Human Mutation - 2002

228 articles | Last updated: 2025-12-03 14:12:57
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Erratum: Spectrum of low density lipoprotein receptor mutations in Czech hypercholesterolemic patients
Low frequency of recurrent BRCA1 and BRCA2 mutations in Spain
Identification of a novel NOG gene mutation (P35S) in an Italian family with symphalangism
The mutational spectrum of human autosomal tetranucleotide microsatellites
Evaluation of Cx26/GJB2 in German hearing impaired persons: mutation spectrum and detection of disequilibrium between M34T (c.101T>C) and -493del10
Mutations spectrum ofGNE in hereditary inclusion body myopathy sparing the quadriceps
eMelanoBase: An online locus-specific variant database for familial melanoma
Mutation scanning by ion-pair reversed-phase high-performance liquid chromatography-electrospray ionization mass spectrometry (ICEMS)
A higher-impactHuman Mutationlaunches web-based submission/peer review andEarlyView rapid publication
BRCA1 germline mutations in Indian familial breast cancer
Novel mutations in the Charcot-Marie-Tooth disease genes PMP22, MPZ, and GJB1
Sequence diversity of<i>KIAA0027/MLC1:</i>are megalencephalic leukoencephalopathy and schizophrenia allelic disorders?
Direct estimates of human per nucleotide mutation rates at 20 loci causing mendelian diseases
ATM mutations on distinct SNP and STR haplotypes in ataxia-telangiectasia patients of differing ethnicities reveal ancestral founder effects
Meta-analysis of indels causing human genetic disease: mechanisms of mutagenesis and the role of local DNA sequence complexity
Two cases of misinterpretation of molecular results in incontinentia pigmenti, and a PCR-based method to discriminate NEMO/IKK? dene deletion
Dynamics of CAG repeat loci revealed by the analysis of their variability
Identification of 36 novel Jagged1 (JAG1) mutations in patients with Alagille syndrome
Glucose-6-phosphate dehydrogenase (G6PD) variants in Malaysian Malays
Splice mutations in the p53 gene: case report and review of the literature
Erratum: Detection of C1 inhibitor (SERPING1/C1NH) mutations in exon 8 in patients with hereditary angioedema: evidence for 10 novel mutations
Identification of 14 novelCTNS mutations and characterization of seven splice site mutations associated with cystinosis
Uniparental disomy of chromosome 2 resulting in lethal trifunctional protein deficiency due to homozygous ?-subunit mutations
Implementation of SMA carrier testing in genetic laboratories: comparison of two methods for quantifying the<i>SMN1</i>gene
D90A-SOD1 mediated amyotrophic lateral sclerosis: A single founder for all cases with evidence for aCis-acting disease modifier in the recessive haplotype
BRCA1 and BRCA2 in Indian breast cancer patients
KCNQ1 and KCNH2 mutations associated with long QT syndrome in a Chinese population
Analysis of<i>ABCA4</i>in mixed Spanish families segregating different retinal dystrophies
Molecular analysis of Turkish mucopolysaccharidosis IVA (Morquio A) patients: identification of novel mutations in the N-acetylgalactosamine-6-sulfate sulfatase (GALNS) gene
Novel mutations in the MYOC/GLC1A gene in a large group of glaucoma patients
Molecular characterisation of GSD III subjects and identification of six novel mutations inAGL
Novel insertions of Bruton tyrosine kinase in patients with X-linked agammaglobulinemia
Missense mutations in the extracellular domain of the human neural cell adhesion molecule L1 reduce neurite outgrowth of murine cerebellar neurons
Increasing evidence that germline mutations in<i>CHEK2</i>do not cause Li-Fraumeni syndrome
SLC26A3 mutations in congenital chloride diarrhea
Proposal for an allele nomenclature system based on the evolutionary divergence of haplotypes
Hereditary breast and ovarian cancer in Asia: genetic epidemiology ofBRCA1 andBRCA2
BRCA1 andBRCA2 sequence variants in Chinese breast cancer families Chinese
<i>BRCA1</i>and<i>BRCA2</i>mutation analysis of early-onset and familial breast cancer cases in Mexico
A double mutant [N543H+2393del9] allele in the LDL receptor gene in familial hypercholesterolemia: effect on plasma cholesterol levels and cardiovascular disease
A common haplotype for the 677T thermolabile variant of the 5,10-methylenetetrahydrofolate reductase gene in thrombophilic patients and controls
GCK and HNF1A mutations in Canadian families with maturity onset diabetes of the young (MODY)
Determination of ?2-adrenergic receptor (ADRB2) haplotypes by a multiplexed polymerase chain reaction assay
DHPLC mutation analysis ofJagged1 (JAG1) reveals six novel mutations in Australian alagille syndrome patients
Hermansky-Pudlak syndrome type 1: gene organization, novel mutations, and clinical-molecular review of non-Puerto Rican cases
The humanSHOX mutation database
NovelPEX1 mutations and genotype-phenotype correlations in Australasian peroxisome biogenesis disorder patients
DHPLC analysis of potassium ion channel genes in congenital long QT syndrome
Different molecular mechanisms underlie genomic deletions in theMLH1 Gene
The LDL receptor-related protein (LRP1/A2MR) and coronary atherosclerosis - novel genomic variants and functional consequences
Clustering of variations and haplotype analysis in the highly variable region of exon 11 ofBRCA1 in Chinese women with sporadic breast cancer
H intragenic polymorphisms and haplotype analysis in the ornithine transcarbamylase (OTC) gene and their relevance for tracking the inheritance of OTC deficiency
A collection of 33 novel human mtDNA homoplasmic variants
Cyclooxygenase 1(COX1) polymorphisms in African-American and caucasian populations
Association of a homozygous (TA)8 promoter polymorphism and a N400D mutation of UGT1A1 in a child with Crigler-Najjar type II syndrome
A low frequency of non-founder BRCA1 mutations in Ashkenazi Jewish breast-ovarian cancer families Ashkenazi Jewish
Epidemiology of the delta globin alleles in southern Italy shows complex molecular, genetic, and phenotypic features
The detection of large deletions or duplications in genomic DNA
Molecular analysis in Japanese patients with Charcot-Marie-Tooth disease: DGGE analysis for PMP22, MPZ, and Cx32/GJB1 mutations
Novel mutations of APOB cause apoB truncations undetectable in plasma and familial hypobetalipoproteinemia
Five novelSLC7A7 variants and y+L gene-expression pattern in cultured lymphoblasts from Japanese patients with lysinuric protein intolerance
Corrigendum: Mutation nomenclature extensions and suggestions to describe complex mutations: A discussion
Ten novel ORF15 mutations confirm mutational hot spot in theRPGR gene in European patients with X-linked retinitis pigmentosa European patients
Detection of C1 inhibitor (SERPING1/C1NH) mutations in exon 8 in patients with hereditary angioedema: evidence for 10 novel mutations
Molecular studies in mutase-deficient (MUT) methylmalonic aciduria: identification of five novel mutations
Mutation screening of the fibrillin-1 (FBN1) gene in 76 unrelated patients with Marfan syndrome or Marfanoid features leads to the identification of 11 novel and three previously reported mutations
Loss of heterozygosity and mutations are the major mechanisms of RB1 gene inactivation in Chinese with sporadic retinoblastoma
Novel O<sup>6</sup>-methylguanine-DNA methyltransferase SNPs: A frequency comparison of patients with familial melanoma and healthy individuals in Sweden
Characterization of a novelCYP2A7/CYP2A6 hybrid allele (CYP2A6*12) that causes reduced CYP2A6 activity
Pyrosequencing for detection of mutations in the connexin 26 (GJB2) and mitochondrial 12S RNA (MTRNR1) genes associated with hereditary hearing loss
Identification of a family with nonspecific mental retardation (MRX79) with the A140V mutation in theMECP2 gene: Is there a need for routine screening?
PTPN11 Mutations in Noonan syndrome type I: detection of recurrent mutations in exons 3 and 13
Broad phenotypic variability in a single pedigree with a novel 1410delC mutation in the PST domain of thePAX6 gene
Evidence of a founder effect for the RETGC1 (GUCY2D) 2943DelG mutation in Leber congenital amaurosis pedigrees of Finnish origin Finnish origin
MECP2 Mutations in Israel: Implications for molecular analysis, genetic counseling, and prenatal diagnosis in Rett syndrome
An analytical method for the detection of methylation differences at specific chromosomal loci using primer extension and ion pair reverse phase HPLC
High throughput mutation screening of the factor VIII gene (F8C) in hemophilia A: 37 novel mutations and genotype-phenotype correlation
rSNP_Guide: An integrated database-tools system for studying SNPs and site-directed mutations in transcription factor binding sites
Mutation analysis ofPEX7 in 60 probands with rhizomelic chondrodysplasia punctata and functional correlations of genotype with phenotype
Erratum: Identification of fifteen novel mutations in the SLC12A3 gene encoding the Na-Cl co-transporter in Italian patients with Gitelman syndrome Italian
One-Step site-directed mutagenesis of ATM cDNA in large (20kb) plasmid constructs
Abnormal mRNA splicing resulting from consensus sequence splicing mutations of ATP7B
Novel mutations and SNPs identified inCCR2 using a new comprehensive denaturing gradient gel electrophoresis assay
Three novel COL4A4 mutations resulting in stop codons and their clinical effects in autosomal recessive Alport syndrome
BRCA1 and BRCA2 mutations in Turkish familial and non-familial ovarian cancer patients: a high incidence of mutations in non-familial cases
Large-scale determination of SNP allele frequencies in DNA pools using MALDI-TOF mass spectrometry
Comparison of DNA- and RNA-Based Methods for Detection of TruncatingBRCA1 Mutations
Intron retention and frameshift mutations result in severe pyruvate carboxylase deficiency in two male siblings
Isolated sulfite oxidase deficiency: identification of 12 novel SUOX mutations in 10 patients
Identification of fifteen novel mutations in the SLC12A3 gene encoding the Na-Cl Co-transporter in Italian patients with Gitelman syndrome
Ten novel mutations in the human neurofibromatosis type 1 (NF1) gene in Italian patients
Progressive AV-block and anomalous venous return among cardiac anomalies associated with two novel missense mutations in theCSX/NKX2-5 Gene
Erratum: Identification of five new mutations of<i>PDS/SLC26A4</i>in Mediterranean families with hearing impairment
Two novel mutations and a new STK11/LKB1 gene isoform in Peutz-Jeghers patients
Mutations in Myosin VIIA (<i>MYO7A</i>) and Usherin (<i>USH2A</i>) in Spanish patients with usher syndrome types I and II, respectively
Hereditary non-polyposis colorectal cancer (HNPCC): phenotype-genotype correlation between patients with and without identified mutation
Germline mutation profile of<i>MEN1</i>in multiple endocrine neoplasia type 1: search for correlation between phenotype and the functional domains of the MEN1 protein
A mutational hot spot in theKCNQ4 gene responsible for autosomal dominant hearing impairment
Frequencies of<i>GJB2</i>mutations in German control individuals and patients showing sporadic non-syndromic hearing impairment
Familial conformational diseases and dementias
Biochemical and mutational analyses of the cathepsin c gene (CTSC) in three North American families with Papillon Lefèvre syndrome
Assessing the relative importance of the biophysical properties of amino acid substitutions associated with human genetic disease
RYR1 mutations causing central core disease are associated with more severe malignant hyperthermia in vitro contracture test phenotypes
Highly multiplexed genotyping of coronary artery disease-associated SNPs using MALDI-TOF mass spectrometry
Novel mutations ofAPOB cause ApoB truncations undetectable in plasma and familial hypobetalipoproteinemia
I591T MEFV mutation in a Spanish kindred: is it a mild mutation, a benign polymorphism, or a variant influenced by another modifier?
The molecular basis of cystathionine ?-synthase deficiency in Australian patients: Genotype-phenotype correlations and response to treatment
Mutation analysis of the<i>spastin</i>gene (<i>SPG4</i>) in patients in Germany with autosomal dominant hereditary spastic paraplegia
An amplification and ligation-based method to scan for unknown mutations in DNA
The UMD-LDLR database: additions to the software and 490 new entries to the database
Mutations in the human ATP-binding cassette transportersABCG5 andABCG8 in sitosterolemia
Identification of five novel WASP mutations in Chinese families with Wiskott-Aldrich syndrome
Rapid detection of novelBRCA1 rearrangements in high-risk breast-ovarian cancer families using multiplex PCR of short fluorescent fragments
Mutational analysis of patients with the diagnosis of choroideremia
Large Family With Maturity-Onset Diabetes of the Young and a Novel V121I Mutation in HNF4A
A founder mutation (R254X) of SLC22A5 (OCTN2) in Chinese primary carnitine deficiency patients
Analysis of thePTCH coding region in human rhabdomyosarcoma
Prevalence of small rearrangements in the factor VIII gene F8C among patients with severe hemophilia A
Splicing mutations, mainly IVS6-1(G&gt;T), account for 70% of fumarylacetoacetate hydrolase (FAH) gene alterations, including 7 novel mutations, in a survey of 29 tyrosinemia type I patients
Data mining of public SNP databases for the selection of intragenic SNPs
TGGE screening of the entire<i>FBN1</i>coding sequence in 126 individuals with marfan syndrome and related fibrillinopathies
Mutations of FBN1 and genotype-phenotype correlations in Marfan syndrome and related fibrillinopathies
SNP databases and pharmacogenetics: great start, but a long way to go
Population genetic implications from DNA polymorphism in random human genomic sequences
Third international meeting on the genetic epidemiology of complex traits, April 4-6, 2002, Cambridge, UK
Analysis of breast cancer susceptibility genesBRCA1 andBRCA2 in Thai familial and isolated early-onset breast and ovarian cancer
Molecular analysis of 30 mucopolysaccharidosis type I patients: evaluation of the mutational spectrum in Italian population and identification of 13 novel mutations Italian population
Identification of seven novel mutations of F8C by DHPLC
Genotype-phenotype studies of six novelLPL mutations in Chinese patients with hypertriglyceridemia Chinese patients
Genetic background of Huntington disease in Croatia: Molecular analysis of CAG, CCG, and ?2642 (E2642del) polymorphisms
Human piebaldism: six novel mutations of the proto-oncogene KIT
Analysis of the glucocerebrosidase gene and mutation profile in 144 Italian gaucher patients
Germline mutations ofBRCA1 andBRCA2 in Korean breast and/or ovarian cancer families
Identification of mutations of Bruton's tyrosine kinase gene (BTK) in Brazilian patients with X-linked agammaglobulinemia
Occurrence of deletion of a COL2A1 allele as the mutation in Stickler syndrome shows that a collagen type II dosage effect underlies this syndrome
Analysis of the CTNS gene in patients of German and Swiss origin with nephropathic cystinosis German and Swiss origin
A robust method for detectingCHK2/RAD53 mutations in genomic DNA
Arab genetic disease database (AGDDB): A population-specific clinical and mutation database
Identification of seven novel missense mutations, two splice-site mutations, two microdeletions and a polymorphic amino acid substitution in the gene for ornithine transcarbamylase (OTC) in patients w
Mutation A1555G in the 12S rRNA gene and its epidemiological importance in German, Hungarian, and Polish patients German, Hungarian, and Polish patients
Structure, genomic DNA typing, and kinetic characterization of the D allozyme of placental alkaline phosphatase (PLAP/ALPP)
Reliability of DHPLC in mutational screening of ?-globin (HBB) alleles
NF1 mutations in neurofibromatosis 1 patients with plexiform neurofibromas
Comparison of SSCP and DHPLC for the detection of LDLR mutations in a New Zealand cohort
GermlineBRCA1 promoter deletions in UK and Australian familial breast cancer patients: Identification of a novel deletion consistent withBRCA1:?BRCA1 recombination
Missense mutations of human homeoboxes: A review
Polymorphisms and HNPCC: PMS2-MLH1 protein interactions diminished by single nucleotide polymorphisms
Making ends meet in genetic analysis using padlock probes
Pyrosequencing?: An accurate detection platform for single nucleotide polymorphisms
High homocysteine and thrombosis without connective tissue disorders are associated with a novel class of cystathionine β-synthase (CBS) mutations
HbVar: A relational database of human hemoglobin variants and thalassemia mutations at the globin gene server
The A8296G mtDNA mutation associated with several mitochondrial diseases does not cause mitochondrial dysfunction in cybrid cell lines
The enigma of theSan Lesmes (response to Langdon, 2002)
Myotonia caused by mutations in the muscle chloride channel geneCLCN1
Pseudoachondroplasia and multiple epiphyseal dysplasia: Mutation review, molecular interactions, and genotype to phenotype correlations
Propionic acidemia: Analysis of mutant propionyl-CoA carboxylase enzymes expressed inEscherichia coli
AHOXA13 allele with a missense mutation in the homeobox and a dinucleotide deletion in the promoter underlies Guttmacher syndrome
Mutation detection 2001: Novel technologies, developments and applications for analysis of the human genome
Crigler-Najjar syndrome type I in Tunisia may be associated with a founder effect related to the Q357R mutation within theUGT1 gene
250 CTG repeats in DMPK is a threshold for correlation of expansion size and age at onset of juvenile-adult DM1
The identification of eight novel glucocerebrosidase (GBA) mutations in patients with Gaucher disease
Genetic epidemiology of hereditary hemorrhagic telangiectasia in a local community in the northern part of Japan
SNP genotyping with fluorescence polarization detection
A quite different view of Maori origins: Genetic evidence of pre-19th century European settlement in New Zealand European settlement
Identification of a novel NOG gene mutation (P35S) in an Italian family with symphalangism Italian
A BRCA1 mutation in Native North American families
Cystic fibrosis: A worldwide analysis ofCFTR mutations?correlation with incidence data and application to screening
The identification and classification of 41 novel mutations in the factor VIII gene (F8C)
A surface invasive cleavage assay for highly parallel SNP analysis
Integrating mutation data and structural analysis of the TP53 tumor-suppressor protein
Characterization of mutations in fifty North American patients with X-linked myotubular myopathy
Analysis of SNPs and other genomic variations using gel-based chips
New developments in high-throughput resequencing and variation detection using high density microarrays
Seven novel sequence variants in the human low density lipoprotein receptor related protein 5 (LRP5) gene
Recurrent BRCA1 and BRCA2 germline mutations in ovarian cancer: A founder mutation of BRCA1 identified in the Chinese population
BRCA1 and BRCA2 mutations in Russian familial breast cancer
Five novel mutations in the C1 inhibitor gene (C1NH) leading to a premature stop codon in patients with type I hereditary angioedema
Mutation detection in the duplicated region of the polycystic kidney disease 1 (PKD1) gene in PKD1-linked Australian families
Novel missense mutations of TMPRSS3 in two consanguineous Tunisian families with non-syndromic autosomal recessive deafness
Molecular basis of familial hypercholesterolemia in Brazil: Identification of seven novel LDLR gene mutations
An update on conformation sensitive gel electrophoresis
Restriction endonuclease fingerprinting enhanced conformation sensitive gel electrophoresis (REF-CSGE) in the analysis ofBRCA1 exon 11 mutations in a high-risk breast cancer cohort
A common frameshift mutation and other variants in GJB4 (connexin 30.3): Analysis of hearing impairment families
Commercial molecular diagnostics in the U.S.: The Human Genome Project to the clinical laboratory
Low frequency of recurrent BRCA1 and BRCA2 mutations in Spain
Erratum: Spectrum of low density lipoprotein receptor mutations in Czech hypercholesterolemic patients
A modified multiplex PCR assay for detection of large deletions inMSH2 andMLH1
Mutations ofRPGR in X-linked retinitis pigmentosa (RP3)
Miniaturized sealed-tube allele-specific PCR
Determining sequence length or content in zero, one, and two dimensions
A review of the phenotypic variation due to the Denys-Drash syndrome-associated germlineWT1 mutation R362X
Low-density DNA microarrays are versatile tools to screen for known mutations in hypertrophic cardiomyopathy
Evaluation and application of denaturing HPLC for mutation detection in Marfan syndrome: Identification of 20 novel mutations and two novel polymorphisms in the<i>FBN1</i>gene
Molecular study of the hydroxymethlybilane synthase gene (HMBS) among Polish patients with acute intermittent porphyria Polish
Sequence variations in the mu-opioid receptor gene (OPRM1) associated with human addiction to heroin
Identification of 33 polymorphisms in the adipocyte-derived leucine aminopeptidase (ALAP) gene and possible association with hypertension
Identification and in vitro expression of novelCDH23 mutations of patients with Usher syndrome type 1D
Sanfilippo syndrome in Turkey: Identification of novel mutations in subtypes A and B
Glucose-6-phosphate dehydrogenase (G6PD) mutations in Thailand: G6PD Viangchan (871G&gt;A) is the most common deficiency variant in the Thai population
Screening of SLC25A13 mutations in early and late onset patients with citrin deficiency and in the Japanese population: Identification of two novel mutations and establishment of multiple DNA diagnosi Japanese population
Characterization of breakpoint sequences of five rearrangements inL1CAM andABCD1 (ALD) genes
DHPLC screening of cystic fibrosis gene mutations
Rapid genotyping of single nucleotide polymorphisms using novel minor groove binding DNA oligonucleotides (MGB probes)
GJB2 mutations in Iranians with autosomal recessive non-syndromic sensorineural hearing loss
Genetic variation screening and association studies of the adenylate cyclase activating polypeptide 1 (ADCYAP1) gene in patients with type 2 diabetes
G6PDdb, an integrated database of glucose-6-phosphate dehydrogenase (G6PD) mutations
Four novel mutations of the PKD2 gene in czech families with autosomal dominant polycystic kidney disease Czech families
Novel germline<i>CDH1</i>mutations in hereditary diffuse gastric cancer families
New insights into ocular albinism type 1 (OA1): Mutations and polymorphisms of the OA1 gene
Wiskott-Aldrich syndrome in Argentina: 17 unique, including nine novel, mutations
Mutations in theRUNX2 gene in patients with cleidocranial dysplasia
A new strategy for mannose-binding lectin gene haplotyping
Mutation analysis in<i>PKD1</i>of Japanese autosomal dominant polycystic kidney disease patients Japanese
NPC1: Complete genomic sequence, mutation analysis, and characterization of haplotypes
Differential occurrence of mutations causative of eye diseases in the Chinese population
Large-scale genotyping of single nucleotide polymorphisms by Pyrosequencing? and validation against the 5?nuclease (Taqman�) assay
GeneTests-GeneClinics: Genetic testing information for a growing audience
Four novel variants in MC1R in red-haired South African individuals of European descent: S83P, Y152X, A171D, P256S individuals of European descent
Screening E-cadherin in gastric cancer families reveals germline mutations only in hereditary diffuse gastric cancer kindred
A non-radioactive protein truncation test for the sensitive detection of all stop and frameshift mutations
Co-existence of frataxin and cardiac troponin T gene mutations in a child with Friedreich Ataxia and familial hypertrophic cardiomyopathy
The IARC TP53 database: New online mutation analysis and recommendations to users
Mutations and polymorphisms in the human ornithine transcarbamylase gene
<i>APC</i>germline mutations identified in Czech patients with familial adenomatous polyposis Czech
An osteopontin (SPP1) polymorphism is associated with systemic lupus erythematosus
Sources of variability in genetic association studies: Insights from the analysis of hepatic lipase (LIPC)
Molecular analysis of the APC gene in 71 Israeli families: 17 novel mutations
Correlation of MFOLD-predicted DNA secondary structures with separation patterns obtained by capillary electrophoresis single-strand conformation polymorphism (CE-SSCP) analysis