European Journal of Human Genetics - 2005

195 articles | Last updated: 2025-12-03 14:12:56
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Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Say what we mean, mean what we say
Copy number variation in regions flanked (or unflanked) by duplicons among patients with developmental delay and/or congenital malformations; detection of reciprocal and partial Williams-Beuren duplic
Multiple Sclerosis: Light at the end of the tunnel
Sex-specific, male-line transgenerational responses in humans
Evaluating the role of the 620W allele of protein tyrosine phosphatase PTPN22 in Crohn's disease and multiple sclerosis
Association study of major risk single nucleotide polymorphisms in the common regulatory region of PARK2 and PACRG genes with leprosy in an Indian population
Hidden population substructures in an apparently homogeneous population bias association studies
Association of the organic cation transporter OCTN genes with Crohn's disease in the Spanish population Spanish population
Large animal models and gene therapy
A novel mutation in PAX9 causes familial form of molar oligodontia
Comprehensive analysis of the LRRK2 gene in sixty families with Parkinson's disease
Family based association analysis of the IL2 and IL15 genes in allergic disorders
BARD1 variants Cys557Ser and Val507Met in breast cancer predisposition
Autosomal recessive mutilating sensory neuropathy with spastic paraplegia maps to chromosome 5p15.31–14.1
Comment on ‘cosegregation of two unlinked mutant alleles in some cases of autosomal dominant familial exudative vitreoretinopathy’
Enlarged parietal foramina caused by mutations in the homeobox genes ALX4 and MSX2: from genotype to phenotype
Myotonic dystrophy-time to improve patient care and prepare for pathogenesis based treatments
Haplotype analysis of tumour necrosis factor receptor genes in 1p36: no evidence for association with systemic lupus erythematosus
Clustering of haplotypes based on phylogeny: how good a strategy for association testing?
Optimal genotype determination in highly multiplexed SNP data
Do we need a uniform regulatory system for biobanks across Europe?
Segmental duplication density decrease with distance to human-mouse breaks of synteny
Clock genes as a link between addiction and obesity
Cancer Transcriptomics: Modeling metastasis
Mouse models: Psoriasis: an epidermal disease after all?
Improving the accuracy of BRCA1/2 mutation prediction: validation of the novel country-customized IC software
Reply to Bottomley et al
Genome-wide linkage scan for spontaneous DZ twinning
Recent advances in array comparative genomic hybridization technologies and their applications in human genetics
Carrier testing in minors: a systematic review of guidelines and position papers
Genetic background of HSH in three Polish families and a patient with an X;9 translocation Polish
Genetics of the Lp(a)/apo(a) system in an autochthonous Black African population from the Gabon Black African
Two candidate genes for low platelet count identified in an Asian Indian kindred by genome-wide linkage analysis: glycoprotein IX and thrombopoietin Asian Indian
Technology: A genome sequencing center in every lab
Replication of IGF2-INS-TH*5 haplotype effect on obesity in older men and study of related phenotypes
Saethre–Chotzen syndrome caused by TWIST 1 gene mutations: functional differentiation from Muenke coronal synostosis syndrome
On the association of the oxidised LDL receptor 1 (OLR1) gene in patients with acute myocardial infarction or coronary artery disease
Association of β2 adrenergic receptor polymorphisms and related haplotypes with triglyceride and LDL-cholesterol levels
Haplotype block structure study of the CFTR gene. Most variants are associated with the M470 allele in several European populations European populations
Two novel and one known mutation of the TGFBR2 gene in Marfan syndrome not associated with FBN1 gene defects
Analysing DNA patents in relation with diagnostic genetic testing
Genetics of human heterotaxias
Evidence of genetic enrichment for exceptional survival using a family approach: the Leiden Longevity Study
Nonlinear association between CGG repeat number and age of menopause in FMR1 premutation carriers
Complex disease: Pleiotropic gene effects in obesity and type 2 diabetes
Stability of BAT26 in tumours of hereditary nonpolyposis colorectal cancer patients with MSH2 intragenic deletion
Molecular diagnosis of human cancer type by gene expression profiles and independent component analysis
SLC25A12 and CMYA3 gene variants are not associated with autism in the IMGSAC multiplex family sample
Evidence for clinical and genetic heterogeneity of syndactyly type I: the phenotype of second and third toe syndactyly maps to chromosome 3p21.31
Management of hereditary dyslipidaemia; the paradigm of autosomal dominant hypercholesterolaemia
Erratum: Mutations in the known genes are not the major cause of MED; distinctive phenotypic entities among patients with no identified mutations
A review of international and UK-based ethical guidelines for researchers conducting nontherapeutic genetic studies in developing countries
Incidence of microduplication 22q11.2 in patients referred for FISH testing for velo cardiofacial and DiGeorge syndromes
Novel and de novo mutations of the IRF6 gene detected in patients with Van der Woude or popliteal pterygium syndrome
Mutation analysis of the WFS1 gene in seven Danish Wolfram syndrome families; four new mutations identified
Association of KCNQ1, KCNE1, KCNH2 and SCN5A polymorphisms with QTc interval length in a healthy population
Interferon regulatory factor-6: a gene predisposing to isolated cleft lip with or without cleft palate in the Belgian population
The molecular genetics of haemochromatosis
Association of the TSHR gene with Graves' disease: the first disease specific locus
Molecular cytogenetic analyses of breakpoints in apparently balanced reciprocal translocations carried by phenotypically normal individuals
Partial iris hypoplasia in a patient with an interstitial subtelomeric 6p deletion not including the forkhead transcription factor gene FOXC1
A new edition of a must have handbook for genetic counsellors
Variable expressivity of the clinical and biochemical phenotype associated with the apolipoprotein E p.Leu149del mutation
Demography: Peopling the Americas
Research network: EuroGentest – a European Network of Excellence aimed at harmonizing genetic testing services
The place of the Basques in the European Y-chromosome diversity landscape European
Biological clock: Biological clocks may modulate drug addiction
Mutation spectrum leading to an attenuated phenotype in dystrophinopathies
Forty-two supernumerary marker chromosomes (SMCs) in 43 273 prenatal samples: chromosomal distribution, clinical findings, and UPD studies
Mosaics of ancient mitochondrial DNA: positive indicators of nonauthenticity
Cancer genetics: Finding the right mix
p.R270X MECP2 mutation and mortality in Rett syndrome
Dimensional phenotypic analysis and functional categorisation of mutations reveal novel genotype–phenotype associations in Rett syndrome
Analysis of four neuroligin genes as candidates for autism
Duplications and copy number variants of 8p23.1 are cytogenetically indistinguishable but distinct at the molecular level
The pick of the crop
Erratum: Measured haplotype analysis of the aldosterone synthase gene and heart size
A most welcome new edition in a fast advancing field
Deletion and duplication screening in the DMD gene using MLPA
Genetic determinants of plasma HDL-cholesterol levels in familial hypercholesterolemia
No evidence for an association between extreme longevity and Microsomal Transfer Protein polymorphisms in a longitudinal study of 1651 nonagenarians
Effect of the APOC3 Sst I SNP on fasting triglyceride levels in men heterozygous for the LPL P207L deficiency
Early onset seizures and Rett-like features associated with mutations in CDKL5
Meta-analysis of four new genome scans for lipid parameters and analysis of positional candidates in positive linkage regions
Research Networks: BioSapiens: a European network for integrated genome annotation
Gene Expression: Growing up together may help genes go their separate ways
Partners of mutation-carriers for Huntington's disease: forgotten persons?
Molecular subtypes and phenotypic expression of Beckwith–Wiedemann syndrome
Polymorphism at 3′ UTR +28 of the prion-like protein gene is associated with sporadic Creutzfeldt–Jakob disease
Molecular characterisation of patients with subtelomeric 22q abnormalities using chromosome specific array-based comparative genomic hybridisation
Ultraconserved regions in multiple sclerosis
Potential harms, anonymization, and the right to withdraw consent to biobank research
Hereditary hearing loss—the updated resource book more needed than ever
Genetic Epidemiology
Genetic nephrology
A classic genetic text about classic genetic texts
PINK1, Parkin, and DJ-1 mutations in Italian patients with early-onset parkinsonism
Genomics: The amazing complexity of the human transcriptome
Communication of pharmacogenetic research results to HIV-infected treated patients: standpoints of professionals and patients
Pedigree construction and disease confirmation: a pilot study in Wales exploring the role of nonclinical personnel
Male-to-male transmission of X-linked Alport syndrome in a boy with a 47,XXY karyotype
Combining the case–control methodology with the small size transmission/disequilibrium test for multiallelic markers
Estrogen receptor beta gene variants are associated with increased risk of Alzheimer's disease in women
Nondisease genetic testing: reporting of muscle SNPs shows effects on self-concept and health orientation scales
Genotype–phenotype studies in nail-patella syndrome show that LMX1B mutation location is involved in the risk of developing nephropathy
Trisomy 7 mosaicism, maternal uniparental heterodisomy 7 and Hirschsprung's disease in a child with Silver–Russell syndrome
Loss of ZDHHC15 expression in a woman with a balanced translocation t(X;15)(q13.3;cen) and severe mental retardation
Paternal deletion of the GNAS imprinted locus (including Gnasxl) in two girls presenting with severe pre- and post-natal growth retardation and intractable feeding difficulties
Cancer Genetics: TSC1, TSC2, TSC3? or mosaicism?
Typing without calling the allele: a strategy for inferring SNP haplotypes
Immunogenetics: Safety in numbers
Hutterite brothers both affected with two forms of limb girdle muscular dystrophy: LGMD2H and LGMD2I
Mitochondrial DNA and ACTN3 genotypes in Finnish elite endurance and sprint athletes
RAR-related orphan receptor A isoform 1 (RORa1) is disrupted by a balanced translocation t(4;15)(q22.3;q21.3) associated with severe obesity
Short tandem repeats haplotyping of the HLA region in preimplantation HLA matching
The population history of the Croatian linguistic minority of Molise (southern Italy): a maternal view
Bioinformatics: Computers or clinicians for complex disease risk assessment?
Disruption of Netrin G1 by a balanced chromosome translocation in a girl with Rett syndrome
X Chromosome Inactivation: No longer ‘all-or-none’
Hereditary nonpolyposis colorectal cancer: pitfalls in deletion screening in MSH2 and MLH1 genes
High-throughput pedigree drawing
Screening of mutations in the CFTR gene in 1195 couples entering assisted reproduction technique programs
The difference between observed and expected prevalence of MCAD deficiency in The Netherlands: a genetic epidemiological study
Construction of a natural panel of 11p11.2 deletions and further delineation of the critical region involved in Potocki–Shaffer syndrome
Erratum: One-third of Danish hypertrophic cardiomyopathy patients with MYH7 mutations have mutations in rod region
Contrasting patterns of Y chromosome and mtDNA variation in Africa: evidence for sex-biased demographic processes
Allele variations in the OCA2 gene (pink-eyed-dilution locus) are associated with genetic susceptibility to melanoma
An investigation of NOS2A promoter polymorphisms in Australian multiple sclerosis patients
Childhood overgrowth in patients with common NF1 microdeletions
Complex Disease: A new vision for age-related macular degeneration
TaqIB polymorphism in CETP gene: the influence on incidence of cardiovascular disease in statin-treated patients with familial hypercholesterolemia
Association of the CTLA-4 gene with rheumatoid arthritis in Chinese Han population Chinese Han population
Association of DLG5 R30Q variant with inflammatory bowel disease
An association study of the N-methyl-D-aspartate receptor NR1 subunit gene (GRIN1) and NR2B subunit gene (GRIN2B) in schizophrenia with universal DNA microarray
Mitochondrial DNA haplogroup K is associated with a lower risk of Parkinson's disease in Italians
Protein studies in dysferlinopathy patients using llama-derived antibody fragments selected by phage display
Univariate and bivariate variance component linkage analysis of a whole-genome scan for loci contributing to bone mineral density
Haplotype construction of the FRDA gene and evaluation of its role in type II diabetes
Hardy–Weinberg equilibrium in genetic association studies: an empirical evaluation of reporting, deviations, and power
Fine mapping of a schizophrenia susceptibility locus at chromosome 6q23: increased evidence for linkage and reduced linkage interval
Twin Research: Exploring female sexuality
A new CARD15 mutation in Blau syndrome
Proopiomelanocortin gene variants are associated with serum leptin and body fat in a normal female population
Most DC-SIGNR transcripts at mucosal HIV transmission sites are alternatively spliced isoforms
Mutational analysis of the TSC1 and TSC2 genes in a diagnostic setting: genotype – phenotype correlations and comparison of diagnostic DNA techniques in Tuberous Sclerosis Complex
Complex trait mapping in isolated populations: Are specific statistical methods required?
Genetic stratification of pathogen-response-related and other variants within a homogeneous Caucasian Irish population Irish population
Interaction of the LMX1B and PAX2 gene products suggests possible molecular basis of differential phenotypes in Nail–Patella syndrome
Kabuki syndrome: new ocular findings but no evidence of 8p22-p23.1 duplications in a clinically defined cohort
Failure to detect an 8p22–8p23.1 duplication in patients with Kabuki (Niikawa–Kuroki) syndrome
Mutations in exon 1 of MECP2B are not a common cause of X-linked mental retardation in males
Testing for triallelism: analysis of six BBS genes in a Bardet–Biedl syndrome family cohort
Novel mutations in BCOR in three patients with oculo-facio-cardio-dental syndrome, but none in Lenz microphthalmia syndrome
Genetic professionals' reports of nondisclosure of genetic risk information within families
Common regulatory elements in the polycystic kidney disease 1 and 2 promoter regions
Homocysteine levels – before and after methionine loading – in 51 Dutch families Dutch
Evolutionary Genetics: The human brain – adaptation at many levels
About the origin and development of hereditary conventional renal cell carcinoma in a four-generation t(3;8)(p14.1;q24.23) family
Schistosomal hepatic fibrosis and the interferon gamma receptor: a linkage analysis using single-nucleotide polymorphic markers
High frequencies of Y chromosome lineages characterized by E3b1, DYS19-11, DYS392-12 in Somali males
COMP mutation screening as an aid for the clinical diagnosis and counselling of patients with a suspected diagnosis of pseudoachondroplasia or multiple epiphyseal dysplasia
FISH of supernumerary marker chromosomes (SMCs) identifies six diagnostically relevant intervals on chromosome 22q and a novel type of bisatellited SMC(22)
A y+LAT-1 mutant protein interferes with y+LAT-2 activity: implications for the molecular pathogenesis of lysinuric protein intolerance
Twin study of genetic and aging effects on X chromosome inactivation
Mutations and sequence variation in the human myosin heavy chain IIa gene (MYH2)
Unclassified variants in disease-causing genes: nonuniformity of genetic testing and counselling, a proposal for guidelines
Functional disomy of the Xq28 chromosome region
Familial nonrandom inactivation linked to the X inactivation centre in heterozygotes manifesting haemophilia A
Frequency of large CFTR gene rearrangements in Italian CF patients
Differential epigenetic modifications in the FMR1 gene of the fragile X syndrome after reactivating pharmacological treatments
Genetic Epidemiology of Cancer: Relatively risky relatives
Exclusion of the dymeclin and PAPSS2 genes in a novel form of spondyloepimetaphyseal dysplasia and mental retardation
Genetic Testing: From chromosomes to DNA, a revolution in prenatal diagnosis
Gene Therapy: The ‘pro-sense’ approach to Duchenne muscular dystrophy
Combination of WAGR and Potocki–Shaffer contiguous deletion syndromes in a patient with an 11p11.2–p14 deletion
Cancer Genetics: Activated Notch takes center stage in T-cell leukemogenesis
Association between SLC11A1 (formerly NRAMP1) and the risk of sarcoidosis in Poland
Low frequency of mtDNA point mutations in patients with PEO associated with POLG1 mutations
Cascade Screening: Whose information is it anyway?
A family-based association study does not support DYX1C1 on 15q21.3 as a candidate gene in developmental dyslexia
Erratum: A new form of autosomal dominant limb-girdle muscular dystrophy (LGMD1G) with progressive fingers and toes flexion limitation maps to chromosome 4p21
Erratum: Loss of lysosomal association of cystatin B proteins representing progressive myoclonus epilepsy, EPM1, mutations
Patients with familial biparental hydatidiform moles have normal methylation at imprinted genes
Polymorphisms in APOA1 and LPL genes are statistically independently associated with fasting TG in men with CAD
Linkage disequilibrium patterns vary substantially among populations
Determination of the ‘critical region’ for cat-like cry of Cri-du-chat syndrome and analysis of candidate genes by quantitative PCR
Confidentiality and serious harm in genetics
Dilemma still not resolved
Sequence variation in the ATP8B1 gene and intrahepatic cholestasis of pregnancy
A common CTLA4 haplotype associated with coeliac disease
Cascade testing in familial hypercholesterolaemia: how should family members be contacted?
Defective protein glycosylation in patients with cutis laxa syndrome
LHON/MELAS overlap syndrome associated with a mitochondrial MTND1 gene mutation
A 2.3 Mb duplication of chromosome 8q24.3 associated with severe mental retardation and epilepsy detected by standard karyotype
Haplotype structure of TNFRSF5-TNFSF5 (CD40–CD40L) and association analysis in systemic lupus erythematosus