Human Genetics - 2003

194 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Chloride channel 7 (CLCN7) gene mutations in intermediate autosomal recessive osteopetrosis
"Alfred Russel Wallace. A Life" (Peter Raby, Pimlico (Random House), ISBN 0-7126-6577-3, softcover, £12.50) / "In Darwin's shadow. The Life and Science of Alfred Russel Wallace" (Michael Shermer, Oxfo
Acknowledgement to referees 2002
Several interacting genes influence the malignant hyperthermia phenotype
C.W.R.J. Cremers, R.J.H. Smith (eds): Genetic hearing impairment—it's clinical presentations. Advances in Oto-Rhino-Laryngology, Vol 61 (Series ed: W. Arnold)
Mutation analysis of the coding sequence of the MECP2 gene in infantile autism
European Academy of Andrology (EAA) International Symposium
Cis-acting variation in the expression of a high proportion of genes in human brain
Maternal serum cell-free fetal DNA levels are increased in cases of trisomy 13 but not trisomy 18
Methylenetetrahydrofolate reductase gene C677T polymorphism, homocysteine, vitamin B12, and DNA damage in coronary artery disease
Average age-specific cumulative risk of breast cancer according to type and site of germline mutations in BRCA1 and BRCA2 estimated from multiple-case breast cancer families attending Australian famil
Examination of sequence homology between human chromosome 20 and the mouse genome: intense conservation of many genomic elements
Recent Literature
Complex haplotypes of IRS2 gene are associated with severe obesity and reveal heterogeneity in the effect of Gly1057Asp mutation
Bone dysplasias: an atlas of genetic disorders of skeletal development, 2nd edition
Characterisation of mutations in 77 patients with X-linked myotubular myopathy, including a family with a very mild phenotype
Human genetic disease caused by de novo mitochondrial-nuclear DNA transfer
Molecular screening of the TGIF gene in holoprosencephaly: identification of two novel mutations
Helen M. Kingston: ABC of Clinical Genetics (3rd edn)
Relation of risk of systemic lupus erythematosus to west African admixture in a Caribbean population west African admixture
Observation of an excess of fragile-X premutations in a population of males referred with spinocerebellar ataxia
Mutations in the calcium-binding motifs of CDH23 and the 35delG mutation in GJB2 cause hearing loss in one family
Founder effect of the C9 R95X mutation in Orientals Orientals
Genotyping microsatellite DNA markers at putative disease loci in inbred/multiplex families with respiratory chain complex I deficiency allows rapid identification of a novel nonsense mutation (IVS1nt
Chromosome 18 replaced by two ring chromosomes of chromosome 18 origin
Gene rearrangements in the glucocerebrosidase-metaxin region giving rise to disease-causing mutations and polymorphisms. Analysis of 25 RecNciI alleles in Gaucher disease patients
The future of association studies of common cancers
Genetic linkage of Francois-Neetens fleck (mouchetée) corneal dystrophy to chromosome 2q35
High level of male-biased Scandinavian admixture in Greenlandic Inuit shown by Y-chromosomal analysis Scandinavian admixture; Greenlandic Inuit
No evidence of fetal DNA persistence in maternal plasma after pregnancy
Autosomal dominant malignant and catecholamine-producing paraganglioma caused by a splice donor site mutation in SDHC
Molecular study of a new family with hereditary renal cell carcinoma and a translocation t(3;8)(p13;q24.1)
Genetic heterogeneity of FG syndrome: a fourth locus (FGS4) maps to Xp11.4-p11.3 in an Italian family
Linkage of autosomal dominant common variable immunodeficiency to chromosome 5p and evidence for locus heterogeneity
Duplication of the MID1 first exon in a patient with Opitz G/BBB syndrome
Biallelic expression of HRAS and MUCDHL in human and mouse
Linkage and association mapping of the LRP5 locus on chromosome 11q13 in type 1 diabetes
Interphase FISH, the structure of reciprocal translocation chromosomes and physical mapping studies rule out the duplication of the NF1 gene at 17q11.2. A reply
Analysis of 15 primary open-angle glaucoma families from Australia identifies a founder effect for the Q368STOP mutation of myocilin
Finnish Disease Heritage I:
A study of cryptic terminal chromosome rearrangements in recurrent miscarriage couples detects unsuspected acrocentric pericentromeric abnormalities
GJB2 deafness gene shows a specific spectrum of mutations in Japan, including a frequent founder mutation
Compound heterozygosity at the sphingomyelin phosphodiesterase-1 (SMPD1) gene is associated with low HDL cholesterol
Genome-wide targeted search for human specific and polymorphic L1 integrations
The interleukin-6 (−174) G/C promoter polymorphism is associated with type-2 diabetes mellitus in Native Americans and Caucasians Native Americans
G. Evers-Kiebooms, M.W. Zoeteweij, P.S. Harper (eds): Prenatal testing for late onset neurogenetic diseases
Methods in molecular biology, vol 204. Molecular cytogenetics: protocols and applications
The Finnish disease heritage III: the individual diseases
ABCA1 gene polymorphisms and their associations with coronary artery disease and plasma lipids in males from three ethnic populations in Singapore
Disruption of exon definition produces a dominant-negative growth hormone isoform that causes somatotroph death and IGHD II
David J. Galas, Stephen J. McCormack (eds): Genomic Technologies — Present and Future. Functional Genomics Series, Vol 1 (Series ed: Milton H. Saier Jr)
Maternal aging and chromosomal abnormalities: new data drawn from in vitro unfertilized human oocytes
Frederick Burkhardt, Duncan M. Porter, Sheila Ann Dean, Jonathan R. Topham, Sarah Wilmot (eds): The Correspondence of Charles Darwin 1864 (Vol. 12)
Structural and molecular basis of skeletal muscle diseases
The novel imprinted carboxypeptidase A4 gene (CPA4) in the 7q32 imprinting domain
Skin pigmentation, biogeographical ancestry and admixture mapping
Genetic demography of Antioquia (Colombia) and the Central Valley of Costa Rica
The signature motif in human glucose-6-phosphate transporter is essential for microsomal transport of glucose-6-phosphate
PA26 is a candidate gene for heterotaxia in humans: identification of a novel PA26-related gene family in human and mouse
Genomic structure of the human mitochondrial chaperonin genes: HSP60 and HSP10 are localised head to head on chromosome 2 separated by a bidirectional promoter
Modulating action of the new polymorphism L436F detected in the GLB1 gene of a type-II GM1 gangliosidosis patient
Polymorphisms in the MLL breakpoint cluster region (BCR)
Variation in the FABP2 promoter alters transcriptional activity and is associated with body composition and plasma lipid levels
Mitochondrial DNA polymorphisms in nine aboriginal groups of Taiwan: implications for the population history of aboriginal Taiwanese
SONIC HEDGEHOG mutations causing human holoprosencephaly impair neural patterning activity
Mucopolysaccharidosis IVA: characterization of a common mutation found in Finnish patients with attenuated phenotype
Arrangement of chromosome 11 and 22 territories, EWSR1 and FLI1 genes, and other genetic elements of these chromosomes in human lymphocytes and Ewing sarcoma cells
Fine structure mapping of CIAS1: identification of an ancestral haplotype and a common FCAS mutation, L353P
Finnish Disease Heritage II: population prehistory and genetic roots of Finns
An Alu-mediated rearrangement as cause of exon skipping in Hunter disease
Genomic basis of cystathioninuria (MIM 219500) revealed by multiple mutations in cystathionine gamma-lyase (CTH)
Linkage analysis of prostate cancer susceptibility: confirmation of linkage at 8p22–23
A novel dysmorphic syndrome with open calvarial sutures and sutural cataracts maps to chromosome 14q13-q21
Hermansky-Pudlak syndrome type 4 (HPS-4): clinical and molecular characteristics
Evidence for asthma susceptibility genes on chromosome 11 in an African-American population
Two alternative exons can result from activation of the cryptic splice acceptor site deep within intron 2 of the dystrophin gene in a patient with as yet asymptomatic dystrophinopathy
Assessment of the CTNNA3 gene encoding human αT-catenin regarding its involvement in dilated cardiomyopathy
A genome-wide scan for primary open-angle glaucoma (POAG): the Barbados Family Study of Open-Angle Glaucoma
Randomly distributed crossovers may generate block-like patterns of linkage disequilibrium: an act of genetic drift
Translocation breakpoint in two unrelated Tourette syndrome cases, within a region previously linked to the disorder
A deletion in the human QP-C gene causes a complex III deficiency resulting in hypoglycaemia and lactic acidosis
Common 5′ β-globin RFLP haplotypes harbour a surprising level of ancestral sequence mosaicism
Mutational analysis in longest known survivor of mucopolysaccharidosis type VII
Neurofibromatosis type 1 gene as a mutational target in a mismatch repair-deficient cell type
Nucleotide and haplotypic diversity of the NOS2A promoter region and its relationship to cerebral malaria
Fragile X syndrome: diagnosis, treatment and research
Novel Artemis gene mutations of radiosensitive severe combined immunodeficiency in Japanese families Japanese
Notch4, a non-HLA gene in the MHC is strongly associated with the most severe form of alopecia areata
Null mutations in the N-acetylglutamate synthase gene associated with acute neonatal disease and hyperammonemia
Genetic analysis of a complex trait in the Utah Genetic Reference Project: a major locus for PTC taste ability on chromosome 7q and a secondary locus on chromosome 16p
Thank you Robert Nussbaum, Welcome Thomas Hudson!
Fetal DNA in maternal serum: does it persist after pregnancy?
Connexin 26 35delG does not represent a mutational hotspot
Hyaluronan is not elevated in urine or serum in Hutchinson-Gilford Progeria Syndrome
Two mismatch repair gene mutations found in a colon cancer patient – which one is pathogenic?
Comparison of strategies for selecting single nucleotide polymorphisms for case/control association studies
Novel types of mutation in the choroideremia (CHM) gene: a full-length L1 insertion and an intronic mutation activating a cryptic exon
Mutational analysis of the human FATE gene in 144 infertile men
Increased variation in mtDNA in patients with familial sensorineural hearing impairment
Genome-wide homozygosity mapping localizes a gene for autosomal recessive non-progressive infantile ataxia to 20q11-q13
Lung cancer risk in germline p53 mutation carriers: association between an inherited cancer predisposition, cigarette smoking, and cancer risk
Telomere instability in a human tumor cell line expressing a dominant-negative WRN protein
Altitude is a phenotypic modifier in hereditary paraganglioma type�1: evidence for an oxygen-sensing defect
The association between Japanese primary open-angle glaucoma and normal tension glaucoma patients and the optineurin gene Japanese
Interaction effect of PTEN and CDKN1B chromosomal regions on prostate cancer linkage
Molecular variation at the apolipoprotein�B gene locus in relation to lipids and cardiovascular disease: a systematic meta-analysis
Association of the mitochondrial DNA 15497G/A polymorphism with obesity in a middle-aged and elderly Japanese population
Identification of transcripts from a subtraction library which might be responsible for the mild phenotype in an intrafamilially variable course of Duchenne muscular dystrophy
Inherited BRCA2 mutations in African Americans with breast and/or ovarian cancer: a study of familial and early onset cases
A common IL-13 Arg130Gln single nucleotide polymorphism among Chinese atopy patients with allergic rhinitis
Mitochondrial DNA sequence polymorphisms of five ethnic populations from northern China
Sex differences in heritability of sensitization to Blomia tropicalis in asthma using regression of offspring on midparent (ROMP) methods
H. Skirton, C. Patch: Genetics for Healthcare Professionals: A lifestyle approach
The cnm locus, a canine homologue of human autosomal forms of centronuclear myopathy, maps to chromosome�2
Mutations
Y-chromosome lineages in Cabo Verde Islands witness the diverse geographic origin of its first male settlers
Analysis of zinc transporter, hZnT4 ( Slc30A4 ), gene expression in a mammary gland disorder leading to reduced zinc secretion into milk
Sequence variation in the CHAT locus shows no association with late-onset Alzheimer's disease
Impact of public health strategies on the birth prevalence of cystic fibrosis in Brittany, France
P.J. Morrison, S.V. Hodgson, N.E. Haites (eds): Familial breast cancer: genetics, screening and management
Nicholas T. Potter (editor) Methods in molecular biology, volume�217. Neurogenetics: methods and protocols
Mutations in COCH that result in non-syndromic autosomal dominant deafness (DFNA9) affect matrix deposition of cochlin
Mutations
Chromosomal phylogeny and evolution of gibbons (Hylobatidae)
Cytometric analysis of cell phenotype and function
Mutations
Surfactant protein�A and B genetic variants predispose to idiopathic pulmonary fibrosis
Y-chromosome lineages in Cabo Verde Islands witness the diverse geographic origin of its first male settlers
Markers informative for ancestry demonstrate consistent megabase-length linkage disequilibrium in the African American population
Increased prevalence of CFTR mutations and variants and decreased chloride secretion in primary sclerosing cholangitis
Allelic variation at alcohol metabolism genes ( ADH1B , ADH1C , ALDH2 ) and alcohol dependence in an American Indian population
A novel method for automatic genotyping of microsatellite markers based on parametric pattern recognition
Making genes, making waves. A social activist in science
Evaluation of the microsomal glutathione S-transferase 3 ( MGST3 ) locus on 1q23 as a Type 2 diabetes susceptibility gene in Pima Indians Pima Indians
Skeletal defects in paternal uniparental disomy for chromosome 14 are re-capitulated in the mouse model (paternal uniparental disomy 12)
Exon skipping caused by an intronic insertion of a young Alu Yb9 element leads to severe hemophilia�A
Novel mutations in the IRF6 gene for Van der Woude syndrome
De novo insertion of an Alu sequence in the coding region of the CLCN5 gene results in Dent's disease
Marion Leboyer, Frank Bellivier (eds): Psychiatric genetics: methods and reviews
Mutations
Tyrosinase gene mutations in oculocutaneous albinism�1 (OCA1): definition of the phenotype
Functional analysis of intra-allelic variation at NACP-Rep1 in the ?-synuclein gene
Genetic association analysis of KCNQ3 and juvenile myoclonic epilepsy in a South Indian population
NF1 exon�7 skipping and sequence alterations in exonic splice enhancers (ESEs) in a neurofibromatosis�1 patient
Hypervariability of the membrane-associated mucin and cancer marker MUC1
DNA sequence variation of the human ABO-secretor locus ( FUT2 ) in New Guinean populations: possible early human migration from Africa
Stratification by CARD15 variant genotype in a genome-wide search for inflammatory bowel disease susceptibility loci
Mutations
The origins and genetic structure of three co-resident Chinese Muslim populations: the Salar, Bo'an and Dongxiang
W.I. Cohen, L. Nadel, M.E. Madnick (eds): Down Syndrome: Visions for the 21st Century
Distribution of CGG repeat sizes within the fragile X mental retardation 1 ( FMR1 ) homologue in a non-human primate population
Relationship between serum HDL-C levels and common genetic variants of the endothelial lipase gene in Japanese school-aged children
Evaluation of bidirectional transfer of plasma DNA through placenta
Association of a promoter variant in the inducible cyclooxygenase-2 gene (PTGS2) with type�2 diabetes mellitus in Pima Indians Pima Indians
Evidence of linkage of HDL level variation to APOC3 in two samples with different ascertainment
On the applicability of a haplotype map to un-assayed populations
Genetic and clinical mosaicism in a patient with neurofibromatosis type 1
Modulation of penetrance by the wild-type allele in dominantly inherited erythropoietic protoporphyria and acute hepatic porphyrias
Localized aggressive periodontitis is linked to human chromosome 1q25
Members of the CDY family have different expression patterns: CDY1 transcripts have the best correlation with complete spermatogenesis
Increased risk for developmental delay in Saethre-Chotzen syndrome is associated with TWIST deletions: an improved strategy for TWIST mutation screening
Evidence for substantial effect modification by gender in a large-scale genetic association study of the metabolic syndrome among coronary heart disease patients
In vivo somatic microsatellite mutations identified in non-malignant human tissue
Susanne Hummel (editor) Ancient DNA typing: methods, strategies and applications
Peter McGuffin, Michael J. Owen, Irving I. Gottesman (editors) Psychiatric genetics and genomics
Small supernumerary marker chromosomes (SMCs): genotype-phenotype correlation and classification
Entropy-based SNP selection for genetic association studies
Mitochondrial portraits of the Madeira and A�ores archipelagos witness different genetic pools of its settlers
Striking differentiation of sub-populations within a genetically homogeneous isolate (Ogliastra) in Sardinia as revealed by mtDNA analysis
Evidence of a founder effect for the 235delC mutation of GJB2 (connexin�26) in east Asians
Y-chromosomal DNA haplogroups and their implications for the dual origins of the Koreans
Evidence for a modifying pathway in SMA discordant families: reduced SMN level decreases the amount of its interacting partners and Htra2-beta1
Mutational analysis of BRAF and K-ras in gastric cancers: absence of BRAF mutations in gastric cancers
No evidence for DUP25 in patients with panic disorder using a quantitative real-time PCR approach
Stephan Beck, Alexander Olek (eds): The Epigenome: Molecular Hide and Seek
Molecular analysis of congenital central hypoventilation syndrome
Refinement of the "Silver syndrome locus" on chromosome 11q12-q14 in four families and exclusion of eight candidate genes
Genomic structure of the human mitochondrial chaperonin genes: HSP60 and HSP10 are localised head to head on chromosome 2 separated by a bidirectional promoter
Genes in the vicinity of CFTR modulate the cystic fibrosis phenotype in highly concordant or discordant F508del homozygous sib pairs
Common variations in noncoding regions of the human natriuretic peptide receptor A gene have quantitative effects
A novel locus for autosomal dominant nonsyndromic hearing loss (DFNA44) maps to chromosome 3q28-29
Three different pathological lesions in the NF1 gene originating de novo in a family with neurofibromatosis type 1
Ian N.M. Day (ed) Molecular genetic epidemiology: a laboratory perspective
Molecular cloning and characterization of the GATA1 cofactor human FOG1 and assessment of its binding to GATA1 proteins carrying D218 substitutions
Sequence analysis of the granulysin and granzyme B genes in familial hemophagocytic lymphohistiocytosis
Surfactant protein B polymorphism and respiratory distress syndrome in premature twins
Mal de Meleda (MDM) caused by mutations in the gene for SLURP-1 in patients from Germany, Turkey, Palestine, and the United Arab Emirates
Mitochondrial DNA polymorphisms associated with longevity in a Finnish population
Skewed X-chromosome inactivation causes intra-familial phenotypic variation of an EBP mutation in a family with X-linked dominant chondrodysplasia punctata
Novel types of COMP mutations and genotype-phenotype association in pseudoachondroplasia and multiple epiphyseal dysplasia
Novel immunoglobulin superfamily gene cluster, mapping to a region of human chromosome 17q25, linked to psoriasis susceptibility
Functional polymorphisms in the mineralocorticoid receptor and amirolide-sensitive sodium channel genes in a patient with sporadic pseudohypoaldosteronism
Unexpectedly high prevalence of the mild form of propionic acidemia in Japan: presence of a common mutation and possible clinical implications
Three duplicons form a novel chimeric transcription unit in the pericentromeric region of chromosome 22q11