Genetics in Medicine - 2011

197 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Expanded carrier screening and the law of unintended consequences: From cystic fibrosis to fragile X
News Briefs
College News
Personalizing medicine with clinical pharmacogenetics
Highlights of This Issue
Regarding cancer predisposition detected by CHG arrays
Response to the letter by Collins and Schimke
College News
Implementing screening for Lynch syndrome among patients with newly diagnosed colorectal cancer: Summary of a public health/clinical collaborative meeting
DNA sequencing of maternal plasma to detect Down syndrome: An international clinical validation study
Cardiovascular findings in duplication 17p11.2 syndrome
Testing for variants in CYP2C19: Population frequencies and testing experience in a clinical laboratory
Autoimmune lymphoproliferative syndrome due to FAS mutations outside the signal transducing death domain: Molecular mechanisms and clinical penetrance
The family history: The first genetic test, and still useful after all those years?
Revisiting the Wilson-Jungner criteria: How can supplemental criteria guide public health in the era of genetic screening?
Decision to abort after a prenatal diagnosis of sex chromosome abnormality: A systematic review of the literature
Competencies for the physician medical geneticist in the 21st century
Highlights of This Issue
College News
Novel recessive BFSP2 and PITX3 mutations: Insights into mutational mechanisms from consanguineous populations
Folic acid and neural tube defects
Costello syndrome: A Ras/mitogen activated protein kinase pathway syndrome (rasopathy) resulting from HRAS germline mutations
Highlights of this Issue
Allelic discrimination of cis-trans relationships by digital polymerase chain reaction: GJB2 (p.V27I/p.E114G) and CFTR (p.R117H/5T)
An evidence-based approach to establish the functional and clinical significance of copy number variants in intellectual and developmental disabilities
Enhancing exposure to genetics and genomics through an innovative medical school curriculum
The National Institutes of Health Undiagnosed Diseases Program: Insights into rare diseases
A large health system's approach to utilization of the genetic counselor CPT® 96040 code
Eligibility criteria in private and public coverage policies for BRCA genetic testing and genetic counseling
High-risk consumersʼ perceptions of preimplantation genetic diagnosis for hereditary cancers: A systematic review and meta-analysis
Can Factor V Leiden and prothrombin G20210A testing in women with recurrent pregnancy loss result in improved pregnancy outcomes? Results from a targeted evidence-based review
Consent to DNA collection in epidemiological studies: Findings from the Whitehall II cohort and the English Longitudinal Study of Ageing
Caregiver opinions about fragile X population screening
How disease advocacy organizations participate in clinical research: A survey of genetic organizations
Assessing the analytic validity of molecular testing for Huntington disease using data from an external proficiency testing survey
Evaluation of newborn screening bloodspot-based genetic testing as second tier screen for bedside newborn hearing screening
von Hippel-Lindau disease: Surveillance strategy for endolymphatic sac tumors
Prader-Willi syndrome
A qualitative secondary evaluation of statewide follow-up interviews for abnormal newborn screening results for cystic fibrosis and sickle cell hemoglobinopathy
Personal privacy, public benefits, and biobanks: A conjoint analysis of policy priorities and public perceptions
Incidence and predictors of positive and negative effects of BRCA1/2 genetic testing on familial relationships: A 3-year follow-up study
A counselee-oriented perspective on risk communication in genetic counseling: Explaining the inaccuracy of the counselees' risk perception shortly after BRCA1/2 test result disclosure
Informed consent and immunohistochemistry screening for Lynch syndrome
Feasibility of a pancreatic cancer surveillance program from a psychological point of view
Reply
Erratum: MLPA as first screening method for the detection of microduplications and microdeletions in patients with X-linked mental retardation: Erratum
Disparities in the diagnostic process of Duchenne and Becker muscular dystrophy
News Briefs
The virtual diagnostic laboratory: A new way of teaching undergraduate medical students about genetic testing
Targeted polymerase chain reaction-based enrichment and next generation sequencing for diagnostic testing of congenital disorders of glycosylation
Addressing gaps in physician education using personal genomic testing
Follow-up of carriers of BRCA1 and BRCA2 variants of unknown significance: Variant reclassification and surgical decisions
College News
Erratum: Genetic counseling and testing for Alzheimer disease: Joint practice guidelines of the American College of Medical Genetics and the National Society of Genetic Counselors: Erratum
The dangers of including nonclassical cystic fibrosis variants in population-based screening panels: p.L997F, further genotype/phenotype correlation data
Clinical utility of family history for cancer screening and referral in primary care: A report from the Family Healthware Impact Trial
Are videoconferenced consultations as effective as face-to-face consultations for hereditary breast and ovarian cancer genetic counseling?
Prevalence and psychosocial correlates of depressive symptoms among adolescents and adults with Klinefelter syndrome
Is there a need for PGxceptionalism?
Copy number variants of schizophrenia susceptibility loci are associated with a spectrum of speech and developmental delays and behavior problems
A novel exonic rearrangement affecting MLH1 and the contiguous LRRFIP2 is a founder mutation in Portuguese Lynch syndrome families Portuguese
To share or not to share: A randomized trial of consent for data sharing in genome research
News Briefs
Section E9 of the American College of Medical Genetics technical standards and guidelines: Fluorescence in situ hybridization
College News
The California Prenatal Screening Program: “Options and choices” not “coercion and eugenics”
Chromosomal microarray testing influences medical management
ABCC8 mutation allele frequency in the Ashkenazi Jewish population and risk of focal hyperinsulinemic hypoglycemia Ashkenazi Jewish population
What questions should newborn screening long-term follow-up be able to answer? A statement of the US Secretary for Health and Human Services' Advisory Committee on Heritable Disorders in Newborns and
American College of Medical Genetics recommendations for the design and performance expectations for clinical genomic copy number microarrays intended for use in the postnatal setting for detection of
Optimizing Bob Guthrie's legacy—Storage and use of residual newborn screening specimens
American College of Medical Genetics standards and guidelines for interpretation and reporting of postnatal constitutional copy number variants
Consideration of patient preferences and challenges in storage and access of pharmacogenetic test results
Technical standards and guidelines for spinal muscular atrophy testing
Storage and use of residual newborn screening blood spots: A public policy emergency
Emergency preparedness for genetics centers, laboratories, and patients: The Southeast Region Genetics Collaborative strategic plan
Family-provider interactions surrounding the diagnosis of Down syndrome
College News
News Briefs
Quality improvement of mitochondrial respiratory chain complex enzyme assays using Caenorhabditis elegans
Public attitudes toward ancillary information revealed by pharmacogenetic testing under limited information conditions
Personalized cancer genetics training for personalized medicine: Improving community-based healthcare through a genetically literate workforce
College of American Pathologists/American College of Medical Genetics proficiency testing for constitutional cytogenomic microarray analysis
Economic evaluation of targeted cancer interventions: Critical review and recommendations
Why is genetic screening for autosomal dominant disorders underused in families? The case of hereditary hemorrhagic telangiectasia
Long-term follow-up of children with confirmed newborn screening disorders using record linkage
The impact of antibodies on clinical outcomes in diseases treated with therapeutic protein: Lessons learned from infantile Pompe disease
COL3A1haploinsufficiency results in a variety of Ehlers-Danlos syndrome type IV with delayed onset of complications and longer life expectancy
Physicians' communication of Down syndrome screening test results: The influence of physician numeracy
Predictors and risk model development for menopausal age in fragile X premutation carriers
Committee report: Considerations and recommendations for national guidance regarding the retention and use of residual dried blood spot specimens after newborn screening
Genetic counseling and testing for Alzheimer disease: Joint practice guidelines of the American College of Medical Genetics and the National Society of Genetic Counselors
Deploying whole genome sequencing in clinical practice and public health: Meeting the challenge one bin at a time
News Briefs
College News
Multiple endocrine neoplasia type 2: An overview
Down syndrome: Coercion and eugenics
Phenylalanine hydroxylase deficiency
Gastric cancer in individuals with Li-Fraumeni syndrome
Consanguineous marriages, pearls and perils: Geneva International Consanguinity Workshop Report
Comparison of compliance for colorectal cancer screening and surveillance by colonoscopy based on risk
Educational needs about cancer family history and genetic counseling for cancer risk among frontline healthcare clinicians in New York City
Active choice but not too active: Public perspectives on biobank consent models
Policy statement on folic acid and neural tube defects
Clinical trials for pharmacogenomics testing for warfarin dosing: Relevance to general community practices
The psychosocial impact of Klinefelter syndrome and factors influencing quality of life
Genetic counseling following the detection of hemoglobinopathy trait on the newborn screen is well received, improves knowledge, and relieves anxiety
Hereditary hemorrhagic telangiectasia: An overview of diagnosis, management, and pathogenesis
Implementation outcomes of a multiinstitutional web-based ethical, legal, and social implications genetics curriculum for primary care residents in three specialties
Cardiovascular abnormalities in late-onset Pompe disease and response to enzyme replacement therapy
A founder mutation in the Ashkenazi Jewish population affecting messenger RNA splicing of the CCM2 gene causes cerebral cavernous malformations Ashkenazi Jewish population
Strengthening the reporting of Genetic Risk Prediction Studies: The GRIPS statement
Lysosomal storage diseases: Diagnostic confirmation and management of presymptomatic individuals
“That's a good question”: University researchers' views on ownership and retention of human genetic specimens
Alu-specific microhomology-mediated deletion of the final exon of SPAST in three unrelated subjects with hereditary spastic paraplegia
Empirical development of improved diagnostic criteria for neurofibromatosis 2
Highlights of This Issue
In Memoriam: Charles J. Epstein, MD
College News
High-resolution methylation polymerase chain reaction for fragile X analysis: Evidence for novel FMR1 methylation patterns undetected in Southern blot analyses
A randomized controlled trial of genotype-based Coumadin initiation
Compliance with periodic surveillance for Von-Hippel-Lindau disease
Natural history of Danon disease
Beyond the first trimester screen: Can we predict who will choose invasive testing?
Informed consent to microsatellite instability and immunohistochemistry screening for Lynch syndrome
Reflex fluorescent in situ hybridization testing for unsuccessful product of conception cultures: A retrospective analysis of 5555 samples attempted by conventional cytogenetics and fluorescent in sit
Secretary's Advisory Committee on Heritable Disorders in Newborns and Children response to the President's Council on Bioethics report: The changing moral focus of newborn screening
Autism spectrum disorders—A genetics review
Underutilization of BRCA1/2 testing to guide breast cancer treatment: Black and Hispanic women particularly at risk
Family communication matters: The impact of telling relatives about unclassified variants and uninformative DNA-test results
Familial Mediterranean fever—A review
College News
Highlights of This Issue
Finnish familial Meniere disease is not linked to chromosome 12p12.3, and anticipation and cosegregation with migraine are not common findings Finnish
Looking ahead, looking behind
Clinical validation of cutoff target ranges in newborn screening of metabolic disorders by tandem mass spectrometry: A worldwide collaborative project
Global analysis of disease-related DNA sequence variation in 10 healthy individuals: Implications for whole genome-based clinical diagnostics
Unifying cancer genetics
Public health genomics: The end of the beginning
Diagnosis and management of familial Mediterranean fever: Integrating medical genetics in a dedicated interdisciplinary clinic
The advent of personal genome sequencing
Downsizing genomic medicine: Approaching the ethical complexity of whole-genome sequencing by starting small
The American College of Medical Genetics, the first 20 years
Quality improvement of newborn screening in real time
Early-onset seizures due to mosaic exonic deletions of CDKL5 in a male and two females
Risk and uncertainty: Shifting decision making for aneuploidy screening to the first trimester of pregnancy
News Briefs
College News
Response to Plon et al.—Genetic testing and cancer risk management recommendations by physicians for at-risk relatives
Copy number variation in the dosage-sensitive 16p11.2 interval accounts for only a small proportion of autism incidence: A systematic review and meta-analysis
How does a simple enquiry compare to a detailed family history questionnaire to identify coronary heart disease or diabetic familial risk?
von Willebrand disease
A grand challenge: Providing benefits of clinical genetics to those in need
Array comparative genomic hybridization analysis in patients with anophthalmia, microphthalmia, and coloboma
Impact of presymptomatic genetic testing for familial amyotrophic lateral sclerosis
Genetics and genomics education: The next generation
Next generation massively parallel sequencing of targeted exomes to identify genetic mutations in primary ciliary dyskinesia: Implications for application to clinical testing
Patient reactions to personalized medicine vignettes: An experimental design
Medical and graduate students' attitudes toward personal genomics
Evidence for the toxicity of bidirectional transcripts and mitochondrial dysfunction in blood associated with small CGG expansions in the FMR1 gene in patients with parkinsonism
How well does family history predict who will get colorectal cancer? Implications for cancer screening and counseling
Changes to perceptions of the pros and cons of genetic susceptibility testing after APOE genotyping for Alzheimer disease risk
Recurrence of perinatal lethal osteogenesis imperfecta in sibships: Parsing the risk between parental mosaicism for dominant mutations and autosomal recessive inheritance
Integrated analysis of unclassified variants in mismatch repair genes
Direct-to-consumer genetic testing: An assessment of genetic counselors' knowledge and beliefs
Genetic risk estimation in the Coriell Personalized Medicine Collaborative
Large-scale population screening for spinal muscular atrophy: Clinical implications
Prospective validation of quantitative fluorescent polymerase chain reaction for rapid detection of common aneuploidies
Genetic testing and cancer risk management recommendations by physicians for at-risk relatives
Novel MLH1 duplication identified in Colombian families with Lynch syndrome
Idursulfase treatment of Hunter syndrome in children younger than 6 years: Results from the Hunter Outcome Survey
Horizon scanning for new genomic tests
Alpha-thalassemia
A review of economic evaluations of genetic testing services and interventions (2004–2009)
Reviewer Acknowledgment
College News
Highlights of This Issue
Response to clinical and genetic aspects of Ehlers-Danlos syndrome, classic type
Reply to the letter to the editor by Marc Williams
Who should be tested for thrombophilia?
Making a definitive diagnosis: Successful clinical application of whole exome sequencing in a child with intractable inflammatory bowel disease
A timely arrival for genomic medicine
The impact of human gene patents on genetic testing in the United Kingdom
Components of family history associated with women's disease perceptions for cancer: A report from the Family Healthware™ Impact Trial
Long-term, open-labeled extension study of idursulfase in the treatment of Hunter syndrome
Teaching with single nucleotide polymorphisms: Learning the right lessons
FMR1 premutation carrier frequency in patients undergoing routine population-based carrier screening: Insights into the prevalence of fragile X syndrome, fragile X-associated tremor/ataxia syndrome, a
Factor V Leiden thrombophilia
A comparison of molecular and cytogenetic techniques for the diagnosis of pregnancy loss
Cystic fibrosis testing 8 years on: Lessons learned from carrier screening and sequencing analysis
Unleashing the power of human genetic variation knowledge: New Zealand stakeholder perspectives
Lessons learned from the introduction of personalized genotyping into a medical school curriculum
Primary care physicians' experience with family history: An exploratory qualitative study
Tracing the use and source of racial terminology in representations of genetic research
Research use of leftover newborn bloodspots: Attitudes of Canadian geneticists regarding storage and informed consent requirements
Regulating direct-to-consumer genetic tests: What is all the fuss about?
Impact of communicating personalized genetic risk information on perceived control over the risk: A systematic review