Human Genetics - 1994

327 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Proceed with much more caution
Single base pair germ-line deletion in the p53 gene in a cancer predisposed family
Supernumerary chromosomes and spermatogenesis in a human male carrier
Identification of deletions in thebtk gene allows unambiguous assessment of carrier status in families with X-linked agammaglobulinaemia
Clinical Case Report
BamHI restriction fragment length polymorphism (RFLP) at the human GST3 gene locus
Dinucleotide repeat polymorphism at 11q23
Toward the complete genomic map and molecular pathology of human chromosome 4
Parental origin of germ-line and somatic mutations in the retinoblastoma gene
Unexpected inactivation of acceptor consensus splice sequence by a −3 C to T transition in intron 2 of the CFTR gene
A novel mosaic Bantu/Benin/Bantu βs haplotype found in several African populations African populations; Bantu; Benin
A human cDNA coding for the Leydig insulin-like peptide (Ley I-L)
A deletion in the 5 ′-region of the neurofibromatosis type 1 (NF1) gene
Announcements
The polymorphism of the plasma inter-α-trypsin inhibitor (ITI) and its relationship to the heavy chain H1 subunit gene (ITIH1) at 3p211-212
Submicroscopic deletions of 17p13.3 in type 1 Lissencephaly
Proceed with caution — but proceed!
Characterization of mutations on the rare duplicated C4/CYP21 haplotype in steroid 21-hydroxylase deficiency
Molecular characterization and clinical use of a polymorphic tandem repeat in an intron of the human alanine: Glyoxylate aminotransferase gene
Chromosomal mapping of human adenylyl cyclase genes type III, type V and type VI
Down's syndrome, Edwards' syndrome, Patau's syndrome —synthesis of glycosaminoglycans
A study on duplications of the dystrophin gene: Evidence of a geographical difference in the distribution of breakpoints by intron
Acceptability of carrier screening for cystic fibrosis during pregnancy in a German population
Genetic polymorphisms of the CST2 locus coding for cystatin SA
Multicolor fluorescence in situ hybridization on metaphase chromosomes and interphase Halo-preparations using cosmid and YAC clones for the simultaneous high resolution mapping of deletions in the dys
The utilization of interphase cytogenetic analysis for the detection of mosaicism
Isolation and mapping of cosmid markers on human chromosome 22, including one within the submicroscopically deleted region of DiGeorge syndrome
The spatial localization of homologous chromosomes in human fibroblasts at mitosis
Mutation screening by a combination of biotin-SSCP and direct sequencing
Refining the genetic map for the region flanking the X-linked hypophosphataemic rickets locus (Xp22.1?22.2)
Prevalence of beta allele of the insulin gene in type II diabetes mellitus
Coamplification on chromosomes 7p12-13 and 9q12-13 identified by reverse chromosome painting in a glioblastoma multiforme
Homozygosity for a mutation in the lipoprotein lipase gene (Gly139?Ser) causes chylomicronaemia in a boy of Spanish descent boy of Spanish descent
Nuclear-encoded subunits of human cytochrome c oxidase: SstI restriction fragment length polymorphism
An additional HpaII polymorphism in exon 2 of the human platelet membrane glycoprotein IIIa gene
Three CA/GT repeat polymorphisms from loci D21S414 and D21S1234 on human chromosome 21
A large family with features of pseudoachondroplasia and multiple epiphyseal dysplasia: exclusion of seven candidate gene loci that encode proteins of the cartilage extracellular matrix
Molecular analysis of esterase D polymorphism
Four novel mutant alleles of the arylsulfatase B gene in two patients with intermediate form of mucopolysaccharidosis VI (Maroteaux-Lamy syndrome)
Contiguous deletion and duplication mutations resulting in type 1 hereditary angioneurotic edema
Isolation of two isoforms of the PAX3 gene transcripts and their tissue-specific alternative expression in human adult tissues
Mutation in a splice-donor site of the APC gene in a family with polyposis and late age of colonic cancer death
Chromosomal damage in sperm of patients surviving Hodgkin's disease following MOPP (nitrogen mustard, vincristine, procarbazine, and prednisone) therapy with and without radiotherapy
A 13 base pair deletion in exon 1 of HPRTIllinois forms a functional GUG initiation codon
Linkage mapping of the spinal muscular atrophy gene
A multiple interval physical map of the pericentromeric region of human chromosome 10
Human familial and sporadic breast cancer: analysis of the coding regions of the 17?-hydroxysteroid dehydrogenase 2 gene (EDH17B2) using a single-strand conformation polymorphism assay
Frequent polymorphism in exon 15 of the adenomatous polyposis coli gene
Machado Joseph disease is not an allele of the spinocerebellar ataxia 2 locus
Chronic childhood spinal muscular atrophy in Germany (West-Th�ringen) ? an epidemiological study
A new highly polymorphic DNA restriction site marker in the 5? region of the human tyrosine hydroxylase gene (TH) detecting loss of heterozygosity in human embryonal rhabdomyosarcoma
Two CA/GT repeat polymorphisms in intron 27 of the human neurofibromatosis type 1 (NF1) gene
Insertion/deletion polymorphism within a polyadenylate stretch at the human atrial natriuretic peptides (hANP) gene locus
?Cryptic? dinucleotide polymorphism in the 3? region of the factor IX gene shows substantial variation among different populations
Duplication of 1F and 1A2 genes in the vitamin D-binding protein (GC) system
Microlesions and polymorphisms in the Duchenne/Becker muscular dystrophy gene
Molecular basis for subtypic differences of the ?a? subunit of coagulation factor XIII with description of the genesis of the subtypes
Mutation analysis of a Sandhoff disease patient in the Maronite community in Cyprus
Linkage analysis of X-linked cleft palate and ankyloglossia in Manitoba Mennonite and British Columbia Native kindreds
Molecular cytogenetic analysis of a duplication Xp in a male: further delineation of a possible sex influencing region on the X chromosome
Exclusion of ferritins and iron-responsive element (IRE)-binding proteins as candidates for the hemochromatosis gene
Chromosomal localization of the human histamine H1-receptor gene
Variability in allelic DNA methylation in spermatozoa
An MspI polymorphism in the X-specific region proximal to the pseudoautosomal boundary. A new example of a unique ?African? marker?
Geographical distribution of haplotypes in Swedish families with Huntington's disease
Identification of three novel mutations in the CFTR gene using temperature-optimized non-radioactive conditions for SSCP analysis
Linkage disequilibrium relationships among four polymorphisms within the human fibrinogen gene cluster
Balanced autosomal translocations and ovarian dysgenesis
Familial resemblance for immunoglobulin levels
Polymorphisms of the apolipoprotein and angiotensin converting enzyme genes in young North Karelian patients with coronary heart disease
Deletion polymorphism in the gene for angiotensin converting enzyme is associated with elevated fasting blood glucose levels
Angiotensin I-converting enzyme (ACE): estimation of DNA haplotypes in unrelated individuals using denaturing gradient gel blots
Exonic polymorphisms in the protein C gene: interethnic comparison between Caucasians and Asians Asians
Genetic fine localization of the arrestin (S-antigen) gene 4 cM distal from D2S172
Parathyroid Water Clear Cell Hyperplasia, an O-allele associated condition
A characteristic sequence of trisomies starting with trisomy 7 in benign thyroid tumors
Sublocalization of a locus at 3p21.3?23 predisposing to hereditary nonpolyposis colon cancer
Genetic analysis of the catalytic domain of the GAP gene in human lung cancer cell lines
Presence of an expressed ?-tubulin gene (TUBB) in the HLA class I region may provide the genetic basis for HLA-linked microtubule dysfunction
Highly polymorphic repeat marker within the ?-amyloid precursor protein gene
Ordering markers in the region of the ataxia-telangiectasia gene (11q22-q23) by fluorescence in situ hybridization (FISH) to interphase nuclei
Quantification of point mutations associated with Leber hereditary optic neuroretinopathy by solid-phase minisequencing
A human gene that restores the DNA-repair defect in SCID mice is located on 8p11.1?q11.1
Achievement of meiosis in XXY germ cells: study of 543 sperm karyotypes from an XY/XXY mosaic patient
Expression of (cac)n/(gtg)n simple repetitive sequences in mRNA of human lymphocytes
Detection of eleven mutations causing acute intermittent porphyria using denaturing gradient gel electrophoresis
Molecular genetic investigations of the mechanism of tumourigenesis in von Hippel-Lindau disease: analysis of allele loss in VHL tumours
Two new mutations in the porphobilinogen deaminase gene and a screening method using PCR amplification of specific alleles
Isolation and characterization of the human genomic locus coding for the putative metastasis control gene nm23-H1
Population screening of lactate dehydrogenase deficiencies in Fukuoka Prefecture in Japan and molecular characterization of three independent mutations in the lactate dehydrogenase-B(H) gene
The T→C mutation at position +96 of the untranslated region 3′ to the terminating codon of the β-globin gene is a rare polymorphism that does not cause a β-thalassemia as previously ascribed
Localisation of the human blue cone pigment gene to chromosome band 7q31.3-32
Detection of a MspI restriction fragment length polymorphism for the human sex hormone-binding globulin (SHBG) gene
Corrections to the human mitochondrial ribosomal RNA sequences
Genetic mapping of two loci, DXS454 and DXS458, with respect to the X-linked agammaglobulinemia gene locus
Editorial help
Announcements
Incidence of chromosome 3, 7, 10, 11, 17 and X disomy in mature human sperm nuclei as determined by nonradioactive in situ hybridization
Human high-affinity Fc?RI (CD64) gene mapped to chromosome 1q21.2-q21.3 by fluorescence in situ hybridization
Exon 9 of the CFTR gene: splice site haplotypes and cystic fibrosis mutations
Nonsense mutations at Arg-1947 in two cases of familial neurofibromatosis type 1 in Japanese
Detection by the polymerase chain reaction of two polymorphisms in exon 14 of the human inter-?-trypsin inhibitor heavy chain H1 gene
The motilin gene: subregional localisation, tissue expression, DNA polymorphisms and exclusion as a candidate gene for the HLA-associated immotile cilia syndrome
A long range restriction map spanning the myxoid liposarcoma breakpoint in the q13-14 region of human chromosome 12
CFTR mutations in Chilean cystic fibrosis patients
Germ line origins of de novo mutations in hemophilia B families
Skipping of multiple CFTR exons is not a result of single exon omissions
A polymorphic poly-A sequence in the 5? region of the aldosynthase (CYP11B2) gene may be useful in genetic diagnosis of 11?-hydroxylase genes defects
Intracellular processing and maturation of mutant gene products in hereditary ?-galactosidase deficiency (?-galactosidosis)
Maternal cell contamination in amniotic fluid samples as a consequence of the sampling technique
Analysis of sperm chromosome complements from a man heterozygous for a pericentric inversion of chromosome 1
G6PD Ferrara I has the same two mutations as G6PD A(-) but a distinct biochemical phenotype
Diagnosis of fragile X syndrome by direct mutation analysis
Detection of carriers of deletions in the dystrophin gene in Bulgarian DMD-BMD families
Polymorphism of pentanucleotide repeats in the 5? flanking region of glutathione S-transferase (GST) ? gene
No amyloid precursor protein 708 mutation in 50 Swedish Alzheimer's disease patients Swedish
Multiple endocrine neoplasia type 1 (MEN1) in two Asian families Asian
Apparent regression of the CGG repeat in FMR1 to an allele of normal size
A novel single-base mutation in the glucose 6-phosphate dehydrogenase gene is associated with chronic non-spherocytic haemolytic anaemia
A pentanucleotide tandem duplication polymorphism in the 3? untranslated region of the HLA-linked heat-shock protein 70-2 (HSP70-2) gene
Complete detection of mutations in cystic fibrosis patients of Native American origin Native American
Oestrogen receptor (ESR) polymorphisms and breast cancer susceptibility
The immunoglobulin heavy chain and disease association: application to pemphigus vulgaris
Characterization of the three genotypes of low Km aldehyde dehydrogenase in a Japanese population Japanese population
Genetically polymorphic ?-l-fucosidase (FUCA1) isozymes detected in blood plasma
Loss of heterozygosity studies in tumors from families with breast-ovarian cancer syndrome
Tyrosinemia type 1 ? complex splicing defects and a missense mutation in the fumarylacetoacetase gene
Leber's hereditary optic neuropathy: no significant evidence for primary or secondary pathogenicity of the 15257 mutation
Sandhoff disease in Argentina: high frequency of a splice site mutation in the HEXB gene and correlation between enzyme and DNA-based tests for heterozygote detection
Aneuploidy and ageing: sex chromosome exclusion into micronuclei
Chromosomal localization of the human histone H2A.X gene to 11q23.2-q23.3 by fluorescence in situ hybridization
A novel case of compound heterozygosity with ?Normandy?/type I von Willebrand disease (vWD). Direct demonstration of the segregation of one allele with a defective expression at the mRNA level causing
Expression of four mutant human ornithine transcarbamylase genes in cultured Cos 1 cells relates to clinical phenotypes
Glycophorin variants and Plasmodium falciparum: protective effect of the Dantu phenotype in vitro
Hypoxanthine-guanine phosphoribosyltransferase (HPRT) deficiency: Identification of point mutations in Japanese patients with Lesch-Nyhan syndrome and hereditary gout and their permanent expression in
Sickle cell anemia, sickle cell ?-thalassemia, and thalassemia major in Albania: characterization of mutations
A steroid 21-hydroxylase allele concomitantly carrying four disease-causing mutations is not uncommon in the Swedish population
Two new Gaucher disease mutations
Definitive assignment of the growth hormone-releasing factor gene to 20q11.2
D3S1229 and D3S1246 correspond to the same dinucleotide repeat polymorphism
Fluorescence in situ hybridization reveals a break in the ?-satellite DNA of chromosome 1 in a family with a balanced whole-arm translocation
Genotype-phenotype correlation between position of constitutional APC gene mutation and CHRPE expression in familial adenomatous polyposis
Mapping of the human C3G gene coding a guanine nucleotide releasing protein for Ras family to 9q34.3 by fluorescence in situ hybridization
Trinucleotide (CAG) repeat expansion in chromosomes of Spanish patients with Huntington's disease
Gene frequencies of alcohol dehydrogenase2 (ADH2) and aldehyde dehydrogenase2 (ALDH2) in five Chinese minorities
Preliminary mutation analysis in the phenylanaline hydroxylase gene in Greek PKU and HPA patients
A novel polymorphism in the coding sequence of the human RET proto-oncogene
Determinants of the factor IX mutational spectrum in haemophilia B: an analysis of missense mutations using a multi-domain molecular model of the activated protein
Expression and chromosomal mapping of the gene encoding the human histone H1.1
Genetic heterogeneity of severe von Willebrand disease type III in the German population
A WAGR region gene between PAX-6 and FSHB expressed in fetal brain
New sites of methylcytosine-rich DNA detected on metaphase chromosomes
Male meiotic segregation of gonosomes analysed by two colour FISH in human interphase spermatozoa
The human RAD51/RecA homologue gene is not a candidate gene for Bloom's syndrome
Exclusion of linkage with chromosome 21 in families with recurrence of non-Down's atrioventricular canal
ICF syndrome: a new case and review of the literature
Identification of trisomy in Macaca fascicularis by fluorescence in situ hybridization with a human chromosome 13 DNA library
Population Genetic Characteristics of the D1S80 locus in seven human populations
No evidence for linkage between familial hypertriglyceridemia and apolipoprotein B, apolipoprotein C-III or lipoprotein lipase genes
Identification of a novel rhodopsin mutation (Met-44-Thr) in a simplex case of retinitis pigmentosa
Factor IX gene mutations causing haemophilia B: comparison of SSC screening versus systematic DNA sequencing and diagnostic applications
DNA sequence polymorphisms in exonic and intronic regions of the human phenylalanine hydroxylase gene aid in the identification of alleles
Y418C: a novel mutation in exon 9 of the glucocerebrosidase gene of a patient with Gaucher disease creates a new Bgl I site
Announcements
Linkage analysis of autosomal dominant atrio ventricular canal defects: exclusion of chromosome 21
WT1 mutations in patients with Denys-Drash syndrome: a novel mutation in exon 8 and paternal allele origin
Assignment of human satellite 1 DNA as revealed by fluorescent in situ hybridization with oligonucleotides
Evidence for genetic heterogeneity underlying hereditary neuropathy with liability to pressure palsies
394delTT: a Nordic cystic fibrosis mutation
Cystic fibrosis in a low-incidence population: two major mutations in Finland
Viability thresholds for partial trisomies and monosomies. A study of 1,159 viable unbalanced reciprocal translocations
Autosomal dominant cyclic hematopoiesis: exclusion of linkage to the major hematopoietic regulatory gene cluster on chromosome 5
Mapping of the human gene encoding the mutual signal-transducing subunit (?-chain) of granulocyte-macrophage colony-stimulating factor (GM-CSF), interleukin-3 (IL-3), and interleukin-5 (IL-5) receptor
Assignment of the human indoleamine 2,3-dioxygenase gene to chromosome 8 using the polymerase chain reaction
Precise localization on chromosome 12 of the ATF-1 gene by fluorescence in situ hybridization
Human aldehyde dehydrogenase: chromosomal assignment of the gene for the isozyme that metabolizes ?-aminobutyraldehyde
Confirmation of the localization of the human recombination activating gene 1 (RAG1) to chromosome 11p13
HaeIII polymorphism in intron 1 of the human p53 gene
Polymorphism in the human ?2 adrenergic receptor gene detected by Restriction Endonuclease digestion with Fnu4HI
Hypomelanosis of Ito in a girl with plexus papilloma and transloction (X;17)
Molecular biology of hypophosphataemic rickets and oncogenic osteomalacia
Large DNA inversions, deletions, and TaqI site mutations in severe haemophilia A
The fragile X syndrome in Finland: demonstration of a founder effect by analysis of microsatellite haplotypes
Putative non-Mendelian transmission of retinoblastoma in males: a phenotypic segregation analysis of 150 pedigrees
Frequency and parental origin of hypermethylated RB1 alleles in retinoblastoma
Three unrelated individuals with perinatally lethal osteogenesis imperfecta resulting from identical Gly502Ser substitutions in the α2-chain of type I collagen
Three novel missense mutations in the antithrombin III (AT3) gene causing recurrent venous thrombosis
At least five polymorphic mutants account for the prevalence of glucose-6-phosphate dehydrogenase deficiency in Algeria
Fluorescence in situ hybridization on paraffin-embedded abortion material as a means of retrospective chromosome analysis
Mammalian adenylyl cyclase family members are randomly located on different chromosomes
Filipino ?-thalassemia due to a large deletion: identification of the deletion end points and polymerase chain reaction (PCR)-based diagnosis Filipino
Detection of more than 50 different CFTR mutations in a large group of German cystic fibrosis patients
Genetic heterogeneity in hypokalemic periodic paralysis (hypoPP)
Localization of the human coproporphyrinogen oxidase gene to chromosome band 3q12
Genetic and physical mapping of the GLUR5 glutamate receptor gene on human chromosome 21
The gene causing familial mediterranean fever maps to the short arm of chromosome 16 in Druze and Moslem Arab families
A new complex polymorphic repeat close to the HLA-A and HLA-E loci
A unique mutation underlying carbonic anhydrase II deficiency syndrome in patients of Arab descent Arab descent
An insertion/deletion polymorphism at the D15S63 locus in the critical Prader-Willi syndrome region in 15q11-13
Two missense mutations causing tyrosinemia type 1 with presence and absence of immunoreactive fumarylacetoacetase
Multiplex PCR screening detects small p53 deletions and insertions in human ovarian cancer cell lines
A novel complex mutation in the LDL receptor gene probably caused by the simultaneous occurrence of deletion and insertion in the same region
Unbiased transmission of mutant alleles at the human retinoblastoma locus
Tight linkage of pyruvate kinase (PKLR) and glucocerebrosidase (GBA) genes
Linkage analysis of the genetic determinants of high density lipoprotein concentrations and composition: evidence for involvement of the apolipoprotein A-II and cholesteryl ester transfer protein loci
Keratin 9 gene mutational heterogeneity in patients with epidermolytic palmoplantar keratoderma
Identification of the mutations in the T-protein gene causing typical and atypical nonketotic hyperglycinemia
Identification of three novel mutations (457 TAT?G, D192G, Q685X) in the Slovenian CF patients Slovenian
Delineation of marker chromosomes by reverse chromosome painting using only a small number of DOP-PCR amplified microdissected chromosomes
PME of Unverricht-Lundborg type in the Mediterranean region: linkage and linkage disequilibrium confirm the assignment to the EPM1 locus
Affected sib-pair analysis of the GLUT1 glucose transporter gene locus in non-insulin-dependent diabetes mellitus (NIDDM): evidence for no linkage
A base substitution at IVS-19 3?-end splice junction causes exon 20 skipping in pro?2(I) collagen mRNA and produces mild osteogenesis imperfecta
Genetic mapping of 14 short tandem repeat polymorphisms on human chromosome 22
A unique origin for Sicilian (??)?-thalassemia in 33 unrelated families and its rapid diagnostic characterization by PCR analysis Sicilian
Polymorphisms in the 3′ untranslated region of the IκB/MAD-3 (NFKBI) gene located on chromosome 14
Autosomal recessive polycystic kidney disease does not map to the second gene locus for autosomal dominant polycystic kidney disease on chromosome 4
Anticipation in hereditary dentatorubral-pallidoluysian atrophy
Assignment of the human 8.5 H gene to chromosome 5, region 5q35
Molecular and genetic characterisation of German families with paramyotonia congenita and demonstration of founder effect in the Ravensberg families
Molecular defects in erythropoietic protoporphyria with terminal liver failure
Assignment of the gene encoding the human gonadotropin-releasing hormone receptor to 4q13.2?13.3 by fluorescence in situ hybridization
Assignment of the gene encoding the human thyrotropin-releasing hormone receptor to 8q23 by fluorescence in situ hybridization
(G)n-Mononucleotide polymorphism in the human D4 dopamine receptor (DRD4) gene
TaqI dimorphic site in a human pancreatic phospholipase A2 (PLA2) gene localized on chromosome 12
Investigation of the polymorphic AvaII site by a PCR-based assay at the human CD18 gene locus
A NlaIII polymorphism within the human factor VII gene
BglII identifies a frequent biallelic DNA polymorphism of the human RT6 gene
No maternal age relationship for polyploidy
Genetics of the human electroencephalogram (EEG) and event-related brain potentials (ERPs): a review
Molecular analysis of aniridia patients for deletions involving the Wilms' tumor gene
Identification, characterisation and clinical applications of cosmids from the telomeric and centromeric regions of the long arm of chromosome 22
A polymorphic alpha satellite sequence specific for human chromosome 13 detected by oligonucleotide primed in situ labelling (PRINS)
Distinct RB1 gene mutations with low penetrance in hereditary retinoblastoma
Chromosome 14 maternal uniparental disomy in the euploid cell line of a fetus with mosaic 46,XX/47,XX,+14 karyotype
Biochemical and molecular studies of 132 patients with galactosemia
No evidence for linkage of long QT syndrome and chromosome 11p15.5 markers in a Chinese family: evidence for genetic heterogeneity Chinese family
Chromosome 4q35 haplotypes and DNA rearrangements segregating in affected subjects of 19 Italian families with facioscapulohumeral musculatur dystrophy (FSHD)
Polymorphisms of the prion protein gene in Italian patients with Creutzfeldt-Jakob disease
Genetic linkage analyses of Romano-Ward syndrome (RWS) in 13 Japanese families
?-Thalassemia mutations in Singapore ? a strategy for prenatal diagnosis
A fluorescent in situ hybridization analysis of X chromosome pairing in early human female meiosis
Molecular analysis of the (CGG)n expansion in the FMR-1 gene in 59 Spanish fragile X syndrome families
DNA haplotype-dependent differences in the amino acid sequence of debrisoquine 4-hydroxylase (CYP2D6): evidence for two major allozymes in extensive metabolisers
Interleukin 1 receptor antagonist gene polymorphism association with lichen sclerosus
Nondisjunction of human acrocentric chromosomes: studies of 432 trisomic fetuses and liveborns
Linkage mapping of the tumor necrosis factor receptor 2 (TNFR2) gene to 1p36.2 using the single-strand conformation polymorphism technique
Parental origin of the extra chromosomes in polysomy X
Fine mapping of human PI 3-kinase associated p85? transcripts in the YAC contig surrounding the spinal muscular atrophy gene
Genetic analysis of Cuban autosomal dominant polycystic kidney disease kindreds using RFLPs and microsatellite polymorphisms linked to the PKD1 locus
Refined localization of TSC1 by combined analysis of 9q34 and 16pl3 data in 14 tuberous sclerosis families
Two novel point mutations in the cytochrome b 558 heavy chain gene, detected in two Japanese patients with X-linked chronic granulomatous disease Japanese
Refined mapping of the human Ets-related gene Elk-1 to Xp11.2–p11.4, distal to the OATL1 region
Etiological aspects of congenital diaphragmatic hernia: results of a case comparison study
Characterisation of a 5-bp deletion in exon 4 of the factor VIII gene: concordance with slipped-mispairing at DNA replication
Characterization of several DNA polymorphic markers in the LIF gene region
Polymorphism in the human E-selectin gene detected by PCR-SSCP
A PvuII polymorphism near exon 2 of the dystrophin gene
Announcements
Heterogeneity in the severity of cystic fibrosis and the role of CFTR gene mutations
Neuropsychological and biochemical investigations in heterozygotes for phenylketonuria during ingestion of high dose aspartame (a sweetener containing phenylalanine)
Amplification of (GACA)n simple repeats in an exceptional 14p+ marker chromosome
Chromosomal localization of human satellites 2 and 3 by a FISH method using oligonucleotides as probes
SRVX, a sex reversing locus in Xp21.2?p22.11
Differential ultrastructural aberrations of collagen fibrils in Ehlers-Danlos syndrome types I?IV as a means of diagnostics and classification
Pure hereditary spastic paraparesis: an exclusion map covering more than 40% of the autosomal genome
Single exon mutation in arylsulfatase A gene has two effects: loss of enzyme activity and aberrant splicing
Incidence of chromosome 18 disomy in human sperm nuclei as detected by nonisotopic in situ hybridization
Prenatal diagnosis of congenital adrenal hyperplasia due to 21-hydroxylase deficiency by allele-specific hybridization and Southern blot
Retrospective study of the cystic fibrosis transmembrane conductance regulator (CFTR) gene mutations in Guthrie cards from a large cohort of neonatal screening for cystic fibrosis
Direct screening of a mitochondrial DNA deletion valuable for Amerindian evolutionary research
Identification of allele-specific p22-phox mutations in a compound heterozygous patient with chronic granulomatous disease by mismatch PCR and restriction enzyme analysis
Unusual genotypes in the COL6A1 gene in parents of children with trisomy 21 and major congenital heart defects
Analysis of the CFTR gene confirms the high genetic heterogeneity of the Spanish population: 43 mutations account for only 78% of CF chromosomes Spanish population
Exclusion mapping of the gene for X-linked neural tube defects in an Icelandic family
A Sau3A polymorphism in the 5? end of the IT15 gene that nonrandomly segregates with the Huntington disease trinucleotide expansion
Mutational analysis of the amyloid precursor protein gene in Japanese familial Alzheimer's disease kindreds
A patient with an interstitial deletion in Xp22.3 locates the gene for X-linked recessive chondrodysplasia punctata to within a one megabase interval
Analysis of the whole CFTR coding regions and splice junctions in azoospermic men with congenital bilateral aplasia of epididymis or vas deferens
Familial unbalanced translocation t(8;15)(p23.3;q11) with uniparental disomy in Angelman syndrome
PstI identifies biallelic DNA polymorphism of the human casein kinase 2? gene (CSNK2A1)
Two new polymorphisms in the human elastin gene (ELN)
Polymorphism of the gene encoding the alpha subunit of the stimulatory G-protein of adenylyl cyclase (GNAS1)
A polymorphic STS in intron 44 of the dystrophin gene
An RsaI polymorphism in the transcribed region of the neurofibromatosis (NF1)-gene
Transferrin types and expression of hereditary hemochromatosis
Verification of the transthyretin met 111 mutation in familial amyloid cardiomyopathy of Danish origin by DNA sequening Danish origin
Announcements
On the molecular nature of the Duarte variant of galactose-1-phosphate uridyl transferase (GALT)
Novel RFLPs and microsatellite repeats increase informativity at four loci mapping to Xq22-q25
Physical mapping in the region of the Bruton's tyrosine kinase and ?-galactosidase A gene loci in proximal Xq22
Rapid screening of myelin genes in CMT1 patients by SSCP analysis: identification of new mutations and polymorphisms in the P0 gene
Genetic heterogeneitiy of Crigler-Najjar syndrome type I: A study of 14 cases
Exclusion of the cartilage link protein and the cartilage matrix protein genes as the mutant loci in several heritable chondrodysplasias
Mammalian meiotic recombination: a reexamination
Presence of chromosomal mosaicism in abnormal preimplantation embryos detected by fluorescence in situ hybridisation
The detection of mitochondrial DNA mutations using single stranded conformation polymorphism (SSCP) analysis and heteroduplex analysis
Location of the gene causing hyperimmunoglobulinemia D and periodic fever syndrome differs from that for familial mediterranean fever
The CL100 gene, which encodes a dual specificity (Tyr/Thr) MAP kinase phosphatase, is highly conserved and maps to human chromosome 5q34
Selected di- and tetranucleotide microsatellites from chromosomes 7, 12, 14, and Y in various Eurasian populations
A Japanese patient with the Costello syndrome Japanese
A Gln-281 to Arg substitution in ?-l-fucosidase is responsible for a common polymorphism detected by isoelectric focusing
Identification of three RFLPs at the HCK locus on chromosome 20
For novel gene mutations in five Japanese male patients with neonatal or late onset OTC deficiency: application of PCR-single-strand conformation polymorphisms for all exons and adjacent introns Japanese
Absence of FMR-1 gene expression can be detected with RNA extracted from dried blood specimens
Numerical chromosome abnormalities in spermatozoa of fertile and infertile men detected by fluorescence in situ hybridization
Evidence against DNA polymerase ? as a candidate gene for Werner syndrome
Novel cystic fibrosis mutation associated with mild disease in Cypriot patients Cypriot
Ancestry of SINE-R.C2 a human-specific retroposon
Frameshift mutations in exons 9 and 10 of the porphobilinogen deaminase gene produce a crossreacting immunological material (CRIM)-negative form of acute intermittent porphyria
A splicing mutation in the cytochrome b5 gene from a patient with congenital methemoglobinemia and pseudohermaphrodism
TGGE and HIEF: a comparison of two methods in the detection of carriers of the Z mutation of the alpha-1-antitrypsin gene
Fanconi anemia cells have a normal gene structure for topoisomerase I
Hypomagensemia with secondary hypocalcemia in a female with balanced X;9 translocation: mapping of the Xp22 chromosome breakpoint
Chromosomal localization of genes required for the terminal steps of oxidative metabolism: ? and ? subunits of ATP synthase and the phosphate carrier
Identification of a polymorphism in intron 2 of the p53 gene
A transcribed polymorphism and sub-localisation of MDM2
Immumoglobulin allotypes in Ecuadorian Cayapa Indians
Molecular analysis of the T17 immunoglobulin CH multigene deletion (del A1-GP-G2-G4-E)
A new missense mutation (Cys297?Phe) of the low density lipoprotein receptor in Italian patients with familial hypercholesterolemia (FHTrieste)
A region-specific microdissection library for human chromosome 2p23?p25 and the analysis of an interstitial deletion of 2p23.3?p25.1
Skewed inactivation of an X chromosome deleted at the dystrophin gene in an asymptomatic mother and her affected daughter
The human vigilin gene: identification, chromosomal localization and expression pattern
A chimaeric animal model for confined placental mosaicism
Mapping of two new markers within the smallest interval harboring the spinal muscular atrophy locus by family and radiation hybrid analysis
Acute intermittent porphyria caused by a single base insertion of C in exon 15 of the porphobilinogen deaminase gene that results in a frame shift and premature stopping of translation
Germline and somatic mosaicism in a female carrier of Duchenne muscular dystrophy
Spectrin ?IIa variant in dominant and non-dominant spherocytosis