Journal of Medical Genetics - 1984

154 articles | Last updated: 2025-12-03 14:12:57
Caucasian
2
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3
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Cat eye syndrome owing to tetrasomy 22pter leads to q11.
The incidence of Down's syndrome over a 19-year period.
Correspondence
Correspondence
Philtrum length and intercommissural distance in newborn infants.
Late infantile autosomal recessive myotonia, mental retardation, and skeletal abnormalities: a new autosomal recessive syndrome.
Familial pericentric inversion (13) detected by antenatal diagnosis.
Interpretation of RFLP linkage data.
Correction
Homozygosity for autosomal dominant Marfan syndrome.
Carrier detection in the testicular feminisation syndrome: deficient 5 alpha-dihydrotestosterone binding in cultured skin fibroblasts from the mothers of patients with complete androgen insensitivity.
Report of the Clinical Genetics Society Working Party on the role and training of clinical geneticists, September 1983.
Interstitial deletion of the short arm of chromosome 4.
Ir Genes. Past, Present, and Future
Editorial
A screening programme for the prospective prevention of Mediterranean anaemia in Latium: results of seven years' work.
Familial pericentric inversion (10) and its effect on two offspring.
Editorial
Biamnial alpha fetoprotein concentration in twins, one with multiple malformations.
A case of 2-methylacetoacetyl CoA thiolase deficiency with coincidental chromosome abnormalities.
Lateral reading 9
Stub thumbs in Israel revisited.
Interstitial deletion of the short arm of chromosome 5 in a mother and three children.
Heritable Disorders of Connective Tissue
Research Ethics
Utilization of Mammalian Specific Locus Studies in Hazard Evaluation and Estimation of Genetic Risk
Editorial
Autosomal dominant anterior polar cataracts associated with a familial 2;14 translocation.
Triploidy with cyclopia and identical HLA alleles in the parents.
Neural tube defects in sibs of children with tracheo-oesophageal dysraphism.
Premature Chromosome Condensation. Application in Basic, Clinical, and Mutation Research
Gossypol induces DNA strand breaks in human fibroblasts and sister chromatid exchanges in human lymphocytes in vitro.
Abstracts of the meeting of the Clinical Genetics Society held on 18 and 19 November 1983 at Guy's Hospital, London
Trisomy 5p: a second case occurring in a previously described kindred.
A case of deletion 2q35----qter and a peculiar phenotype.
Cytological subdivision of the S phase of human cells in asynchronous culture.
A case of partial monosomy 21q22.2 associated with Rieger's syndrome.
Mosaic hexasomy 21.
The clinical features of homozygous alpha 2(I) collagen deficient osteogenesis imperfecta.
Down's syndrome with a recombinant tandem duplication of chromosome 21 derived from a maternal ring.
Trisomy 9p due to unusual maternal translocation (3;9).
Periconceptional vitamin supplementation and the prevention of neural tube defects in south-east England and Northern Ireland.
Anencephaly: a retrospective analysis in Singapore. 1976 to 1980.
Autosomal recessive severe congenital microcephaly: antenatal ultrasonographic diagnosis and head growth from 15 to 24 weeks of gestation
Deleted X chromosomes in patients with the fragile X syndrome.
A malformed girl with duplication of chromosome 9q.
A study of retinitis pigmentosa in the City of Birmingham. I Prevalence.
Paternal Robertsonian translocation t(13q;14q) and maternal reciprocal translocation t(7p;13q) in a couple with repeated fetal loss.
A rare heterochromatic variant of chromosome 4.
Inv dup (15)
Abstracts of the scientific meeting of the Association of Clinical Cytogeneticists held at the Duncan Guthrie Institute of Medical Genetics, Glasgow, on 4 and 5 May 1983
First trimester fetal karyotyping in twin pregnancy.
Duchenne muscular dystrophy.
Minor Malformations in the Neonate
Treated glass coverslips for in situ culture of amniotic cells: better cell adhesion and growth than on plastic.
An unbalanced (6q;13q) translocation in a male with clinical features of Ehlers-Danlos type II syndrome.
Ring (13),t(2;6) associated with familial fragile (16).
Whole arm translocation t(1;13) in an infertile man.
Hypermobility of Joints
Early Mammalian Development: Parthenogenetic Studies
Four cases of trisomy 18 syndrome with limb reduction malformations.
Abstracts of the meeting of the Clinical Genetics Society held on 5 and 6 April 1984 at Salford University, Manchester
Endocrine abnormalities in a patient with partial trisomy 4q.
Deletion of the short arm of chromosome 3: a case report with necropsy findings.
The femoral hypoplasia-unusual facies syndrome.
Freeman-Sheldon (whistling face) syndrome in a Turner mosaic.
Recurrence risk after neural tube defects in a genetic counselling clinic.
Prevention of midline defects.
Translocations, social class, and Adam and Eve.
Polymorphic hydroxylation of perhexiline maleate in man.
The Marshall and Stickler syndromes: objective rejection of lumping.
Balanced rearrangements of the autosomes: results of a longitudinal study of a newborn survey population.
De novo direct tandem duplication of the proximal long arm of chromosome 2: 46,XX,dir dup(2)(q11 X 2q14 X 2).
Multiple endocrine neoplasia type 2 (Sipple's syndrome): clinical and cytogenetic analysis of a kindred.
Familial multiple naevi flammei.
A computerised data base for the diagnosis of rare dysmorphic syndromes.
The 3-M syndrome.
Trisomy 1q24----1q41 in two sibs with an insertion in an inverted chromosome 4.
Location of the retinoblastoma susceptibility gene(s) and the human esterase D locus.
On the identification and frequency of the J and K cholinesterase phenotypes in a Caucasian population.
Risk estimates for neonatal myotonic dystrophy.
An analysis of the parental age effect for inv dup (15).
Fragile site at 12q13 associated with phenotypic abnormalities.
De novo translocation involving chromosomes 2, 8, and 20.
49,XXYY, +18 in a liveborn male.
Genetics of Cardiovascular Disease
Growth hormone inhibition causes increased selenium levels in Duchenne muscular dystrophy: a possible new approach to therapy.
Association of heterocellular HPFH, beta(+)-thalassaemia, and delta beta(0)-thalassaemia: haematological and molecular aspects.
Trichothiodystrophy-neurotrichocutaneous syndrome of Pollitt: a report of two unrelated cases.
Partial trisomy 16p due to maternal balanced translocation.
Genetic heterogeneity in the Freeman-Sheldon syndrome: two adults with probable autosomal recessive inheritance
Parietal foramina in Saethre-Chotzen syndrome
Correction
Partial trisomy 16 as a result of familial 16;20 translocation.
Mosaic Down's syndrome with de novo 45,XX,-21,-22,+t(21q;22q)/46,XX,-21,+t(21q;21q) rearrangement.
Ring chromosome 1 associated with radial ray defect.
A study of retinitis pigmentosa in the City of Birmingham. II Clinical and genetic heterogeneity.
A linkage study between HLA and cutaneous malignant melanoma or precursor lesions or both.
Glycoproteins in cystic fibrosis: a lectin binding study.
Annual Review of Genetics
Inheritance of idiopathic torsion dystonia among Jews. Jews
Chromosome variation in perinatal mortality: a survey of 500 cases.
The origin of ovarian teratomas.
Spondylocostal dysostosis.
Routine diagnostic detection of the fragile X.
Spectrum of anomalies in Fanconi anaemia.
Genetic heterogeneity in Duchenne muscular dystrophy.
Delta beta-thalassaemia in southern Italy: evidence for a single mutational event.
Trisomy 18 phenotype in a patient with an isopseudodicentric 18 chromosome.
Haemoglobin O Arab (B121 Glu-Lys) in Turkish Cypriot population.
Breast cancer, genetics, and age at first pregnancy.
Editorial
Impaired HLA capping capacity of peripheral blood lymphocytes in Duchenne muscular dystrophy.
Clinical and cytogenetic diversity in Fanconi's anaemia.
Inv dup (15) with mental retardation but few dysmorphic features.
A Colour Atlas of Clinical Genetics
Soft Tissue Ossification
Favism: looking for an autosomal gene associated with glucose-6-phosphate dehydrogenase deficiency.
Familial hidradenitis suppurativa: evidence in favour of single gene transmission.
Observations on the epidemiology of club foot in Polynesian and Caucasian populations. Polynesian
Antenatal diagnosis of mucopolysaccharidosis type I (Hurler's disease) is not possible by electron microscopy of uncultured amniotic fluid cells.
A familial insertion involving an active nucleolar organiser within chromosome 12.
Pericentric inversion inv(3)(p11q21).
Interstitial deletion of chromosome band 13q14 associated with squamous cell carcinoma.
Professor C O Carter, MA, DM, FRCP: Director of the MRC Clinical Genetics Unit, Institute of Child Health, London, 1964-1982, and Assistant Editor of Journal of Medical Genetics, 1970-1983: Tributes a
Paracentric inversions in man.
An epidemiological and genetic study of facial clefting in France. II Segregation analysis.
Familial paracentric inversion of chromosome 15 (q15q24).
A complex three way translocation resulting in two sibs with partial trisomy 3p23----3pter.
A live infant with trisomy 14 mosaicism and nuclear abnormalities of the neutrophils.
Blood Relations. Blood Groups and Anthropology
What is the incidence of holoprosencephaly?
Concordant monozygotic twins with bilateral renal agenesis.
Poland-Mobius syndrome associated with dextrocardia.
Mobile Genetic Elements
Familial occurrence of unilateral giant breasts in Nigeria: a possible new genetic entity.
Editorial
Blot hybridisation analysis of genomic DNA.
Orofaciodigital syndrome with mesomelic limb shortening.
Survey of the human acetylator polymorphism in spontaneous disorders.
Tuberous sclerosis: a new estimate of prevalence within the Oxford region.
Familial centric fission of chromosome 4.
Chronic proximal spinal muscular atrophy of childhood and adolescence: sex influence.
Tracheo-oesophageal dysraphism.
Issues and Reviews in Teratology
Correspondence
A genetic combination of silent beta-thalassaemia, high Hb A2 beta-thalassaemia, and single alpha globin gene deletion causing mild thalassaemia intermedia.
Incidence of pyloric stenosis in British Columbia over a 12 year period.
The fragile X syndrome: the patients and their chromosomes.
Spondyloepiphyseal dysplasia tarda with progressive arthropathy.
Developments in Human Reproduction and their Eugenic and Ethical Implications
Hereditary coproporphyria: incidence in a large English family. English family
Abstracts of the scientific meeting of the Association of Clinical Cytogeneticists held at the Institute of Child Health, London, on 2 and 3 May 1984
Ataxia-Telangiectasia. A Cellular and Molecular Link Between Cancer, Neuropathology, and Immune Deficiency