European Journal of Human Genetics - 2012

318 articles | Last updated: 2025-12-03 14:12:56
Caucasian
1
White
0
European
3
Other
3
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Genetic characterization of northeastern Italian population isolates in the context of broader European genetic diversity European genetic diversity
Next-generation sequencing meets genetic diagnostics: development of a comprehensive workflow for the analysis of BRCA1 and BRCA2 genes
Public attitudes towards genetic testing revisited: comparing opinions between 2002 and 2010
Genomic correlates of variability in immune response to an oral cholera vaccine
Genes identified in Asian SLE GWASs are also associated with SLE in Caucasian populations
A compound heterozygous mutation in DPAGT1 results in a congenital disorder of glycosylation with a relatively mild phenotype
Clinical utility gene card for: Dilated Cardiomyopathy (CMD)
Abnormal XPD-induced nuclear receptor transactivation in DNA repair disorders: trichothiodystrophy and xeroderma pigmentosum
Symptomatic lipid storage in carriers for the PNPLA2 gene
Frequency and characterization of DNA methylation defects in children born SGA
A mosaic maternal splice donor mutation in the EHMT1 gene leads to aberrant transcripts and to Kleefstra syndrome in the offspring
Mitochondrial myopathy associated with a novel 5522G>A mutation in the mitochondrial tRNATrp gene
Report of four new patients with protein-truncating mutations in C6orf221/KHDC3L and colocalization with NLRP7
Angiogenetic axis angiopoietins/Tie2 and VEGF in familial breast cancer
A guide to cancer genetics in clinical practice
The EuroGentest Clinical Utility Gene Cards continued
Erratum: Publics and biobanks: Pan-European diversity and the challenge of responsible innovation
Two novel mutations of the GTP cyclohydrolase 1 gene and genotype–phenotype correlation in Chinese Dopa-responsive dystonia patients
Refining genome-wide linkage intervals using a meta-analysis of genome-wide association studies identifies loci influencing personality dimensions
Craniofacial characteristics of fragile X syndrome in mouse and man
Deep-intronic ATM mutation detected by genomic resequencing and corrected in vitro by antisense morpholino oligonucleotide (AMO)
Low prevalence of SLX4 loss-of-function mutations in non-BRCA1/2 breast and/or ovarian cancer families
Genetic ancestry inference using support vector machines, and the active emergence of a unique American population
Chromosomal microarray analysis as a first-line test in pregnancies with a priori low risk for the detection of submicroscopic chromosomal abnormalities
Phenotypic variant of Brachydactyly-mental retardation syndrome in a family with an inherited interstitial 2q37.3 microdeletion including HDAC4
Spanish regulatory approach for Biobanking
A gene-centric analysis of activated partial thromboplastin time and activated protein C resistance using the HumanCVD focused genotyping array
Non-invasive prenatal testing for single gene disorders: exploring the ethics
Changing facial phenotype in Cohen syndrome: towards clues for an earlier diagnosis
Genome-wide paternal uniparental disomy mosaicism in a woman with Beckwith–Wiedemann syndrome and ovarian steroid cell tumour
Clinical utility gene card for: Rothmund–Thomson syndrome
In vitro antisense therapeutics for a deep intronic mutation causing Neurofibromatosis type 2
Can manipulation of splicing offer gene therapy possibilities to those with tumour-prone disorders?
A new double substitution mutation in the MEN1 gene: a limited penetrance and a specific phenotype
A tiered-layered-staged model for informed consent in personal genome testing
The perspective from EASAC and FEAM on direct-to-consumer genetic testing for health-related purposes
Analysis of the effects of rare variants on splicing identifies alterations in GABAA receptor genes in autism spectrum disorder individuals
A focus group study on breast cancer risk presentation: one format does not fit all
Wilms’ tumor in patients with 9q22.3 microdeletion syndrome suggests a role for PTCH1 in nephroblastomas
Genomic analysis of Meckel–Gruber syndrome in Arabs reveals marked genetic heterogeneity and novel candidate genes
The experience of 3 years of external quality assessment of preimplantation genetic diagnosis for cystic fibrosis
How can ethics relate to science? The case of stem cell research
The next controversy in genetic testing: clinical data as trade secrets?
Statistical tests for detecting associations with groups of genetic variants: generalization, evaluation, and implementation
SHAVE: shrinkage estimator measured for multiple visits increases power in GWAS of quantitative traits
Dynamin 2 homozygous mutation in humans with a lethal congenital syndrome
Black Swans and Bell Curves
Authors muscle in on history: The History of a Genetic Disease Duchenne Muscular Dystrophy or Meryon's disease
Deeper than the skin: Genetic Skin Disorders
Severe SMA mice show organ impairment that cannot be rescued by therapy with the HDACi JNJ-26481585
Clinical and molecular cross-sectional study of a cohort of adult type III spinal muscular atrophy patients: clues from a biomarker study
CLCA4 variants determine the manifestation of the cystic fibrosis basic defect in the intestine
The 2q37-deletion syndrome: an update of the clinical spectrum including overweight, brachydactyly and behavioural features in 14 new patients
Low-copy repeats at the human VIPR2 gene predispose to recurrent and nonrecurrent rearrangements
Clinical Utility Gene Card for: incontinentia pigmenti
A novel missense mutation in ANO5/TMEM16E is causative for gnathodiaphyseal dyplasia in a large Italian pedigree
Clinical Utility Gene Card for: campomelic dysplasia
An atypical Dent’s disease phenotype caused by co-inheritance of mutations at CLCN5 and OCRL genes
Prioritising risk pathways of complex human diseases based on functional profiling
Increased rate of missense/in-frame mutations in individuals with NF1-related pulmonary stenosis: a novel genotype–phenotype correlation
The role of GHR and IGF1 genes in the genetic determination of African pygmies’ short stature
Germ-line CAG repeat instability causes extreme CAG repeat expansion with infantile-onset spinocerebellar ataxia type 2
Genome-wide linkage analysis is a powerful prenatal diagnostic tool in families with unknown genetic defects
Vascular and connective tissue anomalies associated with X-linked periventricular heterotopia due to mutations in Filamin A
Clinical utility gene card for: familial polycythaemia vera
Application of custom-designed oligonucleotide array CGH in 145 patients with autistic spectrum disorders
Reply to Brodehl et al
Functional characterization of desmin mutant p.P419S
Familial cosegregation of rare genetic variants with disease in complex disorders
Clinical utility gene card for: osteogenesis imperfecta
Erratum: Clinical utility gene card for: Glanzmann thrombasthenia
EMQN/CMGS best practice guidelines for the molecular genetic testing of Huntington disease
A familial case of alveolar capillary dysplasia with misalignment of pulmonary veins supports paternal imprinting of FOXF1 in human
Refractory epilepsy and mitochondrial dysfunction due to GM3 synthase deficiency
Next-generation sequencing (NGS) as a diagnostic tool for retinal degeneration reveals a much higher detection rate in early-onset disease
Incomplete segregation of MYH11 variants with thoracic aortic aneurysms and dissections and patent ductus arteriosus
14q12 microdeletions excluding FOXG1 give rise to a congenital variant Rett syndrome-like phenotype
Public support and consent preference for biomedical research and biobanking in Jordan
Expanding the MTM1 mutational spectrum: novel variants including the first multi-exonic duplication and development of a locus-specific database
Low-density lipoprotein receptor mutations generate synthetic genome-wide associations
Contemporary paternal genetic landscape of Polish and German populations: from early medieval Slavic expansion to post-World War II resettlements
Clinical utility gene card for: Pseudohypoparathyroidism
Genetic heterogeneity in Finnish hereditary prostate cancer using ordered subset analysis
High prevalence of occult paragangliomas in asymptomatic carriers of SDHD and SDHB gene mutations
Stronger signal of recent selection for lactase persistence in Maasai than in Europeans Europeans
Genetic variant in the telomerase gene modifies cancer risk in Lynch syndrome
Expanding the spectrum of TUBA1A-related cortical dysgenesis to Polymicrogyria
Molecular alterations and expression of succinate dehydrogenase complex in wild-type KIT/PDGFRA/BRAF gastrointestinal stromal tumors
Maternal ABCA1 genotype is associated with severity of Smith–Lemli–Opitz syndrome and with viability of patients homozygous for null mutations
AKT1 fails to replicate as a longevity-associated gene in Danish and German nonagenarians and centenarians Danish and German
A novel locus for autosomal dominant cone-rod dystrophy maps to chromosome 10q
The frequency of an IL-18-associated haplotype in Africans Africans
Connective tissue spectrum abnormalities associated with spontaneous cerebrospinal fluid leaks: a prospective study
Genetic perspectives on the origin of clicks in Bantu languages from southwestern Zambia
Rare DNA copy number variants in cardiovascular malformations with extracardiac abnormalities
WikiGWA: an open platform for collecting and using genome-wide association results
Dilution of candidates: the case of iron-related genes in restless legs syndrome
A rare variant in the osteoarthritis-associated locus GDF5 is functional and reveals a site that can be manipulated to modulate GDF5 expression
Dual copy number variants involving 16p11 and 6q22 in a case of childhood apraxia of speech and pervasive developmental disorder
Fine mapping of whole RB1 gene deletions in retinoblastoma patients confirms PCDH8 as a candidate gene for psychomotor delay
Childhood Apraxia of Speech (CAS) in two patients with 16p11.2 microdeletion syndrome
Utilizing extended pedigree information for discovery and confirmation of copy number variable regions among Mexican Americans
All you ever wanted to know about teratogens and more
Erratum: Identification and characterization of two novel JARID1C mutations: suggestion of an emerging genotype-phenotype correlation
Erratum: Preimplantation genetic diagnosis (PGD) for Huntington’s disease: the experience of three European centres European centres
Quality in genetic counselling for presymptomatic testing — clinical guidelines for practice across the range of genetic conditions
The genetic landscape of Equatorial Guinea and the origin and migration routes of the Y chromosome haplogroup R-V88
Intentions to receive individual results from whole-genome sequencing among participants in the ClinSeq study
Newborn screening for cystic fibrosis: Polish 4 years’ experience with CFTR sequencing strategy
Detecting genetic variants for extreme aging using multiple data sources
Clinical utility gene card for: Lynch syndrome (MLH1, MSH2, MSH6, PMS2, EPCAM) - update 2012
Prevalence of SHANK3 variants in patients with different subtypes of autism spectrum disorders
Clinical utility gene card for: Ehlers–Danlos syndrome types I–VII and variants - update 2012
Missense mutation in the ATPase, aminophospholipid transporter protein ATP8A2 is associated with cerebellar atrophy and quadrupedal locomotion
Novel mutations in the sarcomeric protein myopalladin in patients with dilated cardiomyopathy
Evidence from Y-chromosome analysis for a late exclusively eastern expansion of the Bantu-speaking people
Copy number analysis of 413 isolated talipes equinovarus patients suggests role for transcriptional regulators of early limb development
Identification of SNPs in the cystic fibrosis interactome influencing pulmonary progression in cystic fibrosis
Analyzing age-specific genetic effects on human extreme age survival in cohort-based longitudinal studies
Detection of copy-number variation in AUTS2 gene by targeted exonic array CGH in patients with developmental delay and autistic spectrum disorders
Clinical utility gene card for: MUTYH-associated polyposis (MAP), Autosomal recessive colorectal adenomatous polyposis, Multiple colorectal adenomas, Multiple adenomatous polyps (MAP) - update 2012
FTO levels affect RNA modification and the transcriptome
The CDKL5 disorder is an independent clinical entity associated with early-onset encephalopathy
The importance of E-cadherin binding partners to evaluate the pathogenicity of E-cadherin missense mutations associated to HDGC
16p11.2–p12.2 duplication syndrome; a genomic condition differentiated from euchromatic variation of 16p11.2
Crossing the boundary between research and health care: P3G policy statement on return of results from population studies
Erratum: Mutations in the mitochondrial tRNASer(AGY) gene are associated with deafness, retinal degeneration, myopathy and epilepsy
NF-κB signalling requirement for brain myelin formation is shown by genotype/MRI phenotype correlations in patients with Xq28 duplications
A novel LRSAM1 mutation is associated with autosomal dominant axonal Charcot-Marie-Tooth disease
Using identity by descent estimation with dense genotype data to detect positive selection
A unique MSH2 exon 8 deletion accounts for a major portion of all mismatch repair gene mutations in Lynch syndrome families of Sardinian origin Sardinian origin
Novel findings in patients with primary hyperoxaluria type III and implications for advanced molecular testing strategies
Adaptive clustering and adaptive weighting methods to detect disease associated rare variants
Atrioventricular canal defect in patients with RASopathies
Personalized medicine and access to health care: potential for inequitable access?
A novel mitochondrial tRNA Arg mutation resulting in an anticodon swap in a patient with mitochondrial encephalomyopathy
Identification of homozygous WFS1 mutations (p.Asp211Asn, p.Gln486*) causing severe Wolfram syndrome and first report of male fertility
Smoothed functional principal component analysis for testing association of the entire allelic spectrum of genetic variation
When access is an issue: exploring barriers to predictive testing for Huntington disease in British Columbia, Canada
Clinical utility gene card for: Glanzmann thrombasthenia
Population studies: return of research results and incidental findings Policy Statement
Do regulatory regions matter in FOXG1 duplications?
Variable imprinting of the MEST gene in human preimplantation embryos
Haplotype analysis of the 185delAG BRCA1 mutation in ethnically diverse populations
MLH1 methylation screening is effective in identifying epimutation carriers
Increased corpus callosum volume in children with chromosome 22q11.2 deletion syndrome is associated with neurocognitive deficits and genetic polymorphisms
A variant in the carboxyl-terminus of connexin 40 alters GAP junctions and increases risk for tetralogy of Fallot
A newly identified locus for benign adult familial myoclonic epilepsy on chromosome 3q26.32-3q28
12p13.33 microdeletion including ELKS/ERC1, a new locus associated with childhood apraxia of speech
Improvement of interpretation in cystic fibrosis clinical laboratory reports: longitudinal analysis of external quality assessment data
Developing a policy for paediatric biobanks: principles for good practice
A germline or de novo mutation in two families with Gaucher disease: implications for recessive disorders
Hierarchical clustering analysis of blood plasma lipidomics profiles from mono- and dizygotic twin families
Small effective population size and genetic homogeneity in the Val Borbera isolate
Bardet–Biedl syndrome
Screening of human pluripotent stem cells using CGH and FISH reveals low-grade mosaic aneuploidy and a recurrent amplification of chromosome 1q
Twenty-year trends in the prevalence of Down syndrome and other trisomies in Europe: impact of maternal age and prenatal screening
Toward a roadmap in global biobanking for health
Quality assurance practices in Europe: a survey of molecular genetic testing laboratories
To tell or not to tell? A systematic review of ethical reflections on incidental findings arising in genetics contexts
Novel VCAN mutations and evidence for unbalanced alternative splicing in the pathogenesis of Wagner syndrome
Inherited ichthyoses/generalized Mendelian disorders of cornification
Genetic analysis of SIGMAR1 as a cause of familial ALS with dementia
Can (should) molecular diagnostic labs improve the quality of their services?
14q12 and severe Rett-like phenotypes: new clinical insights and physical mapping of FOXG1-regulatory elements
RNA-Seq and human complex diseases: recent accomplishments and future perspectives
Ehlers–Danlos syndrome type VIII is clinically heterogeneous disorder associated primarily with periodontal disease, and variable connective tissue features
Inferring separate parental admixture components in unknown DNA samples using autosomal SNPs
Erratum: Low prevalence of lactase persistence in Neolithic South-West Europe
Impact of common regulatory single-nucleotide variants on gene expression profiles in whole blood
Aniridia
Agenesis of the corpus callosum and gray matter heterotopia in three patients with constitutional mismatch repair deficiency syndrome
The C9ORF72 expansion mutation is a common cause of ALS+/−FTD in Europe and has a single founder
An urgent need for a change in policy revealed by a study on prenatal testing for Duchenne muscular dystrophy
Expanded spectrum of Pelizaeus–Merzbacher-like disease: literature revision and description of a novel GJC2 mutation in an unusually severe form
Publics and biobanks: Pan-European diversity and the challenge of responsible innovation
Intravitreal delivery of AAV-NDI1 provides functional benefit in a murine model of Leber hereditary optic neuropathy
Partial deletion of GLRB and GRIA2 in a patient with intellectual disability
REGENT: a risk assessment and classification algorithm for genetic and environmental factors
A novel missense mutation in the signal peptide of the human POMC gene: a possible additional link between early-onset type 2 diabetes and obesity
Meta-analysis of genetic association studies under heterogeneity
Best practice guidelines and recommendations on the molecular diagnosis of myotonic dystrophy types 1 and 2
Analytical and simulation methods for estimating the potential predictive ability of genetic profiling: a comparison of methods and results
Copy number variation in patients with cervical artery dissection
Efficiency of trans-ethnic genome-wide meta-analysis and fine-mapping
Effect of mutations in XPD(ERCC2) on pregnancy and prenatal development in mothers of patients with trichothiodystrophy or xeroderma pigmentosum
Clinical utility gene card for: Centronuclear and myotubular myopathies
Phenotypic spectrum and genotype–phenotype correlations of NRXN1 exon deletions
Variants in the 3′UTR of SNCA do not affect miRNA-433 binding and alpha-synuclein expression
Haploinsufficiency of CELF4 at 18q12.2 is associated with developmental and behavioral disorders, seizures, eye manifestations, and obesity
Erratum: Imaging genetics of FOXP2 in dyslexia
Association between the 2-bp deletion polymorphism in the duplicated version of the alpha7 nicotinic receptor gene and P50 sensory gating
Genetic investigation of FOXO3A requires special attention due to sequence homology with FOXO3B
Distinguishing the co-ancestries of haplogroup G Y-chromosomes in the populations of Europe and the Caucasus
Clinical utility gene card for: Familial Hypobetalipoproteinaemia (APOB)
The role of renin–angiotensin–aldosterone system polymorphisms in phenotypic expression of MYBPC3-related hypertrophic cardiomyopathy
PITX2 and FOXC1 spectrum of mutations in ocular syndromes
CNVs leading to fusion transcripts in individuals with autism spectrum disorder
Community of protein complexes impacts disease association
TRAPPC9-related autosomal recessive intellectual disability: report of a new mutation and clinical phenotype
A novel homozygous p.Arg527Leu LMNA mutation in two unrelated Egyptian families causes overlapping mandibuloacral dysplasia and progeria syndrome
De novo microduplication of the FMR1 gene in a patient with developmental delay, epilepsy and hyperactivity
Cardiomyopathy in patients with POMT1-related congenital and limb-girdle muscular dystrophy
Attitudes of general practitioners and midwives towards ethnicity-based haemoglobinopathy-carrier screening
Autosomal dominant late-onset spinal motor neuronopathy is linked to a new locus on chromosome 22q11.2-q13.2
Symptom dimensions as alternative phenotypes to address genetic heterogeneity in schizophrenia and bipolar disorder
Genome-wide scan with nearly 700 000 SNPs in two Sardinian sub-populations suggests some regions as candidate targets for positive selection
Mini-haplotypes as lineage informative SNPs and ancestry inference SNPs
Afghanistan from a Y-chromosome perspective
Quantifying harmful mutations in human populations
Clinical utility gene card for: Nemaline myopathy
Clinical utility gene card for: proximal spinal muscular atrophy
Comprehensive oligonucleotide array-comparative genomic hybridization analysis: new insights into the molecular pathology of the DMD gene
Sampling strategies for rare variant tests in case–control studies
Clinical utility gene card for: Leri-Weill dyschondrosteosis (LWD) and Langer mesomelic dysplasia (LMD)
Pathway-based genome-wide association analysis of coronary heart disease identifies biologically important gene sets
Erratum: Autism multiplex family with 16p11.2p12.2 microduplication syndrome in monozygotic twins and distal 16p11.2 deletion in their brother
Is there a Mendelian transmission ratio distortion of the c.429_452dup(24bp) polyalanine tract ARX mutation?
Concomitant Brugada-like and short QT electrocardiogram linked to SCN5A mutation
De novo and inherited CNVs in MZ twin pairs selected for discordance and concordance on Attention Problems
Novel homozygous, heterozygous and hemizygous FRMD7 gene mutations segregated in the same consanguineous family with congenital X-linked nystagmus
Meta-analyses of genome-wide linkage scans of anxiety-related phenotypes
PDGFRa mutations in humans with isolated cleft palate
Van Maldergem syndrome: further characterisation and evidence for neuronal migration abnormalities and autosomal recessive inheritance
The phenotype associated with a large deletion on MECP2
Non-invasive prenatal diagnosis for fetal sex determination: benefits and disadvantages from the service users’ perspective
Lactose malabsorption is a risk factor for decreased bone mineral density in pancreatic insufficient cystic fibrosis patients
Unravelling fears of genetic discrimination: an exploratory study of Dutch HCM families in an era of genetic non-discrimination acts
The changing landscape of genetic testing and its impact on clinical and laboratory services and research in Europe
Expression QTL analysis of top loci from GWAS meta-analysis highlights additional schizophrenia candidate genes
Promoter alteration causes transcriptional repression of the POMGNT1 gene in limb-girdle muscular dystrophy type 2O
A family-based association test to detect gene–gene interactions in the presence of linkage
A genome-wide search for linkage to allergic rhinitis in Danish sib-pair families
Neonatal progeria: increased ratio of progerin to lamin A leads to progeria of the newborn
Autosomal dominant myofibrillar myopathy with arrhythmogenic right ventricular cardiomyopathy 7 is caused by a DES mutation
A 600 kb triplication in the cat eye syndrome critical region causes anorectal, renal and preauricular anomalies in a three-generation family
Male and female differential reproductive rate could explain parental transmission asymmetry of mutation origin in Hirschsprung disease
Alu-mediated deletion of SOX10 regulatory elements in Waardenburg syndrome type 4
Mutations in the mitochondrial tRNASer(AGY) gene are associated with deafness, retinal degeneration, myopathy and epilepsy
SNP array-based copy number and genotype analyses for preimplantation genetic diagnosis of human unbalanced translocations
Clinical utility gene card for: Biotinidase deficiency
DNA replication is altered in Immunodeficiency Centromeric instability Facial anomalies (ICF) cells carrying DNMT3B mutations
Diagnosis by sequencing: correction of misdiagnosis from FSHD2 to LGMD2A by whole-exome analysis
Gucy2f zebrafish knockdown – a model for Gucy2d-related leber congenital amaurosis
19q13.11 cryptic deletion: description of two new cases and indication for a role of WTIP haploinsufficiency in hypospadias
Dissecting the genetic make-up of North-East Sardinia using a large set of haploid and autosomal markers
High prevalence of genetic variants previously associated with LQT syndrome in new exome data
Reply to Ross' commentary: Reproductive benefit through newborn screening: preferences, policy and ethics
Clinical utility gene card for: Abetalipoproteinaemia
Methylome-wide comparison of human genomic DNA extracted from whole blood and from EBV-transformed lymphocyte cell lines
Spontaneous disclosure of BRCA1/2 genetic test results to employers: a French prospective study
Syndactyly: phenotypes, genetics and current classification
Estimating the contribution of genetic variants to difference in incidence of disease between population groups
Direct-to-consumer genomic testing: systematic review of the literature on user perspectives
Meier–Gorlin syndrome genotype–phenotype studies: 35 individuals with pre-replication complex gene mutations and 10 without molecular diagnosis
TBX5 intragenic duplication: a family with an atypical Holt–Oram syndrome phenotype
Genome-wide analysis of epistasis in body mass index using multiple human populations
Symmetric polymicrogyria and pachygyria associated with TUBB2B gene mutations
One thing leads to another: the cascade of obligations when researchers report genetic research results to study participants
COL4A2 mutation associated with familial porencephaly and small-vessel disease
Erratum: Isolated NIPBL missense mutations that cause Cornelia de Lange syndrome alter MAU2 interaction
Relative frequency of underlying genetic causes for the development of UPD(14)pat-like phenotype
Expanding the molecular basis and phenotypic spectrum of X-linked Joubert syndrome associated with OFD1 mutations
In search of triallelism in Bardet–Biedl syndrome
Intragenic and large NIPBL rearrangements revealed by MLPA in Cornelia de Lange patients
C4ST-1/CHST11-controlled chondroitin sulfation interferes with oncogenic HRAS signaling in Costello syndrome
Proximal microdeletions and microduplications of 1q21.1 contribute to variable abnormal phenotypes
Permutation-based approaches do not adequately allow for linkage disequilibrium in gene-wide multi-locus association analysis
Multiple meiotic errors caused by predivision of chromatids in women of advanced maternal age undergoing in vitro fertilisation
An exploration of genetic health professionals' experience with direct-to-consumer genetic testing in their clinical practice
The 12S rRNA A1555G mutation in the mitochondrial haplogroup D5a is responsible for maternally inherited hypertension and hearing loss in two Chinese pedigrees
Characterization of the intronic portion of cadherin superfamily members, common cancer orchestrators
Gross deletions in TCOF1 are a cause of Treacher–Collins–Franceschetti syndrome
An evaluation of different meta-analysis approaches in the presence of allelic heterogeneity
Two families with sibling recurrence of the 17q21.31 microdeletion syndrome due to low-grade mosaicism
1000 Genomes-based imputation identifies novel and refined associations for the Wellcome Trust Case Control Consortium phase 1 Data
Improved access to life insurance after genetic diagnosis of familial hypercholesterolaemia: cross-sectional postal questionnaire study
Clinical utility gene card for: haemophilia B
A large-sample assessment of possible association between ischaemic stroke and rs12188950 in the PDE4D gene
Consanguinity in Centre d’Étude du Polymorphisme Humain (CEPH) pedigrees
Homozygous SMN2 deletion is a protective factor in the Swedish ALS population
Association between survivin −31G>C promoter polymorphism and cancer risk: a meta-analysis
MLH1 promoter hypermethylation in the analytical algorithm of Lynch syndrome: a cost-effectiveness study
Clinical utility gene card for: familial erythrocytosis
Single-nucleotide polymorphisms in the P2X7 receptor gene are associated with post-menopausal bone loss and vertebral fractures
Legislation on direct-to-consumer genetic testing in seven European countries
Discovery of variants unmasked by hemizygous deletions
A two-stage association study identifies methyl-CpG-binding domain protein 2 gene polymorphisms as candidates for breast cancer susceptibility
Novel and recurrent non-truncating mutations of the MITF basic domain: genotypic and phenotypic variations in Waardenburg and Tietz syndromes
Myotubular myopathy caused by multiple abnormal splicing variants in the MTM1 RNA in a patient with a mild phenotype
Impact of diagnostic misclassification on estimation of genetic correlations using genome-wide genotypes
Disease gene identification strategies for exome sequencing
A major locus on chromosome 3p22 conferring predisposition to human herpesvirus 8 infection
Characterization of mtDNA variation in a cohort of South African paediatric patients with mitochondrial disease
KIF1A missense mutations in SPG30, an autosomal recessive spastic paraplegia: distinct phenotypes according to the nature of the mutations
Clinical utility gene card for: Werner syndrome
Questionable pathogenicity of FOXG1 duplication
Reply to Amor et al
Multiple orbital neurofibromas, painful peripheral nerve tumors, distinctive face and marfanoid habitus: a new syndrome
Duplication 8q12: confirmation of a novel recognizable phenotype with duane retraction syndrome and developmental delay
Deletions in PITX1 cause a spectrum of lower-limb malformations including mirror-image polydactyly
Identification of a novel in-frame de novo mutation in SPTAN1 in intellectual disability and pontocerebellar atrophy
A useful guide for your practice
Erratum: Human balanced translocation and mouse gene inactivation implicate Basonuclin 2 in distal urethral development
DNA and ability to reproduce: the ‘Secret’ of evolution
Autism multiplex family with 16p11.2p12.2 microduplication syndrome in monozygotic twins and distal 16p11.2 deletion in their brother
Rare chromosome abnormalities, prevalence and prenatal diagnosis rates from population-based congenital anomaly registers in Europe
Low prevalence of lactase persistence in Neolithic South-West Europe
Polymorphisms in the P2X7 receptor gene are associated with low lumbar spine bone mineral density and accelerated bone loss in post-menopausal women
A large duplication involving the IHH locus mimics acrocallosal syndrome
Clinical utility gene card for: BEST1-related dystrophies (Bestrophinopathies)
Genomic imbalances detected by array-CGH in patients with syndromal ocular developmental anomalies
ironXS: high-school screening for hereditary haemochromatosis is acceptable and feasible
Association of TCF4 and CLU polymorphisms with Fuchs’ endothelial dystrophy and implication of CLU and TGFBI proteins in the disease process
Phenotype-specific adverse effects of XPD mutations on human prenatal development implicate impairment of TFIIH-mediated functions in placenta
Association of genomic instability, and the methylation status of imprinted genes and mismatch-repair genes, with neural tube defects
Prospective comparison of family medical history with personal genome screening for risk assessment of common cancers
Direct-to-consumer genetic testing services: what are the medical benefits?