European Journal of Human Genetics - 2009

247 articles | Last updated: 2025-12-03 14:12:56
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Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
CASK mutations are frequent in males and cause X-linked nystagmus and variable XLMR phenotypes
Complete mitochondrial DNA sequences provide new insights into the Polynesian motif and the peopling of Madagascar
A gene-based method for detecting gene–gene co-association in a case–control association study
De Barsy syndrome and ATP6V0A2-CDG
Reply to Leao-Teles et al
What you always wanted to know about Huntington's disease
The genomic era and the new frontiers of medicine
Enhancer elements upstream of the SHOX gene are active in the developing limb
Non-invasive prenatal testing: ethical issues explored
Breakpoint analysis of balanced chromosome rearrangements by next-generation paired-end sequencing
Legal and ethical consequences of international biobanking from a national perspective: the German BMB-EUCoop project
Genome scan for loci regulating HDL cholesterol levels in Finnish extended pedigrees with early coronary heart disease
New multiplex PCR-based protocol allowing indirect diagnosis of FSHD on single cells: can PGD be offered despite high risk of recombination?
Genome-wide SNP analysis reveals no gain in power for association studies of common variants in the Finnish Saami
Modulation of aberrant NF1 pre-mRNA splicing by kinetin treatment
A data-driven weighting scheme for family-based genome-wide association studies
Systematic genotype–phenotype analysis of autism susceptibility loci implicates additional symptoms to co-occur with autism
Evaluation of the discriminative accuracy of genomic profiling in the prediction of common complex diseases
Hexose-6-phosphate dehydrogenase: a new risk gene for multiple sclerosis
The (CAG)n tract of Machado–Joseph Disease gene (ATXN3): a comparison between DNA and mRNA in patients and controls
Erratum: CRTAP mutations in lethal and severe osteogenesis imperfecta: the importance of combining biochemical and molecular genetic analysis
Erratum: Caveolinopathies: from the biology of caveolin-3 to human diseases
Single-sperm analysis for recurrence risk assessment of spinal muscular atrophy
Haploinsufficiency of MBD5 associated with a syndrome involving microcephaly, intellectual disabilities, severe speech impairment, and seizures
Hereditary haemorrhagic telangiectasia and genetic thrombophilia
Reply to Bianca et al
Identification of ANKRD11 and ZNF778 as candidate genes for autism and variable cognitive impairment in the novel 16q24.3 microdeletion syndrome
Hereditary haemorrhagic telangiectasia: From symptomatic management to pathogenesis based treatment
Separating the post-Glacial coancestry of European and Asian Y chromosomes within haplogroup R1a European
A rare variant of the TYK2 gene is confirmed to be associated with multiple sclerosis
High-throughput sequencing of microdissected chromosomal regions
Genetic variants in human CLOCK associate with total energy intake and cytokine sleep factors in overweight subjects (GOLDN population)
Coffin–Lowry syndrome
Five novel loci for inherited hearing loss mapped by SNP-based homozygosity profiles in Palestinian families
Ethical implications of the use of whole genome methods in medical research
Reply to Fernández-Fernández
Analysis of allele-specific RNA transcription in FSHD by RNA-DNA FISH in single myonuclei
Copy number variation upstream of PMP22 in Charcot–Marie–Tooth disease
Menkes disease
Hereditary cutaneomucosal venous malformations are caused by TIE2 mutations with widely variable hyper-phosphorylating effects
JEAN B DAUSSET, 19 OCTOBER 1916–6 JUNE 2009
Erratum: Prevalence data on all Ghent features in a cross-sectional study of 87 adults with proven Marfan syndrome
The difficulty to classify complex dysmorphic syndromes on the ward
Familial interstitial Xq27.3q28 duplication encompassing the FMR1 gene but not the MECP2 gene causes a new syndromic mental retardation condition
Long time no see: the Type and Contre-type concept
A syndrome of short stature, microcephaly and speech delay is associated with duplications reciprocal to the common Sotos syndrome deletion
European admixture on the Micronesian island of Kosrae: lessons from complete genetic information European admixture
Array-based comparative genomic hybridization identifies a high frequency of copy number variations in patients with syndromic overgrowth
Chromosome aberrations involving 10q22: report of three overlapping interstitial deletions and a balanced translocation disrupting C10orf11
Drawing the history of the Hutterite population on a genetic landscape: inference from Y-chromosome and mtDNA genotypes
Clinical spectrum associated with recurrent genomic rearrangements in chromosome 17q12
Identification and characterization of seven novel mutations of elastin gene in a cohort of patients affected by supravalvular aortic stenosis
Fine mapping and association studies of a high-density lipoprotein cholesterol linkage region on chromosome 16 in French-Canadian subjects French-Canadian subjects
Polymorphisms in TLR4 and TLR2 genes, cytokine production and survival in rural Ghana
Genomic landscape of positive natural selection in Northern European populations Northern European populations
Genetic profile for five common variants associated with age-related macular degeneration in densely affected families: a novel analytic approach
Identification and characterization of two novel JARID1C mutations: suggestion of an emerging genotype–phenotype correlation
Methionine synthase A2756G polymorphism and cancer risk: a meta-analysis
The emergence of Y-chromosome haplogroup J1e among Arabic-speaking populations
Large-scale parent–child comparison confirms a strong paternal influence on telomere length
Gain-of-function variant in GLUD2 glutamate dehydrogenase modifies Parkinson's disease onset
Comparison of participant information and informed consent forms of five European studies in genetic isolated populations European studies
Sporadic cases are the norm for complex disease
Prader–Willi and Angelman syndromes: genetic counseling
Understanding sickle cell carrier status identified through newborn screening: a qualitative study
Attitudes toward genetic testing in childhood and reproductive decision-making for familial adenomatous polyposis
The 2q23.1 microdeletion syndrome: clinical and behavioural phenotype
Reply to Camprubí et al
High-resolution SNP arrays in mental retardation diagnostics: how much do we gain?
Study of smell and reproductive organs in a mouse model for CHARGE syndrome
Progress in therapeutic antisense applications for neuromuscular disorders
A powerful genome-wide feasible approach to detect parent-of-origin effects in studies of quantitative traits
Traces of sub-Saharan and Middle Eastern lineages in Indian Muslim populations sub-Saharan; Middle Eastern
Functional consequences of mitochondrial tRNATrp and tRNAArg mutations causing combined OXPHOS defects
Comparison of human chromosome 19q13 and syntenic region on mouse chromosome 7 reveals absence, in man, of 11.6 Mb containing four mouse calcium-sensing receptor-related sequences: relevance to famili
Design and evaluation of a panel of single-nucleotide polymorphisms in microRNA genomic regions for association studies in human disease
Comprehensive expression analysis of FSHD candidate genes at the mRNA and protein level
Preliminary evidence of a noncausal association between the X-chromosome inactivation pattern and thyroid autoimmunity: a twin study
Erratum: Profound, prelingual nonsyndromic deafness maps to chromosome 10q21 and is caused by a novel missense mutation in the Usher syndrome type IF gene PCDH15
Ohtahara syndrome in a family with an ARX protein truncation mutation (c.81C>G/p.Y27X)
The CFTR frameshift mutation 3905insT and its effect at transcript and protein level
Genome-wide linkage analysis in a Dutch multigenerational family with attention deficit hyperactivity disorder
An integrated phenomic approach to multivariate allelic association
Novel IL31RA gene mutation and ancestral OSMR mutant allele in familial primary cutaneous amyloidosis
Public interest in predictive genetic testing, including direct-to-consumer testing, for susceptibility to major depression: preliminary findings
Gene silencing of EXTL2 and EXTL3 as a substrate deprivation therapy for heparan sulphate storing mucopolysaccharidoses
A genome scan in affected sib-pairs with familial vesicoureteral reflux identifies a locus on chromosome 5
Impairment of glycosaminoglycan synthesis in mucopolysaccharidosis type IIIA cells by using siRNA: a potential therapeutic approach for Sanfilippo disease
Erratum: Direct to consumer genetic tests
Association of the TGF-β receptor genes with abdominal aortic aneurysm
Obtaining insurance after DNA diagnostics: a survey among hypertrophic cardiomyopathy mutation carriers
The candidate gene approach in asthma: what happens with the neighbours?
Reply to Reijmerink et al
Differential MSH2 promoter methylation in blood cells of Neurofibromatosis type 1 (NF1) patients
Depletion of potential A2M risk haplotype for Alzheimer's disease in long-lived individuals
The common biological basis for common complex diseases: evidence from lipoprotein lipase gene
Septo-optic dysplasia
Functional analysis of Ectodysplasin-A mutations causing selective tooth agenesis
Recurrent copy number changes in mentally retarded children harbour genes involved in cellular localization and the glutamate receptor complex
Atypical Rett syndrome with selective FOXG1 deletion detected by comparative genomic hybridization: case report and review of literature
APOC3 deficiency: from mice to man
SMN transcript levels in leukocytes of SMA patients determined by absolute real-time PCR
DFNB79: reincarnation of a nonsyndromic deafness locus on chromosome 9q34.3
In vitro readthrough of termination codons by gentamycin in the Stüve–Wiedemann Syndrome
Support for the involvement of complement factor I in age-related macular degeneration
The Dutch founder mutation SDHD.D92Y shows a reduced penetrance for the development of paragangliomas in a large multigenerational family
Caveolinopathies: from the biology of caveolin-3 to human diseases
Association of FTO variants with BMI and fat mass in the self-contained population of Sorbs in Germany
Legacy of mutiny on the Bounty: founder effect and admixture on Norfolk Island European ancestry
Comprehensive SNP-chip for retinitis pigmentosa-Leber congenital amaurosis diagnosis: new mutations and detection of mutational founder effects
Gene and pathway-based second-wave analysis of genome-wide association studies
Specific epigenetic alterations of IGF2-H19 locus in spermatozoa from infertile men
A comprehensive approach to haplotype-specific analysis by penalized likelihood
On the use of sibling recurrence risks to select environmental factors liable to interact with genetic risk factors
HPGD mutations cause cranioosteoarthropathy but not autosomal dominant digital clubbing
Triple X syndrome: a review of the literature
Council of Europe adopts protocol on genetic testing for health purposes
An atypical 7q11.23 deletion in a normal IQ Williams–Beuren syndrome patient
CRTAP mutations in lethal and severe osteogenesis imperfecta: the importance of combining biochemical and molecular genetic analysis
Beckwith–Wiedemann syndrome
Comparing population structure as inferred from genealogical versus genetic information
On the origin of Y-chromosome haplogroup N1b
Reply to B Malyarchuk and M Derenko: a need for further investigation of Uralic and Siberian populations in the search for haplogroup N1b's origins
Follow-up of a major linkage peak on chromosome 1 reveals suggestive QTLs associated with essential hypertension: GenNet study
Association of FGFR2 gene polymorphisms with the risk of breast cancer in population of West Siberia
A mutation in an alternative untranslated exon of hexokinase 1 associated with Hereditary Motor and Sensory Neuropathy – Russe (HMSNR)
Cell proliferation-related genetic polymorphisms and gastric cancer risk: systematic review and meta-analysis
Axenfeld–Rieger syndrome and spectrum of PITX2 and FOXC1 mutations
Lessons from BWS twins: complex maternal and paternal hypomethylation and a common source of haematopoietic stem cells
A novel SRY missense mutation affecting nuclear import in a 46,XY female patient with bilateral gonadoblastoma
Phenotypes and genotypes of insulin-like growth factor 1, IGF-binding protein-3 and cancer risk: evidence from 96 studies
Recovering unused information in genome-wide association studies: the benefit of analyzing SNPs out of Hardy–Weinberg equilibrium
Changing perspectives in biobank research: from individual rights to concerns about public health regarding the return of results
A critical assessment of the factors affecting reporter gene assays for promoter SNP function: a reassessment of −308 TNF polymorphism function using a novel integrated reporter system
WNT10A missense mutation associated with a complete Odonto-Onycho-Dermal Dysplasia syndrome
Expression of SNURF–SNRPN upstream transcripts and epigenetic regulatory genes during human spermatogenesis
Novel SOX2 partner-factor domain mutation in a four-generation family
Impact of BRCA1 and BRCA2 variants on splicing: clues from an allelic imbalance study
DNA methylation errors at imprinted loci after assisted conception originate in the parental sperm
A novel microdeletion syndrome involving 5q14.3-q15: clinical and molecular cytogenetic characterization of three patients
Separation of the PROX1 gene from upstream conserved elements in a complex inversion/translocation patient with hypoplastic left heart
A genome-wide scan of 10 000 gene-centric variants and colorectal cancer risk
Mutation in the SLC9A6 gene is not a frequent cause of sporadic Angelman-like syndrome
Preimplantation genetic diagnosis for mitochondrial DNA disorders: ethical guidance for clinical practice
Homozygosity for a null allele of COL3A1 results in recessive Ehlers–Danlos syndrome
Angelman syndrome (AS, MIM 105830)
Erratum: Y-chromosomal evidence of the cultural diffusion of agriculture in southeast Europe
A novel double deletion underscores the importance of characterizing end points of the CFTR large rearrangements
A new diagnostic workflow for patients with mental retardation and/or multiple congenital abnormalities: test arrays first
Characterization of deletions at 9p affecting the candidate regions for sex reversal and deletion 9p syndrome by MLPA
Phosphodiesterase 4D and 5-lipoxygenase activating protein genes and risk of ischemic stroke in Sardinians
Isolated populations as treasure troves in genetic epidemiology: the case of the Basques
Lessons from cutis laxa syndromes: wrinkles due to improper reloading of the extracellular matrix?
Split hand/foot malformation due to chromosome 7q aberrations(SHFM1): additional support for functional haploinsufficiency as the causative mechanism
Autosomal recessive cutis laxa syndrome revisited
The role of mitochondrial genome in essential hypertension in a Chinese Han population
Direct to consumer genetic tests
Copy number variation and association analysis of SHANK3 as a candidate gene for autism in the IMGSAC collection
Functional identification of the promoter of SLC4A5, a gene associated with cardiovascular and metabolic phenotypes in the HERITAGE Family Study
Erratum: Structural variation in Xq28: MECP2 duplications in 1% of patients with unexplained XLMR and in 2% of male patients with severe encephalopathy
Penetrance of FMR1 premutation associated pathologies in fragile X syndrome families
BCOR analysis in patients with OFCD and Lenz microphthalmia syndromes, mental retardation with ocular anomalies, and cardiac laterality defects
Human longevity and 11p15.5: a study in 1321 centenarians
Preimplantation genetic diagnosis for myotonic dystrophy type 1: upon request to child
A heterozygote–homozygote test of Hardy–Weinberg equilibrium
J1-M267 Y lineage marks climate-driven pre-historical human displacements
Risk-reducing surgery for ovarian cancer: outcomes in 300 surgeries suggest a low peritoneal primary risk
Genetic markers and population history: Finland revisited
Diagnostic value of post-heparin lipase testing in detecting common genetic variants in the LPL and LIPC genes
Assessing the impact of FOXP1 mutations on developmental verbal dyspraxia
SOS1 and PTPN11 mutations in five cases of Noonan syndrome with multiple giant cell lesions
Specific association of a CLEC16A/KIAA0350 polymorphism with NOD2/CARD15− Crohn's disease patients
The FAS ligand promoter polymorphism, rs763110 (−844C>T), contributes to cancer susceptibility: evidence from 19 case–control studies
Hereditary haemorrhagic telangiectasia: a clinical and scientific review
Evidence for association with hepatocellular carcinoma at the PAPSS1 locus on chromosome 4q25 in a family-based study
The maternal aborigine colonization of La Palma (Canary Islands)
Reply to Happle
Angioma serpiginosum is not caused by PORCN mutations
Variant on 9p21 strongly associates with coronary heart disease, but lacks association with common stroke
Factors influencing intrafamilial communication of hereditary breast and ovarian cancer genetic information
Prevalence data on all Ghent features in a cross-sectional study of 87 adults with proven Marfan syndrome
Clinical features and molecular modelling of novel MPZ mutations in demyelinating and axonal neuropathies
16p subtelomeric duplication: a clinically recognizable syndrome
The role of sarcomere gene mutations in patients with idiopathic dilated cardiomyopathy
Identification of the minimal combination of clinical features in probands for efficient mutation detection in the FBN1 gene
The interaction index, a novel information-theoretic metric for prioritizing interacting genetic variations and environmental factors
Replication analysis identifies TYK2 as a multiple sclerosis susceptibility factor
Genetic horoscopes: is it all in the genes? Points for regulatory control of direct-to-consumer genetic testing
Segregation analysis in a family at risk for the Maroteaux–Lamy syndrome conclusively reveals c.1151G>A (p.S384N) as to be a polymorphism
Identification and in silico analysis of 14 novel GJB1, MPZ and PMP22 gene mutations
Maternal uniparental heterodisomy of chromosome 17 in a patient with nephropathic cystinosis
Assessment of transmission distortion on chromosome 6p in healthy individuals using tagSNPs
EuroGentest patient information leaflets: a free resource available in over 20 languages
Integrative genomics, personal-genome tests and personalized healthcare: the future is being built today
Y-Chromosome distribution within the geo-linguistic landscape of northwestern Russia
Personal genomics services: whose genomes?
Mutated NDUFS6 is the cause of fatal neonatal lactic acidemia in Caucasus Jews Caucasus Jews
Does δ-sarcoglycan-associated autosomal-dominant cardiomyopathy exist?
Multilocus analysis of age-related macular degeneration
Three independent mutations in the TSC2 gene in a family with tuberous sclerosis
Refinement of the 12q14 microdeletion syndrome: primordial dwarfism and developmental delay with or without osteopoikilosis
Genetic testing in asymptomatic minors: recommendations of the European Society of Human Genetics
Charcot–Marie–Tooth disease
From genotypes to genometypes: putting the genome back in genome-wide association studies
Using biological networks to search for interacting loci in genome-wide association studies
Goltz–Gorlin (focal dermal hypoplasia) and the microphthalmia with linear skin defects (MLS) syndrome: no evidence of genetic overlap
Brachydactyly A-1 mutations restricted to the central region of the N-terminal active fragment of Indian Hedgehog
Genetic testing in asymptomatic minors
A novel mutation in the mitochondrial tRNAPro gene associated with late-onset ataxia, retinitis pigmentosa, deafness, leukoencephalopathy and complex I deficiency
Characterization of two ectrodactyly-associated translocation breakpoints separated by 2.5 Mb on chromosome 2q14.1–q14.2
Allelic heterogeneity of G6PD deficiency in West Africa and severe malaria susceptibility
Biological sample collections from minors for genetic research: a systematic review of guidelines and position papers
Preconceptional ancestry-based carrier couple screening for cystic fibrosis and haemoglobinopathies: what determines the intention to participate or not and actual participation?
Improving pharmacovigilance in Europe: TPMT genotyping and phenotyping in the UK and Spain
Novel promoter and exon mutations of the BMPR2 gene in Chinese patients with pulmonary arterial hypertension Chinese patients
Predicting human height by Victorian and genomic methods
Joint analysis of tightly linked SNPs in screening step of genome-wide association studies leads to increased power
4q32–q35 and 6q16–q22 are valuable candidate regions for split hand/foot malformation
Erratum: Expansion of mutation spectrum, determination of mutation cluster regions and predictive structural classification of SPAST mutations in hereditary spastic paraplegia
Erratum: Array-CGH fine mapping of minor and cryptic HR-CGH detected genomic imbalances in 80 out of 590 patients with abnormal development
Two British women studies replicated the association between the Val66Met polymorphism in the brain-derived neurotrophic factor (BDNF) and BMI
Genetic association analysis of 13 nuclear-encoded mitochondrial candidate genes with type II diabetes mellitus: the DAMAGE study
A novel VPS13B mutation in two brothers with Cohen syndrome, cutis verticis gyrata and sensorineural deafness
Centrotemporal sharp wave EEG trait in rolandic epilepsy maps to Elongator Protein Complex 4 (ELP4)
Increased expression of the Hutchinson–Gilford progeria syndrome truncated lamin A transcript during cell aging
Dystrophia myotonia: why focus on foci?
Genetic analysis of autosomal recessive osteopetrosis in Chuvashiya: the unique splice site mutation in TCIRG1 gene spread by the founder effect
An international external quality assessment for molecular diagnosis of hereditary recurrent fevers: a 3-year scheme demonstrates the need for improvement
The complex interaction between APOE promoter and AD: an Italian case–control study
Chromosome 13q13–q14 locus overlaps mood and psychotic disorders: the relevance for redefining phenotype
Characterization of a t(5;8)(q31;q21) translocation in a patient with mental retardation and congenital heart disease: implications for involvement of RUNX1T1 in human brain and heart development
MTHFR 677 C>T and 1298 A>C polymorphisms and the age of onset of colorectal cancer in hereditary nonpolyposis colorectal cancer
Moors and Saracens in Europe: estimating the medieval North African male legacy in southern Europe
IFIH1-GCA-KCNH7 locus is not associated with genetic susceptibility to multiple sclerosis in French patients
Suggestive linkage of ADHD to chromosome 18q22 in a young genetically isolated Dutch population Dutch population
An 8.9 Mb 19p13 duplication associated with precocious puberty and a sporadic 3.9 Mb 2q23.3q24.1 deletion containing NR4A2 in mentally retarded members of a family with an intrachromosomal 19p-into-19
Type A microsatellite instability in pediatric gliomas as an indicator of Turcot syndrome
Spectrum of MEK1 and MEK2 gene mutations in cardio-facio-cutaneous syndrome and genotype–phenotype correlations
Pharmacogenetics of antipsychotic response in the CATIE trial: a candidate gene analysis
Incidence of non-age-dependent chromosomal abnormalities: a population-based study on 88965 amniocenteses
An evaluation of the genetic-matched pair study design using genome-wide SNP data from the European population European population
Linkage analysis of left ventricular outflow tract malformations (aortic valve stenosis, coarctation of the aorta, and hypoplastic left heart syndrome)
Rational diagnostic strategy for Zellweger syndrome spectrum patients
Ab initio prediction of mutation-induced cryptic splice-site activation and exon skipping
Maternal transmission effects of the PAX genes among cleft case–parent trios from four populations
MYO9B polymorphisms in multiple sclerosis
Global similarity with local differences in linkage disequilibrium between the Dutch and HapMap–CEU populations