors V and VIII Deficiency
Toward an Understanding of the Cause of Mitral Valve Prolapse
Multipoint Oligogenic Analysis of Age-at-Onset Data with Applications to Alzheimer Disease Pedigrees
A Genomewide Screen for Schizophrenia Genes in an Isolated Finnish Subpopulation, Suggesting Multiple Susceptibility Loci isolated Finnish subpopulation
Linkage of Familial Schizophrenia to Chromosome 13q32
SPERMSEG: Analysis of Segregation Distortion in Single-Sperm Data
The Interpretation of the Parameters in the Transmission/Disequilibrium Test
TDT Clarification
Phenotypes in Three Pedigrees with Autosomal Dominant Obesity Caused by Haploinsufficiency Mutations in the Melanocortin-4 Receptor Gene
Complement Factor H Gene Mutation Associated with Autosomal Recessive Atypical Hemolytic Uremic Syndrome
Anticipation in Familial Chronic Lymphocytic Leukemia
Joint Multipoint Linkage Analysis of Multivariate Qualitative and Quantitative Traits. I. Likelihood Formulation and Simulation Results
The Duty to Recontact: Benefit and Harm
Recurrence of Marfan Syndrome as a Result of Parental Germ-Line Mosaicism for an FBN1 Mutation
Cystic Fibrosis as a Disease of Misprocessing of the Cystic Fibrosis Transmembrane Conductance Regulator Glycoprotein
Genetic Diseases of the Eye.
A Note on Power Approximations for the Transmission/Disequilibrium Test
The APC I1307K Allele and BRCA-Associated Ovarian Cancer Risk
Yeast as a Model for Human mtDNA Replication
Mutation and Haplotype Studies of Familial Mediterranean Fever Reveal New Ancestral Relationships and Evidence for a High Carrier Frequency with Reduced Penetrance in the Ashkenazi Jewish Population Ashkenazi Jewish Population
Erratum
An Autosomal Dominant Thrombocytopenia Gene Maps to Chromosomal Region 10p
Clustered 11q23 and 22q11 Breakpoints and 3:1 Meiotic Malsegregation in Multiple Unrelated t(11;22) Families
Fine Mapping of the Split-Hand/Split-Foot Locus (SHFM3) at 10q24: Evidence for Anticipation and Segregation Distortion
Evaluation of Parental Mitochondrial Inheritance in Neonates Born after Intracytoplasmic Sperm Injection
Association of RET Protooncogene Codon 45 Polymorphism with Hirschsprung Disease
Protein Fate in Neurodegenerative Proteinopathies: Polyglutamine Diseases Join the (Mis)Fold
The Molecular Basis of Vascular Disorders
Mutations in the Human UDP-N-Acetylglucosamine 2-Epimerase Gene Define the Disease Sialuria and the Allosteric Site of the Enzyme
FMR1 CGG-Repeat Instability in Single Sperm and Lymphocytes of Fragile-X Premutation Males
An Empirical Exploration of the (Δμ)2 Genetic Distance for 213 Human Microsatellite Markers
Patterns of Instability of Expanded CAG Repeats at the ERDA1 Locus in General Populations
Analysis of Affected Sib Pairs, with Covariates—With and Without Constraints
Inbreeding Effects on Fertility in Humans: Evidence for Reproductive Compensation
A Novel 22q11.2 Microdeletion in DiGeorge Syndrome
Tracing the Origin of HLA-DRB1 Alleles by Microsatellite Polymorphism
Announcements
Congenital End-Plate Acetylcholinesterase Deficiency Caused by a Nonsense Mutation and an A→G Splice-Donor–Site Mutation at Position +3 of the Collagenlike-Tail–Subunit Gene (COLQ): How Does G at Posi
Mapping of a Gene Determining Familial Partial Epilepsy with Variable Foci to Chromosome 22q11-q12
The Genomic Record of Humankind's Evolutionary Roots
Mutations in a Dominant-Negative Isoform Correlate with Phenotype in Inherited Cardiac Arrhythmias
This Month in the Journal
Announcements11Announcements are published free of charge for members of The American Society of Human Genetics (ASHG). Please mail announcements to The American Journal of Human Genetics, Department
Sibling-Based Tests of Linkage and Association for Quantitative Traits
Genomic Structure of the Canalicular Multispecific Organic Anion–Transporter Gene (MRP2/cMOAT) and Mutations in the ATP-Binding–Cassette Region in Dubin-Johnson Syndrome
Transmission/Disequilibrium Tests for Extended Marker Haplotypes
Long Homozygous Chromosomal Segments in Reference Families from the Centre d'Étude du Polymorphisme Humain
Rapid Clearance of Fetal DNA from Maternal Plasma
Characterization and Mutation Analysis of Human LEFTY A and LEFTY B, Homologues of Murine Genes Implicated in Left-Right Axis Development
PEX13 Is Mutated in Complementation Group 13 of the Peroxisome-Biogenesis Disorders