Human Genetics - 1991

321 articles | Last updated: 2025-12-03 14:12:56
Caucasian
1
White
0
European
1
Other
13
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Announcements
Replication asynchrony between homologs 15q11.2: Cytogenetic evidence for genomic imprinting
Polymorphic DNA haplotypes at the phenylalanine hydroxylase locus and their relation to phenotype in Swedish phenylketonuria families
A 48,XXY,+21 Down syndrome patient with additional paternal X and maternal 21
Frequency of the F508 deletion in cystic fibrosis patients from the European part of the USSR European part of the USSR
Aldosterone deficiency II (CMO II deficiency) is not the result of a mutation of an MspI restriction site within the CYP11B gene
Carrier detection in haemophilia A by direct analysis of factor VIII gene lesions
The frequencies of Hbs S and C in Georgia and South Carolina
Is Shwachman syndrome (McKusick 26040) a chromosome breakage syndrome?
X-linked Charcot-Marie-Tooth disease
Genetic heterogeneity of propionic acidemia: Analysis of 15 Japanese patients
Genetic epidemiology of Down's syndrome in Shetland
The physical map of chromosome arm 19q: some new assignments, confirmations and re-assessments
Localisation of the myotonic dystrophy locus to 19q13.2?19q13.3 and its relationship to twelve polymorphic loci on 19q
Population frequency of the arylsulphatase A pseudo-deficiency allele
Genetic polymorphism of inter-alpha-trypsin-inhibitor (ITI): Formal genetic and linkage analyses
HindIII/Eco RI RFLP of the human immunoglobulin IGHE gene detected with a C? probe in the French and Tunisian populations French and Tunisian populations
The size of small polydisperse circular DNA (spcDNA) in angiofibroma-derived cell cultures from patients with tuberous sclerosis (TSC) differs from that in fibroblasts
Regional assignment of the human uroporphyrinogen III synthase (UROS) gene to chromosome 10q25.2?q26.3
A novel missense mutation in exon 8 of the ornithine transcarbamylase gene in two unrelated male patients with mild ornithine transcarbamylase deficiency
Osteogenesis imperfecta due to recurrent point mutations at CpG dinucleotides in the COL1A1 gene of type I collagen
Frequent occurrence of translocations of the short arm of chromosome 15 to other D-group chromosomes
Uridine enhances expression of the fragile X chromosome in human lymphocytes
Polymorphisms in the human X-linked pyruvate dehydrogenase E1? gene
Chromosome abnormalities found among 34910 newborn children: results from a 13-year incidence study in �rhus, Denmark
Assignment by in situ hybridization of a fibroblast growth factor receptor gene to human chromosome band 10q26
Linkage analysis of neurofibromatosis type 1
Mapping of the ribophorin II (RPN II) gene to human chromosome 20q12?q13.1 by in-situ hybridization
Regional chromosomal assignment of human 3-beta-hydroxy-5-ene steroid dehydrogenase to 1p13.1 by non-isotopic in situ hybridisation
Chromosomal assignment of a large tRNA gene cluster (tRNALeu, tRNAGln, tRNALys, tRNAArg, tRNAGly) to 17p13.1
The gene for the type 1 tumor necrosis factor receptor (TNF-R1) is localized on band 12p13
A new ? chain variant hemoglobin A2-Corfu or ?2?2 116 Arg?Cys (G18), detected by ?-globin gene analysis in a Greek family Greek family
Reply to letter by E.M. B�hler
Deletion mapping of interval 6 of the human Y chromosome
Triple trisomy in a 17-week-old fetus
A third allele of the PstI RFLP at DXS94
Letters to the Editor
Confirmation of the chromosomal localization of human lamp genes and their exclusion as candidate genes for Salla disease
Chromosome arrangements in human fibroblasts at mitosis
Genotypic analysis of families with lactate dehydrogenase A(M) deficiency by selective DNA amplification
Chromosomal instability in breast cancer patients
Somatic recombination rather than uniparental disomy suggested as another mechanism by which genetic imprinting may play a role in the etiology of Prader-Willi syndrome
Chromosomal mosaicism: a follow-up study of 39 unselected children found at birth
Human dystrophin gene transfer: production and expression of a functional recombinant DNA-based gene
Comparative mapping of ZFY in the hominoid apes
A test of the production line hypothesis of mammalian oogenesis
A third gene locus for tuberous sclerosis is closely linked to the phenylalanine hydroxylase gene locus
Phenylketonuria in Poland: 66% of PKU alleles are caused by three mutations
The human cardiac troponin I locus: assignment to chromosome 19p13.2?19q13.2
Differential methylation at the 5? and the 3? CCGG sites flanking the X chromosomal hypervariable DXS255 locus
Regional mapping of 22 microclones around the adenomatous polyposis coli (APC) locus on chromosome 5q
Trisomy 16q23?qter arising from a maternal t(13;16)(p12;q23): case report and evidence of the reciprocal balanced maternal rearrangement by the Ag-NOR technique
Chromosome mapping of the human cytidine-5?-triphosphate synthetase (CTPS) gene to band 1p34.1?p34.3 by fluorescence in situ hybridization
A rare insertional translocation of proximal segment with heterochromatic region of 1q into 7p in monozygotic twins and spontaneous abortions
C-anaphase versus premature centromere division
Linkage data suggesting allelic heterogeneity for paramyotonia congenita and hyperkalemic periodic paralysis on chromosome 17
Hypercholesterolemia in five Israeli Christian-Arab kindreds is caused by the ?Lebanese? allele at the low density lipoprotein receptor gene locus and by an additional independent major factor
Detection of the G to A mitochondrial DNA mutation at position 11778 in German families with Leber's hereditary optic neuropathy
Paracentric inversion of chromosome 15(q15q24): description of three families
A sterile male with 45,X0 and a Y;22 translocation
An 11-bp deletion in the arylsulfatase A gene of a patient with late infantile metachromatic leukodystrophy
Constitutional extra chromosomal element in a family with Wilms' tumor
Ehlers-Danlos syndrome type VII: a single base change that causes exon skipping in the type I collagen ?2(I) chain
Localization of the cellular retinoic acid binding protein (CRABP) gene relative to the acute promyelocytic leukemia-associated breakpoint on human chromosome 15
Von Hippel-Lindau (VHL) disease: distinct phenotypes suggest more than one mutant allele at the VHL locus
Analysis of X-chromosome inactivation in X-linked immunodeficiency with hyper-IgM (HIGM1): evidence for involvement of different hematopoietic cell lineages
Fatal hyperammonemia resulting from a C-to-T mutation at a MspI site of the ornithine transcarbamylase gene
Detection of hereditary haemochromatosis in an HLA-identical pedigree showing discordance between HLA class I genes and the disease locus
Identification of common variant alleles of the human guanosine monophosphate reductase gene
A 5′-truncated c-myc gene variant not associated with a risk of cancer
Glutathione S-transferase class ? in French alcoholic cirrhotic patients French
DNA-fingerprinting: a short note on mutation rates
Subregional localization of the chromosome 21 loci D21S24 and D21S26 using physical mapping techniques
Genetic linkage studies of autosomal dominant polycystic kidney disease: search for the second gene in a large Sicilian family Sicilian
Increased melanogenesis in cultured epidermal melanocytes from patients with neurofibromatosis 1 (NF1)
Partial 3q duplication syndrome and assignment of D3S5 to 3q25–3q28
CG dinucleotide transitions in the factor IX gene account for about half of the point mutations in hemophilia B patients: a Seattle series
The mechanism for a 33-nucleotide insertion in mRNA causing sphingolipid activator protein (SAP-1)-deficient metachromatic leukodystrophy
Identification of twelve new RFLP-markers on chromosome 22q11-qter
Normal variants of human mitochondrial DNA and translation products: the building of a reference data base
An RNA splice site mutation in the C1-inhibitor gene causes type I hereditary angio-oedema
A specific point mutation in the mitochondrial genome of Caucasians with MELAS
Analysis of X-chromosome inactivation and presumptive expression of the Wiskott-Aldrich syndrome (WAS) gene in hematopoietic cell lineages of a thrombocytopenic carrier female of WAS
Diagnosis of genetic disease using recombinant DNA. Third edition
Polymorphisms of the gene encoding cholesterol ester transfer protein and serum lipoprotein levels in subjects with and without coronary heart disease
“Spontaneous” FRA16B is a hot spot for sister chromatid exchanges
Nucleotide sequence evidence of the unicentric origin of the ?C mutation in Africa
The molecular genetics of haemophilia A: screening for point mutations in the factor VIII gene using the restriction enzyme TaqI
Chromosomal localization of the human D3 dopamine receptor gene
Regional assignment of the human cell cycle control gene CDC2 to chromosome 10q21 by in situ hybridization
Localisation of the gene coding for the haemopoietic stem cell antigen CD34 to chromosome 1q32
An unusual variant detected using a ?-globin probe for an individual with the sickle cell trait
Segregation of lymphocyte low molecular weight DNA and antinuclear antibodies in a family with systemic lupus erythematosus in first cousins
Deletion of chromosome 21 and normal intelligence: molecular definition of the lesion
Screening for a prevalent LDL receptor mutation in patients with severe hypercholesterolaemia
Cytogenetic analysis reveals clonal proliferation of smooth muscle cells in atherosclerotic plaques
Exclusion of linkage to the pericentromeric region of chromosome 21 in the Canadian pedigree with familial Alzheimer disease
The COL6A1 and COL6A2 genes exist as a gene cluster and detect highly informative DNA polymorphisms in the telomeric region of human chromosome 21q
Cysteine in the triple helical domain of the pro?2(I) chain of type-I collagen in nonlethal forms of osteogenesis imperfecta
The human kininogen gene (KNG) mapped to chromosome 3q26-qter by analysis of somatic cell hybrids using the polymerase chain reaction
The clinical phenotype of two patients with a complete deletion of the iduronate-2-sulphatase gene (mucopolysaccharidosis II ? Hunter syndrome)
DNA diagnosis of hydatidiform mole using the polymerase chain reaction
The length polymorphism in the 5? flanking region of the human ?-globin gene with denaturing gradient gel electrophoresis in a Japanese population Japanese population
Exclusion of COL1A1, COL1A2, and COL3A1 genes as candidate genes for Ehlers-Danlos syndrome type I in one large family
Inheritance of ribosomal gene activity and level of DNA methylation of individual gene clusters in a three generation family
Multipoint linkage analysis in X-linked Alport syndrome
Multipoint linkage analysis in X-linked ocular albinism of the Nettleship-Falls type
Human NK-2 receptor gene maps to chromosome region 10q11?21
The duplication in Charcot-Marie-Tooth disease type 1a spans at least 1100 kb on chromosome 17p11.2
Oto-palato-digital syndrome type I: further evidence for assignment of the locus to Xq28
Xeroderma pigmentosum complementation group H is withdrawn and reassigned to group D
Editorial help
Increased SOD1 enzymatic activity and gene modifications in orangutans: evolutionary implications
Studies on the phylogenetic conservation of the SRY gene
Two unrelated children with partial trisomy 1q and monosomy 6p, presenting with the phenotype of the Larsen syndrome
Synthesis of glycosaminoglycans in fibroblasts from abortuses with trisomy, triploidy, and from children with Down's syndrome
Analysis of synaptonemal complexes in a heterozygous human male carrier of a reciprocal translocation involving an acrocentric chromosome: heterosynapsis without previous homosynapsis
Methods for analysis of multiple cystic fibrosis mutations
The gene for the type II (p75) tumor necrosis factor receptor (TNF-RII) is localized on band 1p36.2?p36.3
Prospects for homologous recombination in human gene therapy
Induction of distamycin A-inducible rare fragile sites and increased sister chromatid exchanges at the fragile site
Non-isotopic detection of chromosome 1 in human meiosis and demonstration of disomic sperm nuclei
High prevalence of aspartylglycosaminuria among school-age children in eastern Finland
Molecular characterization of a patient with del(1)(q23–q25)
The murine Rb(6.16) translocation: evidence for sperm selection and a modulating effect of aging
Cytogenetic investigations in three cell types of a Saudi family with ataxia telangiectasia Saudi
Characterization of seven DA/DAPI-positive bisatellited marker chromosomes by in situ hybridization
Dominant mutations in familial lethal and severe osteogenesis imperfecta
Sister chromatid exchanges are preferentially induced at expressed and nonexpressed common fragile sites
Detection of human spermatid-specific transcripts in peripheral blood lymphocytes of males and females
Dopamine beta-hydroxylase gene excluded in four subtypes of hereditary dystonia
Recurrent ctb(7)(q31.3) and possible laminin involvement in a neonatal cutis laxa with a Marfan phenotype
Inherited ring chromosomes: an analysis of published cases
Assignment of the gene coding for human cytochrome c oxidase subunit VIb to chromosome 19, band q13.1, by fluorescence in situ hybridisation
Three unique base pair changes in a family with Gaucher disease
T296?M, a common mutation causing mild hemophilia B in the Amish and others: founder effect, variability in factor IX activity assays, and rapid carrier detection Amish
X-linked anhidrotic ectodermal dysplasia and de novo t(X;1) in a female
Increased band sharing in DNA fingerprints of an inbred human population
Choroideremia: linkage analysis with physically mapped close DNA-markers
Genotype-phenotype correlation and germline mosaicism in DMD/BMD patients with deletions of the dystrophin gene
Extended MHC haplotypes and CYP21/C4 gene organisation in Irish 21-hydroxylase deficiency families
Human platelet basic protein/connective tissue activating peptide-III maps in a gene cluster on chromosome 4q12?q13 along with other genes of the ?-thromboglobulin superfamily
New distal marker closely linked to the fragile X locus
Recurrent mutation at aa 792 in the LDL receptor gene in a French patient
Human polymorphic probe pE1.8 detects SacI polymorphism in the ribonucleotide reductase M1 subunit gene
Parental origin and mechanism of formation of polysomy X: an XXXXX case and four XXXXY cases determined with RFLPs
Molecular characterization of medium-chain acyl-CoA dehydrogenase (MCAD) deficiency: identification of a lys329 to glu mutation in the MCAD gene, and expression of inactive mutant enzyme protein in E.
Ovarian dysgenesis in individuals with chromosomal abnormalities
Polymorphism in a ferritin H gene from chromosome 6p
Cytogenetic and molecular characterization of a newly established neuroblastoma cell line LS
Isolation and regional localization of a large collection (2,000) of single-copy DNA fragments on human chromosome 3 for mapping and cloning tumor suppressor genes
DNA polymorphism haplotypes of the human lipoprotein lipase gene: possible association with high density lipoprotein levels
Two human genes encoding zinc finger proteins, ZNF12 (KOX 3) and ZNF 26 (KOX 20), map to chromosomes 7p22-p21 and 12q24.33, respectively
The linkage of Hb Valletta [?2?287(F3)Thr?Pro] and Hb F-Malta-I [?2 G?2117(G19)His?Arg] in the Maltese population Maltese population
A marked drop in the incidence of the null allele of the B gene of the fourth component of complement (C4B*Q0) in elderly subjects: C4B*Q0 as a probable negative selection factor for survival
Genetic mapping of 12 marker loci in the Xp22.3-p21.2 region
Rett syndrome: exclusion mapping following the hypothesis of germinal mosaicism for new X-linked mutations
Effects of the apolipoprotein(a) size polymorphism on the lipoprotein(a) concentration in 7 ethnic groups
A method for transforming lymphocytes from very small blood volumes suitable for paediatric samples
Correction of the published sequence for the human proteolipid protein gene
Determination of the origin of nondisjunction in a 49,XXXXY male using hypervariable dinucleotide repeat sequences
Assignment of the gene for human tenascin to the region q32?q34 of chromosome 9
New RFLPs of the immunoglobulin switch alpha region in mesangial IgA glomerulonephritis
A tetranucleotide repeat polymorphism in the cystic fibrosis gene
Announcements
Cystic fibrosis allele frequency, sex ratio anomalies and fertility: a new theory for the dissemination of mutant alleles
Announcements
Acatalasemia
Selection of DNA sequences from interval 6 of the human Y chromosome with homology to a Y chromosomal fertility gene sequence of Drosophila hydei
Chromosome assignment of four RAS-related RAB genes
Spectrum of phenylketonuria mutations in Western Europe and North Africa, and their relation to polymorphic DNA haplotypes at the phenylalanine hydroxylase locus Western Europe and North Africa
Duplication of exons 13, 14 and 15 of the LDL-receptor gene in a patient with heterozygous familial hypercholesterolemia
A diallelic RFLP of the CD3-epsilon chain of the clonotypic T-lymphocyte receptor is not associated with certain autoimmune diseases
A new deletion polymorphism at D5S71 raises the linkage information on adenomatous polyposis coli: implications for presymptomatic diagnosis
Characterization of a frequent polymorphism in the coding sequence of the Tp53 gene in colonic cancer patients and a control population
Some Mexican glucose-6-phosphate dehydrogenase variants revisited
A molecular genetic approach to the identification of isochromosomes of chromosome 21
Predivision in human oocytes at meiosis I: a mechanism for trisomy formation in man
Mapping the gene encoding the human erythroid transcriptional factor NFE1-GF1 to Xp11.23
Identification of a cystic fibros is mutation: deletion of isoleucine506
A novel human multi-locus DNA family detected by pJU78 (DF31)
Localization of the human Rh blood group gene structure to chromosome region 1p34.3–1p36.1 by in situ hybridization
No evidence for sequences structurally related to the RB1 gene in the human genome
Linkage analysis in X-linked adrenoleukodystrophy and application in post-and prenatal diagnosis
Incidence of Menkes disease
Geographical distribution gradients of the major PKU mutations and the linked haplotypes
Characterisation of a Xp21 microdeletion syndrome in a 2-year-old boy with muscular dystrophy, glycerol kinase deficiency and adrenal hypoplasia congenita
Homozygous condition for a BrdU-requiring fragile site on chromosome 12
Physical mapping of two Xp markers DXS16 and DXS143
De novo complex chromosomal rearrangement in a woman with recurrent spontaneous abortion and one healthy daughter
Probe KK5.33 (D5S85) improves indirect genotype analysis in familial adenomatous polyposis
Announcements
No evidence of linkage between the locus for autosomal dominant retinitis pigmentosa and D3S47 (C17) in three Australian families
Molecular genetic analysis of factor X deficiency: gene deletion and germline mosaicism
Frequency and distribution of aneuploidy in human female gametes
No evidence for linkage of autosomal dominant proximal spinal muscular atrophies to chromosome 5q markers
Allelic somatic mutations may explain vascular twin nevi
Apolipoprotein A-IV protein polymorphism: frequency and effects on lipids, lipoproteins, and apolipoproteins among Mexican-Americans in Starr County, Texas
Frequency of the cystic fibrosis mutation ?F508 in Poland
Sequence of the variant thyroxine-binding globulin (TBG) in a Montreal family with partial TBG deficiency
The importance of further cytogenetic and molecular investigation of acrocentric variants: justification by presentation of a case [t(8;14)(q24;p11)]
Evidence of selective interaction between adenosine deaminase and acid phosphatase polymorphisms in fetuses carried by diabetic women
Announcements
Possible mapping of the gene for transient myeloproliferative syndrome at 21q11.2
Reply to letter by M. Krawczak and B. Bockel
Acrosin, the peculiar sperm-specific serine protease
The human transmembrane secretory component (poly-Ig receptor): molecular cloning, restriction fragment length polymorphism and chromosomal sublocalization
3? creatine kinase (M-type) polymorphisms linked to myotonic dystrophy in Italian and Spanish populations Italian and Spanish populations
Cytogenetic studies in leprosy patients before and after chemotherapy
The ITI system in South Koreans and iranians analysed by an improved classification procedure
Hypoxanthine-guanine phosphoribosyltransferase deficiency: analysis of HPRT mutations by direct sequencing and allele-specific amplification
Early preclinical diagnosis of dominant pseudoxanthoma elasticum by specific ultrastructural changes of dermal elastic and collagen tissue in a family at risk
Genetic linkage between Huntington disease and the D4S10 locus in South African families: further evidence against non-allelic heterogeneity
Substitution of Ile-172 to Asn in the steroid 21-hydroxylase B (P450c21B) gene in a Finnish patient with the simple virilizing form of congenital adrenal hyperplasia
Information content of the Centre d'Etude du Polymorphisme Humain (CEPH) family structures for linkage studies
Mitochondrial DNA mutation in an Italian family with Leber hereditary optic neuropathy
A rapid and simple electrophoretic method for the detection of mutations involving small insertion or deletion: application to ?-thalassemia
Recurrent nonsense mutation in exon 7 of the phenylalanine hydroxylase gene
Analysis of 14 cystic fibrosis mutations in five South European populations
A frameshift mutation in exon 2 of the phenylalanine hydroxylase gene linked to RFLP haplotype 1
Rapid detection of alpha-1-antitrypsin deficiency by analysis of a PCR-induced TaqI restriction site
A new definition of genetic distance
Detection of frequent BglII polymorphism by polymerase chain reaction and TaqI restriction fragment length polymorphism for 3?-hydroxysteroid dehydrogenase/?5-?4 isomerase at the human HSD?3 locus (1p
Identification of chromosome 21 DNA polymorphisms for genetic studies in Alzheimer's disease and Down syndrome
Proving paternity of children with deceased fathers
X-linked recessive chondrodysplasia punctata with XY translocation in a stillborn fetus
Cytogenetic and molecular characterization of a small ring chromosome in the complex karyotype of a girl with Turner syndrome
A small deletion and an adjacent base exchange in a potential stem-loop region of the neurofibromatosis 1 gene
Three dimensional reconstruction of human pachytene spermatocyte nuclei of a 17;21 reciprocal translocation carrier: study of XY-autosome relationships
Sister chromatid exchange (SCE) frequencies differ between directly prepared cytotrophoblasts and cultured mesenchymal core cells
A case of Hirschsprung disease with a chromosome 13 microdeletion, del(13)(q32.3q33.2): potential mapping of one disease locus
SstII polymorphic sites in the promoter region of the human cystatin C gene
MAC (morphology antibody chromosomes) technique for in situ chromosome preparations
Multiple sutural synostosis and congenital cataracts
Frequency of the cystic fibrosis mutation ?F508 in Algeria
Relative order determination of four Yp cosmids on metaphase and interphase chromosomes by two-color competitive in situ hybridization
Recurrence of a nonsense mutation in the NF1 gene causing classical neurofibromatosis type 1
High-density genetic and physical mapping of DNA markers near the X-linked Alport syndrome locus: definition and use of flanking polymorphic markers
Genomic structure and expression of human guanosine monophosphate reductase
Low density lipoprotein receptor founder mutations in Afrikaner familial hypercholesterolaemic patients: a comparison of two geographical areas Afrikaner
Molecular deletion patterns in families from southern France with Duchenne/Becker muscular dystrophies
Identification of a mutation in the promoter region of the dystrophin gene in a patient with atypical Becker muscular dystrophy
Chromosome 1 Charcot-Marie-Tooth disease (CMT1B) locus in the Fc? receptor gene region
Multicolor fluorescence in situ hybridization and pulsed field electrophoresis dissect CMT1B gene region
Cytogenetic and molecular analysis of a de novo tandem duplication of chromosome 21
Fine mapping of a human chromosome 6 ferritin heavy chain pseudogene: relevance to haemochromatosis
The phenylketonuria locus: current knowledge about alleles and mutations of the phenylalanine hydroxylase gene in various populations
The identification of two mis-sense mutations at the PAH gene locus in a Turkish patient with phenylketonuria Turkish
An intronic duplication in the alanine: glyoxylate aminotransferase gene facilitates identification of mutations in compound heterozygote patients with primary hyperoxaluria type 1
Linkage mapping of D21S171 to the distal long arm of human chromosome 21 using a polymorphic (AC)n dinucleotide repeat
Spinocerebellar ataxia: multipoint linkage analysis of genes associated with the disease locus
Mechanisms of insertional mutagenesis in human genes causing genetic disease
Persistence of two Y chromosomes through meiotic prophase and metaphase I in an XYY man
Fragile X expression and X inactivation
Orosomucoid (ORM 1) subtyping and formal genetics
A polymorphic region defined by pCN2 (the 3? nontranslated region of N-ras) maps to chromosome 9cen-p12
Cystic fibrosis with three mutations in the cystic fibrosis transmembrane conductance regulator gene
Cytogenetic studies in human sperm
Greig syndrome associated with an interstitial deletion of 7p: confirmation of the localization of Greig syndrome to 7p13
Discrimination between recurrent mutation and identity by descent: application to point mutations in exon 11 of the cystic fibrosis (CFTR) gene
Esterase D and retinoblastoma gene loci are tightly linked to Wilson's disease in Chinese pedigrees from Taiwan
DNA haplotype analysis suggests linkage disequilibrium in the human insulin receptor gene
Status of the search for a major genetic locus for affective disorder in the Old Order Amish
Genetic heterogeneity of the porphobilinogen deaminase gene in Swedish families with acute intermittent porphyria
Labeling of the centromeric region on human chromosome 8 by in situ hybridization
Detection of APC region-specific signals by nonisotopic chromosomal in situ suppression (CISS)-hybridization using a microdissection library as a probe
Isolated lissencephaly sequence associated with a microdeletion at chromosome 17p13
Cytogenetic studies on MIC gas-exposed persons in Bhopal
Identification of mutations in two families with sporadic hemophilia A
The most common mutation causing medium-chain acyl-CoA dehydrogenase deficiency is strongly associated with a particular haplotype in the region of the gene
Association between Rh and plasma iron binding (transferrin)
Mutation analysis of glucose-6-phosphate dehydrogenase (G6PD) variants in Costa Rica
Isodicentric X chromosome in a patient with Turner syndrome ? implications for localization of the X-inactivation center
The fragile X mutation does not have any major effect on the expression of the hypoxanthine phosphoribosyltransferase (HPRT) locus in human fibroblasts
Exclusion of linkage between familial Mediterranean fever and the human serum amyloid A (SAA) gene cluster
Molecular analysis of cystic fibrosis in the Hungarian population
The ?F508 mutation and RFLP-linked loci in Spanish cystic fibrosis families
Announcements
PAH 399 GTA(Val)?GTT(Val), a new silent mutation found in the Chinese
A pooling strategy for heterozygote screening of the ?F508 cystic fibrosis mutation
Consanguinity sans reproche
Type III hyperlipoproteinemia in a patient with idiopathic hemochromatosis
An assay for the rapid detection of the arylsulfatase A pseudodeficiency allele facilitates diagnosis and genetic counseling for metachromatic leukodystrophy
Identification of a break-prone structure in the 9q1 heterochromatic region
Synaptonemal complex analysis in a human male carrier of a 4;6 translocation: heterosynapsis without previous homosynapsis
Linkage relationship between incontinentia pigmenti (IP2) and nine terminal X long arm markers
TaqI reveals two independent alphoid polymorphisms on human chromosomes 13 and 21
Structural organization and polymorphism of the alpha satellite DNA sequences of chromosomes 13 and 21 as revealed by pulse field gel electrophoresis
Fragile sites and chromosome instability: the distribution of breaks induced by cis-diamine-clichloro-platinum (II) in Fanconi anemia lymphocyte cultures
Assignment of the human CD9 gene to chromosome 12 (region P13) by use of human specific DNA probes
Molecular analysis of PKU haplotypes in the population of southern Poland
Hemoglobin Stanleyville II (?78 Asn?Lys) is associated with a 3.7-kb ?-globin gene deletion
Announcements
The codon 408 mutation associated with haplotype 2 is predominant in Polish families with phenylketonuria
Autosomal dominant transmission of the NAME syndrome (nevi, atrial myxoma, mucinosis of the skin and endocrine overactivity)
Gene deletions causing human genetic disease: mechanisms of mutagenesis and the role of the local DNA sequence environment
Genotype-phenotype relationship in various degrees of arylsulfatase A deficiency
Molecular analysis of chromosome region 11p13 in patients with Drash syndrome
The human placental protein 14 (PP14) gene is localized on chromosome 9q34
DNA polymorphisms associated with a new ?1-antitrypsin PI Q0 variant (PI Q0riedenburg)
Hunter syndrome in Jews in Israel: further evidence for prenatal selection favoring the Hunter allele
Localisation of RFLPs of the medium chain acyl-CoA dehydrogenase gene
High incidence of acute infantile spinal atrophy in Hungary
Erratum
Family studies of the LDL receptor gene of relatively severe hereditary hypercholesterolemia associated with Achilles tendon xanthomas
Polymorphism of the T-cell receptor gamma variable and constant region genes in a Chinese population Chinese population
Chromosomal in situ suppression hybridization after Giemsa banding
Frequent deletions at Xq28 indicate genetic heterogeneity in Hunter syndrome
A t(Y;15) translocation with a deletion of the proximal Yq in a boy with mixed gonadal dysgenesis
Assessment of a creatine kinase isoform M defect as a cause of myotonic dystrophy and the characterization of two novel CKMM polymorphisms
Changes of common fragile sites on chromosomes according to the menstrual cycle
Molecular analysis of 4p deletion associated with Wolf-Hirschhorn syndrome moving the ?critical segment? towards the telomere
Autosomal dominant retinitis pigmentosa: a new multi-allelic marker (D3S621) genetically linked to the disease locus (RP4)
The human aldose reductase gene maps to chromosome region 7q35
Localization of DNA probes tightly linked to the Friedreich's ataxia locus by in situ hybridization in a case of pericentric inversion of chromosome 9
A de novo unbalanced reciprocal translocation identified as paternal in origin in the Prader-Willi syndrome
High recurrence of rearrangements involving chromosome 14 in an ataxia telangiectasia lymphoblastoid cell line and in its mutagen-treated derivatives
Non-radioactive in situ hybridization pattern of the M13 minisatellite sequences on human metaphase chromosomes
Karyotype pecularities of human colorectal adenocarcinomas
Duplications of the X chromosome in males: evidence that most parts of the X chromosome can be active in two copies
The gene for MEN 2A is tightly linked to the centromere of chromosome 10