European Journal of Human Genetics - 2007

209 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Provision and quality assurance of preimplantation genetic diagnosis in Europe
Diagnostic dilemma's: The congenital disorders of glycosylation are clinical chameleons
Popper revisited: GWAS here, last year
Polymorphisms in the cardiac sodium channel promoter displaying variant in vitro expression activity
‘It is not in my world’: an exploration of attitudes and influences associated with cystic fibrosis carrier screening
ALS predisposition modifiers: Knock NOX, who's there? SOD1 mice still are
Identification of a nonsense mutation in the very low-density lipoprotein receptor gene (VLDLR) in an Iranian family with dysequilibrium syndrome
Population genetic diversity of the NAT2 gene supports a role of acetylation in human adaptation to farming in Central Asia
The ACTN3 R577X nonsense allele is under-represented in elite-level strength athletes
Carrier screening: look before you leap: Carrier screening for type 1 Gaucher disease: difficult questions
Low prevalence of APP duplications in Swedish and Finnish patients with early-onset Alzheimer's disease
Dissecting the molecular mechanisms in craniofrontonasal syndrome: differential mRNA expression of mutant EFNB1 and the cellular mosaic
Instability of expanded CAG/CAA repeats in spinocerebellar ataxia type 17
The novel hyperekplexia allele GLRA1(S267N) affects the ethanol site of the glycine receptor
Haplotype patterns in cancer-related genes with long-range linkage disequilibrium: no evidence of association with breast cancer or positive selection
Auriculo-condylar syndrome: mapping of a first locus and evidence for genetic heterogeneity
Is the prevalence of Klinefelter syndrome increasing?
Fifth finger camptodactyly maps to chromosome 3q11.2–q13.12 in a large German kindred
Bases, Bits and Disease: Bases, bits and disease: a mathematical theory of human genetics
Exploration of gene–gene interaction effects using entropy-based methods
An assessment of the Irish population for large-scale genetic mapping studies involving epilepsy and other complex diseases
X inactivation in triploidy and trisomy: the search for autosomal transfactors that choose the active X
Defining the phenotype in an autosomal recessive cutis laxa syndrome with a combined congenital defect of glycosylation
A unique case of reversion to normal size of a maternal premutation FMR1 allele in a normal boy
A novel sampling design to explore gene-longevity associations: the ECHA study
Engagement with genetic discrimination: concerns and experiences in the context of Huntington disease
Sex-specific interaction between APOE and APOA5 variants and determination of plasma lipid levels
The impact of genetics and genomics on public health
Mental deficiency in three families with SPG4 spastic paraplegia
Patient mutations alter ATRX targeting to PML nuclear bodies
Molecular screening for familial hypercholesterolaemia: consequences for life and disability insurance
Expanded high-resolution genetic study of 109 Swedish families with Alzheimer's disease
In memoriam: Dr Marina Seabright
Consent and confidentiality: Consent and Confidentiality in Genetic Practice
8p23.1 duplication syndrome; a novel genomic condition with unexpected complexity revealed by array CGH
Alström Syndrome
Y-chromosome diversity characterizes the Gulf of Oman
A deletion in DRCTNNB1A associated with hypomyelination and juvenile onset cataract
Allele-specific regulation of primary cilia function by the von Hippel–Lindau tumor suppressor
A multi-exonic SPG4 duplication underlies sex-dependent penetrance of hereditary spastic paraplegia in a large Brazilian pedigree
Novel FGFR3 mutations in exon 7 and implications for expanded screening of achondroplasia and hypochondroplasia: a response to Heuertz et al
Genetic testing and counselling in Europe: health professionals current educational provision, needs assessment and potential strategies for the future
What? Where? Which? WWW Resources for Geneticists: Bioinformatics for geneticists: a bioinformatics primer for the analysis of genetic data
Abnormal urethra formation in mouse models of Split-hand/split-foot malformation type 1 and type 4
Homozygous PMS2 germline mutations in two families with early-onset haematological malignancy, brain tumours, HNPCC-associated tumours, and signs of neurofibromatosis type 1
Unexpected genetic heterogeneity in a large consanguineous Brazilian pedigree presenting deafness
Identification of a chromosome 8p locus for early-onset coronary heart disease in a French Canadian population
A meta-analysis of association between C677T polymorphism in the methylenetetrahydrofolate reductase gene and hypertension
Comprehensive analysis of Wolf–Hirschhorn syndrome using array CGH indicates a high prevalence of translocations
Simultaneous mutation scanning for gross deletions, duplications and point mutations in the DMD gene
Deletions Revealing Recessive Genes: Deletions that reveal recessive genes
Molecular characterization and structural implications of 25 new ABCB4 mutations in progressive familial intrahepatic cholestasis type 3 (PFIC3)
Czech dysplasia metatarsal type: another type II collagen disorder
Searching for genes influencing a complex disease: the case of coeliac disease
Delineation of large deletions of the MECP2 gene in Rett syndrome patients, including a familial case with a male proband
New genetic evidence supports isolation and drift in the Ladin communities of the South Tyrolean Alps but not an ancient origin in the Middle East
Attitudes regarding carrier testing in incompetent children: a survey of European clinical geneticists European clinical geneticists
Genome-wide linkage scan for exercise participation in Dutch sibling pairs
A simulation-based analysis of chromosome segment sharing among a group of arbitrarily related individuals
Co-introgression of Y-chromosome haplogroups and the sickle cell gene across Africa's Sahel
Japanese and North American/European patients with Beckwith–Wiedemann syndrome have different frequencies of some epigenetic and genetic alterations North American/European patients
Population history and infrequent mutations: how old is a rare mutation? GUCY2D as a worked example
Clinical and molecular genetics of patients with the Carney–Stratakis syndrome and germline mutations of the genes coding for the succinate dehydrogenase subunits SDHB, SDHC, and SDHD
Two-stage association tests for genome-wide association studies based on family data with arbitrary family structure
So that is why you stink!
Molecular Bases of Mental Retardation
Erratum: Association study of major risk single nucleotide polymorphisms in the common regulatory region of PARK2 and PACRG genes with leprosy in an Indian population
En route towards genetic medicine in practice: a clinical genetics guide in the post genomic era
Risk estimation for familial breast cancer: improving the system of counselling
Unmasking of a hemizygous WFS1 gene mutation by a chromosome 4p deletion of 8.3 Mb in a patient with Wolf–Hirschhorn syndrome
Branchio–oto–renal syndrome: detection of EYA1 and SIX1 mutations in five out of six Danish families by combining linkage, MLPA and sequencing analyses
Guidelines for molecular karyotyping in constitutional genetic diagnosis
Role of ethnicity on the association of MAPT H1 haplotypes and subhaplotypes in Parkinson's disease
Whole mitochondrial genome screening in maternally inherited non-syndromic hearing impairment using a microarray resequencing mitochondrial DNA chip
The efficiency of nonsense-mediated mRNA decay is an inherent character and varies among different cells
VEGF C−634G polymorphism is associated with protection from isolated ventricular septal defect: case–control and TDT studies
A functional mutation in the LDLR promoter (−139C>G) in a patient with familial hypercholesterolemia
Evidence of a segregation ratio distortion of SMN1 alleles in spinal muscular atrophy
Patient Information: Patient information for genetic testing
Chromosomal Microdeletions and Genes' Functions: A cluster of chromosomal microdeletions and the deleted genes' functions
Process and outcome in communication of genetic information within families: a systematic review
A sensitive assay for measuring SMN mRNA levels in peripheral blood and in muscle samples of patients affected with spinal muscular atrophy
A new mutation in TP63 is associated with age-related pathology
Genetic analysis of the GRM1 gene in human melanoma susceptibility
Polymorphism of XRCC1 predicts overall survival of gastric cancer patients receiving oxaliplatin-based chemotherapy in Chinese population Chinese population
Mining the literature for relationships between genes
Erratum: Significant variation in haplotype block structure but conservation in tagSNP patterns among global populations
Talking hypotheses
Erratum: A common mutation in the COG7 gene with a consistent phenotype including microcephaly, adducted thumbs, growth retardation, VSD and episodes of hyperthermia
Global distribution of the most prevalent deletions causing hypotonia–cystinuria syndrome
Serum or plasma cartilage oligomeric matrix protein concentration as a diagnostic marker in pseudoachondroplasia: differential diagnosis of a family
Association of PTPN22 single nucleotide polymorphism with rheumatoid arthritis but not with allergic asthma
Partial duplications of the ATRX gene cause the ATR-X syndrome
3rd International Meeting on Cryptic Chromosomal Rearrangements in Mental Retardation and Autism
Functional analysis of pancreatitis-associated missense mutations in the pancreatic secretory trypsin inhibitor (SPINK1) gene
An assessment of written patient information provided at the genetic clinic and relating to genetic testing in seven European countries
Enrichment of HapMap recombination hotspot predictions around human nervous system genes: evidence for positive selection ?
Genetics of the ECG: QT or not QT- A genetic analysis of a complex electrophysiological trait confirms several previously detected associations
Homozygosity for a FBN1 missense mutation: clinical and molecular evidence for recessive Marfan syndrome
Population genetics of familial Mediterranean fever: a review
Candidate genes for congenital diaphragmatic hernia from animal models: sequencing of FOG2 and PDGFRα reveals rare variants in diaphragmatic hernia patients
Tag SNP selection for candidate gene association studies using HapMap and gene resequencing data
Genotype–phenotype correlations in 19 Dutch cases with APC gene deletions and a literature review
A comprehensive screen for SNP associations on chromosome region 5q31–33 in Swedish/Norwegian celiac disease families
How can genetic tests be evaluated for clinical use? Experience of the UK Genetic Testing Network
Linkage disequilibrium analysis of two genes mapping on OFC3: PVR and PVRL2
The MRE11/RAD50/NBS1 complex destabilization in Lynch-syndrome patients
Confirmation of associations between ion channel gene SNPs and QTc interval duration in healthy subjects
No association of ERCC1 C8092A and T19007C polymorphisms to cancer risk: a meta-analysis
Identification of novel deletions of 15q11q13 in Angelman syndrome by array-CGH: molecular characterization and genotype–phenotype correlations
Erratum: A genome-wide search for linkage to asthma phenotypes in the genetics of asthma international network families: evidence for a major susceptibility locus on chromosome 2p
Transcriptional regulation of TLX2 and impaired intestinal innervation: possible role of the PHOX2A and PHOX2B genes
ALOX5AP gene variants and risk of coronary artery disease: an angiography-based study
Vascular Pathologies: Angiogenomics: towards a genetic nosology and understanding of vascular anomalies
Fanconi Anemia: Fanconi anemia, breast and embryonal cancer risk revisited
Differential haplotypic expression of the interleukin-18 gene
A novel locus for syndromic chronic idiopathic intestinal pseudo-obstruction maps to chromosome 8q23–q24
Genetic influences on angina pectoris and its impact on coronary heart disease
Marfan syndrome: clinical diagnosis and management
The federated database – a basis for biobank-based post-genome studies, integrating phenome and genome data from 600 000 twin pairs in Europe
Estimating cancer risk in HNPCC by the GRL method
The clinical relevance of microsatellite alterations in head and neck squamous cell carcinoma: a critical review
Support for involvement of the AHI1 locus in schizophrenia
First case of compound heterozygosity in Na,K-ATPase gene ATP1A2 in familial hemiplegic migraine
Spectrum of CREBBP gene dosage anomalies in Rubinstein–Taybi Syndrome patients
Estimating the odds ratios of Crohn disease for the main CARD15/NOD2 mutations using a conditional maximum likelihood method in pedigrees collected via affected family members
Transgenerational response to nutrition, early life circumstances and longevity
Genotypic and haplotypic associations of the DBH gene with plasma dopamine β-hydroxylase activity in African Americans
Erratum: Molecular analysis of ANT1, TWINKLE and POLG in patients with multiple deletions or depletion of mitochondrial DNA by a dHPLC-based assay
A t(4;6)(q12;p23) translocation disrupts a membrane-associated O-acetyl transferase gene (MBOAT1) in a patient with a novel brachydactyly–syndactyly syndrome
Clinical outcome of preimplantation genetic diagnosis for cystic fibrosis: the Brussels' experience
An explanation for another familial case of Rett syndrome: maternal germline mosaicism
Comment on Gellekink et al
Abundance of the POLG disease mutations in Europe, Australia, New Zealand, and the United States explained by single ancient European founders ancient European founders
Evidence for gene × smoking exposure interactions in a genome-wide linkage screen of asthma and bronchial hyper-responsiveness in EGEA families
Transmission ratio distortion and maternal effects confound the analysis of modulators of cystic fibrosis disease severity on 19q13
Specific combinations of HLA-DR2 and DR3 class II haplotypes contribute graded risk for disease susceptibility and autoantibodies in human SLE
Glycerol kinase deficiency alters expression of genes involved in lipid metabolism, carbohydrate metabolism, and insulin signaling
Inherited PAX6, NF1 and OTX2 mutations in a child with microphthalmia and aniridia
Mutation analysis of candidate genes within the 2q33.3 linkage area for familial early-onset generalised osteoarthritis
Epidemiology and penetrance of Leber hereditary optic neuropathy in Finland
Population screening and cascade testing for carriers of SMA
Communicating genetic information in families – a review of guidelines and position papers
Disruption of the CNTNAP2 gene in a t(7;15) translocation family without symptoms of Gilles de la Tourette syndrome
Segmental overgrowth, lipomatosis, arteriovenous malformation and epidermal nevus (SOLAMEN) syndrome is related to mosaic PTEN nullizygosity
TNF Polymorphism and Cardiovascular Disease: TNF gene polymorphism and quantitative traits related to cardiovascular disease: getting to the heart of the matter
Mutation in the PYK2-binding domain of PITPNM3 causes autosomal dominant cone dystrophy (CORD5) in two Swedish families
Meta-analysis of genome-wide linkage studies for multiple sclerosis, using an extended GSMA method
Mutations in TBX1 genocopy the 22q11.2 deletion and duplication syndromes: a new susceptibility factor for mental retardation
Linkage to chromosome 11p12 in two Maltese families with a highly penetrant form of osteoporosis Maltese
The use of grid computing to drive data-intensive genetic research
Joubert syndrome (and related disorders) (OMIM 213300)
Phenotype selection for detecting variable genes: a survey of cardiovascular quantitative traits and TNF locus polymorphism
Insights into modern disease from our distant evolutionary past
A common mutation in the COG7 gene with a consistent phenotype including microcephaly, adducted thumbs, growth retardation, VSD and episodes of hyperthermia
Cytogenetic Guidelines and Quality Assurance: a common European framework for quality assessment for constitutional and acquired cytogenetic investigations a common European framework
A legal framework for biobanking: the German experience
Does apolipoprotein E determine outcome of infection by varicella zoster virus and by Epstein Barr virus?
Relationship between E23K (an established type II diabetes-susceptibility variant within KCNJ11), polycystic ovary syndrome and androgen levels
Ring chromosome formation as a novel escape mechanism in patients with inverted duplication and terminal deletion
Comment on ‘Nonsense-mediated mRNA decay modulates clinical outcome of genetic disease’
Hidden African Ancestors: Hidden secrets of your ancestors
Heritable skewed X-chromosome inactivation leads to haemophilia A expression in heterozygous females
Reply to Inácio et al
Diagnostic accuracy of methods for the detection of BRCA1 and BRCA2 mutations: a systematic review
Angioma serpiginosum with oesophageal papillomatosis is an X-linked dominant condition that maps to Xp11.3–Xq12
Genetic component of identification, intensity and pleasantness of odours: a Finnish family study
De novo t(12;17)(p13.3;q21.3) translocation with a breakpoint near the 5′ end of the HOXB gene cluster in a patient with developmental delay and skeletal malformations
Legal pathways for cross-border research: building a legal platform for biomedical academia
The X chromosome Alu insertions as a tool for human population genetics: data from European and African human groups European human groups; African human groups
Identification of a candidate genetic variant for the high prevalence of type II diabetes in Polynesians
A common SNP haplotype provides molecular proof of a founder effect of Huntington disease linking two South African populations
Three-dimensional face shape in Fabry disease
Erratum: AHI1, a pivotal neurodevelopmental gene, and C6orf217 are associated with susceptibility to schizophrenia
Distribution of the D15Z1 copy number polymorphism
Undergoing prenatal screening for Down's syndrome: presentation of choice and information in Europe and Asia
Concern, pressure and lack of knowledge affect choice of not wanting to know high-risk status
A deep intronic mutation in the RB1 gene leads to intronic sequence exonisation
Confirmation of EP300 gene mutations as a rare cause of Rubinstein–Taybi syndrome
CHARGE syndrome: an update
Angiotensinogen M235T polymorphism and the risk of myocardial infarction and stroke among hypertensive patients on ACE-inhibitors or β-blockers
Genotype–phenotype correlations to aid in the prognosis of individuals with uncommon 20q13.33 subtelomere deletions: a collaborative study on behalf of the ‘association des Cytogénéticiens de langue F
Identification and characterization of the TRIP8 and REEP3 genes on chromosome 10q21.3 as novel candidate genes for autism
Evaluation of STOX1 as a preeclampsia candidate gene in a population-wide sample
Oculoauriculovertebral spectrum with radial defects: a new syndrome or an extension of the oculoauriculovertebral spectrum? Report of fourteen Brazilian cases and review of the literature
Dopamine transporter, gender, and number of sexual partners among young adults
Ashkenazi Jewish mtDNA haplogroup distribution varies among distinct subpopulations: lessons of population substructure in a closed group
Haplotypes in the human Foxo1a and Foxo3a genes; impact on disease and mortality at old age
Africans in Yorkshire? The deepest-rooting clade of the Y phylogeny within an English genealogy Africans, English
TCF7L2 polymorphisms are associated with type 2 diabetes in northern Sweden
The complexity of reproductive decision-making in asymptomatic carriers of the Huntington mutation
Large genomic rearrangements in NIPBL are infrequent in Cornelia de Lange Syndrome
FGFR2, FGF8, FGF10 and BMP7 as candidate genes for hypospadias
‘Distorted’ mitochondrial DNA sequences in schizophrenic patients
Reply to Bandelt et al
Most pooling variation in array-based DNA pooling is attributable to array error rather than pool construction error
Paleolithic Y-haplogroup heritage predominates in a Cretan highland plateau
Recurrent rearrangements in the proximal 15q11–q14 region: a new breakpoint cluster specific to unbalanced translocations
Linkage and association analysis of CACNG3 in childhood absence epilepsy
Erratum: Germline CHEK2 mutations and colorectal cancer risk: different effects of a missense and truncating mutations?
Association of PDCD1 polymorphisms with childhood-onset systemic lupus erythematosus
Partial duplications of the MSH2 and MLH1 genes in hereditary nonpolyposis colorectal cancer
Progranulin mutations in Dutch familial frontotemporal lobar degeneration Dutch
Methylation analysis of the intergenic differentially methylated region of DLK1-GTL2 in human
Multiple mutations responsible for frequent genetic diseases in isolated populations
Refined genomic localization and ethnic differences observed for the IBD5 association with Crohn's disease
A seventh locus for otosclerosis, OTSC7, maps to chromosome 6q13–16.1
FGF10 missense mutations in aplasia of lacrimal and salivary glands (ALSG)
Significant variation in haplotype block structure but conservation in tagSNP patterns among global populations