Journal of Medical Genetics - 1988

257 articles | Last updated: 2025-12-03 14:12:57
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Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
A simple method for calculating risks before DNA analysis.
Human Gene Mapping 9
Molecular Biology of Homo Sapiens
Topics in Pediatric Genetic Pathology. The Enid Gilbert-Barness Festschrift
Ectrodactyly in sisters and half sisters.
Duchenne Muscular Dystrophy
Intellectual development in Apert's syndrome: a long term follow up of 29 patients.
Familial polyposis coli: no evidence for increased sensitivity to mitomycin C.
Unknown syndrome: mental retardation with postaxial polydactyly, congenital absence of hair, severe seborrhoeic dermatitis, and Perthes' disease of the hip.
Intrafamilial clinical variability of type 1 Gaucher disease in a French-Canadian family. French-Canadian family
Lethal osteogenesis imperfecta associated with 46,XY,inv(7)(p13q22) karyotype.
Human Genetics and Medicine
Veterinary Genetics
Cleft lip and palate, lower lip pits, and limb deficiency defects.
Deletion of band 5q21 in association with a de novo translocation involving 2p and 5q.
Service experience using DNA analysis for genetic prediction in Duchenne muscular dystrophy.
Evidence linking familial thrombosis with a defective antithrombin III gene in two British kindreds.
Teratogen Update: Environmentally Induced Birth Defect Risks
A new high activity plasma cholinesterase variant.
Is the expression of fra(2)(q13) age dependent?
Eleven new cases of del(9p) and features from 80 cases.
Reserpine is not a human teratogen.
The Molecular Basis of Blood Diseases
Dyskeratosis congenita.
Localisation of human alpha globin to 16p13.3----pter.
Murderous Science--Elimination by Scientific Selection of Jews, Gypsies, and others, Germany 1933-1945
Familial ectopic ossification.
Fryns syndrome.
Possible evidence for genetic predisposition to nondisjunction in man.
Can Schizophrenia be Localized in the Brain?
An autosomal dominant multiple pterygium syndrome.
Immunodeficiency, centromeric heterochromatin instability of chromosomes 1, 9, and 16, and facial anomalies: the ICF syndrome.
Hirschsprung disease associated with polydactyly, unilateral renal agenesis, hypertelorism, and congenital deafness: a new autosomal recessive syndrome.
Unusual dual genital duct remnants in true hermaphroditism.
Correspondence
Linkage analysis of X linked retinitis pigmentosa in the Irish population.
Clinical consequences of deletion 1p35.
A duplication/deficient X chromosome in a girl with mental retardation and dysmorphic features.
Martsolf's syndrome in a non-Jewish boy.
Unknown syndrome: microcephaly, facial clefting, and preaxial polydactyly.
Abstracts of the meeting of the Clinical Genetics Society. 20 and 21 November 1987, London. (Joint meeting with the Skeletal Dysplasia Group)
Advances in Human Genetics
A lethal short rib syndrome without polydactyly.
Absence of a vagina and right sided adnexa uteri in the Waardenburg syndrome: a possible clue to the embryological defect.
Clinical features and reproductive patterns in fragile X female heterozygotes.
The influence of culture media on chromosome aberration levels, sister chromatid exchange frequencies, and the rate of cell proliferation: comparison of Iscove's low folate medium with Eagle's MEM.
Translocation (1;22) in a child with bilateral oblique facial clefts.
The value of the study of natural history in genetic disorders and congenital anomaly syndromes.
Unknown syndrome: abnormal facies, hypothyroidism, and severe retardation: a second patient.
Are 'upper' and 'lower' neural tube defects aetiologically different?
Structural and segregation analysis of the type II collagen gene (COL2A1) in some heritable chondrodysplasias.
The telecanthus-hypospadias syndrome.
Pycnodysostosis.
Considerations in using linkage analysis as a presymptomatic test for Huntington's disease.
Anticipation in Huntington's disease is inherited through the male line but may originate in the female.
Heterogeneity in the gene locus for steroid 21-hydroxylase deficiency.
Deletion of a single chromosome band 4q26 in a malformed girl: exclusion of Rieger syndrome associated gene(s) from the 4q26 segment.
Trisomy 3p23----pter and monosomy 11q23----qter in an infant with two translocation carrier parents.
Correction
Genetic Risk, Risk Perception, and Decision Making
Medical genetics around the world
The use of restriction fragment length polymorphisms in prenatal diagnosis of dihydropteridine reductase deficiency.
VATER association: report of a case with three unreported malformations.
Noonan syndrome.
Increased sharing of maternal HLA haplotypes among children exposed to diphenylhydantoin during pregnancy.
Simultaneous trisomy 9q3 and monosomy 5p in two children with der(5),t(5;9)(p15.1;q34.13): report of an extended family.
Arachnoid cysts in a brother and sister.
Counselling for prenatal diagnosis of sickle cell disease and beta thalassaemia major: a four year experience.
Carrier detection through the use of abnormal deletion junction fragments in a case of haemophilia B involving complete deletion of the factor IX gene.
Long arm deletion of chromosome 22.
Familial transmission of autosomal whole arm translocation.
Genetics and Epithelial Cell Dysfunction in Cystic Fibrosis
The Genetics of Renal Tract Disorders
Genomic imprinting: a possible mechanism for the parental origin effect in Huntington's chorea.
Interstitial deletion 2q32.1----q34 in a child with half normal activity of ribulose 5-phosphate 3-epimerase (RPE).
Craniofrontonasal dysplasia.
Lysosomal Storage Disease: Biochemical and Clinical Aspects
Genetic Aspects of Developmental Pathology
Family size limitation: a method for demonstrating recessive inheritance.
Interstitial deletion (6) (q11----q15) in an infant with congenital abnormalities.
Duchenne muscular dystrophy in one of monozygotic twin girls
Application of linkage analysis to genetic counselling in families with hereditary retinoblastoma.
Autosomal recessive inheritance of Nager acrofacial dysostosis.
Prenatal Diagnosis of Heritable Skin Diseases
Screening for fetal and genetic abnormality: social and ethical issues.
The acrocallosal syndrome in first cousins: widening of the spectrum of clinical features and further support for autosomal recessive inheritance.
Primer of Genetic Analysis
John Dalton (1766-1844).
Use of computers in dysmorphology.
Molecular approaches to dysmorphology.
Holoprosencephaly and postaxial polydactyly: another observation.
Mitochondrial myopathy: a genetic study of 71 cases.
Trisomy 18 syndrome with cleft foot.
Restriction enzyme analysis of the mitochondrial genome in mitochondrial myopathy.
Prospective prenatal screening for fetal abnormalities using a quantitative immunoassay for acetylcholinesterase.
Abstracts of the meeting of the Clinical Genetics Society held on 7 and 8 April 1988 at the University of Oxford
Polymorphic acetylation of sulphamethazine in a Zimbabwe population.
Osteoporosis-pseudoglioma syndrome with congenital heart disease: a new association.
Association of an ataxia indistinguishable from Friedreich's ataxia and congenital glaucoma in a family: a new syndrome.
Blepharophimosis, ptosis, epicanthus inversus syndrome (BPES syndrome)
A recognisable short stature syndrome with premature aging and pigmented naevi.
Two whole arm reciprocal translocations.
The population genetics of Duchenne muscular dystrophy.
Annual Review of Genetics
The Man Behind the Syndrome
Evolution from Molecules to Men
Mild and severe muscular dystrophy associated with deletions in Xp21 of the human X chromosome.
Four DNA polymorphisms in the LDL receptor gene: their genetic relationship and use in the study of variation at the LDL receptor locus.
Pathological features and prenatal diagnosis in the newly recognised limb/pelvis-hypoplasia/aplasia syndrome.
Mucosal neuromata syndrome (MEN type IIb (III)).
A new recognisable syndrome in three sibs with congenital heart disease, round face with depressed nasal bridge, short stature, and developmental retardation.
Human chromosome 8.
Prenatal diagnosis of beta thalassaemia by oligonucleotide analysis in Mediterranean populations.
The oculocerebrocutaneous (Delleman) syndrome.
Pubertal development in partial trisomy 14q.
Malay Archipelago
The abuse of genetics. Lessons from the past, lessons for the future
A syndrome of epilepsy, dementia, and amelogenesis imperfecta: genetic and clinical features.
Congenital spinal deformity in a three generation family.
Apparent monosomy 21 owing to a ring 21 chromosome: parental origin revealed by DNA analysis.
Is geroderma osteodysplastica underdiagnosed?
Achondroplasia in sibs of normal parents.
A combinatorial method for grouping cases with multiple malformations.
Correspondence
Human Genes and Diseases
Planning for a Healthy Baby: A Guide to Genetic and Environmental Risks
A reappraisal of the CHARGE association.
Terminal deletion of chromosome 1(q43) in a female infant.
Klippel-Trenaunay-Weber syndrome (angio-osteohypertrophy syndrome).
De novo partial trisomy 15q (proximal type).
Sorsby syndrome: a report on further generations of the original family.
Non-opposable triphalangeal thumb in an Italian family. Italian
Complete absence of external genitalia in limb-body wall complex: two cases.
Partial gene duplication in Duchenne and Becker muscular dystrophies.
Recognition and reanalysis of a cell line from a manifesting female with X linked hypohidrotic ectodermal dysplasia and an X; autosome balanced translocation.
New autosomal recessive faciodigitogenital syndrome.
Oculotrichodysplasia (OTD): a new probably autosomal recessive condition.
Microdeletion syndromes, balanced translocations, and gene mapping.
Dysmorphic syndromes with demonstrable biochemical abnormalities.
Pseudoxanthoma elasticum (Gronblad-Strandberg syndrome).
Osteoporosis-pseudoglioma syndrome: clinical, morphological, and biochemical studies.
Pierre Louis Moreau de Maupertuis (1698-1759).
Leucocyte Typing III: White Cell Differentiation Antigens
Sequential sampling in clinical cytogenetics: a quality control viewpoint.
A probably distinct autosomal recessive thoraco-limb dysplasia.
Linkage analysis of manic depression in an Irish family using H-ras 1 and INS DNA markers.
Oncology and Immunology of Down Syndrome
Association of syndactyly, ectodermal dysplasia, and cleft lip and palate: report of two sibs from Turkey.
Iris coloboma, ptosis, hypertelorism, and mental retardation: a new syndrome.
Royal Society discussion meeting: Prevention and Avoidance of Genetic Disease, held on 29 to 30 April 1987 at the Royal Society.
Expression of fragile X chromosome and possible deletion in successive cell divisions.
A Clinician's View of Neuromuscular Diseases
Malformations in Children from One to Seven Years. A Report from the Collaborative Perinatal Project
The Hemoglobinopathies
The Developmental Field Concept
Practical Genetics
Genetic counselling in hereditary osteo-onychodysplasia (HOOD, nail-patella syndrome) with nephropathy.
Late replication studies and esterase D levels in a case of unbalanced X;autosome translocation, 46,X,t(X;13)(q27;q12).
Chromosome subband 17p11.2 deletion: a minute deletion syndrome.
Autosomal dominant isolated ('uncomplicated') microcephaly.
Palmoplantar keratoderma, nail dystrophy, and hereditary motor and sensory neuropathy: an autosomal dominant trait.
Recent Advances in Inborn Errors of Metabolism
The map of chromosome 20.
Reproductive behaviour and consistent patterns of abnormality in offspring of Vietnam veterans.
Another family with the 'Habsburg jaw'.
The Mammalian Y Chromosome: Molecular Search for the Sex-Determining Factor
A recessive form of congenital contractures and torticollis associated with malignant hyperthermia.
Concurrent de novo interstitial deletion of band 2p22 and reciprocal translocation (3;7)(p21;q22).
Human Genetic Diseases: A Practical Approach
Genetic and Population Studies in Wales
In Vitro Fertilisation: Past, Present and Future
Norrie disease resulting from a gene deletion: clinical features and DNA studies.
Confirmation of prenatal diagnosis of cystic fibrosis by DNA typing of fetal tissues.
Alpha 1 antitrypsin deficiency due to Pi null: clinical presentation and evidence for molecular heterogeneity.
The frequency of consanguineous marriage among British Pakistanis.
Absence of close linkage between benign hereditary chorea and the locus D4S10 (probe G8).
Genetic Disease: Screening and Management
Monoclonals and DNA Probes in Diagnostic and Preventive Medicine
Chorion Villus Sampling
Exclusion of calcitonin as a candidate gene for the basic defect in a family with autosomal dominant supravalvular aortic stenosis.
Inherited deletion of subband Xp21.13 in a male with Duchenne muscular dystrophy.
Type I Gaucher disease.
Malformation syndromes: a review of mouse/human homology.
Auralcephalosyndactyly: a new hereditary craniosynostosis syndrome.
The Child with Multiple Birth Defects
A new centromeric heteromorphism in the short arm of chromosome 20.
Genetics and Malformations in Art
Medical genetics in Hungary.
The Chromosomes and Their Disorders. An Introduction for Clinicians
Gametogenesis and the Early Embryo
A deletion of one nucleotide results in functional deficiency of apolipoprotein CII (apo CII Toronto).
Prediction of consanguinity using human DNA fingerprints.
Heterogeneity of familial porphyria cutanea tarda.
Simultaneous occurrence of heritable t(3;7) and t(14;21) in two sibs.
A new variant of chromosome 3 with unusual staining properties.
The European School of Medical Genetics, Sestri Levante (Genoa), 6 to 12 April 1988
Fetal and Neonatal Pathology
Biological Activities of Alpha1-fetoprotein
Absence of a lateral rectus muscle associated with duplication of the chromosome segment 7q32----q34.
Abstracts of the Annual Scientific Meeting of the Association of Clinical Cytogeneticists held on 30 June to 2 July 1987 at Wills Hall, University of Bristol
Alpha 1 antitrypsin deficiency.
Genetic Disorders and the Fetus
The Dysmorphic Child: An Orthopedic Perspective
Neuromuscular Diseases
Lethal acrodysgenital dwarfism: a severe lethal condition resembling Smith-Lemli-Opitz syndrome.
King's Fund Forum Screening for Fetal and Genetic Abnormality The need for a British Association for Genetic Medicine
Clinical, haematological, and genetic studies of type 2 normal Hb A2 beta thalassaemia.
Sclerosteosis.
De novo 10q23 interstitial deletion.
A family showing apparent X linked inheritance of both anencephaly and spina bifida.
Expression of fra(10)(q25) in peripheral blood and bone marrow in familial neutropenia.
Hypothyroidism and sex chromosomes.
The Balance of Improbabilities: A Scientific Life
The Correspondence of Charles Darwin
Meiotic recombination in the beta globin gene cluster causing an error in prenatal diagnosis of beta thalassaemia.
Are double translocations double trouble?
The Coffin-Lowry syndrome.
Intrauterine death in megacystis-microcolon-intestinal hypoperistalsis syndrome.
Trisomy 3 mosaicism in a patient with Bartter syndrome.
Current Concepts in Craniofacial Anomalies. A Symposium in Honour of Joseph J Bonner
Cloning of the human alpha 1 antichymotrypsin gene and genetic analysis of the gene in relation to alpha 1 antitrypsin deficiency.
C4 null phenotypes among lupus erythematosus patients are predominantly the result of deletions covering C4 and closely linked 21-hydroxylase A genes.
A developing role in genetic counselling.
Unknown syndrome: Hirschsprung's disease, microcephaly, and iris coloboma: a new syndrome of defective neuronal migration.
A further patient with the lethal type of Larsen syndrome.
Molecular Approaches to Human Polygenic Disease
Cytogenetics of Mammalian Embryonic Development
Sickle Cell Anemia and Thalassemia. A Primer for Health Care Professionals
Molecular genetics of neurological and neuromuscular disease
Prenatal diagnosis of inv(X)(q12q28) in a male fetus.
Perinatal Genetics: Diagnosis and Treatment
A progressive cone-rod dystrophy and amelogenesis imperfecta: a new syndrome.
Hirschsprung's disease, hypoplastic nails, and minor dysmorphic features: a distinct autosomal recessive syndrome?
Beta thalassaemia mutations in Turkish Cypriots.
Mammalian Development: A Practical Approach
Hypomelanosis of Ito: a manifestation of mosaicism or chimerism.
Visual evoked potentials in Negro carriers of the gene for tyrosinase positive oculocutaneous albinism. Negro
Analysis of Human Genetic Linkage
Further delineation of the G syndrome: a manageable genetic cause of infantile dysphagia.
Familial spastic paraplegia, bilateral sensorineural deafness, and intellectual retardation associated with a progressive nephropathy.
Anomalous X chromosome inactivation: the link between female zygotes, monozygotic twinning, and neural tube defects?
Theoretical recurrence risks for cleft lip derived from a population of consecutive newborns.
Medical genetics in China.
Duplication 17q mosaicism: an infant with features of Ellis-van Creveld syndrome.
Screening for fetal and genetic abnormality: social and ethical issues.
Genetic markers on chromosome 7.
Birth defects following maternal exposure to ergotamine, beta blockers, and caffeine.
Editorial
Holoprosencephaly, ventricular septal defect, and postaxial polydactyly in a human embryo.
Syndactyly, ectodermal dysplasia, and cleft lip and palate.
Triphalangeal thumb.
Identification of the E1fE1k cholinesterase genotype.
Russell-Silver syndrome.
Sickle Cell Disease
Alport's syndrome.
Prenatal diagnosis of mosaicism for del(18)(q12.2q21.1) and a normal cell line.
Cystic Fibrosis: The Facts