Human Genetics - 1993

321 articles | Last updated: 2025-12-03 14:12:56
Caucasian
2
White
1
European
2
Other
10
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
The pseudoautosomal regions of the human sex chromosomes
A study of the association between schizophrenia and the dopamine D3 receptor gene
Chromosomal breakage, endomitosis, endoreduplication, and hypersensitivity toward radiomimetric and alkylating agents: A possible new autosomal recessive mutation in a girl with craniosynostosis and m
Retrospective study of the parental origin of the extra chromosome in trisomy 18 (Edwards syndrome)
X-inactivation pattern in carriers of X-linked retinitis pigmentosa: A valuable means of prognostic evaluation?
Identification of an uncommon haptoglobin type using DNA and protein analysis
Molecular analysis of a ring chromosome X in a family with fragile X syndrome
The spectrum of mitochondrial DNA mutations in families with Leber hereditary optic neuroretinopathy
Molecular characterization of ?-thalassemia in Hungary
D8S7 is consistently deleted in inverted duplications of the short arm of chromosome 8 (inv dup 8p)
Small frameshift deletions within the COL4A5 gene in juvenile-onset Alport syndrome
A highly informative CA/GT repeat polymorphism in intron 38 of the human neurofibromatosis type 1 (NF1) gene
Deletion of arginine (608) in acid sphingomyelinase is the prevalent mutation among Niemann-Pick disease type B patients from northern Africa
Two novel frameshift mutations associated with the presence of direct repeats of the LDL receptor gene in familial hypercholesterolemia
Heterogeneity of DNA and RNA in Hunter patients
DNA haplotype dependency of debrisoquine 4-hydroxylase (CYP2D6) expression among extensive metabolisers
?Premature anaphase? in a couple with recurrent miscarriages
The molecular defect in propionic acidemia: Exon skipping caused by an 8-bp deletion from an intron in the PCCB allele
Assignment of human ?-galactosidase-A gene to 3p21.33 by fluorescence in situ hybridization
A high-resolution cytogenetic map of human chromosome 12: Localization of 195 new cosmid markers by direct R-banding fluorescence in situ hybridization
A de novo nonsense mutation in exon 28 of the neurofibromatosis type l (NF1) gene
Human complement C81 (C8 A) polymorphism: detection and segregation of new variants
Simultaneous detection of the two most frequent metachromatic leukodystrophy mutations
Chorionic DNA analysis for the prenatal diagnosis of familial hypercholesterolaemia
Homozygosity for inversion (2)(p12q14)
An unreported RFLP for probe 218 EP6 that is useful in linkage analysis of adult polycystic kidney disease
Detection of confined placental mosaicism in trisomy 18 conceptions using interphase cytogenetic analysis
High degree of genetic polymorphism in apolipoprotein(a) associated with plasma lipoprotein(a) levels in Japanese and Chinese populations
Frequent occurrence of familial aggregations of high lipoprotein(a) levels associated with small apolipoprotein(a) isoforms
Localization of the gene for human heart fatty acid binding protein to chromosome 1p32-1p33
RFLP haplotyping and mutation analysis of the phenylalanine hydroxylase gene in Dutch phenylketonuria families
Von Hippel-Lindau disease: identification of deletion mutations by pulsed-field gel electrophoresis
EcoRI restriction fragment length polymorphism in human glycogen synthase gene
A common exonic polymorphism in the human D5 dopamine receptor gene
Topographic pattern of the rearrangement of the dystrophin gene in Japanese Duchenne muscular dystrophy
Analysis of 6 VNTR loci by ?multiplex? PCR and automated fluorescent detection
South African founder mutations in the low-density lipoprotein receptor gene causing familial hypercholesterolemia in the Dutch population
Detection of a high mutation frequency in exon 12 of the porphobilinogen deaminase gene in patients with acute intermittent porphyria
A new polymorphism in the gene for GAP43
Acute intermittent porphyria caused by a G to C mutation in exon 12 of the porphobilinogen deaminase gene that results in exon skipping
Allele frequencies and linkage disequilibrium of polymorphic DNA markers of the Huntington disease region in the German population
Logistic regression model to estimate the risk of unbalanced offspring in reciprocal translocations
Generation of a chromosome-22-specific c-DNA library as confirmed by FISH analysis
Chromosomal assignment of the human smg GDP dissociation stimulator gene to human chromosome 4q21-q25
Human fibronectin gene (FN1) RFLPs: Mapping and linkage disequilibrium analysis
Oocyte selection model for the maternal age-dependence in Down syndrome
A strategy for the characterization of minute chromosome rearrangements using multiple color fluorescence in situ hybridization with chromosome-specific DNA libraries and YAC clones
Familial true hermaphroditism: paternal and maternal transmission of true hermaphroditism (46,XX) and XX maleness in the absence of Y-chromosomal sequences
Somatic pairing of centromeres and short arms of chromosome 15 in the hematopoietic and lymphoid system
Chromosomal localization of 9 KOX zinc finger genes: physical linkages suggest clustering of KOX genes on chromosomes 12, 16, and 19
The human cytochrome b5 gene and two of its pseudogenes are located on chromosomes 18q23, 14q31-32.1 and 20p11.2, respectively
Rapid detection of single nucleotide deletions: application to the ? 6 (-A) mutation of the ?-globin gene and to cystic fibrosis
An EcoRI RFLP in the 5′ region of the human NF1 gene
Announcements
Sequence variability of the tetranucleotide repeat of the human beta-actin related pseudogene H-beta-Ac-psi-2 (ACTBP2) locus
The origin of cytologically unidentifiable chromosome abnormalities: six cases ascertained by targeted chromosome-band painting
Rearrangements between irradiated chromosomes in three-species radiation hybrid cell lines revealed by two-color in situ hybridization
Meiotic recombination in an Irish family with beta-thalassaemia
Altered CYP21 genes in HLA-haplotypes associated with congenital adrenal hyperplasia (CAH): a family study
Absence of linkage to the ataxia telangiectasia locus in familial breast cancer
Physical mapping shows close linkage between the ?-galactosidase A gene (GLA) and the DXS178 locus
Identification of a novel T-insertion polymorphism at the DMD locus
The immunoglobulin ? locus: polymorphism and haplotypes of Caucasoid and non-Caucasoid individuals Caucasoid and non-Caucasoid individuals
Announcements
Molecular and cytogenetic analyses of autism in Taiwan
Molecular analysis of factor VII deficiency in Italy: a frequent mutation (FVII Lazio) in a repeated intronic region
An adult-type metachromatic leukodystrophy caused by substitution of serine for glycine-122 in arylsulfatase A
Supernumerary marker chromosomes in peripheral blood cells of hepatitis B virus chronic carriers
Frequency of glucose-6-phosphate dehydrogenase (G6PD) mutations in Chinese, Filipinos, and Laotians from Hawaii
Spondyloepiphyseal dysplasia and precocious osteoarthritis in a family with an Arg75?Cys mutation in the procollagen type II gene (COL2A1)
Acceptor splice site mutation in the invariant AG of intron 5 of the protein C gene, causing type I protein C deficiency
A rare reciprocal translocation (12;21) segregating for nine generations
A myeloblastin/proteinase-3 cDNA clone identifies a BglII and a PvuII restriction fragment length polymorphism
Screening for point mutations in exon 10 of the low density lipoprotein receptor gene by analysis of single-strand conformation polymorphisms: detection of a nonsense mutation ? FH469?Stop
Physical mapping of chromosome 3p25-p26 by flourescence in situ hybridisation (FISH)
Recurrent mutations in the factor IX gene: founder effect or repeat de novo events
For novel gene mutations in five Japanese male patients with neonatal or late onset OTC deficiency: application of PCR-single-strand conformation polymorphisms for all exons and adjacent introns
No relationship between genetic instability in Bloom's syndrome and DNA hypomethylation of some major repetitive sequences
G2 phase cell cycle disturbance as a manifestation of genetic cell damage
The human complement component C8B gene: structure and phylogenetic relationship
Four new nucleotide sequence polymorphisms in the LDL receptor gene detected by SSCP analysis
Alpha-thalassemia in the four major aboriginal groups in Taiwan
Genetic variation in transforming growth factor alpha: possible association of BamHI polymorphism with bilateral sporadic cleft lip and palate
Insertional inactivation of the WT1 gene in tumour cells from a patient with WAGR syndrome
Gene for hereditary neuropathy with liability to pressure palsies (HNPP) maps to chromosome 17 at or close to the locus for HMSN type 1
PCR-based detection of one BamHI polymorphic site in the human T cell receptor delta gene TCRDV2
High frequency of mutations at position 11778 in mitochondrial ND4 gene in Japanese families with Leber's hereditary optic neuropathy Japanese families
Prothymosin ? gene in humans: organization of its promoter region and localization to chromosome 2
Molecular genetics of GM2-gangliosidosis AB variant: a novel mutation and expression in BHK cells
Human malformations similar to those in the mouse mutation disorganization (Ds)
Parental origin of triploidy in human fetuses: evidence for genomic imprinting
Diverse polymorphism within a short coding region of the human aldehyde dehydrogenase-5 (ALDH5) gene
Paternal duplication of chromosome 5q11.2–5q14 in a male born with craniostenosis, ear tags, kidney dysplasia and several other anomalies
Hereditary triosephosphate isomerase (TPI) deficiency: two severely affected brothers one with and one without neurological symptoms
Molecular analysis of mutations in the gene FMR-1 segregating in fragile X families
Gaucher disease (Norrbottnian type III): probable founders identified by genealogical and molecular studies
Assignment of the human aggrecan gene AGC1 to 15q25?q26.2 by in situ hybridization
A novel Cys-214-Ser mutation in the peripherin/RDS gene in a Japanese family with autosomal dominant retinitis pigmentosa
Centromeric association of a microchromosome in a Turner syndrome patient with a pseudodicentric Y
Announcements
Presence of telomeric and subtelomeric sequences at the fusion points of ring chromosomes indicates that the ring syndrome is caused by ring instability
Aneuploidy detection in human sperm nuclei using fluorescence in situ hybridization
Evaluation of routine prenatal ultrasound examination in detecting fetal chromosomal abnormalities in a low risk population
Polymorphisms in the apolipoprotein B-100 gene contributes to normal variation in plasma lipids in 464 Danish men born in 1948
X-linked myoclonus epilepsy explained as a maternally inherited mitochondrial disorder
Linkage of Van der Woude syndrome (VWS) to REN and exclusion of the candidate gene TGFB2 from the disease locus in a large pedigree
Hereditary recombined three-allele variant of the Gc system
Prevalence of common mutations in the arylsulphatase A gene in metachromatic leukodystrophy patients diagnosed in Britain
Sequence variant of the human cathepsin G gene
Polymorphic tandem repeat region in interleukin-1α intron 6
D21S210: A highly polymorphic (GT)n marker closely linked to the ?-amyloid protein precursor (APP) gene
A denaturing gradient gel electrophoresis assay for sensitive detection of p53 mutations
Localization of a gamma-glutamyl-transferase-related gene family on chromosome 22
High-resolution cytogenetic characterization of telomeric associations in ring chromosome 19
Two new mutations detected by single-strand conformation polymorphism analysis in cystic fibrosis from Russia
Cystic fibrosis in Spain: high frequency of mutation G542X in the Mediterranean coastal area
Two cystic fibrosis patients with the genotype G542X/G551D
DXS539, a polymorphic DNA marker proximal of the fragile-X gene
Exclusion of the biglycan (BGN) gene as a candidate gene for the Happle syndrome, employing an intragenic single-strand conformational polymorphism
Age-related nonrandom chromosomal abnormalities in human low-grade astrocytomas
Polyploidies in abortion material decrease with maternal age
Evidence for involvement of a second genetic locus on chromosome 11q in porphyrin metabolism
Icelandic families with autosomal dominant polycystic kidney disease: families unlinked to chromosome 16p13.3 revealed by linkage analysis Icelandic
Rapid detection of trisomy 21 by quantitative PCR
Differential contribution of C4 and HLA-DQ genes to systemic lupus erythematosus susceptibility
Regional chromosomal assignment of the Kell blood group locus (KEL) to chromosome 7q33-q35 by fluorescence in situ hybridization: evidence for the polypeptide nature of antigenic variation
Isolation and mapping of discrete DXS101 loci in Xq22 near the X-linked agammaglobulinaemia gene locus
A polymorphic CfoI site in exon 6 of the human cytochrome P450 CYP2D6 gene detected by the polymerase chain reaction
Announcements
Prospects for the genetics of human longevity
Evidence for linkage of the gene causing familial Mediterranean fever to chromosome 17q in non-Ashkenazi Jewish families: second locus or type I error? non-Ashkenazi Jewish families
Localisation of the human nuclear factor I/X (NFI/X) gene to chromosome 19p13 and detection of five other related loci at 1p21-22, 1q42-43, 5q15, 11p13 and 20q13 by FISH
Hypomethylation of classical satellite DNA and chromosome instability in lymphoblastoid cell lines
Sex chromosome aberrations and stature: deduction of the principal factors involved in the determination of adult height
New markers for linkage analysis of X-linked hypophosphataemic rickets
Clinical findings in patients with marker chromosomes identified by fluorescence in situ hybridization
Exon skipping due to a mutation in a donor splice site in the WT-1 gene is associated with Wilms' tumor and severe genital malformations
CF2603/4delT, a new frameshift mutation in exon 13 of the cystic fibrosis transmembrane conductance regulator (CFTR) gene
Diagnosis of human genetic disease using recombinant DNA
Loss of heterozygosity and K-ras gene mutations in gastric cancer
Phenylketonuria in Spain: RFLP haplotypes and linked mutations
Retrospective molecular detection of transhyretin Met 111 mutation in a Danish kindred with familial amyloid cardiomyopathy, using DNA from formalin-fixed and paraffin-embedded tissues
Genetic mapping of the erythropoietin receptor gene
Dinucleotide repeat polymorphisms at the lipoprotein lipase (LPL) locus
Linkage of Wiskott-Aldrich syndrome with three marker loci, DXS426, SYP and TFE3, which map to the Xp11.3?p11.22 region
Founder effect in a Belgian-Dutch fragile X population Belgian-Dutch
Genetic and molecular analysis of familial isolated growth hormone deficiency
Long range restriction map of the von Hippel-Lindau gene region on human chromosome 3p
Extended haplotype analysis of cystic fibrosis mutations and its implications for the selective advantage hypothesis
Tight linkage between the Beckwith-Wiedemann syndrome and a microsatellite marker for the TH locus
Localization of X chromosome short arm markers relative to synovial sarcoma- and renal adenocarcinoma-associated translocation breakpoints
Fetal cells in the maternal circulation during first trimester in pregnancies
Announcements
Partial physical map of human chromosome 21 from fibroblast and lymphocyte DNA
Cytogenetic, FISH and DNA studies in 11 individuals from a family with two siblings with dup(21q) Down syndrome
Two novel microsatellite markers for prenatal prediction of spinal muscular atrophy (SMA)
Spectrin ?IIa variant in dominant and non-dominant spherocytosis
C1-inhibitor gene nucleotide insertion causes type II hereditary angio-oedema
Polymorphisms of the apolipoprotein B and E genes and their relationship to plasma lipid variables in healthy Chinese men healthy Chinese men
Presence of fetal cells in maternal circulation after delivery
Duplication detection in Japanese Duchenne muscular dystrophy patients and identification of carriers with partial gene deletions using pulsed-field gel electrophoresis
Human chromosome 11 complements ataxia-telangiectasia cells but does not complement the defect in AT-like Chinese hamster cell mutants
Detection of an exon 53 polymorphism in the dystrophin gene
The phenylketonuria G272X haplotype 7 mutation in European populations European populations
Mucopolysaccharidosis type II (Hunter disease): 13 gene mutations in 52 Japanese patients and carrier detection in four families
Two new polymorphisms in introns 2 and 3 of the human porphobilinogen deaminase gene
A complex chromosomal rearrangement detected prenatally and studied by fluorescence in situ hybridization
Molecular analysis of G6PD variants in northern Italy: a study on the population from the Ferrara district
Prosaposin deficiency: further characterization of the sphingolipid activator protein-deficient sibs
Restoration of the cholesterol metabolism in 3T3 cell lines derived from the sphingomyelinosis mouse (spm/spm) by transfer of a human chromosome 18
Down syndrome: effects of demographic factors and prenatal diagnosis on the future livebirth prevalence
Exclusively paternal X chromosomes in a girl with short stature
Affinity differences for vitamin D metabolites associated with the genetic isoforms of the human serum carrier protein (DBP)
The human skeletal muscle adenine nucleotide translocator gene maps to chromosome 4q35 in the region of the facioscapulohumeral muscular dystrophy locus
Polymerase chain reaction detection of a novel human KIT (mast/stem cell growth factor receptor) gene polymorphism by single-strand conformation polymorphism analysis or by SmaI or BstNI cleavage
Cytogenetic findings in crossed renal ectopia with pelvic lipomatosis
Duplication in the hypoxanthine phosphoribosyl-transferase gene caused by Alu-Alu recombination in a patient with Lesch Nyhan syndrome
Localization of the intronless gene coding for calmodulin-like protein CLP to human chromosome 10p13-ter
Genetic linkage analysis of Canadian spinal muscular atrophy kindreds using flanking microsatellite 5q13 polymorphisms
A new polymorphic marker (D10S97) tightly linked to the multiple endocrine neoplasia type 2A (MEN2A) locus
Polymorphisms and linkage disequilibrium in the COL6A1 and COL6A2 gene cluster: novel DNA polymorphisms in the region of a candidate gene for congenital heart defects in Down's syndrome
Molecular evaluation of an Alu repeat including a polymorphic variable poly(dA) (AluVpA) in the vitamin D binding protein (DBP) gene
The human interleukin-6 receptor ? chain gene is localized on chromosome 1 band q21
X chromosome linkage studies in familial Rett syndrome
Exclusion of two candidate pigment loci, c and b, part of chromosome 11p, and 33 random polymorphic markers as the locus for tyrosinase-positive oculocutaneous albinism
Apolipoprotein B signal peptide polymorphism in patients with myocardial infarction and controls
Linkage mapping of the cystathionine ?-synthase (CBS) gene on human chromosome 21 using a DNA polymorphism in the 3? untranslated region
Distribution of DYZ2 repetitive sequences on the human Y chromosome
A polymorphism in the 5? region of coagulation factor VII gene (F7) caused by an inserted decanucleotide
Reevaluation of the chromosome 4q candidate region for early onset periodontitis
Fetal nucleated cells in maternal peripheral blood: frequency and relationship to gestational age
SSCP detection of a Gly565Val substitution in the pro?(I) collagen chain resulting in osteogenesis imperfecta type II
Demographic reductions and genetic bottlenecks in humans: minisatellite allele distributions in oceania
Loss of heterozygosity on chromosome 11p13 in primary bladder carcinoma
Increased chromosome fragility in lymphocytes of short normal children treated with recombinant human growth hormone
Inter-ethnic polymorphism of the ?-globin gene locus control region (LCR) in sickle-cell anemia patients
Analysis of human extrachromosomal DNA elements originating from different ?-satellite subfamilies
The pattern of spontaneous germ-line mutation: relative rates of mutation at or near CpG dinucleotides in the factor IX gene
Physical localisation of the chromosomal marker D13S31 places the Wilson disease locus at the junction of bands q14.3 and q21.1 of chromosome 13
Molecular abnormality of G6PD Konan and G6PD Ube, the most common glucose-6-phosphate dehydrogenase variants in Japan
A frequent EcoRI polymorphism in the bcl-2 gene
Choroid plexus cysts diagnosed prenatally as an independent risk factor for cytogenetic abnormality
Hereditary hydronephrosis and the short arm of chromosome 6
Relation of cardiovascular risk factors to atherosclerosis in type III hyperlipoproteinemia
Prenatal sex determination from maternal peripheral blood using the polymerase chain reaction
Molecular study of chromosome 15 in 22 patients with Angelman syndrome
Cloning and chromosome mapping of human retinoid X receptor ?: selective amino acid sequence conservation of a nuclear hormone receptor in mammals
Decreased extracellular deposition of fibrillin and decorin in neonatal Marfan syndrome fibroblasts
Chromosomal analysis of unfertilized human oocytes prepared by a gradual fixation-air drying method
Linkage studies in Italian families with familial adenomatous polyposis
A study of genetic linkage heterogeneity in 35 adult-onset polycystic kidney disease families
Flow cytometric and cytogenetic analyses in human spontaneous abortions
Analysis of a genetic mutation in an electrophoretic variant of the human lactate dehydrogenase-B(H) subunit
Structure and expression analysis of a member of the human glutamate dehydrogenase (GLUD) gene family mapped to chromosome 10p11.2
Identification of two new nucleotide mutations (HPRTUtrecht and HPRTMadrid) in exon 3 of the human hypoxanthine-guanine phosphoribosyltransferase (HPRT) gene
Between-generation differences in ascertainment and penetrance: relevance to genetic hypotheses in fragile X
The human apolipoprotein B 3? hypervariable region: detection of eight new alleles and comparisons of allele frequencies in blacks and whites
Identification of a splice-site mutation in the low density lipoprotein receptor gene by denaturing gradient gel electrophoresis
Physical mapping in the region of human Xq12-21.1 using pulsed field gel electrophoresis
A new polymorphic restriction site at the human atrial natriuretic peptide (hANP) gene locus
Two new polymorphisms in the coding sequence of the LDL receptor (LDLR) gene
H-Y (SDM) antibody specifically binds M�llerian inhibiting substance
Loss of heterozygosity in malignant gliomas involves at least three distinct regions on chromosome 10
Molecular analysis in patients with mucopolysaccharidosis type II suggests that DXS466 maps within the Hunter gene
An Ala/Thr variation in the coding region of the human cystatin C gene (CST3) detected as a SstII polymorphism
Arginase deficiency manifesting delayed clinical sequelae and induction of a kidney arginase isozyme
Four separate regions on chromosome 17 show loss of heterozygosity in familial breast carcinomas
Mapping of the gene for X-chromosomal split-hand/split-foot anomaly to Xq26?q26.1
Rapid detection and prevalence of cholesteryl ester transfer protein deficiency caused by an intron 14 splicing defect in hyperalphalipoproteinemia
Physical mapping identifies DXS265 as a useful genetic marker for carrier detection and prenatal diagnosis of X-linked agammaglobulinemia
Why are some genetic diseases common?
A new human brain cDNA molecule: assignment to chromosome 11q21-q23.1 and description of two polymorphisms studied by the polymerase chain reaction
Identification and characterization of sporadic and inherited mutations in exon 31 of the neurofibromatosis (NF1) gene
Detection and characterization of new genetic mutations in individuals heterozygous for lactate dehydrogenase-B(H) deficiency using DNA conformation polymorphism analysis and silver staining
A novel nonsense mutation in the protein C (PROC) gene (Trp-29?Term) causing recurrent venous thrombosis
Reproductive hormone genes in mothers of spontaneous dizygotic twins: an association study
Molecular cytogenetic study of patients with Pallister-Killian syndrome
Three Finnish incontinentia pigmenti (IP) families with recombinations with the IP loci at Xq28 and Xp11
Characterization of genetic markers in the 5? flanking region of the apo A1 gene
Linkage disequilibrium of three polymorphic RFLP markers in the apolipoprotein AI-CIII gene cluster on chromosome 11
A PvuII polymorphism of the low density lipoprotein receptor gene is not associated with plasma concentrations of low density lipoproteins including LP(a)
Efficient identification of marker chromosomes in 27 patients by stepwise hybridization with alpha-satellite DNA probes
Isolation of a new cDNA clone encoding an Rh polypeptide associated with the Rh blood group system
Changes of telomere lengths in human intracranial tumours
High prevalence of a point mutation in the porphobilinogen deaminase gene in Dutch patients with acute intermittent porphyria
A missense mutation in the low density lipoprotein receptor gene causes familial hypercholesterolemia in Sephardic Jews Sephardic Jews
Are the nail-patella syndrome and the autosomal Goltz-like syndrome the phenotypic expressions of different alleles at the COL5A1 locus?
Deletion breakpoints associated with the Prader-Willi and Angelman syndromes (15q11-q13) are not sites of high homologous recombination
Prothymosin ? gene in humans: organization of its promoter region and localization to chromosome 2
Human breast cancer: frequent p53 allele loss and protein overexpression
An ?-spectrin mutation responsible for hereditary elliptocytosis associated in cis with the ?V/41 polymorphism
A missense mutation, S349P, completely inactivates phenylalanine hydroxylase in North African Jews with phenylketonuria North African Jews
Genetic and population study of a Y-linked tetranucleotide repeat DNA polymorphism with a simple non-isotopic technique
Physical mapping of microdeletions of the chromosome 17 short arm associated with Smith-Magenis syndrome
A study of the genetic polymorphism of human inter-alpha-trypsin-inhibitor (ITI) in the Han population, Chengdu, China
Announcements
Molecular defect in human erythropoietic protoporphyria with fatal liver failure
Support for founder effect for two lipoprotein lipase (LPL) gene mutations in French Canadians by analysis of GT microsatellites flanking the LPL gene
Patterns of deletions of the dystrophin gene in different European populations
A ?-galactosidase gene mutation identified in both Morquio B disease and infantile GM1 gangliosidosis
Announcements
Chromosomal localization of four human zinc finger cDNAs
Nucleotide substitutions at the -6 position in the promoter region of the factor IX gene result in different severity of hemophilia B Leyden: consequences for genetic counseling
Colocalization of the genes coding for the ?3 and ?3 subunits of soluble guanylyl cyclase to human chromosome 4 at q31.3?q33
A recombinant Friedreich's ataxia family
Data on the CGG repeat at the fragile X site in the non-retarded Japanese population and family suggest the presence of a subgroup of normal alleles predisposing to mutate
Presymptomatic direct detection of adenomatous polyposis coli (APC) gene mutations in familial adenomatous polyposis
HLA-A/B haplotye frequencies among U.S. Hispanic and African-American populations Hispanic; African-American
Functional disomy of Xp22-pter in three males carrying a portion of Xp translocated to Yq
Elevated frequency of an ETS-1 restriction fragment polymorphism in chronic B-cell leukaemia
Charcot-Marie-Tooth disease 1A (CMT1A) associated with a maternal duplication of chromosome 17p11.2?12
Polymorphism in human IL-1 receptor antagonist gene intron 2 is caused by variable numbers of an 86-bp tandem repeat
Detection of a cryptic paracentric inversion within band 11p13 in familial aniridia by fluorescence in situ hybridization
Genetic epidemiology of sensorimotor polyneuropathy with or without agenesis of the corpus callosum in northeastern Quebec
A novel mutation in exon 3 of the CFTR gene
The 11p15.5 ribonucleotide reductase M1 subunit locus is not imprinted in Wilms' tumour and hepatoblastoma
Parathyroid hormone gene analysis in autosomal hypoparathyroidism using an intragenic tetranucleotide (AAAT) n polymorphism
Polymorphism of glucose dehydrogenase (GDH, EC 1.1.1.47): formal and population genetic data
G6PD Mediterranean accounts for the high prevalence of G6PD deficiency in Kurdish Jews
The relationship between meiotic chromosome pairing and chiasma formation
Announcements
Single-strand conformational polymorphism and direct sequencing applied to carrier testing in families with ornithine transcarbamylase deficiency
Analysis of a second family with hereditary non-chromaffin paragangliomas locates the underlying gene at the proximal region of chromosome 11q
Autosomal recessive transmission of hemophilia A due to a von Willebrand factor mutation
A parental combination analysis for ABO-HP interaction in a Bengali population
Molecular cytogenetic characterization of three familial cases of satellited Y chromosomes
Development of a sequence-tagged site for the centromere of chromosome 10: its use in cytogenetic and physical mapping
Deletion of 19 base pairs in intron 13 of the gene for the pro?2(I) chain of type-I procollagen (COL1A2) causes exon skipping in a proband with type-I osteogenesis imperfecta
Identification of the 408 valine to methionine mutation in the low density lipoprotein receptor in a German family with familial hypercholesterolemia
Chromosome 1 Charcot-Marie-Tooth disease (CMT1B) locus in the Fc? receptor gene region
Immunophenotyping of mitotic cells from long-term cultures of chorionic villi
FFU complex: an analysis of 491 cases
Human ?2-glycoprotein I: molecular analysis of DNA and amino acid polymorphism
A 40-nucleotide repeat polymorphism in the human dopamine transporter gene
Human reciprocal translocations: is the unbalanced mode at birth predictable?
The immunoglobulin ? locus: polymorphism and haplotypes of Caucasoid and non-Caucasoid individuals
Epidemiological data on Werdnig-Hoffmann disease in Germany (West-Th�ringen)
An interleukin-8 (IL-8) cDNA clone identifies a frequent HindIII polymorphism
Absence of familial defective apolipoprotein B-100 in Israeli patients with dominantly inherited hypercholesterolemia and in offspring with parental history of myocardial infarction
The two locus control of Leber hereditary optic neurophathy and a high penetrance in Japanese pedigrees
Molecular heterogeneity of autosomal dominant cerebellar ataxia: analysis of flanking microsatellites of the spinocerebellar ataxia 1 locus in a northern European family unequivocally demonstrates non northern European family
Excess of multifocal tumors in nephroblastoma: implications for mechanisms of tumor development and genetic counseling
Human zinc finger gene ZNF23 (Kox16) maps to a zinc finger gene cluster on chromosome 16q22, and ZNF32 (Kox30) to chromosome region 10q23-?q24
Focal epithelial hyperplasia: human-papillomavirus-induced disease with a genetic predisposition in a Venezuelan family
Duplication of the short arm of the X chromosome in mother and daugther
Steroid 21-hydroxylase (P450c21): a new allele and spread of mutations through the pseudogene
Analysis of 160 CF chromosomes: detection of a novel mutation in exon 20
The effect of the apolipoprotein E phenotype on plasma lipids is not influenced by environmental variability: results of a Dutch twin study Dutch
Chrosomal mapping of the human gene for the tricyclic antidepressant-sensitive noradrenaline transporter
Distinct molecular origins for Denys-Drash and Frasier syndromes
A null allele frequent in non-Jewish Tay-Sachs patients
Identification of an alternative 5? untranslated region of the adenomatous polyposis coli gene
A sequence variation in the human cystatin D gene resulting in an amino acid (Cys/Arg) polymorphism at the protein level
Hypomelanosis of Ito in a girl with plexus papilloma and translocation (X;17)
An RFLP for probe 26-6 that is useful in linkage diagnosis for adult polycystic kidney disease
An alphoid DNA sequence conserved in all human and great ape chromosomes: evidence for ancient centromeric sequences at human chromosomal regions 2q21 and 9q13
Detection of complete and partial chromosome gains and losses by comparative genomic in situ hybridization
A single amino acid deletion in the ?2(I) chain of type I collagen produces osteogenesis imperfecta type III
Regional assignment of the gene coding for a human Graves' disease autoantigen to 10q21.3?q22.1
Routine diagnosis of DiGeorge syndrome by fluorescent in situ hybridization
Detection of amplified DNA sequences by reverse chromosome painting using genomic tumor DNA as probe