European Journal of Human Genetics - 2004

217 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
Evolutionary Genetics: Genetics of lactase persistence – fresh lessons in the history of milk drinking
Information and informed consent in a longitudinal screening involving children: a questionnaire survey
Association of BDNF with restricting anorexia nervosa and minimum body mass index: a family-based association study of eight European populations European populations
Identification of a novel mevalonate kinase gene mutation in combination with the common MVK V377I substitution and the low-penetrance TNFRSF1A R92Q mutation
Statistical Genetics: Usual suspects in complex disease
Research Network: EUROGLYCANET: a European network focused on congenital disorders of glycosylation a European network
Segmental haplosufficiency: transmitted deletions of 2p12 include a pancreatic regeneration gene cluster and have no apparent phenotypic consequences
CNGB3 mutations account for 50% of all cases with autosomal recessive achromatopsia
X-chromosome as a marker for population history: linkage disequilibrium and haplotype study in Eurasian populations
Genetic and clinical characteristics of maturity-onset diabetes of the young in Chinese patients
New year, new faces and new copy
Somatic mosaicism for a heterozygous deletion of the survival motor neuron (SMN1) gene
Paternal isodisomy for chromosome 2 as the cause of Crigler–Najjar type I syndrome
Unexpected high frequency of P46L TNFRSF1A allele in sub-Saharan West African populations
Mutation screening of EXT1 and EXT2 by direct sequence analysis and MLPA in patients with multiple osteochondromas: splice site mutations and exonic deletions account for more than half of the mutatio
Genomics: The human genome, revisited
Margareta Mikkelsen, 4 November 1923–28 June 2004
Mosaic imprinting defect in a patient with an almost typical expression of the Prader–Willi syndrome
FHR-4A: a new factor H-related protein is encoded by the human FHR-4 gene
A neurological phenotype in nail patella syndrome (NPS) patients illuminated by studies of murine Lmx1b expression
Novel length variant of the polypyrimidine tract within the splice acceptor site in intron 8 of the CFTR gene: consequences for genetic testing using standard assays
Possible role of USP26 in patients with severely impaired spermatogenesis
Corneal dystrophies and degenerations: a molecular genetics approach
Huntington's disease, third edition: Oxford monographs on medical genetics
Linkage and mutational analysis of familial thyroid dysgenesis demonstrate genetic heterogeneity implicating novel genes
MVK mutations and associated clinical features in Italian patients affected with autoinflammatory disorders and recurrent fever
Evolutionary Genetics: Evolutionary path to the heart
A large-scale study of the random variability of a coding sequence: a study on the CFTR gene
Genomics: Polymorphic landscape of the human genome
A genomewide linkage analysis for prostate cancer susceptibility genes in families from Germany
Quantification of allele-specific G-protein β3 subunit mRNA transcripts in different human cells and tissues by Pyrosequencing
Diagnostic investigations in individuals with mental retardation: a systematic literature review of their usefulness
Haplotype structure of the beta adrenergic receptor genes in US Caucasians and African Americans African Americans
Mutations in the known genes are not the major cause of MED; distinctive phenotypic entities among patients with no identified mutations
A further mutation of the FGFR2 tyrosine kinase domain in mild Crouzon syndrome
No germline FH mutations in familial breast cancer patients
Biological variations, genetic polymorphisms and familial resemblance of TNF-α and IL-6 concentrations: STANISLAS cohort
Mutation screening and association analysis of six candidate genes for autism on chromosome 7q
PARK11 is not linked with Parkinson's disease in European families European families
Y chromosome evidence for a founder effect in Ashkenazi Jews
Phenylbutyrate increases SMN gene expression in spinal muscular atrophy patients
Uroplakin III is not a major candidate gene for primary vesicoureteral reflux
Epistatic interaction between the monoamine oxidase A and serotonin transporter genes in anorexia nervosa
Population genetics: Female migration rate might not be greater than male rate
Supernumerary marker chromosomes in man: parental origin, mosaicism and maternal age revisited
Mutation in the 5′ alternatively spliced region of the XNP/ATR-X gene causes Chudley–Lowry syndrome
Erratum: The geography of HFE mutations: molecular diagnosis of haemochromatosis and the globalization of genetic testing
Congenital afibrinogenaemia caused by uniparental isodisomy of chromosome 4 containing a novel 15-kb deletion involving fibrinogen Aα-chain gene
Deep genomics in shallow times: the finished sequence of human chromosomes 13 and 19
Association of haplotypes in the β-chemokine locus with multiple sclerosis
Genome-wide screening using array-CGH does not reveal microdeletions/microduplications in children with Kabuki syndrome
Microarray-based mutation analysis of the ABCA4 (ABCR) gene in autosomal recessive cone–rod dystrophy and retinitis pigmentosa
Single-nucleotide polymorphisms in genes relating to homocysteine metabolism: how applicable are public SNP databases to a typical European population? typical European population
Screening for FXTAS
No association between three xeroderma pigmentosum group C and one group G gene polymorphisms and risk of cutaneous melanoma
Evaluation of NSD2 and NSD3 in overgrowth syndromes
Loss of lysosomal association of cystatin B proteins representing progressive myoclonus epilepsy, EPM1, mutations
Computer-assisted prenatal aneuploidy screening for chromosome 13, 18, 21, X and Y based on multiplex ligation-dependent probe amplification (MLPA)
A combination of three common inherited mitochondrial DNA polymorphisms promotes longevity in Finnish and Japanese subjects
Screening for FMR-1 premutations in 122 older Flemish males presenting with ataxia
Genotype-based screening for hereditary haemochromatosis. I: Technical performance, costs and clinical relevance of a German pilot study
Mutations including the promoter region of myocilin/TIGR gene
Pedigree linkage disequilibrium mapping of quantitative trait loci
Delineation of mechanisms and regions of dosage imbalance in complex rearrangements of 1p36 leads to a putative gene for regulation of cranial suture closure
Complex segregation analysis of nasopharyngeal carcinoma in Guangdong, China: evidence for a multifactorial mode of inheritance (complex segregation analysis of NPC in China)
One third of Danish hypertrophic cardiomyopathy patients have mutations in MYH7 rod region
Distinct effects of single amino-acid changes to tuberin on the function of the tuberin–hamartin complex
Duchenne Muscular Dystrophy: Stalled at the junction?
Mutation analysis in the fibroblast growth factor 14 gene: frameshift mutation and polymorphisms in patients with inherited ataxias
New tools for preimplantation genetic diagnosis of Huntington's disease and their clinical applications
Subcellular distribution of HP1 proteins is altered in ICF syndrome
Situs ambiguus in a female fetus with balanced (X;21) translocation – evidence for functional nullisomy of the ZIC3 gene?
Phenotypic variability in Angelman syndrome: comparison among different deletion classes and between deletion and UPD subjects
Family-based association study of DYX1C1 variants in autism
Familial pericentric inversion of chromosome 18: behavioral abnormalities in patients heterozygous for either the dup(18p)/del(18q) or dup(18q)/del(18p) recombinant chromosome
New insights on the evolution of the SMN1 and SMN2 region: simulation and meta-analysis for allele and haplotype frequency calculations
Interaction between obesity-susceptibility loci in chromosome regions 2p25-p24 and 13q13-q21
Overdispersion of allele frequency differences between populations: implications for meta-analyses of genotypic disease associations
Association of the mitochondrial DNA haplogroup J with longevity is population specific
A second locus mapping to 2q35–36 for familial pseudohyperkalaemia
A novel PTPN11 gene mutation bridges Noonan syndrome, multiple lentigines/LEOPARD syndrome and Noonan-like/multiple giant cell lesion syndrome
Model-fitting and linkage analysis of sodium–lithium countertransport
Detection of the founder effect in Finnish CADASIL families
An excess of chromosome 1 breakpoints in male infertility
CD40 ligand gene and Kawasaki disease
Variation in exon 1 coding region and promoter of MECP2 in Rett syndrome and controls
Molecular evidence for absence of Y-linkage of the Hairy Ears trait
Detect and adjust for population stratification in population-based association study using genomic control markers: an application of Affymetrix Genechip® Human Mapping 10K array
Three consecutive triploidy pregnancies in a woman: genetic predisposition?
TLR4/Asp299Gly, CD14/C-260T, plasma levels of the soluble receptor CD14 and the risk of coronary heart disease: The PRIME Study
The common PPAR-γ2 Pro12Ala variant is associated with greater insulin sensitivity
Fcγ receptor IIA genotype and susceptibility to P. aeruginosa infection in patients with cystic fibrosis
A new form of autosomal dominant limb-girdle muscular dystrophy (LGMD1G) with progressive fingers and toes flexion limitation maps to chromosome 4p21
Penetrances of breast and ovarian cancer in a large series of families tested for BRCA1/2 mutations
Extension of the mutation spectrum in Friedreich's ataxia: detection of an exon deletion and novel missense mutations
Genotyping in 46 patients with tentative diagnosis of Treacher Collins syndrome revealed unexpected phenotypic variation
Molecular diversity at the CYP2D6 locus in the Mediterranean region
Combining the transmission disequilibrium test and case–control methodology using generalized logistic regression
The geography of HFE mutations: molecular diagnosis of haemochromatosis and the globalization of genetic testing
Monogenic X-linked mental retardation: Is it as frequent as currently estimated? The paradox of the ARX (Aristaless X) mutations
QTLs for height: results of a full genome scan in Dutch sibling pairs
Accurate determination of microsatellite allele frequencies in pooled DNA samples
Homozygous loss of a cysteine residue in the glucocerebrosidase gene results in Gaucher's disease with a hydropic phenotype
Strategies for the rapid prenatal diagnosis of chromosome aneuploidy
Genome-wide association study identifies ITGB3 as a QTL for whole blood serotonin
Mitochondrial DNA mutations in patients with postlingual, nonsyndromic hearing impairment
A susceptibility gene for premature ovarian failure (POF) maps to proximal Xq28
Breast cancer: role of polymorphisms in biotransformation enzymes
Clinical features and molecular analysis of seven British kindreds with hereditary hyperferritinaemia cataract syndrome
Reduced genetic structure of the Iberian peninsula revealed by Y-chromosome analysis: implications for population demography
Congenital deficiency of alpha feto-protein
Multivariate QTL linkage analysis suggests a QTL for platelet count on chromosome 19q
Genetics of mitochondrial diseases
Chromosome Abnormalities and Genetic Counselling
Claes Lundsteen—in Memoriam
Lipoxygenases at the heart of atherosclerosis susceptibility
Erratum: Systemic lupus erythematosus (SLE) and chromosome 16: confirmation of linkage to 16q12–13 and evidence for genetic heterogeneity
A trio family study showing association of the lymphotoxin-α N26 (804A) allele with coronary artery disease
Mutation analysis of five candidate genes in Chinese patients with hypospadias Chinese patients
Inverted duplications: how many of them are mosaic?
Complete genomic structure of the human nebulin gene and identification of alternatively spliced transcripts
Polymorphisms of the PRNP gene in Chinese populations and the identification of a novel insertion mutation
Handling missing values in population data: consequences for maximum likelihood estimation of haplotype frequencies
A double cryptic chromosome imbalance is an important factor to explain phenotypic variability in Wolf–Hirschhorn syndrome
1024C>T (R342X) is a recurrent PHF6 mutation also found in the original Börjeson–Forssman–Lehmann syndrome family
RNAi of COL1A1 in mesenchymal progenitor cells
Cox proportional hazards survival regression in haplotype-based association analysis using the Stochastic-EM algorithm
Paraoxonase 1 polymorphisms and survival
Modulating effect of the A-278C promoter polymorphism in the cholesterol 7alpha-hydroxylase gene on serum lipid levels in normolipidaemic and hypertriglyceridaemic individuals
Effect of genetic variation in the human S-adenosylhomocysteine hydrolase gene on total homocysteine concentrations and risk of recurrent venous thrombosis
Familial correlations and inter-relationships of four asthma-associated quantitative phenotypes in 320 French EGEA families ascertained through asthmatic probands
Establishment of genetic associations for complex diseases is independent of early study findings
The peptide nucleic acids (PNAs), powerful tools for molecular genetics and cytogenetics
CTLA4+49 A/G and CT60 polymorphisms in Dutch coeliac disease patients Dutch
Noninvasive diagnosis of the 3243A>G mitochondrial DNA mutation using urinary epithelial cells
Screening of the ARX gene in 682 retarded males
Fluorescence in situ hybridization characterization of apparently balanced translocation reveals cryptic complex chromosomal rearrangements with unexpected level of complexity
Survival motor neuron SMN1 and SMN2 gene promoters: identical sequences and differential expression in neurons and non-neuronal cells
Haplotype analysis of BRCA1 gene reveals a new gene rearrangement: characterization of a 19.9 KBP deletion
Difference in allelic expression of the CLCN1 gene and the possible influence on the myotonia congenita phenotype
A transmission disequilibrium test for general pedigrees that is robust to the presence of random genotyping errors and any number of untyped parents
Tools for molecular risk-stratification for clinical purposes: CLL as a prototype
Remarkable variability in renal disease in a large Slovenian family with Fabry disease
Refined genotype–phenotype correlations in cases of chromosome 6p deletion syndromes
Evidence for CTLA4 as a susceptibility gene for systemic lupus erythematosus
Localizing a putative mutation as the major contributor to the development of sporadic Hirschsprung disease to the RET genomic sequence between the promoter region and exon 2
BRCA1/2 predictive testing: a study of uptake in two centres
Systemic lupus erythematosus (SLE) and chromosome 16: confirmation of linkage to 16q12–13 and evidence for genetic heterogeneity
BRCA1 and sex ratio
Association between a polymorphism in the carboxyl ester lipase gene and serum cholesterol profile
Genetic isolates in Corsica (France): linkage disequilibrium extension analysis on the Xq13 region
Application of microarrays to the analysis of the inactivation status of human X-linked genes expressed in lymphocytes
Genetic and phenotypic characterization of mutations in myosin-binding protein C (MYBPC3) in 81 families with familial hypertrophic cardiomyopathy: total or partial haploinsufficiency
TEAM: a tool for the integration of expression, and linkage and association maps
Isolation and characterisation of GTF2IRD2, a novel fusion gene and member of the TFII-I family of transcription factors, deleted in Williams–Beuren syndrome
Are common disease susceptibility alleles the same in outbred and founder populations?
Efficient two-trait-locus linkage analysis through program optimization and parallelization: application to hypercholesterolemia
Hereditary hemochromatosis: Is the gene race over?
Professor Robin Michael Winter: 1950–2004. An appreciation
Erratum: Distribution and frequencies of PDS (SLC26A4) mutations in Pendred syndrome and nonsyndromic hearing loss associated with enlarged vestibular aqueduct: a unique spectrum of mutations in Japan
Association between schizophrenia and DRD3 or HTR2 receptor gene variants
Physical and transcript map of the autosomal dominant colobomatous microphthalmia locus on chromosome 15q12–q15 and refinement to a 4.4 Mb region
Autosomal dominant Brody disease cosegregates with a chromosomal (2;7)(p11.2;p12.1) translocation in an Italian family
β-Globin mutation detection by tagged single-base extension and hybridization to universal glass and flow-through microarrays
Three Rett patients with both MECP2 mutation and 15q11–13 rearrangements
Haplotype associations define target regions for susceptibility loci in systemic lupus erythematosus
Unbalanced segregation of a complex four-break 5q23–31 insertion in the 5p13 band in a malformed child
Refined genetic mapping of autosomal recessive chronic distal spinal muscular atrophy to chromosome 11q13.3 and evidence of linkage disequilibrium in European families European families
Features of chromosomal abnormalities in spontaneous abortion cell culture failures detected by interphase FISH analysis
Failure to detect DUP25 in lymphoblastoid cells derived from patients with panic disorder and control individuals representing European and American populations European and American populations
Candidate gene approach in association studies: would the factor V Leiden mutation have been found by this approach?
A novel point mutation in the mitochondrial tRNATrp gene produces a neurogastrointestinal syndrome
Linkage disequilibrium in young genetically isolated Dutch population
Decreased guanine nucleotide exchange factor activity in eIF2B-mutated patients
Depletion of PKD1 by an antisense oligodeoxynucleotide induces premature G1/S-phase transition
Maternal MTHFR interacts with the offspring's BCL3 genotypes, but not with TGFA, in increasing risk to nonsyndromic cleft lip with or without cleft palate
New breast cancer gene suggests a role for BRCA2 in sporadic cases
The genome after 50 years after Watson and Crick Genomes 2
Haplotype study in Dutch SCA3 and SCA6 families: evidence for common founder mutations
A comparison of different metaphase CGH methods for the detection of cryptic chromosome aberrations of defined size
Haplotype diversity and SNP frequency dependence in the description of genetic variation
Glycerol kinase deficiency: residual activity explained by reduced transcription and enzyme conformation
Founder mutations among the Dutch
Segmental maternal heterodisomy of the proximal part of chromosome 15 in an infant with Prader–Willi syndrome
A translocation breakpoint disrupts the ASPM gene in a patient with primary microcephaly
Genetic analysis of 2299delG and C759F mutations (USH2A) in patients with visual and/or auditory impairments
Complete germline deletion of the STK11 gene in a family with Peutz–Jeghers syndrome
Polymorphisms in the prion protein gene and in the doppel gene increase susceptibility for Creutzfeldt–Jakob disease
Angiotensin I-converting enzyme polymorphisms, ACE level and blood pressure among Nigerians, Jamaicans and African-Americans
Erratum: Genome-wide scanning for linkage in Finnish breast cancer families
Admixture, migrations, and dispersals in Central Asia: evidence from maternal DNA lineages
Autosomal dominant polycystic kidney disease (ADPKD, MIM 173900, PKD1 and PKD2 genes, protein products known as polycystin-1 and polycystin-2)
Proximal 11p deletion syndrome (P11pDS): additional evaluation of the clinical and molecular aspects
Detection of genotyping errors by Hardy–Weinberg equilibrium testing
FMF revisited
Advanced parental age in maternal uniparental disomy (UPD): implications for the mechanism of formation
Ciliary neurotrophic factor (CNTF) genotype and body composition
Transmission disequilibrium test (TDT) for case–control studies
Analysis of the CARD15 variants R702W, G908R and L1007fs in Italian IBD patients
The deleterious G15498A mutation in mitochondrial DNA-encoded cytochrome b may remain clinically silent in homoplasmic carriers
Who supports the support workers? Cross-sectional survey of support workers’ experience and views
Expansion to full mutation of a FMR1 intermediate allele over two generations
RHD maternal–fetal genotype incompatibility and schizophrenia: extending the MFG test to include multiple siblings and birth order
Surfactant protein C gene variation in the Finnish population – association with perinatal respiratory disease
Is haplotype tagging the panacea to association mapping studies?
Serotonin transporter 5HTTLPR polymorphism and affective disorders: no evidence of association in a large European multicenter study European multicenter study
Exclusion of an extracolonic disease modifier locus on chromosome 1p33–36 in a large Swiss familial adenomatous polyposis kindred
Vlax Roma history: what do coalescent-based methods tell us?
Familial thoracic aortic aneurysm/dissection with patent ductus arteriosus: genetic arguments for a particular pathophysiological entity
Molecular characterization of an 11q14.3 microdeletion associated with leukodystrophy
Analysis of heavy neurofilament subunit gene polymorphism in Russian patients with sporadic motor neuron disease (MND)
Association between COL1A1 gene polymorphisms and bone size in Caucasians
Advances in AAV-mediated gene transfer for the treatment of inherited disorders
MtDNA evidence for a genetic bottleneck in the early history of the Ashkenazi Jewish population
Absence of COCH mutations in patients with Meniere disease
Electronic EJHG: The Web and the Wider World
Erratum: Y chrosomal heritage of Croatian population and its island isolates Croatian population