Genetics in Medicine - 2015

195 articles | Last updated: 2025-12-03 14:12:56
Caucasian
0
White
0
European
0
Other
1
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Recommendations from the EGAPP Working Group: does the use of Oncotype DX tumor gene expression profiling to guide treatment decisions improve outcomes in patients with breast cancer?
In this Issue
News Briefs
News Briefs
In this Issue
Response to Cederbaum
Interpreting sequence variants in a clinical context
Correction: Corrigendum: Whole-exome sequencing reveals diverse modes of inheritance in sporadic mild to moderate sensorineural hearing loss in a pediatric population
In this Issue
News Briefs
Gene–environment interactions
Response to Saul
Molecular diagnostic testing
In this Issue
News Briefs
Next-generation sequencing to estimate the prevalence of a great unknown: McArdle disease
Response to Nogales-Gadea et al.
In sickness and in health: context matters when considering potential benefits and risks of genome-wide sequencing
Response to Strong
Response to ten Broeke and Nielsen
A PMS2-specific colorectal surveillance guideline
In this Issue
Correction: Corrigendum: Treacher Collins syndrome: a clinical and molecular study based on a large series of patients
News Briefs
Haploinsufficiency of the MYT1L gene causes intellectual disability frequently associated with behavioral disorder
Retracted: Validation of a multiplex genotyping platform using a novel genomic database approach
Scope of practice: a statement of the American College of Medical Genetics and Genomics (ACMG)
American College of Medical Genetics and Genomics: revised scope of practice and strategic plan
Correction: Corrigendum: CRIM-negative infantile Pompe disease: characterization of immune responses in patients treated with ERT monotherapy
In this Issue
News Briefs
Reproducing Genetics
The challenge of defining pathogenicity: the example of AHI1
Erratum: A genome sequencing program for novel undiagnosed diseases
Correction: Corrigendum: Too much, too soon?: Commercial provision of noninvasive prenatal screening for subchromosomal abnormalities and beyond
In this Issue
Response to Heller and Bolz
News Briefs
The cost-effectiveness of routine testing for Lynch syndrome in newly diagnosed patients with colorectal cancer in the United States: corrected estimates
Returning pharmacogenetic secondary findings from genome sequencing: let’s not put the cart before the horse
News Briefs
Erratum: Blood ammonia and glutamine as predictors of hyperammonemic crises in patients with urea cycle disorder
In this Issue
Can targeted genetic testing offer useful health information to adoptees?
Frequency and spectrum of actionable pathogenic secondary findings in 196 Korean exomes
Key emerging themes for assessing the cost-effectiveness of reporting incidental findings
Is there a link between COQ6 and schwannomatosis?
Response to Trevisson et al.
Is maternal plasma DNA testing impacting serum-based screening for aneuploidy in the United States?
Response to Phillips et al.
Correction: Corrigendum: Results of clinical genetic testing of 2,912 probands with hypertrophic cardiomyopathy: expanded panels offer limited additional sensitivity
In this Issue
Fatty acid oxidation flux predicts the clinical severity of VLCAD deficiency
News Briefs
Pushing the envelope in genomics education
Navigating the current landscape of clinical genetic testing for inherited retinal dystrophies
A genome sequencing program for novel undiagnosed diseases
Too much, too soon?: Commercial provision of noninvasive prenatal screening for subchromosomal abnormalities and beyond
Stakeholder engagement in policy development: challenges and opportunities for human genomics
Ultra-orphan diseases: a quantitative analysis of the natural history of molybdenum cofactor deficiency
Clinical utility of genetic and genomic services: a position statement of the American College of Medical Genetics and Genomics
Standards and guidelines for the interpretation of sequence variants: a joint consensus recommendation of the American College of Medical Genetics and Genomics and the Association for Molecular Pathol
Lysosomal storage disease in the brain: mutations of the β-mannosidase gene identified in autosomal dominant nystagmus
CRIM-negative infantile Pompe disease: characterization of immune responses in patients treated with ERT monotherapy
Development of clinical decision support alerts for pharmacogenomic incidental findings from exome sequencing
Determining the prevalence of McArdle disease from gene frequency by analysis of next-generation sequencing data
The importance of an integrated analysis of clinical, molecular, and functional data for the genetic diagnosis of familial hypercholesterolemia
Legislation in the genomic era: the Affordable Care Act and genetic testing for cancer risk assessment
Mutations of P4HA2 encoding prolyl 4-hydroxylase 2 are associated with nonsyndromic high myopia
Assessing multilevel determinants of adoption and implementation of genomic medicine: an organizational mixed-methods approach
Erratum: In This Issue
ADDENDUM: Reviewer Acknowledgment 2014
In this Issue
News Briefs
Whole-exome sequencing reveals diverse modes of inheritance in sporadic mild to moderate sensorineural hearing loss in a pediatric population
The expanding phenotype of COL4A1 and COL4A2 mutations: clinical data on 13 newly identified families and a review of the literature
Savior siblings and Fanconi anemia: analysis of success rates from the family’s perspective
Training future physicians in the era of genomic medicine: trends in undergraduate medical genetics education
Haplotype-based approach for noninvasive prenatal tests of Duchenne muscular dystrophy using cell-free fetal DNA in maternal plasma
In This Issue
Erratum: Carrier testing in children: exploration of genetic health professionals’ practices in Australia
News Briefs
How do students react to analyzing their own genomes in a whole-genome sequencing course?: outcomes of a longitudinal cohort study
An effective strategy to prevent allopurinol-induced hypersensitivity by HLA typing
Results of clinical genetic testing of 2,912 probands with hypertrophic cardiomyopathy: expanded panels offer limited additional sensitivity
Whole-exome sequencing in undiagnosed genetic diseases: interpreting 119 trios
Family history and the natural history of colorectal cancer: systematic review
Acceptability and feasibility of a virtual counselor (VICKY) to collect family health histories
Racial variation in frequency and phenotypes of APC and MUTYH mutations in 6,169 individuals undergoing genetic testing
Assessing the utility of confirmatory studies following identification of large-scale genomic imbalances by microarray
Symptom-driven idiopathic disease gene identification
Response to Dalal et al.
News Briefs
Erratum: Comprehensive CFTR gene analysis of the French cystic fibrosis screened newborn cohort: implications for diagnosis, genetic counseling, and mutation-specific therapy
Correction: Corrigendum: A clinical appraisal of different Z-score equations for aortic root assessment in the diagnostic evaluation of Marfan syndrome
Implications of polygenic risk-stratified screening for prostate cancer on overdiagnosis
Identification of false-negative mutations missed by next-generation sequencing in retinitis pigmentosa patients: a complementary approach to clinical genetic diagnostic testing
Assessment of incidental findings in 232 whole-exome sequences from the Baylor–Hopkins Center for Mendelian Genomics
A preliminary investigation of genetic counselors’ information needs when receiving a variant of uncertain significance result: a mixed methods study
Identifying gene disruptions in novel balanced de novo constitutional translocations in childhood cancer patients by whole-genome sequencing
Economic evaluation of genetic screening for Lynch syndrome in Germany
Small-scale high-throughput sequencing–based identification of new therapeutic tools in cystic fibrosis
Practical guidelines for managing adults with 22q11.2 deletion syndrome
In This Issue
Maternal cell-free DNA–based screening for fetal microdeletion and the importance of careful diagnostic follow-up
Guidance for pharmacogenomic biomarker testing in labels of FDA-approved drugs
Preliminary validation of a consumer-oriented colorectal cancer risk assessment tool compatible with the US Surgeon General’s My Family Health Portrait
SG-ADVISER CNV: copy-number variant annotation and interpretation
Is there a duty to recontact in light of new genetic technologies? A systematic review of the literature
Prevalence of mutations in a panel of breast cancer susceptibility genes in BRCA1/2-negative patients with early-onset breast cancer
The clinical utility of molecular karyotyping for neurocognitive phenotypes in a consanguineous population
Researchers’ views on informed consent for return of secondary results in genomic research
Diagnosis and management of mitochondrial disease: a consensus statement from the Mitochondrial Medicine Society
A high-resolution copy-number variation resource for clinical and population genetics
Challenges in managing genetic cancer risk: a long-term qualitative study of unaffected women carrying BRCA1/BRCA2 mutations
Blood ammonia and glutamine as predictors of hyperammonemic crises in patients with urea cycle disorder
Genetics educational needs in China: physicians’ experience and knowledge of genetic testing
Clinical utility of gene-expression profiling in women with early breast cancer: an overview of systematic reviews
Comprehensive analysis of patients with Stargardt macular dystrophy reveals new genotype–phenotype correlations and unexpected diagnostic revisions
Parents are interested in newborn genomic testing during the early postpartum period
Panel-based genetic diagnostic testing for inherited eye diseases is highly accurate and reproducible, and more sensitive for variant detection, than exome sequencing
The hidden harm behind the return of results from personal genome services: a need for rigorous and responsible evaluation
Congenital hypogonadotropic hypogonadism with split hand/foot malformation: a clinical entity with a high frequency of FGFR1 mutations
The cost-effectiveness of returning incidental findings from next-generation genomic sequencing
Toward an improved definition of the genetic and tumor spectrum associated with SDH germ-line mutations
A practice guideline from the American College of Medical Genetics and Genomics and the National Society of Genetic Counselors: referral indications for cancer predisposition assessment
Reporting genomic secondary findings: ACMG members weigh in
Inbreeding among Caribbean Hispanics from the Dominican Republic and its effects on risk of Alzheimer disease
Is it time for BRCA1/2 mutation screening in the general adult population?: impact of population characteristics
Correction: Corrigendum: Alu-mediated nonallelic homologous and nonhomologous recombination in the BMPR2 gene in heritable pulmonary arterial hypertension
Clinically relevant lessons from Family HealthLink: a cancer and coronary heart disease familial risk assessment tool
Hearts and hands as the starting point
Consanguinity and rare mutations outside of MCCC genes underlie nonspecific phenotypes of MCCD
Genotype–phenotype correlation and mutation spectrum in a large cohort of patients with inherited retinal dystrophy revealed by next-generation sequencing
Enhanced utility of family-centered diagnostic exome sequencing with inheritance model–based analysis: results from 500 unselected families with undiagnosed genetic conditions
Peripatetic southern cytogenetics
Assessing copy number from exome sequencing and exome array CGH based on CNV spectrum in a large clinical cohort
Prenatal diagnosis in India is not limited to sex selection
ACMG policy statement: updated recommendations regarding analysis and reporting of secondary findings in clinical genome-scale sequencing
BRCA1, BRCA2, PALB2, and CDKN2A mutations in familial pancreatic cancer: a PACGENE study
Is it all Lynch syndrome?: An assessment of family history in individuals with mismatch repair–deficient tumors
An overview of recommendations and translational milestones for genomic tests in cancer
Celebrity disclosures and information seeking: the case of Angelina Jolie
Summarizing polygenic risks for complex diseases in a clinical whole-genome report
Contribution of copy-number variation to Down syndrome–associated atrioventricular septal defects
Development of a tiered and binned genetic counseling model for informed consent in the era of multiplex testing for cancer susceptibility
Mortality of New York children with sickle cell disease identified through newborn screening
Two specific mutations are prevalent causes of recessive retinitis pigmentosa in North American patients of Jewish ancestry Jewish ancestry
Development of DNA Confirmatory and High-Risk Diagnostic Testing for Newborns Using Targeted Next-Generation DNA Sequencing
Long-term developmental progression in infants and young children taking sapropterin for phenylketonuria: a two-year analysis of safety and efficacy
Carrier testing in children: exploration of genetic health professionals’ practices in Australia
Naked bodies, naked genomes: the special (but not exceptional) nature of genomic information
Fabry disease in infancy and early childhood: a systematic literature review
Excess of runs of homozygosity is associated with severe cognitive impairment in intellectual disability
Single-nucleotide polymorphism arrays and unexpected consanguinity: considerations for clinicians when returning results to families
Genomic screening of the general adult population: key concepts for assessing net benefit with systematic evidence reviews
Surveying the current landscape of clinical genetics residency training
Whole-mitochondrial genome sequencing in primary open-angle glaucoma using massively parallel sequencing identifies novel and known pathogenic variants
Solving the molecular diagnostic testing conundrum for Mendelian disorders in the era of next-generation sequencing: single-gene, gene panel, or exome/genome sequencing
Disparities in uptake of BRCA1/2 genetic testing in a randomized trial of telephone counseling
Novel copy-number variants in a population-based investigation of classic heterotaxy
Refinement of the critical 2p25.3 deletion region: the role of MYT1L in intellectual disability and obesity
Primary-care providers’ perceived barriers to integration of genetics services: a systematic review of the literature
Fragile X full mutation expansions are inhibited by one or more AGG interruptions in premutation carriers
Good survival outcome of metastatic SDH-deficient gastrointestinal stromal tumors harboring SDHA mutations
Return of individual genetic results in a high-risk sample: enthusiasm and positive behavioral change
Informed consent for biobanking: consensus-based guidelines for adequate comprehension
Outcomes of individuals with profound and partial biotinidase deficiency ascertained by newborn screening in Michigan over 25 years
Adverse events in cancer patients with sickle cell trait or disease: case reports
Comprehensive CFTR gene analysis of the French cystic fibrosis screened newborn cohort: implications for diagnosis, genetic counseling, and mutation-specific therapy
Early-onset autosomal recessive cerebellar ataxia associated with retinal dystrophy: new human hotfoot phenotype caused by homozygous GRID2 deletion
Exceptional aggressiveness of cerebral cavernous malformation disease associated with PDCD10 mutations
Increased frequency of FBN1 truncating and splicing variants in Marfan syndrome patients with aortic events
Discordant noninvasive prenatal testing and cytogenetic results: a study of 109 consecutive cases
Identification of OSBPL2 as a novel candidate gene for progressive nonsyndromic hearing loss by whole-exome sequencing
Delineating the 15q13.3 microdeletion phenotype: a case series and comprehensive review of the literature
Molecular genetic testing for cystic fibrosis: laboratory performance on the College of American Pathologists external proficiency surveys
The impact of reporting incidental findings from exome and whole-genome sequencing: predicted frequencies based on modeling
Evidence for autism spectrum disorder in Jacobsen syndrome: identification of a candidate gene in distal 11q
Whole-exome sequencing identifies rare pathogenic variants in new predisposition genes for familial colorectal cancer
Horizontal integration of OMIM across the medical school preclinical curriculum for early reinforcement of clinical genetics principles
Improved molecular diagnosis by the detection of exonic deletions with target gene capture and deep sequencing
Multiplex genetic testing: reconsidering utility and informed consent in the era of next-generation sequencing
The Genetics of Luck
Cigarette smoking in women after BRCA1/2 genetic test disclosure: a 5-year follow-up study of the GENEPSO PS cohort
Agalsidase alfa and agalsidase beta in the treatment of Fabry disease: does the dose really matter?
State-based surveillance for selected hemoglobinopathies
The translational potential of research on the ethical, legal, and social implications of genomics
Molecular testing for the BRCA1 and BRCA2 Ashkenazi Jewish founder mutations: a report on the College of American Pathologists proficiency testing surveys
Characteristics associated with genetic counseling referral and BRCA1/2 testing among women in a large integrated health system
A systematic review and critical assessment of 11 discordant meta-analyses on reduced-function CYP2C19 genotype and risk of adverse clinical outcomes in clopidogrel users
Evidence synthesis and guideline development in genomic medicine: current status and future prospects
Differences in BRCA counseling and testing practices based on ordering provider type
Neurofibromatosis type 1 and chronic neurological conditions in the United States: an administrative claims analysis
Judith G. Hall: a genetic journey