European Journal of Human Genetics - 2006

210 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Mutation screening of brain-expressed X-chromosomal miRNA genes in 464 patients with nonsyndromic X-linked mental retardation
Cystic Fibrosis: Cystic fibrosis and lactase persistence: a possible correlation
Filaggrin mutations p.R501X and c.2282del4 in ichthyosis vulgaris
Functional analysis of human S-adenosylhomocysteine hydrolase isoforms SAHH-2 and SAHH-3
Methods for the selection of tagging SNPs: a comparison of tagging efficiency and performance
No contribution of angiotensin-converting enzyme (ACE) gene variants to severe obesity: a model for comprehensive case/control and quantitative cladistic analysis of ACE in human diseases
A counter-clockwise northern route of the Y-chromosome haplogroup N from Southeast Asia towards Europe
Are genome-wide association studies all that we need to dissect the genetic component of complex human diseases?
Genetic screening for autosomal recessive nonsyndromic mental retardation in an isolated population in Israel
Enhanced linkage of a locus on chromosome 2 to premature coronary artery disease in the absence of hypercholesterolemia
Multiple QTL influence the serum Lp(a) concentration: a genome-wide linkage screen in the PROCARDIS study
Reply to Jaskowski et al
Preselection of cases through expert clinical and radiological review significantly increases mutation detection rate in multiple epiphyseal dysplasia
Stability of BAT26 in Lynch syndrome colorectal tumours
Using HapMap data: a cautionary note
Erratum: Novel FGFR3 mutations creating cysteine residues in the extracellular domain of the receptor cause achondroplasia or severe forms of hypochondroplasia
Erratum: A test of homogeneity of Hardy–Weinberg disequilibrium across strata
Erratum: The emergence of an ethical duty to disclose genetic research results: international perspectives
Replication of reported linkages for dyslexia and spelling and suggestive evidence for novel regions on chromosomes 4 and 17
Detection of small genomic imbalances using microarray-based multiplex amplifiable probe hybridization
Germline CHEK2 mutations and colorectal cancer risk: different effects of a missense and truncating mutations?
The mitochondrial 13513G>A mutation is most frequent in Leigh syndrome combined with reduced complex I activity, optic atrophy and/or Wolff–Parkinson–White
Comprehensive mutational analysis of a cohort of Swedish Cornelia de Lange syndrome patients
Autozygosity mapping of Bardet–Biedl syndrome to 12q21.2 and confirmation of FLJ23560 as BBS10
Pairwise linkage disequilibrium under disease models
Allele dosage-dependent penetrance of RET proto-oncogene in an Israeli-Arab inbred family segregating Hirschsprung disease
Cortical dysplasia of the left temporal lobe might explain severe expressive-language delay in patients with duplication of the Williams–Beuren locus
A genome-wide scan for naevus count: linkage to CDKN2A and to other chromosome regions
Identification and molecular modelling of a novel familial mutation in the SRY gene implicated in the pure gonadal dysgenesis
Y-chromosomal evidence for a limited Greek contribution to the Pathan population of Pakistan Greek
Implication of abnormal epigenetic patterns for human diseases
Diagnostics: Genomic copy number analysis in mental retardation: finding the needles in the haystack
Association analysis of the ACTN3 R577X polymorphism and complex quantitative body composition and performance phenotypes in adolescent Greeks
A two base pair deletion in the PQBP1 gene is associated with microphthalmia, microcephaly, and mental retardation
Repeat expansion in spinocerebellar ataxia type 17 alleles of the TATA-box binding protein gene: an evolutionary approach
Towards mapping phenotypical traits in 18p− syndrome by array-based comparative genomic hybridisation and fluorescent in situ hybridisation
Rapid and reliable genotyping of polymorphic loci modifying correct splicing of CFTR pre-mRNA using mass spectrometry
The single-nucleotide polymorphism 309 in the MDM2 gene contributes to the Li–Fraumeni syndrome and related phenotypes
Mutation screening of BMP4, BMP7, HOXA4 and HOXB6 genes in Chinese patients with hypospadias Chinese
Vasoactive intestinal peptide gene alterations in patients with idiopathic pulmonary arterial hypertension
Cystatin B: mutation detection, alternative splicing and expression in progressive myclonus epilepsy of Unverricht-Lundborg type (EPM1) patients
A balanced perspective of psychiatric genetics: Psychiatric Genetics and Genomics
A breath of fresh air: Respiratory Genetics
A recent genetic link between Sami and the Volga-Ural region of Russia
Novel deletion variants of 9q13–q21.12 and classical euchromatic variants of 9q12/qh involve deletion, duplication and triplication of large tracts of segmentally duplicated pericentromeric euchromati
Sotos syndrome
Molecular genetic analysis of the human dihydrofolate reductase gene: relation with plasma total homocysteine, serum and red blood cell folate levels
X-linked mental retardation: a comprehensive molecular screen of 47 candidate genes from a 7.4 Mb interval in Xp11
Neurofibromatosis 1
A novel R486Q mutation in BMPR1B resulting in either a brachydactyly type C/symphalangism-like phenotype or brachydactyly type A2
The scale and nature of Viking settlement in Ireland from Y-chromosome admixture analysis
Changing rates of genetic subtypes of Prader–Willi syndrome in the UK
Identification of cryptic imbalance in phenotypically normal and abnormal translocation carriers
Heterotaxy and cardiac defect in a girl with chromosome translocation t(X;1)(q26;p13.1) and involvement of ZIC3
Otopalatodigital syndrome spectrum disorders: otopalatodigital syndrome types 1 and 2, frontometaphyseal dysplasia and Melnick-Needles syndrome
Erratum: The population history of the Croatian linguistic minority of Molise (southern Italy): a maternal view
Erratum: Meta-analysis of TNF-α promoter −308 A/G polymorphism and SLE susceptibility
Novel FGFR3 mutations creating cysteine residues in the extracellular domain of the receptor cause achondroplasia or severe forms of hypochondroplasia
Strong linkage on 2q33.3 to familial early-onset generalized osteoarthritis and a consideration of two positional candidate genes
The Börjeson–Forssman–Lehman syndrome (BFLS, MIM #301900)
Refinement of the locus for hereditary congenital facial palsy on chromosome 3q21 in two unrelated families and screening of positional candidate genes
Ulnar–mammary syndrome with dysmorphic facies and mental retardation caused by a novel 1.28 Mb deletion encompassing the TBX3 gene
A novel CSX/NKX2-5 mutation causes autosomal-dominant AV block: are atrial fibrillation and syncopes part of the phenotype?
Three different ABCA4 mutations in the same large family with several consanguineous loops affected with autosomal recessive cone–rod dystrophy
An utter refutation of the ‘Fundamental Theorem of the HapMap’ by Terwilliger and Hiekkalinna
The challenges of Proteus syndrome: diagnosis and management
Rubinstein–Taybi syndrome
Tuberous sclerosis
The emergence of an ethical duty to disclose genetic research results: international perspectives
A test of homogeneity of Hardy-Weinberg disequilibrium across strata
DISCERN-Genetics: quality criteria for information on genetic testing
An intronic variable number of tandem repeat polymorphisms of the cold-induced autoinflammatory syndrome 1 (CIAS1) gene modifies gene expression and is associated with essential hypertension
Recruiting first-degree relatives for prevention research: a comparison of clinician and proband-led methods of contact in Crohn's disease
Rett syndrome: new clinical and molecular insights
A practical guide for your daily activity: Atlas of Metabolic Diseases – Second Edition
Erratum: Optimal genotype determination in highly multiplexed SNP data
Practical genetics series introduction: Information overload, a double-edged sword
Gene mapping: Balance among quality, quantity and cost of data in the era of whole-genome mapping for complex disease
A functional candidate screen for coeliac disease genes
Parkinson's Disease: The LRRK2-G2019S mutation: opening a novel era in Parkinson's disease genetics
Alcoholism: Study boosts evidence on linkage regions associated with alcoholism
Increased skewing of X chromosome inactivation in Rett syndrome patients and their mothers
Pitfalls of homozygosity mapping: an extended consanguineous Bardet–Biedl syndrome family with two mutant genes (BBS2, BBS10), three mutations, but no triallelism
Epigenetics or ephemeral genetics?
Detection of a large genomic deletion in the pancreatic secretory trypsin inhibitor (SPINK1) gene
Reply to Senn
The value of gene-based selection of tag SNPs in genome-wide association studies
Handy Book on Cancer Genetics Risk Assessment
Association of a 31 bp VNTR in the CBS gene with postload homocysteine concentrations in the Framingham Offspring Study
DNA repair gene XRCC3 polymorphisms and cancer risk: a meta-analysis of 48 case–control studies
Association study of the G-protein signaling 4 (RGS4) and proline dehydrogenase (PRODH) genes with schizophrenia: a meta-analysis
Syndrome identification based on 2D analysis software
Simple detection of genomic microdeletions and microduplications using QMPSF in patients with idiopathic mental retardation
TBP as a candidate gene for mental retardation in patients with subtelomeric 6q deletions
ADAM33 haplotypes are associated with asthma in a large Australian population
The downstream modulator of interferon-γ, STAT1 is not genetically associated to the Dutch coeliac disease population
A novel missense mutation in ACTG1 causes dominant deafness in a Norwegian DFNA20/26 family, but ACTG1 mutations are not frequent among families with hereditary hearing impairment Norwegian
AHI1, a pivotal neurodevelopmental gene, and C6orf217 are associated with susceptibility to schizophrenia
Nonsense-mediated mRNA decay modulates clinical outcome of genetic disease
The role of mutagenesis in defining genes in behaviour
Molecular genetics of the fruit-fly circadian clock
The genetic basis of emotional behaviour in mice
Molecular genetic studies of schizophrenia
The genetics of developmental dyslexia
Genetics of intelligence
Focus on behavioural genetics
Genetics of autism spectrum disorder
A fascination with chromosome rescue in uniparental disomy: Mendelian recessive outlaws and imprinting copyrights infringements
A locus for sacral/anorectal malformations maps to 6q25.3 in a 0.3 Mb interval region
Variance components model with disequilibria
Y-chromosome diversity in Sweden – A long-time perspective
Genetic testing in Italy, year 2004
Skin Cancer: Basal cell carcinoma: genetic homogeneity in a tumour type displaying phenotypic diversity
Genetics of affective (mood) disorders
Genetics and pathophysiology of mental retardation
Assessing the pathogenicity of MLH1 missense mutations in patients with suspected hereditary nonpolyposis colorectal cancer: correlation with clinical, genetic and functional features
The influence of the alpha-adducin G460W polymorphism and angiotensinogen M235T polymorphism on antihypertensive medication and blood pressure
OLR1 gene and coronary artery disease/acute myocardial infarction: replication in an independently collected sample
Reply to Novelli
Delineation of the ADULT syndrome phenotype due to arginine 298 mutations of the p63 gene
A multistep mutation mechanism drives the evolution of the CAG repeat at MJD/SCA3 locus
Variation in ITGB3 is associated with whole-blood serotonin level and autism susceptibility
A simple method to localise pleiotropic susceptibility loci using univariate linkage analyses of correlated traits
Rapid genotyping of common deficient thiopurine S-methyltransferase alleles using the DNA-microchip technique
Cystic Fibrosis: Using genetic association to identify modifiers of disease variability in cystic fibrosis
Association Studies: A genome-wide association approach to mapping the genetic determinants of the transcriptome in human populations
Pigmentary Diversity: Identifying the genes causing human diversity
Covariate-based linkage analysis: application of a propensity score as the single covariate consistently improves power to detect linkage
Array comparative genomic hybridization in patients with congenital diaphragmatic hernia: mapping of four CDH-critical regions and sequencing of candidate genes at 15q26.1–15q26.2
New mutations in the NHS gene in Nance–Horan Syndrome families from the Netherlands
The effective size of the Icelandic population and the prospects for LD mapping: inference from unphased microsatellite markers
A summary statistic approach to sequence variation in noncoding regions of six schizophrenia-associated gene loci
Chromosome 5 and Parkinson disease
Reply to Hochstenbach et al
Segregation ratio in cranio-cerebello-cardiac syndrome
No evidence for association of a European-specific chromosome 17 inversion with multiple sclerosis European-specific
2nd International Meeting on Cryptic Chromosomal Rearrangements in Mental Retardation and Autism
Mosaicism for mitochondrial DNA polymorphic variants in placenta has implications for the feasibility of prenatal diagnosis in mtDNA diseases
KCNJ11 activating mutations are associated with developmental delay, epilepsy and neonatal diabetes syndrome and other neurological features
Genistein-mediated inhibition of glycosaminoglycan synthesis as a basis for gene expression-targeted isoflavone therapy for mucopolysaccharidoses
Localization of candidate regions for a novel gene for Kartagener syndrome
Germline fumarate hydratase mutations in patients with ovarian mucinous cystadenoma
Reply to Professor Haig
Congenital bilateral absence of the vas deferens and recombination at CFTR
Molecular analysis of ANT1, TWINKLE and POLG in patients with multiple deletions or depletion of mitochondrial DNA by a dHPLC-based assay
Linkage of autosomal-dominant common variable immunodeficiency to chromosome 4q
Expanding the phenotype of craniofrontonasal syndrome: two unrelated boys with EFNB1 mutations and congenital diaphragmatic hernia
The interface between assisted reproductive technologies and genetics: technical, social, ethical and legal issues
The need for interaction between assisted reproduction technology and genetics
Assisted reproduction and genetics
Clinical genetics: Medical genetics
Differences in methylation patterns in the methylation boundary region of IDS gene in hunter syndrome patients: implications for CpG hot spot mutations
Parental and chromosomal origins of microdeletion and duplication syndromes involving 7q11.23, 15q11-q13 and 22q11
Sequence variations in the 5′ upstream regions of the FBN1 gene associated with Marfan syndrome
Scientific rationality, uncertainty and the governance of human genetics: an interview study with researchers at deCODE genetics
Identification of cis- and trans-acting factors possibly modifying the risk of epimutations on chromosome 15
Evidence from autoimmune thyroiditis of skewed X-chromosome inactivation in female predisposition to autoimmunity
SLC26A4 gene is frequently involved in nonsyndromic hearing impairment with enlarged vestibular aqueduct in Caucasian populations
Haplotype-based association analysis of 56 functional candidate genes in the IBD6 locus on chromosome 19
Interstitial 9q22.3 microdeletion: clinical and molecular characterisation of a newly recognised overgrowth syndrome
Evolutionary Genetics: Is brain evolution still continuing in modern humans?
Deletions of 2q14 that include the homeobox engrailed 1 (EN1) transcription factor are compatible with a normal phenotype
Confirmation of the R653Q polymorphism of the trifunctional C1-synthase enzyme as a maternal risk for neural tube defects in the Irish population
New variants in the mitochondrial genomes of schizophrenic patients
Huntington's Disease: A transcriptional report card from the peripheral blood: Can it measure disease progression in Huntington's disease?
Postzygotic mutation and germline mosaicism in the otopalatodigital syndrome spectrum disorders
Use of phenotypic covariates in association analysis by sequential addition of cases
Two de novo mutations in the Na,K-ATPase gene ATP1A2 associated with pure familial hemiplegic migraine
A novel mutation in JARID1C gene associated with mental retardation
Human Genome: Which proteins contribute to human-chimpanzee differences?
Williams–Beuren Syndrome: More or less? Segmental duplications and deletions in the Williams–Beuren syndrome region provide new insights into language development
MORM syndrome (mental retardation, truncal obesity, retinal dystrophy and micropenis), a new autosomal recessive disorder, links to 9q34
A text-mining analysis of the human phenome
Extreme heterogeneity in CARD15 and DLG5 Crohn disease-associated polymorphisms between German and Norwegian populations
The impact of data quality on the identification of complex disease genes: experience from the Family Blood Pressure Program
Schizophrenia genetics: uncovering positional candidate genes
3000 years of solitude: extreme differentiation in the island isolates of Dalmatia, Croatia
Gross genomic rearrangements involving deletions in the CFTR gene: characterization of six new events from a large cohort of hitherto unidentified cystic fibrosis chromosomes and meta-analysis of the
Role of interferon-γ gene polymorphisms in susceptibility to IgA nephropathy: a family-based association study
Systematic re-examination of carriers of balanced reciprocal translocations: a strategy to search for candidate regions for common and complex diseases
Exonic microdeletions in the X-linked PQBP1 gene in mentally retarded patients: a pathogenic mutation and in-frame deletions of uncertain effect
Molecular analysis of a human PAX6 homeobox mutant
Molecular characterization of a novel PAX9 missense mutation causing posterior tooth agenesis
An utter refutation of the ‘Fundamental Theorem of the HapMap’
It's ‘back to school’ for genetic screening
Phenotypic and genotypic heterogeneity in the Lynch syndrome: diagnostic, surveillance and management implications
Influence of serotonin receptor 2A His452Tyr polymorphism on brain temporal structures: a volumetric MR study
Y-chromosomal STR haplotype analysis reveals surname-associated strata in the East-German population
Identification of probable genotyping errors by consideration of haplotypes
Highly discrepant proportions of female and male Scandinavian and British Isles ancestry within the isolated population of the Faroe Islands Scandinavian and British Isles ancestry
The adiponectin gene is associated with adiponectin levels but not with characteristics of the insulin resistance syndrome in healthy Caucasians
Meta-analysis of TNF-α promoter −308 A/G polymorphism and SLE susceptibility
Confirmation of mosaicism and uniparental disomy in amniocytes, after detection of mosaic chromosome abnormalities in chorionic villi
Mutation screening in patients with syndromic craniosynostoses indicates that a limited number of recurrent FGFR2 mutations accounts for severe forms of Pfeiffer syndrome
Compound heterozygosity for two MSH6 mutations in a patient with early onset of HNPCC-associated cancers, but without hematological malignancy and brain tumor
Ovarian Cancer: Identification of remodeling and spacing factor 1 (rsf-1, HBXAP) at chromosome 11q13 as a putative oncogene in ovarian cancer
Reply to Dr Martin
Epigenetics: Sins of the fathers, and their fathers
Reply to Tenesa et al ‘Association of DLG5 and inflammatory bowel disease across populations’
A genome-wide search for linkage to asthma phenotypes in the genetics of asthma international network families: evidence for a major susceptibility locus on chromosome 2p
The associations of ACE polymorphisms with physical, physiological and skill parameters in adolescents
Validity of tagging SNPs across populations for association studies
Abolishing Trp53-dependent apoptosis does not benefit spinal muscular atrophy model mice
Association of DLG5 and inflammatory bowel disease across populations
Linkage and potential association of obesity-related phenotypes with two genes on chromosome 12q24 in a female dizygous twin cohort
Microarray-based genome investigation: molecular karyotyping or segmental aneuploidy profiling?
Personalized Medicine Europe: Health, Genes and Society: Tel-Aviv University, Tel-Aviv, Israel, June 19–21, 2005
Transmission ratio distortion in the myotonic dystrophy locus in human preimplantation embryos
Reply to Daly and Rioux response
Prion disease genetics