European Journal of Human Genetics - 2002

146 articles | Last updated: 2025-12-03 14:12:56
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T A T A T A T A
The importance of plasma apolipoprotein E concentration in addition to its common polymorphism on inter-individual variation in lipid levels: results from Apo Europe
Identification of a locus on chromosome 2q11 at which recessive amelogenesis imperfecta and cone-rod dystrophy cosegregate
Molecular and biochemical characterisation of a novel sulphatase gene: Arylsulfatase G (ARSG)
Delineation of an estimated 6.7 MB candidate interval for an anophthalmia gene at 3q26.33-q28 and description of the syndrome associated with visible chromosome deletions of this region
New BAGE (B melanoma antigen) genes mapping to the juxtacentromeric regions of human chromosomes 13 and 21 have a cancer/testis expression profile
Two large French pedigrees with non syndromic sensorineural deafness and the mitochondrial DNA T7511C mutation: evidence for a modulatory factor French
The significance of paired MEFV mutations in individuals without symptoms of familial Mediterranean fever
Author index to volume 10
Family-based association tests for quantitative traits using pooled DNA
Haplotype and linkage disequilibrium analysis to characterise a region in the calcium channel gene CACNA1A associated with idiopathic generalised epilepsy
Novel fibroblast growth factor receptor 3 (FGFR3) mutations in bladder cancer previously identified in non-lethal skeletal disorders
BRCA2 founder mutation in Slovenian breast cancer families
Clinical variability in calpainopathy: What makes the difference?
Keyword index to volume 10
Is DFNA5 a susceptibility gene for age-related hearing impairment?
Homologous sequences at human chromosome 9 bands p12 and q13-21.1 are involved in different patterns of pericentric rearrangements
Meiotic outcomes in reciprocal translocation carriers ascertained in 3-day human embryos
Erratum: De novo mutations in familial adenomatous polyposis (FAP)
European-wide opposition against the breast cancer gene patents European-wide
Cardiovascular and diabetes mortality determined by nutrition during parents' and grandparents' slow growth period
Mutational spectrum of the CHAC gene in patients with chorea-acanthocytosis
Maternal uniparental isodisomy 20 in a foetus with trisomy 20 mosaicism: clinical, cytogenetic and molecular analysis
CFTR gene mutations in sarcoidosis
Cardiovascular Genetics for Clinicians
Spectrum and expression analysis of KRIT1 mutations in 121 consecutive and unrelated patients with Cerebral Cavernous Malformations
Prenatal testing for Huntington's disease: a European collaborative study
Systematic analysis of the regulatory and essential myosin light chain genes: genetic variants and mutations in hypertrophic cardiomyopathy
Null mutation in human ciliary neurotrophic factor gene confers higher body mass index in males
Detection of putative functional angiotensinogen (AGT) gene variants controlling plasma AGT levels by combined segregation-linkage analysis
Evaluation of BMP4 and its specific inhibitor NOG as candidates in human neural tube defects (NTDs)
Marfan syndrome in the third Millennium
Genomic rearrangements of EYA1 account for a large fraction of families with BOR syndrome
Overgrowth and trisomy 15q26.1-qter including the IGF1 receptor gene: report of two families and review of the literature
Androgen receptor CAG repeat length in Jewish Israeli women who are BRCA1/2 mutation carriers: association with breast/ovarian cancer phenotype
A novel gene, FAM11A, associated with the FRAXF CpG island is transcriptionally silent in FRAXF full mutation
An 11p;17p telomeric translocation in two families associated with recurrent miscarriages andMiller-Dieker syndrome
Diagnosis of Hb-pathies
Time to take epigenetic inheritance seriously
High resolution mapping of quantitative trait loci by linkage disequilibrium analysis
Demographics of the UK cystic fibrosis population: implications for neonatal screening
Parametric and non-parametric linkage analysis of several candidate regions for genes for human handedness
Increased frequency of the homozygous II ACE genotype in Italian Olympic endurance athletes
De novo mutations in familial adenomatous polyposis (FAP)
Testing for BRCA1 mutations: a cost-effectiveness analysis
The impact of genotyping error on haplotype reconstruction and frequency estimation
A frameshift insertion in the cone cyclic nucleotide gated cation channel causes complete achromatopsia in a consanguineous family from a rural isolate
Evidence of a founder effect for the tissue-nonspecific alkaline phosphatase (TNSALP) gene E174K mutation in hypophosphatasia patients
DHPLC analysis as a platform for molecular diagnosis of congenital disorders of glycosylation (CDG)
Clinical and biochemical characteristics and genotype–phenotype correlation in Finnishvariegate porphyria patients
Physical map of an asthma susceptibility locus in 7p15-p14 and an association study of TCRG
Comment on ‘increased frequency of combined methylenetetrahydrofolate reductase C677T and A1298C mutated alleles in spontaneously aborted embryos’
Reply to ‘MTHFR C677T and A1298C polymorphisms and mutated sequences occurring in cis’
Preimplantation genetic diagnosis for Huntington's disease with exclusion testing
New initiatives from EJHG, ESHG and Nature Publishing Group
X-linked Coffin-Lowry syndrome (CLS, MIM 303600, RPS6KA3 gene, protein product known under various names: pp90rsk2, RSK2, ISPK, MAPKAP1)
Characterisation of the human voltage-gated potassium channel gene, KCNA7, a candidate gene for inherited cardiac disorders, and its exclusion as cause of progressive familial heart block I (PFHBI)
Merosin-deficient congenital muscular dystrophy, autosomal recessive (MDC1A, MIM#156225, LAMA2 gene coding for α2 chain of laminin)
Emery-Dreifuss muscular dystrophy
Somatic mosaicism for a MECP2 mutation associated with classic Rett syndrome in a boy
Physical and transcriptional map of the critical region for keratolytic winter erythema (KWE) on chromosome 8p22-p23 between D8S550 and D8S1759
Lack of expression of XIST from a small ring X chromosome containing the XIST locus in a girl with short stature, facial dysmorphism and developmental delay
The transcriptional map of the common eliminated region 1 (C3CER1) in 3p21.3
Human chromosome 15q11-q14 regions of rearrangements contain clusters of LCR15 duplicons
Second family with hearing impairment linked to 19q13 and refined DFNA4 localisation
A centenarian-only approach for assessing gene–gene interaction in human longevity
An evaluation of the variance components approach: type I error, power and size of the estimated effect
4th International Meeting on Single Nucleotide Polymorphism and Complex Genome AnalysisVarious Uses for DNA Variations
The differential contribution of MEFV mutant alleles to the clinical profile of familial Mediterranean fever
Do reduced levels of steroid 21-hydroxylase confer a survival advantage in fetuses affected by sex chromosome aberrations?
A novel recessive hyperekplexia allele GLRA1 (S231R): genotyping by MALDI-TOF mass spectrometry and functional characterisation as a determinant of cellular glycine receptor trafficking
Inherited and de novo mutations in sporadic cases of DYT1-dystonia
MEHMO (Mental retardation, Epileptic seizures, Hypogenitalism, Microcephaly, Obesity): a new X-linked mitochondrial disorder
Succinate dehydrogenase and human diseases: new insights into a well-known enzyme
Multiplex PCR combining deltaF508 mutation and intragenic microsatellites of the CFTR gene for pre-implantation genetic diagnosis (PGD) of cystic fibrosis
Analysis of alterations of WFDC1, a new putative tumour suppressor gene, in hepatocellular carcinoma
Positive association to IgE levels and a physical map of the 13q14 atopy locus
Sharing of a conserved haplotype suggests a susceptibility gene for multiple sclerosis at chromosome 17p11
European combined analysis of the CTG18.1 and the ERDA1 CAG/CTG repeats in bipolar disorder European combined analysis
Prenatal detection of the 17p11.2 duplication in Charcot-Marie-Tooth disease type 1A: necessity of a multidisciplinary approach for heterogeneous disorders
Guidelines for the appropriate use of genetic tests in infertile couples
Genetic analysis of Paraoxonase (PON1) locus reveals an increased frequency of Arg192 allele in centenarians
A patient severely affected by spinal neurofibromas carries a recurrent splice site mutation in the NF1 gene
Comparison of family based haplotype methods using intragenic SNPs in candidate genes
Foetal haemoglobin in normal healthy adults: relationship with polymorphic sequences cis to the β globin gene
Combined segregation and linkage analysis of HLA markers in familial psoriasis
A complex DNA-repeat structure within the Selenoprotein P promoter contains a functionally relevant polymorphism and is genetically unstable under conditions of mismatch repair deficiency
The elastin gene is disrupted in a family with a balanced translocation t(7;16)(q11.23;q13) associated with a variable expression of the Williams-Beuren syndrome
Non-syndromic recessive deafness in Jordan: mapping of a new locus to chromosome 9q34.3 and prevalence of DFNB1 mutations
Chromosome analysis of epididymal and testicular spermatozoa in patients with azoospermia
Fine mapping the candidate region for peripheral neuropathy with or without agenesis of the corpus callosum in the French Canadian population French Canadian population
Linkage disequilibrium and demographic history of the isolated population of the Faroe Islands
Locus for susceptibility for familial capillary malformation (‘port-wine stain’) maps to 5q
Segregation analysis of HDL cholesterol in the NHLBI Family Heart Study and in Utah pedigrees
C677T mutation in the 5,10-MTHFR gene and risk of Down syndrome in Italy
Apolipoprotein E gene in frontotemporal dementia: an association study and meta-analysis
A cautionary note: false homozygosity for BRCA2 6174delT mutation resulting from a single nucleotide polymorphism masking the wt allele
The 3′-untranslated region of the dystrophin gene – conservation and consequences of loss
WFS1 mutations in Spanish patients with diabetes mellitus and deafness
Worldwide mutation spectrum in cartilage-hair hypoplasia: ancient founder origin of the major70A→G mutation of the untranslated RMRP
Pathogenic mutations and rare variants of the APC gene identified in 75 Belgian patients with familial adenomatous polyposis by fluorescent enzymatic mutation detection (EMD)
Connexin 26 mutations in cases of sensorineural deafness in eastern Austria
MECP2 gene mutation analysis in Chinese patients with Rett syndrome
Thirty distinct CACNA1F mutations in 33 families with incomplete type of XLCSNB and Cacna1f expression profiling in mouse retina
Identification of novel SDHD mutations in patients with phaeochromocytoma and/or paraganglioma
Single nucleotide polymorphisms in the transcobalamin gene: relationship with transcobalamin concentrations and risk for neural tube defects
USH3A transcripts encode clarin-1, a four-transmembrane-domain protein with a possible role in sensory synapses
Both common and unique susceptibility genes in different rat strains with pristane-induced arthritis
Rapid detection of common autosomal aneuploidies by quantitative fluorescent PCR on uncultured amniocytes
Different genetic components in the Norwegian population revealed by the analysis of mtDNA and Y chromosome polymorphisms
Unique (Y;13) translocation in a male with oligozoospermia: cytogenetic and molecular studies
Low frequency of MECP2 mutations in mentally retarded males
A novel polymorphism in exon 11 of the WKL1 gene, shows no association with schizophrenia
Mutations of Cx26 gene (GJB2) for prelingual deafness in Taiwan
The mutation spectrum of hyperphenylalaninaemia in the Republic of Ireland: the population history of the Irish revisited
A genome scan for loci influencing anti-atherogenic serum bilirubin levels
Genetic influences contributing to LDL particle size in familial combined hyperlipidaemia
Gaucher disease in Romanian patients: incidence of the most common mutations and phenotypic manifestations
Refinement of the NHS locus on chromosome Xp22.13 and analysis of five candidate genes
High-resolution genetic mapping of the ACE-linked QTL influencing circulating ACE activity
Finer linkage mapping of a primary hip osteoarthritis susceptibility locus on chromosome 6
Two exonic single nucleotide polymorphisms in the microsomal epoxide hydrolase gene are jointly associated with preeclampsia
Relation between tumour necrosis factor polymorphism TNFα-308 and risk of asthma
BRCA mutations in Italian breast/ovarian cancer families Italian
Polymorphisms in the C-terminal domain of MECP2 in mentally handicapped boys: implications for genetic counselling
A large deletion including most of GJB6 in recessive non syndromic deafness: a digenic effect?
A detailed transcriptional map of the chromosome 12p12 tumour suppressor locus
Increased frequency of combined methylenetetrahydrofolate reductase C677T and A1298C mutated alleles in spontaneously aborted embryos
DNA methylation, imprinting and cancer
Optimal selection strategies for QTL mapping using pooled DNA samples
Leigh disease associated with a novel mitochondrial DNA ND5 mutation
A human interstitial telomere associates in vivo with specific TRF2 and TIN2 proteins
Editorial
DFNB31, a recessive form of sensorineural hearing loss, maps to chromosome 9q32-34
Predictive DNA-testing for Huntington's disease and reproductive decision making: a European collaborative study
The ABCA4 2588G>C Stargardt mutation: single origin and increasing frequency from South-West to North-East Europe
Hirschsprung associated GDNF mutations do not prevent RET activation
Determination of the relative contribution of three genes–the cystic fibrosis transmembrane conductance regulator gene, the cationic trypsinogen gene, and the pancreatic secretory trypsin inhibitor ge
A detailed genetic map of the chromosome 7 bronchial hyper-responsiveness locus
Spinocerebellar ataxia type 1 (SCA1): Phenotype-genotype correlation studies in intermediate alleles
Chronic recurrent multifocal osteomyelitis (CRMO): evidence for a susceptibility gene located on chromosome 18q21.3-18q22
Postaxial polydactyly type A/B (PAP-A/B) is linked to chromosome 19p13.1-13.2 in a chinese kindred chinese
Sex stratification of an inflammatory bowel disease genome search shows male-specific linkage to the HLA region of chromosome 6
Three novel human VMD2-like genes are members of the evolutionary highly conserved RFP-TM family
Mutations in a protein target of the Pim-1 kinase associated with the RP9 form of autosomal dominant retinitis pigmentosa
Fine mapping of the locus for Shwachman-Diamond syndrome at 7q11, identification of shared disease haplotypes, and exclusion of TPST1 as a candidate gene
Alpha-thalassemia/mental retardation syndrome, X-Linked (ATR-X, MIM #301040, ATR-X/XNP/XH2 gene MIM #300032)