Human Genetics - 2018

102 articles | Last updated: 2025-12-03 14:12:56
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De novo and inherited loss-of-function variants of ATP2B2 are associated with rapidly progressive hearing impairment
The contribution of parent-to-offspring transmission of telomeres to the heritability of telomere length in humans
A novel ISLR2-linked autosomal recessive syndrome of congenital hydrocephalus, arthrogryposis and abdominal distension
Ultra-deep amplicon sequencing indicates absence of low-grade mosaicism with normal cells in patients with type-1 NF1 deletions
Complement component 4 variations may influence psychopathology risk in patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency
Chromosome 18 gene dosage map 2.0
SACS variants are a relevant cause of autosomal recessive hereditary motor and sensory neuropathy
Analyses of LMNA-negative juvenile progeroid cases confirms biallelic POLR3A mutations in Wiedemann–Rautenstrauch-like syndrome and expands the phenotypic spectrum of PYCR1 mutations
RNA sequencing-based transcriptomic profiles of embryonic lens development for cataract gene discovery
Standards and guidelines for canine clinical genetic testing laboratories
Genetic association and differential expression of PITX2 with acute appendicitis
Human eye conditions: insights from the fly eye
The RNA world of human ageing
Ways of improving precise knock-in by genome-editing technologies
“Gardner and Sutherland’s chromosome abnormalities and genetic counseling” by R.J. McKinlay Gardner, David J. Amor. Oxford University Press
Mixed Blessings from a Cambridge Union, Elizabeth N Anionwu
Lowry-Wood syndrome: further evidence of association with RNU4ATAC, and correlation between genotype and phenotype
Delineation of LZTR1 mutation-positive patients with Noonan syndrome and identification of LZTR1 binding to RAF1–PPP1CB complexes
Genetics of anophthalmia and microphthalmia. Part 2: Syndromes associated with anophthalmia–microphthalmia
The impact of GJA8 SNPs on susceptibility to age-related cataract
Personalised medicine and population health: breast and ovarian cancer
Genome-wide association study of primary open-angle glaucoma in continental and admixed African populations
Genome-wide association studies for corneal and refractive astigmatism in UK Biobank demonstrate a shared role for myopia susceptibility loci European ancestry
Implication of non-coding PAX6 mutations in aniridia
Replication of a rare risk haplotype on 1p36.33 for autism spectrum disorder
De novo unbalanced translocations have a complex history/aetiology
Rare loss of function variants in candidate genes and risk of colorectal cancer
The genetic architecture of aniridia and Gillespie syndrome
Knockout of ush2a gene in zebrafish causes hearing impairment and late onset rod-cone dystrophy
Phenotype–genotype correlations and emerging pathways in ocular anterior segment dysgenesis
Correction to: The study of human Y chromosome variation through ancient DNA
Application of CRISPR/Cas9 technologies combined with iPSCs in the study and treatment of retinal degenerative diseases
Genetic landscape of isolated pediatric cataracts: extreme heterogeneity and variable inheritance patterns within genes
Non-coding RNAs in retinal development and function
Genetic variants in components of the NALCN–UNC80–UNC79 ion channel complex cause a broad clinical phenotype (NALCN channelopathies)
Correction to: Australia: regulating genomic data sharing to promote public trust
Novel candidate genes and variants underlying autosomal recessive neurodevelopmental disorders with intellectual disability
Rare coding variant analysis in a large cohort of Ashkenazi Jewish families with inflammatory bowel disease Ashkenazi Jewish
South Korea: in the midst of a privacy reform centered on data sharing
Australia: regulating genomic data sharing to promote public trust
Germany: a fair balance between scientific freedom and data subjects’ rights?
Correction to: Canada: will privacy rules continue to favour open science?
Conclusion: harmonisation in genomic and health data sharing for research: an impossible dream?
Correction to: China: concurring regulation of cross-border genomic data sharing for statist control and individual protection
Introduction: the why and whither of genomic data sharing
Genome-wide investigation of an ID cohort reveals de novo 3′UTR variants affecting gene expression
United Kingdom: transfers of genomic data to third countries
United States: law and policy concerning transfer of genomic data to third countries
International data-sharing norms: from the OECD to the General Data Protection Regulation (GDPR)
Multiplexed assays of variant effects contribute to a growing genotype–phenotype atlas
The hedgehog pathway and ocular developmental anomalies
Whole-exome sequencing identifies rare genetic variations in German families with pulmonary sarcoidosis
Identification of likely pathogenic and known variants in TSPEAR, LAMB3, BCOR, and WNT10A in four Turkish families with tooth agenesis
The coexistence of copy number variations (CNVs) and single nucleotide polymorphisms (SNPs) at a locus can result in distorted calculations of the significance in associating SNPs to disease
A genome scan for genes underlying adult body size differences between Central African hunter-gatherers and farmers
China: concurring regulation of cross-border genomic data sharing for statist control and individual protection
Canada: will privacy rules continue to favour open science?
Phenotypic and genotypic overlap between mosaic NF2 and schwannomatosis in patients with multiple non-intradermal schwannomas
Integrated analysis of human genetic association study and mouse transcriptome suggests LBH and SHF genes as novel susceptible genes for amyloid-β accumulation in Alzheimer’s disease
Admixture mapping and fine-mapping of birth weight loci in the Black Women’s Health Study
Extreme clustering of type-1 NF1 deletion breakpoints co-locating with G-quadruplex forming sequences
MPZL2 is a novel gene associated with autosomal recessive nonsyndromic moderate hearing loss
Expanding the phenotype of the X-linked BCOR microphthalmia syndromes
Genetics of congenital eye malformations: insights from chick experimental embryology
A variant in LMX1A causes autosomal recessive severe-to-profound hearing impairment
IFT88 mutations identified in individuals with non-syndromic recessive retinal degeneration result in abnormal ciliogenesis
De novo variants in GREB1L are associated with non-syndromic inner ear malformations and deafness
A dominant variant in the PDE1C gene is associated with nonsyndromic hearing loss
Genotype imputation for Han Chinese population using Haplotype Reference Consortium as reference Han Chinese population
De novo FBXO11 mutations are associated with intellectual disability and behavioural anomalies
Correction to: Assessing the causal relationship between obesity and venous thromboembolism through a Mendelian Randomization study
Leveraging epigenomics and contactomics data to investigate SNP pairs in GWAS
Heterozygous missense variants of LMX1A lead to nonsyndromic hearing impairment and vestibular dysfunction
Correction to: A zebrafish model of foxe3 deficiency demonstrates lens and eye defects with dysregulation of key genes involved in cataract formation in humans
De novo mutations in MED13, a component of the Mediator complex, are associated with a novel neurodevelopmental disorder
Pronounced maternal parent-of-origin bias for type-1 NF1 microdeletions
Evidence of distinct RELN and TGFB1 genetic associations in familial and non-familial otosclerosis in a British population
High-depth whole genome sequencing of an Ashkenazi Jewish reference panel: enhancing sensitivity, accuracy, and imputation
A zebrafish model of foxe3 deficiency demonstrates lens and eye defects with dysregulation of key genes involved in cataract formation in humans
ELMOD3, a novel causative gene, associated with human autosomal dominant nonsyndromic and progressive hearing loss
Loss of function mutations in VARS encoding cytoplasmic valyl-tRNA synthetase cause microcephaly, seizures, and progressive cerebral atrophy
Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
Genotype imputation performance of three reference panels using African ancestry individuals
Next-generation sequencing reveals genetic landscape in 46, XY disorders of sexual development patients with variable phenotypes
Congenital glaucoma and CYP1B1: an old story revisited
De novo apparent loss-of-function mutations in PRR12 in three patients with intellectual disability and iris abnormalities
New GJA8 variants and phenotypes highlight its critical role in a broad spectrum of eye anomalies
Inferring causal relationships between phenotypes using summary statistics from genome-wide association studies
Correction to: The CAPOS mutation in ATP1A3 alters Na/K-ATPase function and results in auditory neuropathy which has implications for management
Two microcephaly-associated novel missense mutations in CASK specifically disrupt the CASK–neurexin interaction
Robust identification of mosaic variants in congenital heart disease
Genetic and functional analysis of SHROOM1-4 in a Chinese neural tube defect cohort
Pathway-induced allelic spectra of diseases in the presence of strong genetic effects
Deep sequencing of the mitochondrial genome reveals common heteroplasmic sites in NADH dehydrogenase genes
Importance of complete phenotyping in prenatal whole exome sequencing
Genomic structure of the native inhabitants of Peninsular Malaysia and North Borneo suggests complex human population history in Southeast Asia
Identification of rare RTN3 variants in Alzheimer’s disease in Han Chinese
Reconstructing the demographic history of the Himalayan and adjoining populations
Complex signatures of natural selection at GYPA
Genomic trade-offs: are autism and schizophrenia the steep price of the human brain?
De novo variants in SETD1B are associated with intellectual disability, epilepsy and autism
The CAPOS mutation in ATP1A3 alters Na/K-ATPase function and results in auditory neuropathy which has implications for management