Human Genetics - 2005

230 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Large-scale characterization of public database SNPs causing non-synonymous changes in three ethnic groups
Evidence for novel loci for late-onset Parkinson’s disease in a genetic isolate from the Netherlands
Extreme skewing of X chromosome inactivation in mothers of homosexual men
Allelic diversity in the TGFB1 regulatory region: characterization of novel functional single nucleotide polymorphisms
Propensity for paternal inheritance of de novo mutations in Alexander disease
Novel and recurrent rearrangements in the CFTR gene: clinical and laboratory implications for cystic fibrosis screening
Polymorphic micro-inversions contribute to the genomic variability of humans and chimpanzees
Peptidoglycan recognition proteins Pglyrp3 and Pglyrp4 are encoded from the epidermal differentiation complex and are candidate genes for the Psors4 locus on chromosome 1q21
Functional polymorphisms of FGA, encoding α fibrinogen, are associated with susceptibility to venous thromboembolism in a Taiwanese population
First steps in antenatal diagnosis, 1956
Searching for signals of evolutionary selection in 168 genes related to immune function
Detecting genome wide haplotype sharing using SNP or microsatellite haplotype data
Equal proportions of affected cells in muscle and blood of a mosaic carrier of facioscapulohumeral muscular dystrophy
Aberrant splicing in MLH1 and MSH2 due to exonic and intronic variants
Towards compendia of negative genetic association studies: an example for Alzheimer disease
CTLA4 is differently associated with autoimmune diseases in the Dutch population
The euchromatic 9p+ polymorphism is a locus-specific amplification caused by repeated copies of a small DNA segment mapping within 9p12
Molecular evaluation of foetuses with holoprosencephaly shows high incidence of microdeletions in the HPE genes
Evaluating HapMap SNP data transferability in a large-scale genotyping project involving 175 cancer-associated genes
Activation of cryptic splice sites is a frequent splicing defect mechanism caused by mutations in exon and intron sequences of the OPA1 gene
Short/branched-chain acyl-CoA dehydrogenase deficiency due to an IVS3+3A>G mutation that causes exon skipping
Phylogenetic relationship of the populations within and around Japan using 105 short tandem repeat polymorphic loci
SNP array-based homozygosity mapping reveals MCPH1 deletion in family with autosomal recessive mental retardation and mild microcephaly
Variants in Deleted in AZoospermia-Like (DAZL) are correlated with reproductive parameters in men and women
Analysis of families with common variable immunodeficiency (CVID) and IgA deficiency suggests linkage of CVID to chromosome 16q
Two-locus genome-wide linkage scan for prostate cancer susceptibility genes with an interaction effect
Molecular analysis of a constitutional complex genome rearrangement with 11 breakpoints involving chromosomes 3, 11, 12, and 21 and a ∼0.5-Mb submicroscopic deletion in a patient with mild mental reta
Human gene mutations
Generation or birth cohort effect on cancer risk in Li–Fraumeni syndrome
Kieran C. Murphy, Peter J. Scambler (eds): Velo-cardio-facial syndrome: a model for understanding microdeletion disorders (2005)
Human F7 sequence is split into three deep clades that are related to FVII plasma levels
Variants of the SFTPA1 and SFTPA2 genes and susceptibility to tuberculosis in Ethiopia
Novel human pathological mutations
Linkage methods in human genetics before the computer
Population stratification confounds genetic association studies among Latinos Latinos
A clinical and molecular study of 26 females with Xp deletions with special emphasis on inherited deletions
Genome-wide linkage of febrile seizures and epilepsy to the FEB4 locus at 5q14.3-q23.1 and no MASS1 mutation
Admixture-matched case-control study: a practical approach for genetic association studies in admixed populations
Novel human pathological mutations
Localization of a novel locus for alopecia with mental retardation syndrome to chromosome 3q26.33–q27.3
Ring chromosome 15: characterization by array CGH
Contrasting patterns of Y-chromosome variation in South Siberian populations from Baikal and Altai-Sayan regions
A novel autosomal recessive non-syndromic hearing impairment locus (DFNB47) maps to chromosome 2p25.1-p24.3
Variation in genes involved in the RANKL/RANK/OPG bone remodeling pathway are associated with bone mineral density at different skeletal sites in men
Disruptions of the novel KIAA1202 gene are associated with X-linked mental retardation
Truncation of the CNS-expressed JNK3 in a patient with a severe developmental epileptic encephalopathy
Impaired transcriptional upregulation of Parkin promoter variant under oxidative stress and proteasomal inhibition: clinical association
A major locus for hereditary prostate cancer in Finland: localization by linkage disequilibrium of a haplotype in the HPCX region
Mapping autosomal dominant progressive limb-girdle myopathy with bone fragility to chromosome 9p21-p22: a novel locus for a musculoskeletal syndrome
The neurobeachin gene spans the common fragile site FRA13A
Localization of PSORS1 to a haplotype block harboring HLA-C and distinct from corneodesmosin and HCR
Genomic rearrangement at 10q24 in non-syndromic split-hand/split-foot malformation
A new mutation in exon 7 of NEMO gene: late skewed X-chromosome inactivation in an incontinentia pigmenti female patient with immunodeficiency
A novel locus for autosomal-dominant dilated cardiomyopathy maps to chromosome 7q22.3-31.1
The EPAS1 gene influences the aerobic–anaerobic contribution in elite endurance athletes
Comparison of three methods to estimate genetic ancestry and control for stratification in genetic association studies among admixed populations genetic ancestry; admixed populations
Correction of cellular phenotypes of Hutchinson-Gilford Progeria cells by RNA interference
An analysis of genetic variation across the MBL2 locus in Dutch Caucasians indicates that 3′ haplotypes could modify circulating levels of mannose-binding lectin
Systemic lupus erythematosus susceptibility loci defined by genome scan meta-analysis
Molecular characterization of histidinemia: identification of four missense mutations in the histidase gene
Acyl-CoA: cholesterol acyltransferase-2 gene polymorphisms and their association with plasma lipids and coronary artery disease risks
Examination of ancestry and ethnic affiliation using highly informative diallelic DNA markers: application to diverse and admixed populations and implications for clinical epidemiology and forensic me
The cystic fibrosis transmembrane conductance regulator gene and ion channel function in patients with idiopathic pancreatitis
Allelic imbalance analysis of oral tongue squamous cell carcinoma by high-density single nucleotide polymorphism arrays using whole-genome amplified DNA
Genetic prion disease: the EUROCJD experience
A common founder for amyotrophic lateral sclerosis type 8 (ALS8) in the Brazilian population
Geography is a better determinant of human genetic differentiation than ethnicity
Severe autosomal recessive retinitis pigmentosa maps to chromosome 1p13.3–p21.2 between D1S2896 and D1S457 but outside ABCA4
A type II collagen mutation also results in oto-spondylo-megaepiphyseal dysplasia
A new locus (RP31) for autosomal dominant retinitis pigmentosa maps to chromosome 9p
One step closer to fixing association studies: evidence for age- and gender-specific allele frequency variations and deviations from Hardy-Weinberg expectations in controls
Comprehensive genetic evaluation of common E-cadherin sequence variants and prostate cancer risk: strong confirmation of functional promoter SNP
Genetic linkage of systemic lupus erythematosus to 13q32 in African American families with affected male members African American
Extensive Sequencing of the CFTR gene: lessons learned from the first 157 patient samples
Identification of a locus for nongoitrous congenital hypothyroidism on chromosome 15q25.3-26.1
A genetic and cultural odyssey. The life and work of L. Luca Cavalli-Sforza (2005). By Linda Stone, Columbia University Press, 248 pages, 40,50 Euro, ISBN 0-231-13396-0
Interaction between inflammation-related gene polymorphisms and cigarette smoking on the risk of myocardial infarction in the Physician’s Health Study
Genetic variability in a genomic region with long-range linkage disequilibrium reveals traces of a bottleneck in the history of the European population European population
IL-10 promoter single nucleotide polymorphisms are significantly associated with resistance to leprosy
Molecular analysis of a constitutional complex genome rearrangement with 11 breakpoints involving chromosomes 3, 11, 12, and 21 and a ∼0.5-Mb submicroscopic deletion in a patient with mild mental reta
A novel homozygous missense mutation in FGF23 causes Familial Tumoral Calcinosis associated with disseminated visceral calcification
Mortality and cancer incidence in women with extra X chromosomes: a cohort study in Britain
Independent methods for evolutionary genetic dating provide insights into Y-chromosomal STR mutation rates confirming data from direct father–son transmissions
Mitochondrial polymorphisms and susceptibility to type 2 diabetes-related traits in Finns Finns
Michael Schmid, Indrajit Nanda (eds): Chromosomes Today, Vol 14, Kluwer, 2004, ISBN 1-4020-0091-X, hardcover, £76
Major histocompatibility complex and alveolar epithelial apoptosis in idiopathic pulmonary fibrosis
DNA Methylation and Replication: Implications for the “Deletion Hotspot” Region of FMR1
Polymorphisms of complement receptor 1 and interleukin-10 genes and systemic lupus erythematosus: a meta-analysis
Direct duplication 12p11.21–p13.31 mediated by segmental duplications: a new recurrent rearrangement?
The Indian Genome Variation database (IGVdb): a project overview
Familial aggregation in lone atrial fibrillation
Analysis of missense variants in the PKHD1-gene in patients with autosomal recessive polycystic kidney disease (ARPKD)
Meprin β metalloprotease gene polymorphisms associated with diabetic nephropathy in the Pima Indians
The position of premature termination codons in the hepatocyte nuclear factor −1 beta gene determines susceptibility to nonsense-mediated decay
TDT-association analysis of EKN1 and dyslexia in a Colorado twin cohort
Insights into the mutational history and prevalence of SCA1 in the Indian population through anchored polymorphisms
Molecular pathogenesis of Wilson disease: haplotype analysis, detection of prevalent mutations and genotype–phenotype correlation in Indian patients
Alport syndrome caused by inversion of a 21 Mb fragment of the long arm of the X-chromosome comprising exon 9 through 51 of the COL4A5 gene
Dominantly inherited cutaneous small-vessel lymphocytic vasculitis maps to chromosome 6q26–q27
Splicing mutation associated with Rett syndrome and an experimental approach for genetic diagnosis
Meta-analysis of the association of CTLA-4 exon-1 +49A/G polymorphism with rheumatoid arthritis
William Bateson, human genetics and medicine
Haploinsufficiency of novel FOXG1B variants in a patient with severe mental retardation, brain malformations and microcephaly
A gene locus for progressive familial heart block type II (PFHBII) maps to chromosome 1q32.2-q32.3
Targeted disruption of mouse Coch provides functional evidence that DFNA9 hearing loss is not a COCH haploinsufficiency disorder
Haplotypes within genes of β-chemokines in 17q11 are associated with multiple sclerosis: a second phase study
Maternal mosaicism for mutations in the ARX gene in a family with X linked mental retardation
Susceptibility to typhoid fever is associated with a polymorphism in the cystic fibrosis transmembrane conductance regulator (CFTR)
High-resolution array-CGH profiling of germline and tumor-specific copy number alterations on chromosome 22 in patients affected with schwannomas
Maternal lineages and Alzheimer disease risk in the Old Order Amish
Heightened stress response in primary fibroblasts expressing mutant eIF2B genes from CACH/VWM leukodystrophy patients
Reciprocal translocations: a trap for cytogenetists?
Use of autosomal loci for clustering individuals and populations of East Asian origin
Structural and functional analysis of a novel mutation of CYP21B in a heterozygote carrier of 21-hydroxylase deficiency
CTLA4 is differentially associated with autoimmune diseases in the Dutch population
Intercellular adhesion molecule-1 and childhood asthma
A novel TMPRSS3 missense mutation in a DFNB8/10 family prevents proteolytic activation of the protein
Genetic association analyses of PHOX2B and ASCL1 in neuropsychiatric disorders: evidence for association of ASCL1 with Parkinson’s disease
Complex HTR2C linkage disequilibrium and promoter associations with body mass index and serum leptin
DNA sequencing of CREBBP demonstrates mutations in 56% of patients with Rubinstein–Taybi syndrome (RSTS) and in another patient with incomplete RSTS
Ten novel mutations in the molybdenum cofactor genes MOCS1 and MOCS2 and in vitro characterization of a MOCS2 mutation that abolishes the binding ability of molybdopterin synthase
Loss-of-function mutation of the AF9/MLLT3 gene in a girl with neuromotor development delay, cerebellar ataxia, and epilepsy
Human Molecular Genetics, 3rd edition, by Tom Strachan, Andrew Read. Garland Science, ISBN 0-8153-4184-9, paperback
Silvia Garagna (ed) Mouse genetics after the mouse genome. Karger, ISBN 3-805-57783-4, hardcover
Yury Verlinsky and Anver Kuliev (eds) Atlas of preimplantation genetic diagnosis, 2nd edition. Taylor & Francis, ISBN 1-842-14245-3, hardcover
A systematic analysis of LINE-1 endonuclease-dependent retrotranspositional events causing human genetic disease
David N. Cooper (ed) The molecular genetics of lung cancer (2005). Springer, ISBN 3-540-22985-X, hardcover, €106.99
A homozygous COL6A2 intron mutation causes in-frame triple-helical deletion and nonsense-mediated mRNA decay in a patient with Ullrich congenital muscular dystrophy
Significant genetic differentiation between Poland and Germany follows present-day political borders, as revealed by Y-chromosome analysis
Genome scan for quantitative trait loci influencing HDL levels: evidence for multilocus inheritance in familial combined hyperlipidemia
Locus heterogeneity in autosomal recessive congenital cataracts: linkage to 9q and germline HSF4 mutations
Upstream stimulatory factor 1 associated with familial combined hyperlipidemia, LDL cholesterol, and triglycerides
Acknowledgement to Referees 2004
Human Gene Mutations
The Q283P amino-acid change in HFE leads to structural and functional consequences similar to those described for the mutated 282Y HFE protein
SNP microarray analysis for genome-wide detection of crossover regions
Observation of a parental inversion variant in a rare Williams–Beuren syndrome family with two affected children
The genetic legacy of western Bantu migrations
Sex differential in methylation patterns of selected genes in Singapore Chinese Singapore Chinese
Microsatellite variation and evolution of human lactase persistence
FMR1 repeat sizes in the gray zone and high end of the normal range are associated with premature ovarian failure
Fabry disease: correlation between structural changes in α-galactosidase, and clinical and biochemical phenotypes
Unusual segregation products in sperm from a pericentric inversion 17 heterozygote
Monozygous triplets discordant for transient neonatal diabetes mellitus and for imprinting of the TNDM differentially methylated region
Atlas of human chromosome heteromorphisms, by Wyandt HE, Tonk VS (eds), 2004, Kluwer, Dordrecht, ISBN 1-4020-1303-5, £97.00, $154.00, hardcover
Genetic Predisposition to Cancer, 2nd edition, by R.A. Eeles, D.F. Easton, B.A.J. Ponder, C. Eng (editors) Arnold, London, 2004, ISBN 0-340-76254-3, hardcover, £ 95.00
Linkage analysis of a completely ascertained sample of familial schizophrenics and bipolars from Palau, Micronesia
The heretic in Darwin’s Court: the life of Alfred Russel Wallace, by Ross Slotten. 2004. Columbia University Press, ISBN 0231130104, $39.50
Lymphoedema-distichiasis and FOXC2: unreported mutations, de novo mutation estimate, families without coding mutations
Genetic dissection of gene expression observed in whole blood samples of elderly Danish twins
Fetal DNA detection in maternal plasma throughout gestation
Evidence for a novel glaucoma locus at chromosome 3p21-22
Haplotype structure and phylogenetic shadowing of a hypervariable region in the CAPN10 gene
A major locus for hereditary prostate cancer in Finland: localization by linkage disequilibrium of a haplotype in the HPCX region
Association tests of interleukin-6 (IL-6) and type II tumor necrosis factor receptor (TNFR2) genes with bone mineral density in Caucasians using a re-sampling approach
Decreased transcription of the human FCGR2B gene mediated by the -343 G/C promoter polymorphism and association with systemic lupus erythematosus
Functional evaluation of Dent’s disease-causing mutations: implications for ClC-5 channel trafficking and internalization
The ratio of maternal to paternal UPD associated with recessive diseases
Identifying nineteenth century genealogical links from genotypes
Molecular and genealogical characterization of the R1443X BRCA1 mutation in high-risk French-Canadian breast/ovarian cancer families
Anatomy of a founder effect: myotonic dystrophy in Northeastern Quebec
Molecular characterisation of the pericentric inversion that distinguishes human chromosome 5 from the homologous chimpanzee chromosome
Gersen SL, Keagle MB (eds): The principles of clinical cytogenetics, 2nd edn. Humana Press, 2005 (ISBN 1-58829-300-9), hardcover, $145.00
SNPs in the neural cell adhesion molecule 1 gene (NCAM1) may be associated with human neural tube defects
Localisation of merosin-positive congenital muscular dystrophy to chromosome 4p16.3
Eric Lander, David Page, Aravinda Chakravarti (eds): Annual review of genomics and human genetics, volume 5. Annual Reviews, Palo Alto, 2004 (ISBN 0-8243-3705-0), hardcover
A century later Farabee has his mutation
A case of autism and uniparental disomy of chromosome 1
Evolution versus constitution: differences in chromosomal inversion
The development of human genetics in Germany; a personal view
A mutation within the saposin D domain in a Gaucher disease patient with normal glucocerebrosidase activity
The importance of modelling heterogeneity in complex disease: application to NIMH Schizophrenia Genetics Initiative data
ATM haplotypes and associated mutations in Iranian patients with ataxia–telangiectasia: recurring homozygosity without a founder haplotype
Genetic analysis of adiponectin and obesity in Hispanic families: the IRAS Family Study
A newly identified RET proto-oncogene polymorphism is found in a high number of endocrine tumor patients
Identification of deletions and duplications of the DMD gene in affected males and carrier females by multiple ligation probe amplification (MLPA)
Gly118Asp is a SCA14 founder mutation in the Dutch ataxia population
A locus for familial generalized lentiginosis without systemic involvement maps to chromosome 4q21.1–q22.3
Mutational analysis of the mitochondrial 12S rRNA gene in Chinese pediatric subjects with aminoglycoside-induced and non-syndromic hearing loss Chinese
Human Gene Mutations
Variation in ITGB3 has sex-specific associations with plasma lipoprotein(a) and whole blood serotonin levels in a population-based sample
Dorian J. Pritchard, Bruce R. Korf (Eds): Medical Genetics at a Glance. Blackwell (2003) ISBN 0632063736, paperback, 120 pages, 48 illustrations, £15.95
De novo t(7;10)(q33;q23) translocation and closely juxtaposed microdeletion in a patient with macrocephaly and developmental delay
Association between the neuron-specific RNA-binding protein ELAVL4 and Parkinson disease
Biochemical characterisation of the proteins encoded by the DiGeorge critical region 6 (DGCR6) genes
AHSG gene variant is associated with leanness among Swedish men
Functional promoter polymorphism in the TBX21 gene associated with aspirin-induced asthma
Genetic evidence in support of a shared Eurasian-North African dairying origin Eurasian, North African
Ancestral origins of the prion protein gene D178N mutation in the Basque Country
A homozygous nonsense mutation in SOX9 in the dominant disorder campomelic dysplasia: a case of mitotic gene conversion
Evidence for genetic anticipation in hereditary non-polyposis colorectal cancer
Expression of mutant JAGGED1 alleles in patients with Alagille syndrome
Different population histories of the Mundari- and Mon-Khmer-speaking Austro-Asiatic tribes inferred from the mtDNA 9-bp deletion/insertion polymorphism in Indian populations
On the evolutionary mutation rate at Y-chromosome STRs: comments on paper by Di Giacomo et al. (2004)
Extensively high load of internal tumors determined by whole body MRI scanning in a patient with neurofibromatosis type 1 and a non-LCR-mediated 2-Mb deletion in 17q11.2
Microarray analysis of the Df1 mouse model of the 22q11 deletion syndrome
A neutral variant involved in a complex CFTR allele contributes to a severe cystic fibrosis phenotype
Matrix Gla protein and osteopontin genetic associations with coronary artery calcification and bone density: the CARDIA study
FISH analysis of hematological neoplasias with 1p36 rearrangements allows the definition of a cluster of 2.5�Mb included in the minimal region deleted in 1p36 deletion syndrome
Rapid genotyping for most common TGFBI mutations with real-time polymerase chain reaction
Human genetics: historical and personal perspectives
Julia Bell and the Treasury of Human Inheritance
A large interstitial deletion encompassing the amelogenin gene on the short arm of the Y chromosome
Array CGH detection of a cryptic deletion in a complex chromosome rearrangement
Homeodomain revisited: a lesson from disease-causing mutations
Genes and human elite athletic performance
BRCA1 variants in a family study of African-American and Latina women African-American and Latina
TLR2 Arg677Trp polymorphism in leprosy: revisited
The 8818G allele of the agouti signaling protein (ASIP) gene is ancestral and is associated with darker skin color in African Americans
Single-nucleotide polymorphisms of the KCNS3 gene are significantly associated with airway hyperresponsiveness
Molecular analysis of congenital scoliosis: a candidate gene approach
Genotype, enzyme activity, glutathione level, and clinical phenotype in patients with glutathione synthetase deficiency
The keeshond defect in cardiac conotruncal development is oligogenic1
DFNB48, a new nonsyndromic recessive deafness locus, maps to chromosome 15q23-q25.1
Association of susceptibility to the development of lung adenocarcinoma with the heme oxygenase-1 gene promoter polymorphism
CTLA-4 polymorphisms and systemic lupus erythematosus (SLE): a meta-analysis
A common insertion/deletion polymorphism of the thymidylate synthase (TYMS) gene is a determinant of red blood cell folate and homocysteine concentrations
Non-recombining chromosome Y haplogroups and centromeric HindIII RFLP in relation to blood pressure in 2,743 middle-aged Caucasian men from the UK
Molecular characterization of histidinemia: identification of four missense mutations in the histidase gene
Molecular distinction between true centric fission and pericentric duplication-fission
Human Gene Mutations
Characterization of Usher syndrome type I gene mutations in an Usher syndrome patient population
Signature of recent historical events in the European Y-chromosomal STR haplotype distribution European
Genetic confirmation of facioscapulohumeral muscular dystrophy in a case with complex D4Z4 rearrangments
Association of Ala72Ser polymorphism with COMT enzyme activity and the risk of schizophrenia in Koreans
Oculopharyngeal muscular dystrophy (OPMD): analysis of the PABPN1 gene expansion sequence in 86 patients reveals 13 different expansion types and further evidence for unequal recombination as the muta
A genomewide scan of male sexual orientation
Aubrey Milunsky (Ed): Genetic disorders and the fetus. Diagnosis, prevention and treatment (fifth edition). The Johns Hopkins University Press (2004), ISBN 0-8018-7928-0, hardcover, �160.50
Bisulphite sequencing of the transient neonatal diabetes mellitus DMR facilitates a novel diagnostic test but reveals no methylation anomalies in patients of unknown aetiology
Methylenetetrahydrofolate reductase (MTHFR) and susceptibility for (pre)neoplastic cervical disease