Clinical Genetics - 2003

225 articles | Last updated: 2025-12-03 14:12:56
Caucasian
3
White
2
European
4
Other
30
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
“GENETICS AND HEALTH CARE”
The effects of dietary vitamin B12 deficiency on sperm maturation in developing and growing male rats
Molecular pathology of human cerebral malformations
Prenatal diagnosis and fetal therapy of congenital cystic adenomatoid malformation type I of the lung: a report of five cases
Reproductive risk factors in unilateral and bilateral renal agenesis
Drugs during Pregnancy and Lactation Handbook of Prescription Drugs and Comparative Risk Assessment
NOTICE TO AUTHORS
Effects of oyster extract on the reproductive function of zinc-deficient mice: Bioavailability of zinc contained in oyster extract
FGFR2 mutation in a patient with Apert syndrome associated with humeroradial synostosis
The interplay of genetic and environmental factors in craniofacial morphogenesis: holoprosencephaly and the role of cholesterol
Opposite effects of the maternal immune system activated by interleukin-lp vs. PSK and OK432 on 5-azacytidine-induced birth defects
Effects of supplemental L-methionine on E-64 [trans-epoxysuccinyl-1-leucyl-amido (4-guanido) butane]-induced dysmorphology in rat embryos cultured in vitro
Trend of congenital anomalies over 20 years ascertained by population-based monitoring in Ishikawa Prefecture, Japan
2004 JAPANESE TERATOLOGY SOCIETY MEMBERS
Amelioration of sodium valproate-induced neural tube defects in mouse fetuses by maternal folic acid supplementation during gestation
A quantitative study of the facial nerve in mice prenatally exposed to ethanol
Activities and Announcement
Curly vibrissae, a new mutation in the Wistar-derived rat
NOTICE TO AUTHORS
Subject index
Author index
The allelic loss of chromosome 3p25 with <i>c</i>‐<i>myc</i> gain is related to the development of clear‐cell renal cell carcinoma Japanese
BRCA1 interacts directly with the Fanconi anemia protein FANCA 
Folias A et al. (2002) 
Hum Mol Genet 11: 2591–2597
DNA crosslink‐dependent RAD50/MRE11/NBS1 subnuclear assembly requires the Fanconi anemia C protein 
Pichierri P et al. (2002) 
Hum Mol Genet 11: 2531–2546
Updated investigations of the role of methylenetetrahydrofolate reductase in human neural tube defects
Segregation of the V804L mutation and S836S polymorphism of exon 14 of the <i>RET</i> gene in an extended kindred with familial medullary thyroid cancer Hungarian
The contribution of USH1C mutations to syndromic and non‐syndromic deafness in the UK Greek Cypriot origin
Failure of prenatal diagnosis of diploid–triploid mosaicism after amniocentesis
Detection of five new mutations in the APC gene using denaturing high‐performance liquid chromatography
Author, Subject and Volume Indices
Defective regulation of extracellular ion homeostasis causes peripheral neuropathy associated with agenesis of the corpus callosum
Nature's accounting: the gains, losses and human cost of duplicon‐mediated genomic imbalance
Searching the vast array of genomic disorders
CARD15/NOD2 mutational analysis in Japanese patients with Crohn's disease
Limb girdle muscular dystrophy: use of dHPLC and direct sequencing to detect sarcoglycan gene mutations in a New Zealand cohort
Absence of overt iron overload in two individuals compound heterozygotes for a 22 base pair deletion of exon 2 and the C282Y missense mutation of the <i>HFE</i> gene
The I allele of the angiotensin‐converting enzyme gene is associated with an increased percentage of slow‐twitch type I fibers in human skeletal muscle
Landmarks in genetics through philately: the tools used by dysmorphologists
Mutation analysis of <i>Connexin 31</i> (<i>GJB3</i>) in sporadic non‐syndromic hearing impairment
Genetic counseling for prostate cancer risk African–American
Identification of a deletion in the mismatch repair gene, MSH2, using mouse–human cell hybrids monosomal for chromosome 2
Effects of a promoter variation in the hepatic glucokinase gene on promoter activity and glucose tolerance in Southern Chinese subjects Southern Chinese subjects
Ehlers–Danlos syndrome type IV: unusual congenital anomalies in a mother and son with a <i>COL3A1</i> mutation and a normal collagen III protein profile
A submicroscopic deletion of 11p13 associated with the WAGR syndrome
Genetic heterogeneity for a Nijmegen breakage‐like syndrome
Tangier disease with unusual clinical manifestations
A spectrum of neurological phenotypes caused by mutations in the X‐linked aristaless‐related homeobox gene, ARX
The developing heart and congenital heart defects: a make or break situation
Low prevalence of the deafness‐associated 35delG mutation in the connexin‐26 (GJB2) gene in a Sicilian population Sicilian population
Errata
Chromosome 22: a little chromosome that presents a larger understanding of genomic disorders
Index
Unmasking the hidden ID of congenital ID causation
Rapid detection methods for five HGO gene mutations causing alkaptonuria "most ethnic groups"; reference to Slovakia (country)
The natural history of sclerosteosis
De novo translocation (1; 2)(q32; p25) associated with bilateral renal dysplasia
Genetic counselling protocols for hereditary non‐polyposis colorectal cancer: a survey of UK regional genetics centres
Analysis of Sanfilippo A gene mutations in a large pedigree
Molecular characterization of a unique <i>de novo</i> 15q deletion associated with Prader–Willi syndrome and central visual impairment
The complicity of segmental duplicity in human genetic disease
Landmarks in genetics through philately: Down syndrome
Erratum
<i>USH1C</i>: a rare cause of USH1 in a non‐Acadian population and a founder effect of the Acadian allele Acadian; non-Acadian populations; mentions Pakistan, Canada, Germany
Advocating a gene‐based template of care for congenital intellectual disability
Genetic control of serum IgE levels: a study of low molecular weight protein tyrosine phosphatase Italian population; English and Italian populations
Identification of a novel <i>BMPR1A</i> germline mutation in a Korean juvenile polyposis patient without <i>SMAD4</i> mutation
Cystic fibrosis mutation frequencies in an Irish population Irish population
A novel mutation in exon 7 in a family with mild tricho–rhino–phalangeal syndrome type I
The R608del mutation in the acid sphingomyelinase gene (<i>SMPD1</i>) is the most prevalent among patients from Gran Canaria Island with Niemann‐Pick disease type B
The PPAR‐gamma P12A polymorphism modulates the relationship between dietary fat intake and components of the metabolic syndrome: results from the Québec Family Study
Biallelic inactivation of BRCA2 in Fanconi anemia 
Howlet NG et al. (2002) 
Science 297: 606–609
Two novel mutations in the α‐galactosidase A gene in Chinese patients with Fabry disease Chinese; Chinese population; Chinese families
Cerebro–oculo–facial–lymphatic syndrome
Glucocerebrosidase mutation T369M appears to be another polymorphism
Erratum
Genetic epidemiology of amyotrophic lateral sclerosis
Ileal adenocarcinoma in a mild phenotype of abetalipoproteinemia
Erratum
Sporadic and familial blepharophimosis –ptosis–epicanthus inversus syndrome: <i>FOXL2</i> mutation screen and MRI study of the superior levator eyelid muscle
Skeletal dysplasias caused by a disruption of skeletal patterning and endochondral ossification
<i>KCNQ1</i> mutations in patients with a family history of lethal cardiac arrhythmias and sudden death
Spectrum of clinical variability in familial deletion 22q11.2: from full manifestation to extremely mild clinical anomalies
Violence begets violence; or does it? A brain enzyme protects victims of childhood abuse from becoming antisocial and criminal
Aortic root diameter and nasal intermittent positive airway pressure treatment in Marfan's syndrome
Presumed mutation in a microsatellite marker mimicking segmental uniparental disomy in a case of a small supernumerary marker chromosome detected at prenatal diagnosis
Cryptic chromosomal rearrangement screening in 30 patients with mental retardation and dysmorphic features
Refining the primary open‐angle glaucoma <i>GLC1C</i> region on chromosome 3 by haplotype analysis Greek; American (Oregon)
The dichotomy of causation <i>vs</i> consequence in ID
Screening for Down's syndrome in early and late first and second trimester using six maternal serum markers
Paternal origin of <i>LMNA</i> mutations in Hutchinson–Gilford progeria
Vitamin D receptor gene variants of <i>Bsm</i>I, <i>Apa</i>I, <i>Taq</i>I, and <i>Fok</i>I polymorphisms in spinal tuberculosis
Cerebellar ataxia as atypical manifestation of the 3243A&gt;G MELAS mutation
An integrated approach to management of Marfan syndrome caused by an FBN1 exon 18 mutation in an Australian Aboriginal family
A novel R1347Q mutation in the predicted voltage sensor segment of the P/Q‐type calcium‐channel α<sub>1A</sub>‐subunit in a family with progressive cerebellar ataxia and hemiplegic migraine
Arg120stop nonsense mutation in the <i>RP2</i> gene: mutational hotspot and germ line mosaicism? family of German origin
Predictive testing for Huntington's disease: relationship with partners after testing
<i>SDHD</i> mutation analysis in seven German patients with sporadic carotid body paraganglioma: one novel mutation, no Dutch founder mutation and further evidence that G12S is a polymorphism German; Dutch
Cytogenetic and molecular analysis of a family with three brothers afflicted with germ‐cell cancer
Willingness to donate blood samples for genetic research: a survey from a community in Singapore
Another gene to screen in polyposis disorders?
Mutation spectrum and polymorphisms in <i>ATP7B</i> identified on direct sequencing of all exons in Chinese Han and Hui ethnic patients with Wilson's disease Han, Hui, ethnic Chinese, different ethnic backgrounds
Notch signaling in development and disease
Predictive testing for persons at risk for homozygosity for CAG expansion in the Huntington disease gene
Unmasking Kabuki syndrome: chromosome 8p22–8p23.1 duplication revealed by comparative genomic hybridization and BAC‐FISH different races
Involvement of gene–diet/drug interaction in DNA methylation and its contribution to complex diseases: from cancer to schizophrenia
A reversal of fate? Left‐right asymmetry, the inversin gene and childhood renal cystic disease
Mutational analysis of forkhead transcriptional factor 2 (<i>FOXL2</i>) in Korean patients with blepharophimosis–ptosis–epicanthus inversus syndrome
Autosomal dominant velopharyngeal insufficiency: father‐to‐son transmission confirmed
Ring Y chromosome in an azoospermic male with short stature: additional evidence for a distinct ring Y syndrome in non‐mosaic patients?
Elevated frequencies of the 35delG allele of the <i>connexin 26</i> gene in Corsica, France
Chromosome 2 deletion encompassing the <i>MAP2</i> gene in a patient with autism and Rett‐like features
Broadening the spectrum of genetic disease mechanisms: making (anti)sense out of α‐thalassemia
Frequency of three <i>BRCA1</i> gene founder mutations in breast/ovarian cancer families from the Pomerania–Kujawy region of Poland
Intronic L1 insertion and F268S, novel mutations in RPS6KA3 (RSK2) causing Coffin–Lowry syndrome
Genetic epidemiology of alpha‐1 antitrypsin deficiency in North America and Australia/New Zealand: Australia, Canada, New Zealand and the United States of America
Association of <i>EDNRA</i>, but not <i>WNK4</i> or <i>FKBP1B</i>, polymorphisms with essential hypertension Anglo‐Celtic white Australians
A−61C and C−101G Hp gene promoter polymorphisms are, respectively, associated with ahaptoglobinaemia and hypohaptoglobinaemia in Ghana Ghanaians; Asian populations
Peroxisome proliferator‐activated receptor γ C161T polymorphisms and survival of Japanese patients with immunoglobulin A nephropathy
Omphalocele in trisomy 3q: further delineation of phenotype
Genetic susceptibility to neural tube defect pregnancy varies with offspring phenotype
FH‐Pyrgos: a novel mutation in the promoter (−45delT) of the low‐density lipoprotein receptor gene associated with familial hypercholesterolemia
Mechanism‐specific treatment of a polyglutamine disorder
Co‐occurrence of three different mutations in the bilirubin UDP‐glucuronosyltransferase gene in a Chinese family with Crigler–Najjar syndrome type I and Gilbert's syndrome
Postural anomaly of the head‐neck‐shoulder alignment in patients with deletion 22q11.2 (DiGeorge/velocardiofacial syndrome)
Genetic variation in the promoter and 5′ UTR of the copper transporter, <i>ATP7B</i>, in patients with Wilson disease patients of European ancestry; Sardinian WND patients
Mutations in components of the dynein motor protein complex cause motor neuron disease
Hemochromatosis gene mutations in the Croatian and Slovenian populations
Do these genes make me look fat? Obesity and melanocortin‐4 receptor gene deficiencies
Huntington's disease: do future physicians and lawyers think eugenically?
Population data suggest that deletions of 1p36 are a relatively common chromosome abnormality
Use of cancer susceptibility testing among primary care physicians
Niemann–Pick disease type C
The effects of the Pro12Ala polymorphism of the <i>PPARγ‐2</i> gene on lipid metabolism interact with body size at birth
Mutation spectrum in a large cohort of unrelated consecutive patients with hypertrophic cardiomyopathy
Molecular mechanisms in lymphangiogenesis: model systems and implications in human disease
Split hand foot malformation is associated with a reduced level of Dactylin gene expression
Psychological consequences and predictors of adverse events in the first 5 years after predictive testing for Huntington's disease
Genetic landmarks through philately: Georges Marinesco (1863–1938)
A link between the repair gene <i>EXOZ</i> and tumorigenesis
Redefining xeroderma pigmentosum complementation group E
A new locus for inheritance of malignant melanoma
To tell or not to tell: barriers and facilitators in family communication about genetic risk
Screening the <i>SLC26A4</i> gene in probands with deafness and goiter (Pendred syndrome) ascertained from a large group of students of the schools for the deaf in Turkey
Ring chromosome 17: phenotype variation by deletion size
Two new point mutations of the SRY gene identified in two Italian 46,XY females with gonadal dysgenesis
Genetic analysis of males from intracytoplasmic sperm injection couples
Pure partial trisomy of 2q22‐q23 secondary to a paternally inherited direct insertion: a rare duplication
Identification of three novel <i>SEDL</i> mutations, including mutation in the rare, non‐canonical splice site of exon 4 Italian family; Slovak patient; Belgian patient
Personal theories of inheritance, coping strategies, risk perception and engagement in hereditary non‐polyposis colon cancer families offered genetic testing
No justification of routine screening for 22q11 deletions in patients with overt cleft palate
The first nonsense mutation in alsin results in a homogeneous phenotype of infantile‐onset ascending spastic paralysis with bulbar involvement in two siblings
Germline hMLH1 promoter mutation in a Newfoundland HNPCC kindred
<i>PMX2B</i>, a new candidate gene for Hirschsprung's disease
Rare compound heterozygosity for IVS2 +1G&gt;A and R170P in an Italian patient with Gaucher disease type 1 Italian patient
<i>ROR2</i> is mutated in hereditary brachydactyly with nail dysplasia, but not in Sorsby syndrome
Association of autism severity with a monoamine oxidase A functional polymorphism
No evidence of submicroscopic deletion or segmental uniparental disomy within the candidate regions 7p11.2‐p13 and 7q31‐qter in a series of non‐uniparental disomy Silver–Russell syndrome cases
Cholesterol ester transfer protein, apolipoprotein E and lipoprotein lipase genotypes in patients with coronary artery disease in the Turkish population
Low mutation rate of <i>hMSH2</i> and <i>hMLH1</i> in Taiwanese hereditary non‐polyposis colorectal cancer Taiwanese; western countries
Mutations located in exon 24 of the <i>CFTR</i> gene are associated with a mild cystic fibrosis phenotype
Analysis of <i>RPGR</i> in a South African family with X‐linked retinitis pigmentosa: research and diagnostic implications mixed ancestry
Clinical, pathological and genetic features of women at high familial risk of breast cancer undergoing prophylactic mastectomy
UDP‐glucuronosyltransferase 1 gene promoter polymorphism is associated with increased serum bilirubin levels and cholecystectomy in patients with sickle cell anemia
X‐linked myotubular myopathy in a family with three adult survivors
The road to IRAK: mutations in the toll‐like receptor signaling pathway cause susceptibility to pyogenic bacterial infections
Something lost in the translation: ‘premutations’ in the <i>FMR1</i> gene cause Fragile X tremor/ataxia syndrome (FXTAS)
Unique origin and low penetrance of the 946delGAG mutation in Valencian DYT1 families Valencian, Spain, Castilla‐La Mancha, populations with different ethnic and geographic origins, ling
Two new PROP1 gene mutations responsible for compound pituitary hormone deficiency
Who gets the information about genetic testing for cancer risk? The role of race/ethnicity, immigration status, and primary care clinicians race/ethnicity; immigrant and ethnic populations
Conspicuous GTG‐banding results of the centromere‐near region can be caused by alphoid DNA heteromorphism
Nine novel mutations in the protoporphyrinogen oxidase gene in Swedish families with variegate porphyria
A novel molecular defect of the carnitine acylcarnitine translocase gene in a Saudi patient
Mucopolysaccharidosis VII: clinical, biochemical and molecular investigation of a Brazilian family
Syndromes of disordered chromatin remodeling
The genetics of pre‐eclampsia: a feto‐placental or maternal problem?
Hepcidin's handiwork in hereditary hemochromatosis
Evidence that the Cys282Tyr mutation of the <i>HFE</i> gene originated from a population in Southern Scandinavia and spread with the Vikings Northern European origin; Germanic Iron Age population; Celtic group of peoples; Vikings; populations in Northern/Central/Sout
A cluster of autosomal recessive spondylocostal dysostosis caused by three newly identified <i>DLL3</i> mutations segregating in a small village
Tremor, ataxia and dementia in older men may indicate a carrier of the fragile X syndrome
A quantitative polymerase chain reaction method for determining copy number within the Prader–Willi/Angelman syndrome critical region
A novel mutation in the<i>TWIST</i>gene, implicated in Saethre–Chotzen syndrome, is found in the original case of Robinow–Sorauf syndrome
Association of the myocilin mt.1 promoter variant with the worsening of glaucomatous disease over time
Gaucher's disease: identification of novel mutant alleles and genotype–phenotype relationships
Frequencies of gap‐ and tight‐junction mutations in Turkish families with autosomal‐recessive non‐syndromic hearing loss
Semen cryoconservation in men with AZFc microdeletion
XL PCR for the detection of large trinucleotide expansions in juvenile Huntington's disease
Discoveries in sphingolipid metabolism, spinocerebellar ataxia and autoimmune disease
A new mechanism for spinocerebellar ataxia involving mutations in protein kinase Cγ
Neurological presentation of Ehlers–Danlos syndrome type IV in a family with parental mosaicism
A novel dominant missense mutation – D179N – in the <i>GJB2</i> gene (Connexin 26) associated with non‐syndromic hearing loss
Mapping a gene for 46,XY gonadal dysgenesis by linkage analysis
Overestimation of genetic risks owing to small sample sizes in cardiovascular studies
Germline mutations of the <i>MEN1</i> gene in Korean families with multiple endocrine neoplasia type 1 (MEN1) or MEN1‐related disorders Korean
Predictive, pre‐natal and diagnostic genetic testing for Huntington's disease: the experience in Canada from 1987 to 2000
Ankyrin‐B mutations in familial cardiac arrhythmia
Gene discovery in the allelic disorders Smith–McCort Dysplasia and Dyggve–Melchior–Clausen syndrome
Can we throw the master‐switch in autoimmune disease?
A novel syndrome of combined immunodeficiency, autoimmunity and spondylometaphyseal dysplasia
Analysis of splice‐site mutations of the α‐galactosidase A gene in Fabry disease
Genetic epidemiology of alpha‐1 antitrypsin deficiency in southern Europe: France, Italy, Portugal and Spain racial subgroups; southern Europe; France, Italy, Portugal, Spain; Europe
Endoglin gene mutations and polymorphisms in Italian patients with hereditary haemorrhagic telangiectasia Italian
Intact fetal cell isolation from maternal blood: improved isolation using a simple whole blood progenitor cell enrichment approach (RosetteSep<sup>™</sup>)
Ion‐ing out the genetic basis of peripheral neuropathy associated with agenesis of the corpus callosum: mutations in a cation transporter cause ACCPN
Development of the thyroid gland: lessons from congenitally hypothyroid mice and men
The molecular genetics of Usher syndrome
Familial predisposition to tufted angioma: identification of blood and lymphatic vascular components
It's only teeth – are there limits to genetic testing?
Interaction between SREBP‐1a and APOB polymorphisms influences total and low‐density lipoprotein cholesterol levels in patients with coronary artery disease Brazilian population of European descent
Pulmonary involvement in Type 1 Gaucher disease: functional and exercise findings in patients with and without clinical interstitial lung disease
<i>APOA5</i>‐1131T&gt;C polymorphism is associated with triglyceride levels in Chinese men
Five new subjects with ring chromosome 22
Congenital universal hypertrichosis with deafness and dental anomalies inherited as an X‐linked trait
Triple A syndrome: genotype–phenotype assessment
Discordant clinical manifestations in monozygotic twins with the identical mutation in the TSC2 gene
Evaluation of a Tay‐Sachs Disease screening program Ashkenazi Jewish population; Melbourne Jewish community (Australia)
Exclusion of <i>PTPN11</i> mutations in Costello syndrome: further evidence for distinct genetic etiologies for Noonan, cardio–facio–cutaneous and Costello syndromes
New mutations, new etiologies for Parkinson disease
Vascular malformations: localized defects in vascular morphogenesis
Ironing out hemochromatosis heterogeneity
Mutations for a cytochrome c oxidase deficiency found by a novel strategy – up front computation makes the genomic haystack more manageable
Cystic fibrosis in Greece: molecular diagnosis, haplotypes, prenatal diagnosis and carrier identification amongst high‐risk individuals Greek; our population; general population subjects
Analysis of marker or complex chromosomal rearrangements present in pre‐ and post‐natal karyotypes utilizing a combination of G‐banding, spectral karyotyping and fluorescence in situ hybridization
Hotspots
Hotspots
"GENETICS AND HEALTH CARE". CALL FOR ABSTRACTS