Human Genetics - 1992

383 articles | Last updated: 2025-12-03 14:12:56
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Molecular analysis of aberrations of Xp and Yq
Intra- and extragenic marker haplotypes of CFTR mutations in cystic fibrosis families
Sperm chromosome complements from two human reciprocal translocation heterozygotes
Rapid generation of chromosome-specific alphoid DNA probes using the polymerase chain reaction
Mutational analysis of SRY: nonsense and missense mutations in XY sex reversal
Transferrin subtypes in 51 Danish patients with hereditary haemochromatosis and in 847 normal subjects
The unbalanced offspring of the male carriers of the 11q;22q translocation: nondisjunction at meiosis II in a balanced spermatocyte
Further characterization of the new marker at DXS115 with regard to carrier detection in hemophilia A
Reply to the letter by Kling et al.
Influence of HLA genotype on birth weight of patients with Turner syndrome
Haplotype analysis at the low density lipoprotein receptor locus: application to the study of familial hypercholesterolemia in Israel
Identification of factor IX mutations in haemophilia B: application of polymerase chain reaction and single strand conformation analysis
Chromosome 1 in human colorectal tumors
The Wiskott-Aldrich syndrome: refinement of the localization on Xp and identification of another closely linked marker locus, OATL1
Association of apolipoprotein B gene variants with plasma apoB and low density lipoprotein (LDL) cholesterol levels
Maternal origin of deletion 15q11–13 in 25/25 cases of Angelman syndrome
Allelic dimorphism in the human tissue-type plasminogen activator (TPA) gene as a result of an Alu insertion/deletion event
Molecular characterization of β-thalassemia in Czechoslovakia
The role of the sex-determining region of the Y chromosome (SRY) in the etiology of 46,XX true hermaphroditism
Polymorphisms in the apolipoprotein (apo) AI-CIII-AIV gene cluster: detection of genetic variation determining plasma apo AI, apo CIII and apo AIV concentrations
Carrier detection and prenatal diagnosis of cystic fibrosis using an intragenic TA-repeat polymorphism
Cytogenetics of human oocytes, zygotes, and embryos after in vitro fertilization
Cytogenetic and molecular characterization of marker chromosomes in patients with mosaic 45,X karyotypes
A possible mosaic form of delayed centromere separation and aneuploidy
Announcements
PKU mutations R408Q and F299C in Norway: Haplotype associations, geographic distributions and phenotype characteristics
Lung involvement, the ΔF508 mutation and DNA haplotype analysis in cystic fibrosis
Genotype of Yupik Eskimos with congenital adrenal hyperplasia due to 21-hydroxylase deficiency Yupik Eskimos
Mucopolysaccharidosis type I (Hurler syndrome): Linkage disequilibrium indicates the presence of a major allele
Genetic structures in the Po Delta: Principal components, systemic functions and the relative age of the beta-thalassemia polymorphism
Molecular detection of a translocation (Y;11)(q11.2;q24) in a 45,X male with signs of Jacobsen syndrome
Pyruvate dehydrogenase (PDH) deficiency caused by a 21-base pair insertion mutation in the Elα subunit
Molecular heterogeneity underlying the G6PD Mediterranean phenotype
Ataxia-telangiectasia: Linkage analysis in highly inbred Arab and Druze families and differentiation from an ataxia-microcephaly-cataract syndrome
Frequency of the ΔF508 deletion and G551D, R553X and G542X mutations in Yugoslav CF patients
Two intragenic polymorphisms of the APC-gene detected by PCR and enzymatic digestion
A novel missense mutation in the antithrombin III gene (Ser349→Pro) causing recurrent venous thrombosis
PGD Port Elizabeth: A new variant found in South Africa
A 20-year-old male with partial trisomy 18q —as diagnosed by in situ hybridization
Human triosephosphate isomerase: Substitution of Arg for Gly at position 122 in a thermolabile electromorph variant, TPI-Manchester
Detection by DGGE of a new polymorphism closely linked to the adenomatous polyposis coli region
Characterization of centromere arrangements and test for random distribution in G0, G1, S, G2, G1, and early S′ phase in human lymphocytes
Physical mapping of an Xq-proximal interstitial duplication in a male
Assignment of the slow troponin T (TNNT1) gene to chromosome 19 using polymerase chain reaction
PCR assay for a polymorphicDdeI site in the promoter region of the human cystatin C gene
Molecular basis of group A xeroderma pigmentosum: A missense mutation and two deletions located in a zinc finger consensus sequence of the XPAC gene
The molecular defect in a family with mild atypical osteogenesis imperfecta and extreme joint hypermobility: Exon skipping caused by an 11-bp deletion from an intron in one COL1A2 allele
Spontaneous abortion and confined chromosomal mosaicism
Assignment of the gene encoding the catalytic subunit Cβ of CAMP-dependent protein kinase to the p36 band on chromosome
Mapping of the Menkes locus to Xq13.3 distal to the X-inactivation center by an intrachromosomal insertion of the segment Xq13.3-q21.2
X-linked retinitis pigmentosa: New map studies of XLRP2, and a possible human centromere effect
The point mutation of hypoxanthine-guanine phosphoribosyltransferase (HPRTEdinburgh) and detection by allele-specific polymerase chain reaction
Regional chromosomal assignment of genes encoding the α and β subunits of human complement protein C8 to 1p32
Population cytogenetics of aphidicolin-induced fragile sites
Characterization of a new mutation (R292G) and a deletion at the human uroporphyrinogen decarboxylase locus in two patients with hepatoerythropoietic porphyria
?I/65 Hereditary elliptocytosis in Southern Italy: Evidence for an African origin African origin
Novel promoter and splice junction defects add to the genetic, clinical or geographic heterogeneity of ?-thalassaemia in the Portuguese population
Refined regional assignment of the human tissue factor pathway inhibitor (TFPI) gene to chromosome band 2q32 by non-isotopic in situ hybridization
A novel mutation in the ?-protein coding region of the amyloid ?-protein precursor (APP) gene
Two PstI polymorphisms for the urokinase-type plasminogen activator receptor gene (PLAUR)
Further evidence of a duplication in 17p11.2 in families with recurrence of HMSN Ia (Charcot-Marie-Tooth neuropathy type Ia)
Molecular analysis of type I-A (tyrosinase negative) oculocutaneous albinism
Identification of CpG islands around the DXS178 locus in the region of the X-linked agammaglobulinaemia gene locus in Xq22
Detection of a new polymorphism of the human prothrombin (F2) gene by combination of PASA and mutated primer-mediated PCR-RFLP
Deletion of the 5?-region in one or two alleles of HEXB in 15 out of 30 patients with Sandhoff disease
On genetic components in autoimmunity: a critical review based on evolutionarily oriented rationality
A familial mutation in the testis-determining gene SRY shared by both sexes
Molecular analysis of five independent Japanese mutant genes responsible for hypoxanthine guanine phosphoribosyltransferase (HPRT) deficiency Japanese
Variants of the anti-M�llerian hormone gene in a compound heterozygote with the persistent M�llerian duct syndrome and his family
Alcohol dehydrogenase genes: restriction fragment length polymorphisms for ADH4 (?-ADH) and ADH5 (?-ADH) and construction of haplotypes among different ADH classes
Identification of a nonsense mutation in the amelogenin gene (AMELX) in a family with X-linked amelogenesis imperfecta (AIH1)
Analysis of ?-globin gene haplotypes in Asian Indians: origin and spread of ?-thalassaemia on the Indian subcontinent
Genetic studies of antithrombin III with IEF and ASO hybridization
?-1-Antichymotrypsin variant detected by PCR-single strand conformation polymorphism (PCR-SSCP) and direct sequencing
Aplasia cutis congenita reminiscent of the lines of Blaschko
A rare DNA variant in exon 15 of the cystic fibrosis transmembrane conductance regulator (CFTR) gene
Editorial help
Huntington disease in Finland: a molecular and genealogical study
Genetics of neurofibromatosis 1 in Japan: mutation rate and paternal age effect
Missense mutations and the magnitude of functional deficit: the example of factor IX
Human ?-globin gene expression is silenced by terminal truncation of chromosome 16p beginning immediately 3? of the ?-globin gene
Protease inhibitor (Pi) locus, fertility and twinning
A novel sickle cell mutation of yet another origin in Africa: the Cameroon type
No evidence for constitutional chromosome instability in testicular cancer
Highly informative dinucleotide repeat polymorphism at the D11S29 locus on chromosome 11q23
Detection of a frequent polymorphism in exon 10 of the low-density lipoprotein receptor gene
Three DNA markers for hypophosphataemic rickets
The interleukin-7 receptor gene is at 5pl3
DNA analyses of XX and XX-hypospadiac males
The gene encoding human transmembrane secretory component (locus PIGR) is linked to D1S58 on chromosome 1
The apolipoprotein (a) gene: a transcribed hypervariable locus controlling plasma lipoprotein (a) concentration
Preparation of a rat brain histidine decarboxylase (HDC) cDNA probe by PCR and assignment of the human HDC gene to chromosome 15
Absence of Turner stigmata in a 46,XYp-female
A homozygous missense arginine to histidine substitution at position 482 of the ?-galactosidase in an Italian infantile GM1-gangliosidosis patient
Tissue segregation of a heteroplasmic mtDNA mutation in MERRF (Myoclonic epilepsy with ragged red fibers) encephalomyopathy
Linkage to Xq28 in a family with nonspecific X-linked mental retardation
Isolation of DNTR polymorphisms from yeast artificial chromosomes encompassing X chromosomal loci PGK1 and DXS56
Characterization and mapping of the 5? portion of von Willebrand factor pseudogene
The gene for bone morphogenetic protein 2A (BMP2A) is localized to human chromosome 20pl2 by radioactive and nonradioactive in situ hybridization
A single-base change at a splice acceptor site in the ornithine aminotransferase gene causes abnormal RNA splicing in gyrate atrophy
Mutations in the conserved domain of SRY are uncommon in XY gonadal dysgenesis
Molecular diagnosis of the Prader-Willi and Angelman syndromes by detection of parent-of-origin specific DNA methylation in 15q11-13
A family with X-linked deafness showing linkage to the proximal Xq region of the X chromosome
BglII RFLP in DXS498 between the pigment gene repeat unit, RCP and GCP
Investigation of the polymorphic ScaI site by a PCR-based assay at the human atrial natriuretic peptides (hANP) gene locus
Of palindromes and peptides
A 47,XXY female with unusual genitalia
Analysis of segregation and expression of an identified mutation at the neuroflbromatosis type 1 locus
Bloom's syndrome
Detection of fetal cells with 47,XY,+21 karyotype in maternal peripheral blood
Complete characterization of a large marker chromosome by reverse and forward chromosome painting
Non-radioactive detection of the most common mutations in the cystic fibrosis transmembrane conductance regulator gene by multiplex allele-specific polymerase chain reaction
A germ line mutation within the coding sequence for the putative 5-phosphoribosyl-1-pyrophosphate binding site of hypoxanthine-guanine phosphoribosyltransferase (HPRT) in a Lesch-Nyhan patient: missen
The intron 7 donor splice site transition: a second Tay-Sachs disease mutation in French Canada
Mapping of X chromosome translocation breakpoints in females with Duchenne muscular dystrophy with respect to exons of the dystrophin gene
Molecular characterization of ?-thalassemia in Azerbaijan
Alport syndrome: a genetic study of 31 families
New chromosome 21 DNA markers isolated by pulsed field gel electrophoresis from an ETS2-containing Down syndrome chromosomal region
Chromosomal assignment and linkage analysis of the human glutathione S-transferase ? gene (GSTM1) using intron specific polymerase chain reaction
A single base pair polymorphism in the WT1 gene detected by single-strand conformation polymorphism analysis
Molecular characterization of a 17q11.2 translocation in a malignant schwannoma cell line
A very conservative region of ApoB-100 in the putative binding region to the LDL receptor in the Toulouse population
Analysis of 30 known cystic fibrosis mutations: 10 mutations account for 27% of non-?F508 chromosomes in Southern France
A novel missense mutation in the antithrombin III gene (Ala387?Val) causing recurrent venous thrombosis
Announcements
Point mutations and polymorphisms in the human dystrophin gene identified in genomic DNA sequences amplified by multiplex PCR
Phenotype of disease in three patients with identical mutations in methylmalonyl CoA mutase
Discovery of a genetic polymorphism of human plasma protein C inhibitor (PCI): genetic survey utilizing isoelectric focusing followed by immunoblotting, immunological and biochemical characterization
HLA haplotype segregation and ultrastructural study in familial immotile-cilia syndrome
Linkage disequilibrium detected between myotonic dystrophy and the anonymous marker D19S63 in the Spanish population
Pericentric inversion of chromosome 12; a three family study
Loss of normal allele of the APC gene in an adrenocortical carcinoma from a patient with familial adenomatous polyposis
Chromosomal findings in fetuses with prenatally diagnosed cysts of the choroid plexus
Deletion ΔF508 and haplotype analysis of CFTR gene region in Slovak CF patients Slovak
Trisomy 8p: unusual origin detected by fluorescence in situ hybridization
RNA analysis from newborn screening dried blood specimen
The molecular basis of β-thalassemia in Turkey
Direct estimate of the haemophilia B (factor IX deficiency) mutation rate and of the ratio of the sex-specific mutation rates in Sweden
Mutation analysis of phenylketonuria in Spain: prevalence of two Mediterranean mutations
?-Thalassemia major resulting from a compound heterozygosity for the ?-globin gene mutation: further evidence for multiple origin and migration of the thalassemia gene
The human gene (DSG3) coding for the pemphigus vulgaris antigen is, like the genes coding for the other two known desmogleins, assigned to chromosome 18
Gene frequencies of alcohol dehydrogenase2 and aldehyde dehydrogenase2 in Northwest Coast Amerindians
Transthyretin Pro55, a variant associated with early-onset, aggressive, diffuse amyloidosis with cardiac and neurologic involvement
A rare FokI RFLP in the human dopamine D2 receptor gene (DRD2)
A polymorphic PstI site in intron 2 of the human apolipoprotein C-II gene detected by polymerase chain reaction
DNA-fingerprinting: a further note on mutation rates
Molecular characterization of genetic mutations in human lactate dehydrogenase (LDH) B (H) variant
Isolation and mapping of polymorphic cosmid clones used for sublocalization of the multiple endocrine neoplasia type 1 (MEN1) locus
Polymerase chain reaction amplification of two polymorphic simple repeat sequences within the von Willebrand factor gene: application to family studies in von Willebrand disease
A new polymorphism of thyroxin-binding globulin in three African groups (Mali) with endemic nodular goitre
Multipoint linkage analysis of the short arm of chromosome 11 in non-insulin dependent diabetes including maturity onset diabetes of youth
Variation in gene copy number and polymorphism of the human salivary amylase isoenzyme system in Caucasians
Prenatal diagnosis of familial hypercholesterolemia caused by the ?Lebanese? mutation at the low density lipoprotein receptor locus Lebanese
Expression of RPS4X in fibroblasts from patients with structural aberrations of the X chromosome
Polymorphism in the RD (D6S45) gene
Evidence for an ancestral alphoid domain on the long arm of human chromosome 2
Reduced recombination and paternal age effect in Klinefelter syndrome
Evidence for genetic heterogeneity in hereditary hydronephrosis caused by pelvi-ureteric junction obstruction, with one locus assigned to chromosome 6p
PCR detection of a BclI RFLP in the G6PD gene of Caucasians
A single nucleotide substitution in the phosphoglycerate kinase (PGK)-1 gene occurred after the separation of PGK-1 and PGK-2
Identification of TaqI polymorphism in the mitochondrial acetoacetyl-CoA thiolase gene and familial analysis of 3-ketothiolase deficiency
Generation and characterization of radiation reduced cell hybrids and isolation of probes from the proximal short arm of the human X chromosome
The spectrum of CFTR mutations in south-west German cystic fibrosis patients
A termination mutation (2143delT) in the CFTR gene of German cystic fibrosis patients
Assessment of iduronate-2-sulfatase mRNA expression in Hunter syndrome (mucopolysaccharidosis type II)
A critical analysis of data presented in eight studies favouring X-linkage of bipolar illness with special emphasis on formal genetic aspects
Rapid identification of mutations in the glucocerebrosidase gene of Gaucher disease patients by analysis of single-strand conformation polymorphisms
A novel CFTR mutation, 4035delA, detected by non-radioactive SSCP analysis
PCR detection of two RFLPs in exon I of the ?-L-iduronidase (IDUA) gene
Cytogenetic, oncogenetic, and histopathologic characteristics of colorectal carcinomas with 17p abnormalities
Risk calculations for hereditary effects of ionizing radiation in humans
Genetic and blood coagulation characterization of ?Swedish? families with von Willebrand's disease types I and III: New aspects of heredity Swedish
Differential termination of primer extension: a novel, quantifiable method for detection of point mutations
Detection of multiple cystic fibrosis mutations by reverse dot blot hybridization: a technology for carrier screening
The polymorphism ApoB/4311 in patients with myocardial infarction and controls: the ECTIM study
Cytogenetic studies in motile sperm from normal men
Repair of human sperm chromosome aberrations in the hamster egg
Estimation of the male and female mutation rates in Duchenne muscular dystrophy (DMD)
Wiskott-Aldrich syndrome carrier detection with the hypervariable marker M27β
The human fumarylacetoacetase gene: characterisation of restriction fragment length polymorphisms and identification of haplotypes in tyrosinemia type 1 and pseudodeficiency
Localization of the human insulin-like growth-factor-binding protein 4 gene to chromosomal region 17q12?21.1
The occurrence of various non-?F508 CFTR gene mutations among Hungarian cystic fibrosis patients
Absence of p53 germ-line mutations in bilateral breast cancer patients
A 530kb YAC contig tightly linked to the Friedreich ataxia locus contains five CpG clusters and a new highly polymorphic microsatellite
Absence of mutations in the promoter region of the low density lipoprotein receptor gene in a large number of familial hypercholesterolaemia patients as revealed by denaturing gradient gel electrophor
Increased expression of 5q31 fragile site in a Bloom syndrome family
A review of the molecular basis of hypoxanthine-guanine phosphoribosyltransferase (HPRT) deficiency
Deletions in exon 5 of the human rhodopsin gene causing a shift in the reading frame and autosomal dominant retinitis pigmentosa
Point mutation in the steroid-binding domain of the androgen receptor gene in a family with complete androgen insensitivity syndrome (CAIS)
The potassium channel gene HK1 maps to human chromosome 11p14.1, close to the FSHB gene
Sperm chromosome complements from two human reciprocal translocation heterozygotes
Detection of small RB1 gene deletions in retinoblastoma by multiplex PCR and high-resolution gel electrophoresis
Confirmation of linkage of benign familial neonatal convulsions to D20S19 and D20S20
Allotype distribution of human T cell receptor ? and ? chain genes in Caucasians, Asians and Australian Aborigines: Relevance to chronic hepatitis B Asians and Australian Aborigines
Linkage disequilibrium between phenylketonuria and RFLP haplotype 1 at the phenylalanine hydroxylase locus in Portugal
Isolation of anonymous DNA markers for human chromosome 22q11 from a flow-sorted library, and mapping using hybrids from patients with DiGeorge syndrome
Assignment of casein kinase 2 alpha sequences to two different human chromosomes
The French Canadian Tay-Sachs disease deletion mutation: identification of probable founders
Screening for nonsense mutations in patients with severe hemophilia A can provide rapid, direct carrier detection
Canadian Mennonites and individuals residing in the Friesland region of the Netherlands share the same molecular basis of 17?-hydroxylase deficiency Canadian Mennonites; individuals residing in the Friesland region of the Netherlands
?s Haplotypes in various world populations
Regional chromosomal assignment of the human platelet phosphofructokinase gene to 10p15
The gene for the human IgA Fc receptor maps to 19q13.4
Glucose-6-phosphate dehydrogenase (G6PD) electrophoretic variants and the PvuII polymorphism in Southern African populations
Sperm chromosome analysis of a man heterozygous for a pericentric inversion of chromosome 20
A rare MspI RFLP of the DMD probe p20 (DXS269)
Highly polymorphic region of the human prothrombin (F2) gene
A comment on the paper: Ovarian dysgenesis in individuals with chromosomal abnormalities, by C. Cunniff, K. Lyons Jones, and K. Benirschke
Announcements
Homozygous acute intermittent porphyria: compound heterozygosity for adjacent base transitions in the same codon of the porphobilinogen deaminase gene
Prenatal diagnosis of 21-hydroxylase deficiency congenital adrenal hyperplasia using the polymerase chain reaction
Genotype mosaicism in fragile X fetal tissues
Alport syndrome caused by a 5′ deletion within the COL4A5 gene
Mild dominant osteogenesis imperfecta with intrafamilial variability: the cause is a serine for glycine ?1(I) 901 substitution in a type-I collagen gene
A new polymorphic site in the G6PD gene
Assignment of the human CRABP-II gene to chromosome 1q21 by nonisotopic in situ hybridization
Detection of two missense mutations and characterization of a repeat polymorphism in the factor VII gene (F7)
Exclusion of stromelysin-1, stromelysin-2, interstitial collagenase and fibronectin genes as the mutant loci in a family with recessive epidermolysis bullosa dystrophica and a form of cerebellar ataxi
Paternal selection favoring mutant alleles of the retinoblastoma susceptibility gene
Metabolism of GM1 ganglioside in cultured skin fibroblasts: anomalies in gangliosidoses, sialidoses, and sphingolipid activator protein (SAP, saposin) 1 and prosaposin deficient disorders
A non-alphoid repetitive DNA sequence from human chromosome 21
Detection of a common mutation of the catalase gene in Japanese acatalasemic patients Japanese
CFTR illegitimate transcription in lymphoid cells: quantification and applications to the investigation of pathological transcripts
Quantitative correlation between the residual activity of β-hexosaminidase A and arylsulfatase A and the severity of the resulting lysosomal storage disease
Nested polymerase chain reaction on cellular DNA in plasma: a rapid method to investigate the collagen type I A2 MspI polymorphic restriction site in alcoholic patients
In situ hybridization of PCR amplified inter-Alu sequences from a hybrid cell line
CYP21/C4 gene organisation in Italian 21-hydroxylase deficiency families
Polymorphisms at the GLUT1 (HepG2) and GLUT4 (muscle/adipocyte) glucose transporter genes and non-insulin-dependent diabetes mellitus (NIDDM)
Genetic linkage analysis of bipolar affective disorder in an Old Order Amish pedigree Old Order Amish
The human vitronectin (complement S-protein) gene maps to the centromeric region of 17q
Pseudoautosomal repeat displays higher variability in Blacks than in Caucasians Blacks
Protein C deficiency and thromboembolism: recurrent mutation at Arg 306 in the protein C gene
Characterization of two novel polymorphisms at the human parathyroid hormone gene locus
Localization of the human gene encoding heterogeneous nuclear RNA ribonucleoprotein G (hnRNP-G) to chromosome 6p12
Selective advantage of fra(X) heterozygotes compared with mothers of Down syndrome probands?
Mothers and grandmothers of Down's syndrome patients as controls for fra(X) carriers
Announcements
Sex determination and sex reversal: genotype, phenotype, dogma and semantics
Microdeletions in interval 6 of the Y chromosome of males with idiopathic sterility point to disruption of AZF, a human spermatogenesis gene
Complementation study of peroxisome-deficient disorders by immunofluorescence staining and characterization of fused cells
Genetic concepts in Greek literature from the eighth to the fourth century B.C.
Complementation of a DNA repair deficiency in six human tumor cell lines by chromosome 11
Molecular genetic evidence for a founder effect in familial hypercholesterolemia among French Canadians
Screening for cystic fibrosis gene mutations by multiplex DNA amplification
Search for putative suppressor genes in meningioma: significance of chromosome 22
PCR-assisted localization of the human SRPR gene
De novo complex chromosome rearrangement in identical twins with multiple congenital anomalies
Identification of crossovers in Wilson disease families as reference points for a genetic localization of the gene
Omission of exon 12 in cystic fibrosis transmembrane conductance regulator (CFTR) gene transcripts
Physical fine mapping of genes underlying X-linked deafness and non fra(X)-X-linked mental retardation at Xq21
Two different missense mutations at Arg 178 of the protein C (PROC) gene causing recurrent venous thrombosis
Molecular screening and fetal diagnosis of ?-thalassemia in the Italian population
The majority of the marker chromosomes in Japanese patients with stigmata of turner syndrome are derived from Y chromosomes
Identification of a missense phenylketonuria mutation at codon 408 in Chinese
Molecular cytogenetic analysis of a familial 8p23.1 deletion associated with minimal dysmorphic features, seizures, and mild mental retardation
A haplotype-linked four base pair deletion upstream of the A? globin gene coincides with decreased gene expression
A dominant mutation in the COL1A1 gene that substitutes glycine for valine causes recurrent lethal osteogenesis imperfecta
Crossed renal ectopia with pelvic lipomatosis: a new syndrome involving chromosome 1
A novel homozygous missense mutation in the protein C (PROC) gene causing recurrent venous thrombosis
A HindIII/BglII dystrophin gene polymorphism in the African-American population African-American population
DNA analysis in Turkish Duchenne/Becker muscular dystrophy families
Incidence and expression of the N1303K mutation of the cystic fibrosis (CFTR) gene
Announcements
Molecular studies of parental origin and mosaicism in 45,X conceptuses
Exclusion mapping of the X-linked dominant chondrodysplasia punctata/ichthyosis/cataract/short stature (Happle) syndrome: possible involvement of an unstable pre-mutation
Fragile site (16) (q22)
A novel NcoI polymorphism creates a fifth haplotype in the 3? untranslated region of CKM
No abnormalities in the NAD+ ADP-ribosyltransferase (polymerizing) gene of transformed cells from a Fanconi's anemia patient
No evidence for linkage of familial hypertrophic cardiomyopathy and chromosome 14q1 locus D14S26 in a chinese family: evidence for genetic heterogeneity chinese family
?-Globin gene cluster haplotypes in Yanomama Indians from the Amazon region of Brazil
Ornithine transcarbamylase (OTC) deficiency in a female patient with a de novo deletion of the paternal X chromosome
Intrachromosomal insertions: a case report and a review
Chromosome-band-specific painting: chromosome in situ suppression hybridization using PCR products from a microdissected chromosome band as a probe pool
Point mutations in the upstream region of the ?-galactosidase A gene exon 6 in an atypical variant of Fabry disease
Analysis of the 5? flanking sequence of the G? globin gene by denaturing gradient gel electrophoresis confirms the heterogeneity of the Bantu ?s haplotype Bantu
Polymerase chain reaction analysis of fragile X mutations
Variable number of tandem repeat (VNTR) polymorphism at locus D17S5 (YNZ22) in four ethnically defined human populations
Mitochondrial gene segregation in mammals: is the bottleneck always narrow?
Different chromosomal localization of two adenylyl cyclase genes expressed in human brain
Commingling and segregation analysis of serum uric acid in five North American populations: the Lipid Research Clinics family study
Molecular genotyping of N-acetylation polymorphism to predict phenotype
CpG hotspot causes second mutation in codon 408 of the phenylalanine hydroxylase gene
Chromosome aberrations in 450 sperm complements from eight controls and lack of increase after chemotherapy in two patients
Transthyretin Pro 36 associated with familial amyloidotic polyneuropathy in an Ashkenazic Jewish kindred Ashkenazic Jewish
Frequent polymorphism in the 13th exon of the adenomatous polyposis coli gene
Linkage study in a large pedigree with Stickler syndrome: exclusion of COL2A1 as the mutant gene
Splicing defect of the glycoasparaginase gene in two Japanese siblings with apartylglucosamimiria Japanese
Multiple minute marker chromosomes derived from Y identified by FISH in an intersexual infant
Two new alleles in the tetranucleotide repeat polymorphism at the lipoprotein lipase (LPL) locus
Geographic distribution and genealogy of mutation 207 of the lipoprotein lipase gene in the French Canadian population of Québec
Two new human hemoglobin variants caused by unusual mutational events: Hb Zaïre contains a five residue repetition within the α-chain and Hb Duino has two residues substituted in the β-chain
Assignment of the gene for human spasmolytic protein (hSP/SML1) to chromosome 21
Confirmation of the human cathepsin B gene (CTSB) assignment to chromosome 8
Dual fluorescent in situ hybridisation for simultaneous detection of X and Y chromosome-specific probes for the sexing of human preimplantation embryonic nuclei
Molecular cytogenetic analysis of XX males using Y-specific DNA sequences, including SRY
Oocyte selection: a new model for the maternal-age dependence of Down syndrome
Molecular and genetic characterization and physical mapping of 11 new markers detecting multiallele restriction fragment length polymorphisms on the short arm of human chromosome 3
The mutational spectrum of single base-pair substitutions in mRNA splice junctions of human genes: Causes and consequences
Significance of the clonal and sporadic chromosome abnormalities in non-neoplastic renal tissue
The murine Rb(6.16) translocation: alterations in the proportion of alternate sperm segregants effecting fertilization in vitro and in vivo
A genetic model for the Prader-Willi syndrome and its implication for angelman syndrome
A genetic study of the human low-voltage electroencephalogram
The QM gene is X-linked and therefore not involved in suppression of tumorigenesis in Wilms' tumor
Significantly higher frequency of the MspI 2.2 kb allele of the Duchenne muscular dystrophy intragenic probe P-20 in the Chinese population Chinese population
De novo mutation within the intron-exon junction in the PiZ allele of the alpha-1-antitrypsin gene
Sperm chromosome analysis of two males heterozygous for a t(2;17)(q35;p13) and t(3;8)(p13;p21) reciprocal translocation
Letters to the editors
Chromosome 1 in human colorectal tumors
Announcements
Anonymous markers located on chromosome 6 in the HLA-A class I region: allelic distribution in genetic haemochromatosis
ααααanti-3.7 type II: a new α-globin gene rearrangement suggesting that the α-globin gene duplication could be caused by intrachromosomal recombination
Abnormal lymphokine production: a novel feature of the genetic disease Fanconi anemia
Plasminogen with type-I mutation is polymorphic in the Japanese population
Detection of seven point mutations in the porphobilinogen deaminase gene in patients with acute intermittent porphyria, by direct sequencing of in vitro amplified cDNA
Characterization of hypervariable locus-specific probes derived from a (CAC)5/(GTG)5 multilocus fingerprint in various Eurasian populations
Prenatal diagnosis of Duchenne muscular dystrophy by fetal muscle biopsy
Detection of GST1 gene deletion by the polymerase chain reaction and its possible correlation with stomach cancer in Japanese
Molecular genetic analysis of 67 patients with duchenne/becker muscular dystrophy
Mapping of a gene for epidermolytic palmoplantar keratoderma to the region of the acidic keratin gene cluster at 17q12?q21
A minority of 46,XX true hermaphrodites are positive for the Y-DNA sequence including SRY
No association between RFLPs at the porphobilinogen deaminase gene and schizophrenia
Haplotype distribution and mutations at the PAH locus in Croatia
Mapping of the human COL5A1 gene to chromosome 9q34.3
Autosomal dominant congenital cataract and microphthalmia associated with a familial t(2;16) translocation
Rearrangements of the X chromosome and Turner syndrome
Premature centromere division
Involvement of 3:1 disjunction in the common reciprocal translocation t(11;22)(q23.3;q11.2)
Proving paternity of children with deceased fathers
Huntington disease in black African populations black African populations
Birth and population prevalence of Duchenne muscular dystrophy in the Netherlands
Heterozygote deficiency, population substructure and their implications in DNA fingerprinting
Ewing's tumor X mouse hybrids expressing the MIC2 antigen: analyses using fluorescence CDD-banding and non-isotopic ISH
Single-strand conformation polymorphism (SSCP) analysis of exon 11 of the CFTR gene reliably detects more than one third of non-?F508 mutations in German cystic fibrosis patients German
Chromosomal localization of the human glycoasparaginase gene to 4q32?q33
Exclusion map of Salla disease: attempts to localize the disease gene using a computer program
Sib pair linkage analysis of renin gene haplotypes in human essential hypertension
Apolipoprotein E phenotypes and hyperlipidemia in patients under maintenance hemodialysis
Heterogeneity of mutations in the uroporphyrinogen III synthase gene in congenital erythropoietic porphyria
A 27-bp deletion from one allele of the type III collagen gene (COL3A1) in a large family with Ehlers-Danlos syndrome type IV
A family with RP3 type of X-linked retinitis pigmentosa: an association with ciliary abnormalities
Molecular abnormality of a Japanese glucose-6-phosphate dehydrogenase variant (G6PD Tokyo) associated with hereditary non-spherocytic hemolytic anemia
Localisation of the gene for Norrie disease to between DXS7 and DXS426 on Xp
Dinucleotide (CA/GT) repeat polymorphism in intron 17B of the cystic fibrosis transmembrane conductance regulator (CFTR) gene
A possible example of gene conversion with a common ?-thalassemia mutation and Chi sequence present in the ?-globin gene
Germinal ?mosaicism? ? germline mutation or chimerism?
Prader-Willi or Angelman syndrome in familial 15q11?q13 deletion of maternal origin?
Triple trisomy in a spontaneous abortion
High population incidence of the 15p marker D15Z1 mapping to the short arm of one homologue 14
Chromosome 15p marker D15Z1 frequently maps to the short arm of other D-group chromosomes
Announcements
Carrier detection and prenatal diagnosis of alpha-thalassemia of Southeast Asian deletion by polymerase chain reaction
Parental origin and germline mosaicism of deletions and duplications of the dystrophin gene: a European study a European study
Preferential mutation of the neurofibromatosis type 1 gene in paternally derived chromosomes
Mosaicism in 45,X Turner syndrome: does survival in early pregnancy depend on the presence of two sex chromosomes?
Cloning of the human ?2-macroglobulin gene and detection of mutations in two functional domains: the bait region and the thiolester site
Estimating the stability of the proposed imprinted state of the fragile-X mutation when transmitted by females
Distribution of ADH2 and ALDH2 genotypes in different populations
Familial synovial chondromatosis combined with dwarfism
A rare genetic variant of the T cell receptor gamma joining segment TRGJI
The segregation of a translocation t(1;4) in two male carriers heterozygous for the translocation
Loss of heterozygosity on chromosome 11 in sporadic gastrinomas
Data on the interaction of ABO blood groups and the haptoglobin system
The epidemiology of Huntington's disease
Genetic heterogeneity of early-onset familial breast cancer
Frequency of ?F508 and haplotype association in Austrian cystic fibrosis families
Hereditary cystatin C amyloid angiopathy: identification of the disease-causing mutation and specific diagnosis by polymerase chain reaction based analysis
Differences in apolipoprotein(a) polymorphism in West Greenland Eskimos and Caucasian Danes
Simple repeat sequences on the human Y chromosome are equally polymorphic as their autosomal counterparts
Molecular analysis of the gene for the human vitamin-D-binding protein (group-specific component): allelic differences of the common genetic GC types
Reciprocal translocation between the proximal regions of the long arms of chromosomes 13 and 15 resulting in unbalanced offspring: characterization by fluorescence in situ hybridization and DNA analys
Genetic and biochemical heterogeneity in patients with the rhizomelic form of chondrodysplasia punctata ? a complementation study
Paracentric inversion 11q in Canadian Hutterites
Single-strand conformational polymorphisms (SSCP): detection of useful polymorphisms at the dystrophin locus
The Kell blood group locus is close to the cystic fibrosis locus on chromosome 7
Molecular diagnosis of the transthyretin (TTR) Met111 mutation in familial amyloid cardiomyopathy of Danish origin Danish origin
Consanguinity and Down syndrome in the Shetland Islands
A point mutation changes the polymorphisms pattern in a cystic fibrosis carrier family
Mutation analysis and prenatal diagnosis in a Lesch-Nyhan family showing non-random X-inactivation interfering with carrier detection tests
A single base mutation in the gene for type III collagen (COL3A1) converts glycine 847 to glutamic acid in a family with Ehlers-Danlos syndrome type IV. An unaffected family member is mosaic for the m
Deletions in the dystrophin gene: analysis of Duchenne and Becker muscular dystrophy patients in Quebec
Structural gene aberrations in mucopolysaccharidosis II (Hunter)
Familial pericentric inversion (3)(p12q24)
Frequency of ?F508 mutation and haplotype analysis in Austrian cystic fibrosis families