Journal of Medical Genetics - 1981

141 articles | Last updated: 2025-12-03 14:12:57
Caucasian
0
White
0
European
0
Other
1
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Myotonic Dystrophy
Inherited Disorders of Carbohydrate Metabolism
Genetic Disorders and the Fetus. Diagnosis, Prevention, and Treatment
Risks to the offspring of patients with some common congenital heart defects.
Beta-Thalassaemia types in southern Sardinia.
Prenatal detection of Turner's syndrome in conjunction with trisomy 20 mosaicism (45,X/46, X, +0).
'Pseudo-dominant' inheritance in Friedreich's ataxia.
Fetal cells in the blood of pregnant mothers.
Hereditary ectodermal dysplasia, olivopontocerebellar degeneration, short stature, and hypogonadism.
The Principles of Human Biochemical Genetics
Autosomal dominant hypoparathyroidism: a proband with concurrent nephrogenic diabetes insipidus.
A dental approach to carrier screening in X linked hypohidrotic ectodermal dysplasia.
PiPclifton: a new  1-antitrypsin allele in an American Negro family American Negro family
Retinitis pigmentosa, metaphyseal chondrodysplasia, and brachydactyly: an affected brother and sister.
Human Genetics. Problems and Approaches
Congenital hydrocephalus in two pregnancies following the birth of a child with a neural tube defect: aetiology and management.
A case of trisomy of chromosome 15
Familial partial 14 trisomy.
Correction
Evaluation of information-guidance genetic counselling.
Confirmation of the multifactorial threshold model for congenital structural talipes equinovarus.
Phenotype of partial trisomy 8 (p21 leads to qter) in two unrelated patients with de novo translocation.
Human Gene Mapping 5
Recurrence rates for neural tube defects and vitamin supplementation
The Patterson syndrome, leprechaunism, and pseudoleprechaunism.
Asplenia and polysplenia syndromes with abnormalities of lateralisation in a sibship.
Ring chromosome 14: a distinct clinical entity.
Hydrocephalus, agyria, pseudoencephalocele, retinal dysplasia, and anterior chamber anomalies.
Genetic counselling for handicapped school leavers.
Complete trisomy 9 in two liveborn infants.
Normal psychomotor development in a child with mosaic trisomy and pericentric inversion of chromosome 9.
18p-- syndrome with a single central maxillary incisor
Hereditary motor and sensory neuropathy.
Correspondence
Hereditary multiple exostoses: report of a kindred.
Genetic aspects of autosomal dominant late onset cerebellar ataxia.
Cherchez les femmes (or the personal touch in the laboratory).
Down syndrome associated with father's age in Norway.
Variable expression in Pfeiffer syndrome.
Theory of Population Genetics and Evolutionary Ecology: An Introduction
Monozygotic twins discordant for exstrophy of the urinary bladder.
A family study of protracted diarrhoea in infancy.
Ectodermal dysplasia in females and inversion of chromosome 9.
Clinical Genetics Society. Abstracts of scientific papers presented on 18 and 19 September 1980 in Aberdeen
Structural aberration of the X chromosome in a patient with gonadal dysgenesis: an approach to karyotype-phenotype correlation.
Anal atresia and the Klein-Waardenburg syndrome.
The bristol registry of bone dysplasias: the first 10 years.
Phenotypic and quantitative relationship of red cell acid phosphatase with haemoglobin, haptoglobin, and G6PD phenotypes.
Clinical Genetics Society: Posters available during various breaks, 18/19 September 1980
A 5;7, 5;12 double reciprocal translocation in a normal mother and a 5;7 translocation with a recombinant chromosome 5 in her normal child.
Tetraploidy in a liveborn infant with spina bifida and other anomalies.
Retardation of ovarian growth in male-sterile mice carrying an autosomal translocation.
Trehalase activity in genetically diabetic mice (serum, kidney, and liver).
Partial trisomy 12q: report of a case and review.
Season and interval for recurrence of neural tube defects.
Objective knowledge about Huntington's disease and attitudes towards predictive tests of persons at risk.
Two brothers with the Marden-Walker syndrome: case report and review
A 13-year-old girl with karyotype 47,XX,+i(22)(qll)
Familial chromosome translocation t(3;18)(p21;p11).
Propionyl coenzyme A carboxylase deficiency presenting as non-ketotic hyperglycinaemia.
Principles of Gene Manipulation. An Introduction to Genetic Engineering
Development, Growth and Ageing
Recurrence risks for neural tube defects in a genetic counseling clinic population.
Dominant transmission of Sprengel's shoulder and cleft palate
A clinical study of a family with Cockayne's syndrome
Human acetylator polymorphism: estimate of allele frequency in Libya and details of global distribution.
Antenatal diagnosis of Niemann-Pick disease in a twin pregnancy.
5-Fluoro-2'-deoxyuridine induction of the fragile site on Xq28 associated with X linked mental retardation.
Diplospermy II indicated as the origin of a liveborn human triploid (69,XXX).
Ectrodactyly, cleft lip and palate in two half sibs.
Correspondence: Gonadal dysgenesis with 46,X,Xt(qter->p221:: p223->qter) karyotype
Correspondence
Practical Genetic Counselling
Genetics of Gastrointestinal Disease
Genes for super-intelligence?
Are congenital vertebral anomalies and spina bifida cystica aetiologically related?
Multiple pterygium syndrome.
Differences between the events preceding spina bifida and anencephaly.
Trisomy 14 mosaicism in a translocation 14q15q carrier: probable dissociation and isochromosome formation.
Monosomy 22 with mosaicism
The aetiology of the cat eye syndrome reconsidered.
Familial dentinogenesis imperfecta, blue sclerae, and wormian bones without fractures: another type of osteogenesis imperfecta?
Syndromes of microcephaly, microphthalmia, cataracts, and joint contractures
Partial trisomy 12q.
Congenital dislocation of the knees in a child with Down-mosaic Turner syndrome
Prenatal diagnosis for adenosine deaminase deficiency.
Huntington's disease in Tanzania.
Inheritance of a ring 14 chromosome.
Partial trisomy 6p: 46,XX, -10, der(10),t(6;10) (p22;q26)pat and HLA localisation.
An infant with ring 17 chromosome and unusual dermatoglyphs: a new syndrome?
Effectiveness of one tube osmotic fragility screening in detecting beta-thalassaemia trait.
Cystic fibrosis and the month of birth
Correspondence
Recurrence risk of neural tube defects.
Adenosine deaminase polymorphism. Associations at clinical level suggest a role in cell functions and immune reactions.
Genetic Metabolic Diseases. Early Diagnosis and Prenatal Analysis
Inborn Errors of Metabolism
Prenatal Diagnosis
Distal symphalangism associated with camptodactyly.
HLA and renal transplantation: yet another approach.
Partial proximal trisomy of the long arm of chromosome 5 (q13 leads to q22) resulting from maternal insertion der ins (10;5).
Prenatal diagnosis of thalassaemia major resulting from Lepore/ beta-thalassaemia genotype.
A case of the orocraniodigital (Juberg-Hayward) syndrome.
A new case of Prader-Willi syndrome with chromosomal aberration.
A female with XO/XY mosaicism and partial trisomy 9p.
Partial trisomy for long arm of chromosome 16.
A genetic study of Duchenne muscular dystrophy in West Midlands.
Temporal increase in the rate of Down syndrome livebirths to older mothers in New York State.
Interaction of  - and   0-thalassaemia: haematological features and globin chain synthesis analysis
Trisomy 10p produced by recombination involving maternal inversion inv(10)(pllq26).
Advances in Human Genetics
Coincidence of neurofibromatosis and myotonic dystrophy in a kindred.
Birth frequency of bilateral renal agenesis.
Children of those treated surgically for Hirschsprung's disease.
Presentation of mucopolysaccharidosis VII (beta-glucuronidase deficiency) in infancy.
Advances in Human Genetics
Genetics
Genes and the Mind. Inheritance of Mental Illness
A family study of hydrocephalus resulting from aqueduct stenosis.
Genetic and clinical patterns of heritable cerebellar ataxias in adults. II. Clinical manifestations.
Monozygotic twins discordant for rubinstein-taybi syndrome.
Poland-Mobius syndrome.
Risk counselling in autosomal dominant disorders with undetermined penetrance.
The 'fragile' X chromosome in the Martin-Bell-Renpenning syndrome and in males with other forms of familial mental retardation.
Fetal phenotype in a case of partial trisomy 21 and partial monosomy 22 detected prenatally.
A Handbook of Clinical Genetics
Translocation (X;6) in a female with Duchenne muscular dystrophy: implications for the localisation of the DMD locus.
Homodicentric chromosomes: a distinctive type of dicentric chromosome.
Duplication-deletion with partial trisomy lq and partial monosomy 3p resulting from a maternal reciprocal translocation rcp (1;3) (q32;p25).
Neuronal ceroid lipofuscinosis and arthropathy: a family study.
Inherited abnormalities of collagen.
A new probably autosomal recessive cardiomelic dysplasia with mesoaxial hexadactyly
The Management of Genetic Disorders
Localisation of male determining factors in man: a thorough review of structural anomalies of the Y chromosome.
A method for studying the skeleton of human fetuses.
Dermatoglyphs in congenital heart disease.
Meiotic behaviour of two human reciprocal translocations.
Absence of constitutive heterochromatin in a partially identified supernumerary marker chromosome.
The development of clinical genetics.
Symmetrical infantile thalamic degeneration in two sibs
Unilateral radial aplasia and trisomy 22 mosaicism.