European Journal of Human Genetics - 2001

161 articles | Last updated: 2025-12-03 14:12:56
Caucasian
1
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European
5
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7
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Polymorphism of trinucleotide repeats in loci DM, DRPLA and SCA1 in East European populations East European populations
Familial defective apolipoprotein B-100 in a group of hypercholesterolaemic patients in Poland. Identification of a new mutation Thr3492Ile in the apolipoprotein B gene
High serum endostatin levels in Down syndrome: implications for improved treatment and prevention of solid tumours
Comparative study of the two more frequent HFE mutations (C282Y and H63D): significant different allelic frequencies between the North and South of Portugal
Effect of misspecification of gene frequency on the two-point LOD score
Familial Mediterranean Fever: association of elevated IgD plasma levels with specific MEFV mutations
ATB0/SLC1A5 gene. Fine localisation and exclusion of association with the intestinal phenotype of cystic fibrosis
Analysis of TSC2 stop codon variants found in tuberous sclerosis patients
A mutation (V260M) in the middle of the M2 pore-lining domain of the glycine receptor causes hereditary hyperekplexia
Indication of linkage and genetic heterogeneity of asthma according to age at onset on chromosome 7q in 107 French EGEA families
LDL receptor-GFP fusion proteins: new tools for the characterisation of disease-causing mutations in the LDL receptor gene
Evidence of a normal mean telomere fragment length in patients with Ullrich-Turner syndrome
Analysis of the genotypes and phenotypes of 37 unrelated patients with inherited factor VII deficiency
PCAP is the major known prostate cancer predisposing locus in families from south and west Europe
Letter
Human α-N-acetylgalactosaminidase (α-NAGA) deficiency: no association with neuroaxonal dystrophy?
A high-resolution integrated map spanning the SDHD gene at 11q23: a 1.1-Mb BAC contig, a partial transcript map and 15 new repeat polymorphisms in a tumour-suppressor region
The impact of genotyping error on family-based analysis of quantitative traits
Patterns of inter- and intra-group genetic diversity in the Vlax Roma as revealed by Y chromosome and mitochondrial DNA lineages
Maternally inherited deafness associated with a T1095C mutation in the mDNA
XLMR genes: update 2000
Maternal repression of the human GRB10 gene in the developing central nervous system; evaluation of the role for GRB10 in Silver-Russell syndrome
Premature termination mutations in exon 3 of the SMN1 gene are associated with exon skipping and a relatively mild SMA phenotype
Attempts to detect retrotransposition and de novo deletion of Alus and other dispersed repeats at specific loci in the human genome
Letter
Monosomy for the most telomeric, gene-rich region of the short arm of human chromosome 16 causes minimal phenotypic effects
Short tandem repeat (STR) haplotypes in HLA: an integrated 50-kb STR/linkage disequilibrium/gene map between the RING3 and HLA-B genes and identification of STR haplotype diversification in the class
A nonsense mutation is responsible for the RNA-negative phenotype in human citrullinaemia
NEDD4L on human chromosome 18q21 has multiple forms of transcripts and is a homologue of the mouse Nedd4-2 gene
Alu insertion polymorphisms and the genetic structure of human populations from the Caucasus
3rd International Meeting on Single Nucleotide Polymorphism and Complex Genome Analysis: SNPs: ‘Some Notable Progress’
Evaluation of first trimester maternal serum and ultrasound screening for Down's syndrome in Eastern and Northern Finland
Linear increase of diploidy in human sperm with age: A four-colour FISH study
N219Y, a new frequent mutation among mut° forms of methylmalonic acidemia in Caucasian patients
Novel PKD1 deletions and missense variants in a cohort of Hellenic polycystic kidney disease families Hellenic
Investigations of a CA repeat in the oestrogen receptor β gene in patients with Alzheimer's disease
Author index to volume 9
Keyword index to volume 9
High-resolution physical and transcript map of human chromosome 2p21 containing the sitosterolaemia locus
Saturating density of STSs (1/6 kb) in a 1.1 Mb region on 3q28-q29: a valuable resource for cloning of disease genes
A molecular genetic service for diagnosing individuals with familial hypercholesterolaemia (FH) in the United Kingdom
A personal view on reviewing the psychological consequences of predictive genetic testing for late onset disease
Meiotic segregation analysis in a t(4;8) carrier: comparison of FISH methods on sperm chromosome metaphases and interphase sperm nuclei
Men at risk of being a mutation carrier for hereditary breast/ovarian cancer: an exploration of attitudes and psychological functioning during genetic testing
Incorporation of covariates in multipoint model-free linkage analysis of binary traits: how important are unaffecteds?
A new locus for Seckel syndrome on chromosome 18p11.31-q11.2
Medical genomics
Annual Review of Genomics and Human Genetics
Teaching undergraduates about familial breast cancer: comparison of a computer assisted learning (CAL) package with a traditional tutorial approach
Spectrum of dominant mutations in the desmosomal cadherin desmoglein 1, causing the skin disease striate palmoplantar keratoderma
Brain studies of mouse models for neurogenetic disorders using in vivo magnetic resonance imaging (MRI)
Best practice guidelines for molecular analysis in spinal muscular atrophy
Partial tetrasomy 12pter-12p12.3 in a girl with Pallister-Killian syndrome: extraordinary finding of an analphoid, inverted duplicated marker
A 31 bp VNTR in the cystathionine β-synthase (CBS) gene is associated with reduced CBS activity and elevated post-load homocysteine levels
Clinical and radiographic features of multiple epiphyseal dysplasia not linked to the COMP or type IX collagen genes
Identification of a nonsense mutation in the PAX9 gene in molar oligodontia
Spectrum of CLCN1 mutations in patients with myotonia congenita in Northern Scandinavia
Evidence from skewed X inactivation for trisomy mosaicism in Silver-Russell syndrome
Distribution of the M129V polymorphism of the prion protein gene in a Turkish population suggests a high risk for Creutzfeldt-Jakob disease
A novel automated strategy for screening cryptic telomeric rearrangements in children with idiopathic mental retardation
The R482Q lamin A/C mutation that causes lipodystrophy does not prevent nuclear targeting of lamin A in adipocytes or its interaction with emerin
Multiple origins of the mtDNA 7472insC mutation associated with hearing loss and neurological dysfunction
Haemochromatosis gene mutations in a clustered Italian population: evidence of high prevalence in people of Celtic ancestry Celtic ancestry; Italian population
Use of haplotype information to test involvement of the LRP gene in Alzheimer's disease in the French population French population
Genetic linkage of autosomal dominant primary open angle glaucoma to chromosome 3q in a Greek pedigree
Physical and transcriptional map of the hereditary inclusion body myopathy locus on chromosome 9p12-p13
Spectrum of mutations and genotype–phenotype analysis in Currarino syndrome
Refinement of the PARK3 locus on chromosome 2p13 and the analysis of 14 candidate genes
Mapping of a new autosomal dominant nonsyndromic hearing loss locus (DFNA30) to chromosome 15q25-26
The evidence of mtDNA haplogroup F in a European population and its ethnohistoric implications European population
Mapping of the second locus for the Van der Woude syndrome to chromosome 1p34
Cryptic subtelomeric translocation t(2;16)(q37;q24) segregating in a family with unexplained stillbirths and a dysmorphic, slightly retarded child
The mitochondrial DNA mutation T12297C affects a highly conserved nucleotide of tRNALeu(CUN) and is associated with dilated cardiomyopathy
Association between quantitative traits underlying asthma and the HLA-DRB1 locus in a family-based population sample
BRCA1 and BRCA2 mutations among 233 unselected Finnish ovarian carcinoma patients
Linkage analysis in multiple sclerosis of chromosomal regions syntenic to experimental autoimmune disease loci
Cytogenetic analyses of culture failures by comparative genomic hybridisation (CGH)–Re-evaluation of chromosome aberration rates in early spontaneous abortions
TP63 gene mutation in ADULT syndrome
A genome screen for multiple sclerosis in Sardinian multiplex families Sardinian
Complete exon-intron structure of the RPGR-interacting protein (RPGRIP1) gene allows the identification of mutations underlying Leber congenital amaurosis
Multiple lipomas linked to an RB1 gene mutation in a large pedigree with low penetrance retinoblastoma
Organization of the mevalonate kinase (MVK) gene and identification of novel mutations causing mevalonic aciduria and hyperimmunoglobulinaemia D and periodic fever syndrome
A Rett syndrome patient with a ring X chromosome: further evidence for skewing of X inactivation and heterogeneity in the aetiology of the disease
A novel locus for autosomal dominant, non-syndromic hearing impairment (DFNA18) maps to chromosome 3q22 immediately adjacent to the DM2 locus
Parental mosaicism of JAG1 mutations in families with Alagille syndrome
Molecular analysis of MVK mutations and enzymatic activity in hyper-IgD and periodic fever syndrome
Is mitochondrial DNA depletion involved in Alzheimer's disease?
A placental diploid cell line is not essential for ongoing trisomy 13 or 18 pregnancies
Reply to letter from G Evers-Kiebooms
Multiple founder effects in spinal and bulbar muscular atrophy (SBMA, Kennedy disease) around the world
The spectrum of Familial Mediterranean Fever (FMF) mutations
No mutations in the coding region of the Rett syndrome gene MECP2 in 59 autistic patients
Screening for subtelomeric chromosome abnormalities in children with idiopathic mental retardation using multiprobe telomeric FISH and the new MAPH telomeric assay
A new locus for autosomal dominant Charcot-Marie-Tooth disease type 2 (CMT2F) maps to chromosome 7q11-q21
Erratum: Organization of the mevalonate kinase (MVK) gene and identification of novel mutations causing mevalonic aciduria and hyperimmunoglobulinaemia D and periodic fever syndrome
X-linked recessive inheritance of radial ray deficiencies in a family with four affected males
Acid-sensing ion channel (ASIC) 4 gene: physical mapping, genomic organisation, and evaluation as a candidate for paroxysmal dystonia
A genome-wide scan for preeclampsia in the Netherlands
Genome-wide linkage analysis of Scandinavian affected sib-pairs supports presence of susceptibility loci for celiac disease on chromosomes 5 and 11
Allergic rhinitis – a total genome-scan for susceptibility genes suggests a locus on chromosome 4q24-q27
Comprehensive methylation analysis in typical and atypical PWS and AS patients with normal biparental chromosomes 15
Haplotype analysis of the myotonic dystrophy type 1 (DM1) locus in Taiwan: implications for low prevalence and founder mutations of Taiwanese myotonic dystrophy type 1
Analysis of FMR1 (CGG)n alleles and DXS548-FRAXAC1 haplotypes in three European circumpolar populations: traces of genetic relationship with Asia European circumpolar populations
Genetic refinement and physical mapping of a chromosome 16q candidate region for inflammatory bowel disease
Genomic organisation of the ∼1.5 Mb Smith-Magenis syndrome critical interval: Transcription map, genomic contig, and candidate gene analysis
Molecular characterisation of glutamate dehydrogenase gene defects in Japanese patients with congenital hyperinsulinism/hyperammonaemia
Mitochondrial DNA analysis of the putative heart of Louis XVII, son of Louis XVI and Marie-Antoinette
Sensorineural hearing loss and the incidence of Cx26 mutations in Austria
Parental origin of de novo MECP2 mutations in Rett syndrome
Haplotypes vs single marker linkage disequilibrium tests: what do we gain?
Molecular characterisation of 34 patients with biotinidase deficiency ascertained by newborn screening and family investigation
An alpha1-antitrypsin enhancer polymorphism is a genetic modifier of pulmonary outcome in cystic fibrosis
Genetic analysis in Finnish families with inflammatory bowel disease supports linkage to chromosome 3p21
Fine mapping of a gene responsible for regulating dietary cholesterol absorption; founder effects underlie cases of phytosterolaemia in multiple communities
Molecular genetic basis and prevalence of glycogen storage disease type IIIA in the Faroe Islands
Mutational spectrum of the ED1 gene in X-linked hypohidrotic ectodermal dysplasia
Genetic polymorphism of MUC7: Allele frequencies and association with asthma
Novel RET mutations in Hirschsprung's disease patients from the diverse South African population diverse South African population
Lack of replication of association findings in complex disease: an analysis of 15 polymorphisms in prior candidate genes for sporadic Alzheimer's disease
Erratum: Parental mosaicism of JAG1 mutations in families with Alagille syndrome
Mutation frequency of Familial Mediterranean Fever and evidence for a high carrier rate in the Turkish population
DNA sequence variability of IGHG3 alleles associated to the main G3m haplotypes in human populations
Absence of the HIV-1 protective Δccr5 allele in most ethnic populations of India ethnic populations
The angiotensin converting enzyme I/D polymorphism in Russian athletes
An mtDNA mutation, 14453G→A, in the NADH dehydrogenase subunit 6 associated with severe MELAS syndrome
Haplotype analysis in Icelandic and Finnish BRCA2 999del5 breast cancer families
HFE gene mutations analysis in Basque hereditary haemochromatosis patients and controls Basque
Low incidence of UPD in spontaneous abortions beyond the 5th gestational week
The level of the mitochondrial mutation A3243G decreases upon ageing in epithelial cells from individuals with diabetes and deafness
Mutation detection for exons 2 to 10 of the Polycystic Kidney Disease 1 (PKD1)-gene by DGGE
MECP2 mutations in Danish patients with Rett syndrome: High frequency of mutations but no consistent correlations with clinical severity or with the X chromosome inactivation pattern
A single mutated MEFV allele in Israeli patients suffering from familial Mediterranean fever and Behçet's disease (FMF-BD)
Different types of repeat expansion in the TATA-binding protein gene are associated with a new form of inherited ataxia
The family based association test method: strategies for studying general genotype–phenotype associations
Analytic power calculation for QTL linkage analysis of small pedigrees
Genetic association studies of schizophrenia using the 8p21-22 genes: prepronociceptin (PNOC), neuronal nicotinic cholinergic receptor alpha polypeptide 2 (CHRNA2) and arylamine N-acetyltransferase 1
Analysis of the methylation status of the KCNQ1OT and H19 genes in leukocyte DNA for the diagnosis and prognosis of Beckwith–Wiedemann syndrome
Familial Mediterranean fever: prevalence, penetrance and genetic drift
MUC1 gene polymorphism in the gastric carcinogenesis pathway
Functional characterization of novel mutations in the human cytochrome b gene
Replication and extension studies of inflammatory bowel disease susceptibility regions confirm linkage to chromosome 6p (IBD3)
Mitochondrial DNA characterisation of European isolates: The Maragatos from Spain European isolates
Serum myeloperoxidase concentration in a healthy population: biological variations, familial resemblance and new genetic polymorphisms
Paradoxes in longevity: sequence analysis of mtDNA haplogroup J in centenarians
Mutation and linkage disequilibrium in human mtDNA
The western Swedish BRCA1 founder mutation 3171ins5; a 3.7 cM conserved haplotype of today is a reminiscence of a 1500-year-old mutation
Y-chromosome SNP haplotypes suggest evidence of gene flow among caste, tribe, and the migrant Siddi populations of Andhra Pradesh, South India
Frequency gradients of DHCR7 mutations in patients with Smith-Lemli-Opitz syndrome in Europe: evidence for different origins of common mutations
An apparently dominant bipolar affective disorder (BPAD) locus on chromosome 20p11.2–q11.2 in a large Turkish pedigree
Mutation analysis of the DCX gene and genotype/phenotype correlation in subcortical band heterotopia
Relative fitness of carriers of the mitochondrial DNA mutation 3243A > G
Tumor necrosis factor receptor-associated periodic syndrome (TRAPS) in a Dutch family: evidence for a TNFRSF1A mutation with reduced penetrance
Major decrease in the incidence of trisomy 21 at birth in south Belgium: mass impact of triple test?
Linkage disequilibrium narrows locus for venous malformation with glomus cells (VMGLOM) to a single 1.48 Mbp YAC
Y chromosome analysis reveals a sharp genetic boundary in the Carpathian region
Classic, atypically severe and neonatal Marfan syndrome: twelve mutations and genotype–phenotype correlations in FBN1 exons 24–40
R32W variant in Connexin 31: mutation or polymorphism for deafness and skin disease?
Maternally inherited hearing impairment in a family with the mitochondrial DNA A7445G mutation
Familial Mediterranean fever in Lebanon: mutation spectrum, evidence for cases in Maronites, Greek orthodoxes, Greek catholics, Syriacs and Chiites and for an association between amyloidosis and M694V
Haplogroup-specific deviation from the stepwise mutation model at the microsatellite loci DYS388 and DYS392
CFTR and asthma in the French EGEA study