Genetics in Medicine - 2009

138 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Section E6.5 of the ACMG technical standards and guidelines: Chromosome studies for solid tumor abnormalities
Genotype to phenotype—discovery and characterization of novel genomic disorders in a “genotype-first” era
Pseudoxanthoma elasticum: Wide phenotypic variation in homozygotes and no signs in heterozygotes for the c.3775delT mutation in ABCC6
Variability in interpreting and reporting copy number changes detected by array-based technology in clinical laboratories
Translation of research discoveries to clinical care in arrhythmogenic right ventricular cardiomyopathy in Newfoundland and Labrador: Lessons for health policy in genetic disease
Lessons from arrhythmogenic right ventricular cardiomyopathy research
Long-term speech and language developmental issues among children with Duarte galactosemia
Realizing the potential of genomics: Translation is not translational research
Multiple endocrine neoplasia type 1 (MEN1): Not only inherited endocrine tumors
“Am I my genes?”: Questions of identity among individuals confronting genetic disease
Translation research is an essential but not sufficient ingredient for translation of genomic medicine into population health benefits
Capturing all disease-causing mutations for clinical and research use: Toward an effortless system for the Human Variome Project
Erratum
College News
Genotype–phenotype analysis of TCF4 mutations causing Pitt-Hopkins syndrome shows increased seizure activity with missense mutations
A comparison of male attendees and nonattendees at a familial cancer clinic
Immunohistochemistry staining for the mismatch repair proteins in the clinical care of patients with colorectal cancer
FG syndrome, an X-linked multiple congenital anomaly syndrome: The clinical phenotype and an algorithm for diagnostic testing
The Origin
A gene dosage map of Chromosome 18: A map with clinical utility
Evaluation of a breast/ovarian cancer genetics referral screening tool in a mammography population
Life expectancy and cause of death in males and females with Fabry disease: Findings from the Fabry Registry
Screening for fetal aneuploidy and neural tube defects
PTEN hamartoma tumor syndrome: An overview
Disentangling the Babylonian speech confusion in genetic counseling: An analysis of the reliability and validity of the nomenclature for BRCA1/2 DNA-test results other than pathogenic
Impact of false-positive newborn metabolic screening results on early health care utilization
Reply to “Practice guidelines for short stature”
Erratum: ACMG practice guideline: Genetic evaluation of short stature: Erratum
Use of complementary and alternative medicine by patients with lysosomal storage diseases
Endothelial nitric oxide synthase gene polymorphisms and diabetic nephropathy: A HuGE review and meta-analysis
The ethical use of existing samples for genome research
Breast cancer risk communication: Assessment of primary care physicians by standardized patients
Communication, encouragement, and cancer screening in families with and without mutations for hereditary nonpolyposis colorectal cancer: A pilot study
Factors associated with preimplantation genetic diagnosis acceptance among women concerned about hereditary breast and ovarian cancer
To the Editor
Use of Factor V Leiden genetic testing in practice and impact on management
Comparative effectiveness research and genomic medicine: An evolving partnership for 21st century medicine
Barriers to the use of genetic testing: A study of racial and ethnic disparities
Diagnosis of miscarriages by molecular karyotyping: Benefits and pitfalls
Neurofibromatosis 2 [Bilateral acoustic neurofibromatosis, central neurofibromatosis, NF2, neurofibromatosis type II]
Conference report: Second conference of the Middle East and North Africa newborn screening initiative: Partnerships for sustainable newborn screening infrastructure and research opportunities
Timing of BRCA1/BRCA2 genetic testing in women with ovarian cancer
Patient education and informed consent for preimplantation genetic diagnosis: Health literacy for genetics and assisted reproductive technology
Hands down: Reflecting on the 50th anniversary of the description of Trisomy 21
Reply to letter from Drs. Ledbetter, Saul, and Moeschler
Down syndrome: The crucible for treating genomic imbalance
Technical standards and guidelines: Prenatal screening for Down syndrome that includes first-trimester biochemistry and/or ultrasound measurements
Cost-effectiveness of population-based BRCA1/2 testing and ovarian cancer prevention for Ashkenazi Jews: A call for dialogue Ashkenazi Jews
The 50th anniversary of the discovery of trisomy 21: The past, present, and future of research and treatment of Down syndrome
Comments on the “genotype first diagnosis” controversy
Population-based BRCA1/BRCA2 screening in Ashkenazi Jews: A call for evidence Ashkenazi Jews
The Scientific Foundation for Personal Genomics: Recommendations from a National Institutes of Health–Centers for Disease Control and Prevention Multidisciplinary Workshop
Health care provider and consumer awareness, perceptions, and use of direct-to-consumer personal genomic tests, United States, 2008
Characteristics of users of online personalized genomic risk assessments: Implications for physician-patient interactions
Erratum
Personalized medicine and disruptive innovation: Implications for technology assessment
Personal utility and genomic information: Look before you leap
Direct to consumer genetic testing: Avoiding a culture war
Evaluation of risk prediction updates from commercial genome-wide scans
Erratum
Evaluating the utility of personal genomic information
Low adherence to national guidelines for thyroid screening in Down syndrome
Clinical and genetic aspects of primary ciliary dyskinesia/Kartagener syndrome
Long-term monitoring of patients with infantile-onset Pompe disease on enzyme replacement therapy using a urinary glucose tetrasaccharide biomarker
Technical standards and guidelines for myotonic dystrophy type 1 testing
Are electronic health records ready for genomic medicine?
Distress and burnout among genetic service providers
The current state of cancer family history collection tools in primary care: a systematic review
A commentary on the President's Council on Bioethics report: the changing moral focus of newborn screening
Application of dual-genome oligonucleotidearray-based comparative genomic hybridization to the molecular diagnosis of mitochondrial DNA deletion and depletion syndromes
The Genomic Applications in Practice and Prevention Network
Racial differences in the interaction between family history and risk factors associated with diabetes in the National Health and Nutritional Examination Survey, 1999–2004
Newborn dried bloodspot screening: mapping the clinical and public health components and activities
The nonmotile ciliopathies
A 4-year study of the efficacy and tolerability of enzyme replacement therapy with agalsidase alfa in 36 women with Fabry disease
Newborn screening as a system from birth through lifelong care
ACMG practice guideline: Genetic evaluation of short stature
The emerging role of genetics professionals in forensic kinship DNA identification after a mass fatality: lessons learned from Hurricane Katrina volunteers
Attendance of men at the familial cancer clinic: what they value from the consultation
Miglustat in late-onset Tay-Sachs disease: a 12-month, randomized, controlled clinical study with 24 months of extended treatment
Osteogenesis imperfecta: Recent findings shed new light on this once well-understood condition
Emergency preparedness for newborn screening and genetic services
CD14 C-260T gene polymorphism and ischemic heart disease susceptibility: A HuGE review and meta-analysis
The long-term outcomes of presymptomatic infants transplanted for Krabbe disease: Report of the workshop held on July 11 and 12, 2008, Holiday Valley, New York
Commentary on: “Newborn screening for Krabbe Disease: the New York state model” and “The long-term outcomes of presymptomatic infants transplanted for Krabbe disease. A report of the workshop held on
Expanded newborn screening in Puerto Rico and the US Virgin Islands: education and barriers assessment
Developing a National Registry for conditions identifiable through newborn screening
Targeted comparative genomic hybridization array for the detection of single- and multiexon gene deletions and duplications
Interest in genetic testing among affected men from hereditary prostate cancer families and their unaffected male relatives
Transillumination of the fingers for vascular anomalies: a novel method for evaluating hereditary hemorrhagic telangiectasia
Response to Saul and Moeschler “How best to use CGH arrays in the clinical setting”
Dynamic modification strategy of the Israeli prenatal carrier screening protocol: inclusion of the oriental Jewish group to the cystic fibrosis panel—update oriental Jewish
Expanded newborn screening in Texas: a survey and educational module addressing the knowledge of pediatric residents
Mitochondrial DNA deletion and sarcopenia
AsktheGeneticistSM: five years of online experience
Smith-Lemli-Opitz syndrome and inborn errors of cholesterol synthesis: summary of the 2007 SLO/RSH Foundation scientific conference sponsored by the National Institutes of Health
Retention of medical genetics knowledge and skills by medical students
Impact of genotype-first diagnosis: the detection of microdeletion and microduplication syndromes with cancer predisposition by aCGH
Highlights in this Issue
Clinical outcomes after long-term treatment with alglucosidase alfa in infants and children with advanced Pompe disease
The association between family history of asthma and the prevalence of asthma among US adults: National Health and Nutrition Examination Survey, 1999–2004
How best to use CGH arrays in the clinical setting
An empirical comparison of meta-analyses of published gene-disease associations versus consortium analyses
Validation of Fanconi anemia complementation Group A assignment using molecular analysis
Diagnostic criteria and tumor screening for individuals with isolated hemihyperplasia
Verification of consumers' experiences and perceptions of genetic discrimination and its impact on utilization of genetic testing
Factors influencing parental decision about genetics evaluation for their deaf or hard-of-hearing child
Physicians' attitudes toward race, genetics, and clinical medicine
Utilization of genetic counseling after diagnosis of a birth defect—trends over time and variables associated with utilization
The interface of Medicare coverage decision-making and emerging molecular-based laboratory testing
HFE-associated hereditary hemochromatosis
The impact of patents on the development of genome-based clinical diagnostics: an analysis of case studies
Array CGH in patients with learning disability (mental retardation) and congenital anomalies: updated systematic review and meta-analysis of 19 studies and 13,926 subjects
Prevalence and nonrandom distribution of exonic mutations in interferon regulatory factor 6 in 307 families with Van der Woude syndrome and 37 families with popliteal pterygium syndrome
Evaluation of a low dose, after a standard therapeutic dose, of agalsidase beta during enzyme replacement therapy in patients with Fabry disease
Genetic testing for melanoma risk: a prospective cohort study of uptake and outcomes among Australian families
Veterans' attitudes regarding a database for genomic research
Gene prioritization based on biological plausibility over genome wide association studies renders new loci associated with type 2 diabetes
Is there evidence for neuropsychological and neurobehavioral phenotypes among adults without FXTAS who carry the FMR1 premutation? A review of current literature
Guidelines for the prenatal diagnosis of fetal skeletal dysplasias
Dose-response relationships for enzyme replacement therapy with imiglucerase/alglucerase in patients with Gaucher disease type 1
The prevalence of PTEN mutations in a clinical pediatric cohort with autism spectrum disorders, developmental delay, and macrocephaly
Mitochondrial DNA analysis by multiplex denaturing high-performance liquid chromatography and selective sequencing in pediatric patients with cardiomyopathy
Dosing enzyme replacement therapy for Gaucher disease: older, but are we wiser?
College News
New at GeneTests
Dynamic modification strategy of the Israeli carrier screening protocol: inclusion of the Oriental Jewish Group to the cystic fibrosis panel
Barriers to adopting genomics into public health education: a mixed methods study
Multiple myeloma and Gaucher genes
EGAPP supplementary evidence review: DNA testing strategies aimed at reducing morbidity and mortality from Lynch syndrome
Can UGT1A1 genotyping reduce morbidity and mortality in patients with metastatic colorectal cancer treated with irinotecan? An evidence-based review
Reviewer Acknowledgment
Recommendations from the EGAPP Working Group: genetic testing strategies in newly diagnosed individuals with colorectal cancer aimed at reducing morbidity and mortality from Lynch syndrome in relative
Challenges and opportunities for evidence-based genetics practice
Recommendations from the EGAPP Working Group: can tumor gene expression profiling improve outcomes in patients with breast cancer?
The Evaluation of Genomic Applications in Practice and Prevention (EGAPP) initiative: methods of the EGAPP Working Group
Recommendations from the EGAPP Working Group: can UGT1A1 genotyping reduce morbidity and mortality in patients with metastatic colorectal cancer treated with irinotecan?
Erratum