Genetics in Medicine - 2013

196 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Reviewer Acknowledgment 2013
In This Issue
News Briefs
Processes and preliminary outputs for identification of actionable genes as incidental findings in genomic sequence data in the Clinical Sequencing Exploratory Research Consortium
Correction: Corrigendum: Frequency of Prader–Willi syndrome in births conceived via assisted reproductive technology
News Briefs
Standard enrichment methods for targeted next-generation sequencing in high-repeat genomic regions
ACMG statement on access to reproductive options after prenatal diagnosis
Finding common ground
Correction: Corrigendum: The utility of the traditional medical genetics diagnostic evaluation in the context of next-generation sequencing for undiagnosed genetic disorders
In this Issue
Integration of genomics into the electronic health record: mapping terra incognita
News Briefs
Glossary
Correction: Corrigendum: Long-term, open-labeled extension study of idursulfase in the treatment of Hunter syndrome
“I prefer a child with …”: designer babies, another controversial patent in the arena of direct-to-consumer genomics
Genetic medicine and incidental findings: it is more complicated than deciding whether to disclose or not
Practical challenges in integrating genomic data into the electronic health record
A survey of informatics approaches to whole-exome and whole-genome clinical reporting in the electronic health record
The undiscovered country: the future of integrating genomic information into the EHR
ACMG Standards and Guidelines for constitutional cytogenomic microarray analysis, including postnatal and prenatal applications: revision 2013
Personalized medicine and genetic malpractice
Opportunities for genomic clinical decision support interventions
Minimizing liability risks under the ACMG recommendations for reporting incidental findings in clinical exome and genome sequencing
Ethical, legal, and social implications of incorporating genomic information into electronic health records
Stakeholder engagement: a key component of integrating genomic information into electronic health records
In This Issue
Response to Rosenberg et al.
Paternalism and the ACMG recommendations on genomic incidental findings: patients seen but not heard
Response to Townsend et al.
Electronic health record design and implementation for pharmacogenomics: a local perspective
Some experiences and opportunities for big data in translational research
ACMG recommendations on incidental findings are flawed scientifically and ethically
Runs of homozygosity and parental relatedness
Editorial
Points to consider for informed consent for genome/exome sequencing
Storing and interpreting genomic information in widely deployed electronic health record systems
The EGAPP initiative: lessons learned
Incorporating genomic data into multivariate risk models for lung cancer
In This Issue
News Briefs
Erratum: Clinical genetics evaluation in identifying the etiology of autism spectrum disorders: 2013 guideline revisions
Genetic incidental findings: autonomy regained?
Recommendations for returning genomic incidental findings? We need to talk!
ACMG clinical laboratory standards for next-generation sequencing
Clinical genomics in the world of the electronic health record
In This Issue
News Briefs
Erratum: Novel candidate genes and regions for childhood apraxia of speech identified by array comparative genomic hybridization
Incidental findings in clinical genomics: a clarification
Researchers’ views on return of incidental genomic research results: qualitative and quantitative findings
ACMG recommendations for reporting of incidental findings in clinical exome and genome sequencing
ACMG Standards and Guidelines for fragile X testing: a revision to the disease-specific supplements to the Standards and Guidelines for Clinical Genetics Laboratories of the American College of Medica
The Electronic Medical Records and Genomics (eMERGE) Network: past, present, and future
Return of results to the families of children in genomic sequencing: tallying risks and benefits
In This Issue
News Briefs
When is a medical finding “incidental”?
Return of incidental findings in genomic medicine: measuring what patients value—development of an instrument to measure preferences for information from next-generation testing (IMPRINT)
Let us ask better questions
Analysis of left ventricular mass in untreated men and in men treated with agalsidase-β: data from the Fabry Registry
The use of next-generation sequencing in clinical diagnosis of familial hypercholesterolemia
Changes in plasma and urine globotriaosylceramide levels do not predict Fabry disease progression over 1 year of agalsidase alfa
Self-reported reproductive health in women with tuberous sclerosis complex
Preserving personal autonomy in a genomic testing era
Response to Lindor et al.
Avicenna’s view on medical genetics
Correction: Corrigendum: The effects of learning about one’s own genetic susceptibility to alcoholism: a randomized experiment
In This Issue
News Briefs
Renal growth in isolated methylmalonic acidemia
Underutilization of Lynch syndrome screening in a multisite study of patients with colorectal cancer
Experiences and attitudes of genome investigators regarding return of individual genetic test results
Self-guided management of exome and whole-genome sequencing results: changing the results return model
ACMG position statement on prenatal/preconception expanded carrier screening
American College of Medical Genetics and Genomics technical standards and guidelines: microarray analysis for chromosome abnormalities in neoplastic disorders
A mosaic PTEN mutation causing Cowden syndrome identified by deep sequencing
Clinical predictors of genetic testing outcomes in hypertrophic cardiomyopathy
Growth behavior of plexiform neurofibromas after surgery
Implementation of routine screening for Lynch syndrome in university and safety-net health system settings: successes and challenges
Insurance coverage of medical foods for treatment of inherited metabolic disorders
Discussing the psychiatric manifestations of 22q11.2 deletion syndrome: an exploration of clinical practice among medical geneticists
NCI think tank concerning the identifiability of biospecimens and “omic” data
Alu-mediated nonallelic homologous and nonhomologous recombination in the BMPR2 gene in heritable pulmonary arterial hypertension
The association of low socioeconomic status and the risk of having a child with Down syndrome: a report from the National Down Syndrome Project
Description and pilot results from a novel method for evaluating return of incidental findings from next-generation sequencing technologies
ACMG statement on noninvasive prenatal screening for fetal aneuploidy
Density matters: comparison of array platforms for detection of copy-number variation and copy-neutral abnormalities
Response to Benn
News Briefs
Prenatal counseling and the detection of copy-number variants
Response to Stoll and Resta
Erratum: Technical report: ethical and policy issues in genetic testing and screening of children
Considering the cost of expanded carrier screening panels
In This Issue
Hereditary ataxias: overview
Clinical genetics evaluation in identifying the etiology of autism spectrum disorders: 2013 guideline revisions
Use of genomic panels to determine risk of developing type 2 diabetes in the general population: a targeted evidence-based review
Recommendations from the EGAPP Working Group: does genomic profiling to assess type 2 diabetes risk improve health outcomes?
Positive cell-free fetal DNA testing for trisomy 13 reveals confined placental mosaicism
High apolipoprotein E4 allele frequency in FXTAS patients
Newborn screening 50 years later: access issues faced by adults with PKU
We screen newborns, don’t we?: realizing the promise of public health genomics
Cognitive characteristics of PTEN hamartoma tumor syndromes
A prospective study of brachytelephalangic chondrodysplasia punctata: identification of arylsulfatase E mutations, functional analysis of novel missense alleles, and determination of potential phenoco
In This Issue
News Briefs
Correction: Corrigendum: Effective communication of molecular genetic test results to primary care providers
The responses of research participants and their next of kin to receiving feedback of genetic test results following participation in the Australian Ovarian Cancer Study
Utilization of epidermal growth factor receptor (EGFR) testing in the United States: a case study of T3 translational research
“It was the missing piece”: adolescent experiences of predictive genetic testing for adult-onset conditions
Modeling uncertain outcomes of genetic testing: factor V Leiden mutation and pregnant women
What does it mean to be genomically literate?: National Human Genome Research Institute Meeting Report
Managing incidental genomic findings: legal obligations of clinicians
Recommendations from the EGAPP Working Group: can testing of tumor tissue for mutations in EGFR pathway downstream effector genes in patients with metastatic colorectal cancer improve health outcomes
Assessing genotype–phenotype correlation in Costello syndrome using a severity score
Genotypic classification of patients with Wolfram syndrome: insights into the natural history of the disease and correlation with phenotype
Technical report: ethical and policy issues in genetic testing and screening of children
Incorporating genomics into breast and prostate cancer screening: assessing the implications
How can polygenic inheritance be used in population screening for common diseases?
Morbidity and mortality in type B Niemann–Pick disease
Return of research results from genomic biobanks: a call for data
News Briefs
In This Issue
Return of results in genomic biobank research: ethics matters
Secondary variants and human subjects research
Erratum: Medical foods: inborn errors of metabolism and the reimbursement dilemma
An approach to family-centered coordinated co-management for individuals with conditions identified through newborn screening
Attitudes of Canadian researchers toward the return to participants of incidental and targeted genomic findings obtained in a pediatric research setting
Beyond the genomics blueprint: the 4th Human Variome Project Meeting, UNESCO, Paris, 2012
Creation of a national resource with linked genealogy and phenotypic data: the Veterans Genealogy Project
American College of Medical Genetics and Genomics: standards and guidelines for documenting suspected consanguinity as an incidental finding of genomic testing
Risk categorization for oversight of laboratory-developed tests for inherited conditions
Cascade carrier testing after a child is diagnosed with cystic fibrosis through newborn screening: investigating why most relatives do not have testing
The arrival of genomic medicine to the clinic is only the beginning of the journey
Implementing genomic medicine in the clinic: the future is here
A clinical appraisal of different Z-score equations for aortic root assessment in the diagnostic evaluation of Marfan syndrome
Primary-care physicians’ access to genetic specialists: an impediment to the routine use of genomic medicine?
Argininosuccinic aciduria: from a monogenic to a complex disorder
Autism genetic testing: a qualitative study of awareness, attitudes, and experiences among parents of children with autism spectrum disorders
ACMG Practice Guideline: lack of evidence for MTHFR polymorphism testing
Comprehensive next-generation sequence analyses of the entire mitochondrial genome reveal new insights into the molecular diagnosis of mitochondrial DNA disorders
Louis J. “Skip” Elsas II, MD, FACMG
Erratum: A comprehensive survey of cancer risks in extended families
News Briefs
Correction: Corrigendum: Stakeholder assessment of the evidence for cancer genomic tests: insights from three case studies
In This Issue
Estimates of penetrance for recurrent pathogenic copy-number variations
Informatics-based, highly accurate, noninvasive prenatal paternity testing
Comparison of chromosome analysis and chromosomal microarray analysis: what is the value of chromosome analysis in today’s genomic array era?
Effective communication of molecular genetic test results to primary care providers
Developing a comprehensive, effective patient-friendly website to enhance decision making in predictive testing for Huntington disease
Risk prediction for complex diseases: application to Parkinson disease
Cell-free fetal DNA testing: who is driving implementation?
Achieving the “triple aim” for inborn errors of metabolism: a review of challenges to outcomes research and presentation of a new practice-based evidence framework
Mapping the incidentalome: estimating incidental findings generated through clinical pharmacogenomics testing
“Trust is not something you can reclaim easily”: patenting in the field of direct-to-consumer genetic testing
Comparative analysis of IRF6 variants in families with Van der Woude syndrome and popliteal pterygium syndrome using public whole-exome databases
Perspectives of surrogate decision makers for critically ill patients regarding gene variation research
Ethical dilemmas associated with genetic testing: which are most commonly seen and how are they managed?
A risk–benefit analysis of factor V Leiden testing to improve pregnancy outcomes: a case study of the capabilities of decision modeling in genomics
Can a decision aid enable informed decisions in neonatal nursery recruitment for a fragile X newborn screening study?
A clinical evaluation tool for SNP arrays, especially for autosomal recessive conditions in offspring of consanguineous parents
Bortezomib in the rapid reduction of high sustained antibody titers in disorders treated with therapeutic protein: lessons learned from Pompe disease
Fragile X–related element 2 methylation analysis may provide a suitable option for inclusion of fragile X syndrome and/or sex chromosome aneuploidy into newborn screening: a technical validation study
Getting our priorities straight: a novel framework for stakeholder-informed prioritization of cancer genomics research
Lifting the lid on unborn lethal Mendelian phenotypes through exome sequencing
Including the initial newborn screening bloodspot collection device serial number on birth certificates: basis and recommendations from the Secretary of Health and Human Services’ Advisory Committee o
Congenital short bowel syndrome as the presenting symptom in male patients with FLNA mutations
Duplications, deletions, and single-nucleotide variations: the complexity of genetic arithmetic
Leveraging the electronic health record to implement genomic medicine
Sickle cell disease incidence among newborns in New York State by maternal race/ethnicity and nativity
Health behaviors and cancer screening among Californians with a family history of cancer
1q21.1 Microduplication expression in adults
An informatics approach to analyzing the incidentalome
Behavioral genetics and population health interventions for alcohol problems: at odds or oddly in agreement?
Complex genetics of radial ray deficiencies: screening of a cohort of 54 patients
Improving mutation notification when new genetic information is identified in research: a trial of two strategies in familial breast cancer
An empirical estimate of carrier frequencies for 400+ causal Mendelian variants: results from an ethnically diverse clinical sample of 23,453 individuals
Informatics and clinical genome sequencing: opening the black box
Cost-effectiveness of the 21-gene recurrence score assay in the context of multifactorial decision making to guide chemotherapy for early-stage breast cancer
Improving the efficiency and relevance of evidence-based recommendations in the era of whole-genome sequencing: an EGAPP methods update
Women’s experiences receiving abnormal prenatal chromosomal microarray testing results
Return of research results from genomic biobanks: cost matters
The effects of learning about one’s own genetic susceptibility to alcoholism: a randomized experiment
A systematic analysis of small supernumerary marker chromosomes using array CGH exposes unexpected complexity
Age-specific Parkinson disease risk in GBA mutation carriers: information for genetic counseling
Clinical and radiological features in young individuals with nevoid basal cell carcinoma syndrome
Avoiding genetic genocide: understanding good intentions and eugenics in the complex dialogue between the medical and disability communities
Clinical application of massively parallel sequencing in the molecular diagnosis of glycogen storage diseases of genetically heterogeneous origin
Homozygosity for aquaporin 7 G264V in three unrelated children with hyperglyceroluria and a mild platelet secretion defect
Identification of constitutional MLH1 epimutations and promoter variants in colorectal cancer patients from the Colon Cancer Family Registry
Survival among people with Down syndrome: a nationwide population-based study in Denmark
Incidental copy-number variants identified by routine genome testing in a clinical population
Regions of homozygosity identified by SNP microarray analysis aid in the diagnosis of autosomal recessive disease and incidentally detect parental blood relationships
Stakeholder perspectives on decision-analytic modeling frameworks to assess genetic services policy