Clinical Genetics - 1999

205 articles | Last updated: 2025-12-03 14:12:56
Caucasian
6
White
1
European
4
Other
22
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Fetal gene therapy – a focus on prevention versus convention.
Molecular recipe for a human tumour
HotSpots: Neurogenesis challenges age old dogma
Epigenetic evidence: hypomethylation results in hypermutation
Novel exon skipping mutation in the fibrillin‐1 gene: Two ‘hot spots’ for the neonatal Marfan syndrome
Interpupillary distance in a normal black population
Autosomal dominant cataracts and Peters anomaly in a large Australian family
Scalp‐ear‐nipple (Finlay–Marks) syndrome: a familial case with renal involvement
Pharmacogenetics and pharmacogenomics: why is this relevant to the clinical geneticist?
Normolipidemia and hypercholesterolemia in persons heterozygous for the same 1592+5G→A splice site mutation in the low‐density lipoprotein receptor gene Danish
X‐inactivation and marker studies in three families with incontinentia pigmenti: implications for counselling and gene localisation
Intra‐amniotic viral gene transfer highlights the potential for <i>in utero</i> molecular therapies
Centromere–telomere (12;8p) fusion, telomeric 12q translocation, and i(12p) trisomy 1
Preaxial polydactyly in an infant with Down’s syndrome
Ionizing radiation‐induced signaling pathways in ataxia telangiectasia
An unbalanced half‐cryptic translocation involving the 6q subtelomeric region and 2p25.3 in a child with mental retardation: uses and limitations of fluorescence <i>in</i><i>situ</i> hybridization
Allele distribution at the <i>FMR1</i> locus in the general Chinese population
Psychological and social determinants of women's decisions to undergo genetic counseling and testing for breast cancer
Association between <i>AGT</i> codon 235 polymorphism and variation in serum concentrations of creatinine and urea in Canadian Oji‐Cree Canadian Oji‐Cree; aboriginal Canadians
Assessment of <i>RS1</i> in X‐linked juvenile retinoschisis and sporadic senile retinoschisis
Determination of the prevalence of cystic fibrosis in the United Arab Emirates by genetic carrier screening
Cohen syndrome: evaluation of its cardiac, endocrine and radiological features Finnish descent
Distal arthrogryposis type IIB: probable autosomal recessive inheritance
Physical activity modulates the effect of a lipoprotein lipase mutation (D9N) on plasma lipids and lipoproteins Dutch men and women
Noncoding germline mutations in <i>p16/CDKN2A</i> in melanoma‐prone families
PIK3CA: determining its role in cellular proliferation and ovarian cancer
Genetics of sexual orientation
Polyvariant mutant CFTR genes in patients with chronic pancreatitis Italian population
Molecular genetics of Turner syndrome: correlation with clinical phenotype and response to growth hormone therapy Greek children
Postaxial polydactyly and Dandy–Walker malformation. Further nosological comments
Search for uniparental disomy 14 in balanced Robertsonian translocation carriers
A <i>de novo</i> heterozygous deletion of 42 base‐pairs in the noggin gene of a <i>fibrodysplasia ossificans</i><i>progressiva</i> patient
Multi‐organellar disorders of pigmentation: tied up in traffic
Transcription factors in dysmorphology
Effect of vitamin E on chromosomal aberrations in lymphocytes from patients with Down’s syndrome
Rapid detection of polymorphisms in exons 10, 11 and 12 of the low density lipoprotein receptor gene (<i>LDLR</i>) and their use in a clinical genetic diagnostic setting
<i>Fok</i>I polymorphism at the human vitamin D receptor gene locus in Europeans and Africans Europeans and Africans; Europeans and Africans
Triple aneuploidy in spontaneous abortions
Molecular and clinical characterization of a patient with duplication of 1p36.3 and metopic synostosis
A Japanese patient homozygous for the H1085R mutation in the CFTR gene presents with a severe form of cystic fibrosis
Correspondence
Internet resources for the clinical geneticist
FISH analysis of terminal deletions in patients diagnosed with cri‐du‐chat syndrome
Interleukin‐4 receptor variant Q576R: ethnic differences and association with atopy
The assent of a nation: genethics and Iceland
Renal‐coloboma syndrome: a multi‐system developmental disorder caused by <i>PAX2</i> mutations
Molecular mechanisms controlling lung morphogenesis
Utility of the predictors of coronary heart disease mortality in a longitudinal study of elderly Finnish men aged 65 to 84 years is dependent on context defined by <i>Apo E</i> genotype and area of re Finnish men; cohorts in Eastern and Southwestern Finland (regional population descriptors)
The long and the short of it: developmental genetics of the skeletal dysplasias
Alternative splicing of exon 37 of <i>FBN1</i> deletes part of an ‘eight‐cysteine’ domain resulting in the Marfan syndrome
Ataxia‐telangiectasia, cancer and the pathobiology of the <i>ATM</i> gene
Partial trisomy 17p detected by spectral karyotyping
Homozygosity for two mild glucocerebrosidase mutations of probable Iberian origin Iberian origin
Short rib‐polydactyly syndrome: more evidence of a continuous spectrum
Serum total IgE levels and <i>CD14</i> on chromosome 5q31
Multipaint FISH: a rapid and reliable way to define cryptic and complex abnormalities
Genetic and environmental sources of QT interval variability in Israeli families: the kibbutz settlements family study
The tools of gene therapy can create new insights in developmental biology
Accurate determination of the number of CAG repeats in the Huntington disease gene using a sequence‐specific internal DNA standard
Recombinant proteins for genetic disease
Schizophrenia susceptibility gene locus at Xp22.3
Vaginal uterine agenesis associated with amastia in a phenotypic female with a <i>de novo</i> 46,XX,t(8;13)(q22.1;q32.1) translocation
<i>STK11</i>/<i>LKB1</i> germline mutations are not identified in most Peutz–Jeghers syndrome patients
Three novel mutations in the COL4A5 gene in Mexican Alport syndrome patients
Adult‐onset familial hypertrophic cardiomyopathy caused by a novel mutation, R694C, in the <i>MYH7</i> gene
The ups and downs of parting COMPany Poly‐aspartic acid tract instability: a novel expansion–contraction mutation
Role of the Pro23Leu mutation in a family affected by retinitis pigmentosa in the Basque Country
Analysis of infertile brothers with congenital bilateral absence of vas deferens for mutations in the CFTR gene
Confirmation of linkage in X‐linked infantile spasms (West syndrome) and refinement of the disease locus to Xp21.3‐Xp22.1
Founder <i>BRCA1</i> and <i>BRCA2</i> mutations in French Canadian ovarian cancer cases unselected for family history French ancestry; French Canadian; French
Dysmorphic phenotype and neurological impairment in 22 retinoblastoma patients with constitutional cytogenetic 13q deletion
Germline mosaicism in X‐linked myotubular myopathy
Aicardi–Goutières syndrome: monogenic recessive disease, genetically heterogeneous disease, or multifactorial disease?
Fetal anticonvulsant syndrome and mutation in the maternal MTHFR gene
Genetic and segregation analysis of congenital cataract in the Indian population
Cerebrotendinous xanthomatosis without xanthomas
An extra idic(21)(q22.1) in a child with some features of Down’s syndrome
Procedure to protect confidentiality of familial data in community genetics and genomic research
Partial DiGeorge syndrome in two patients with a 10p rearrangement
Mucopolysaccharidosis type I: Characterization of novel mutations affecting α‐ <scp>l</scp>‐iduronidase activity
Genetic counselling in multiple sclerosis: risks to sibs and children of affected individuals
Kabuki syndrome: description of dental findings in 8 patients mixed Aboriginal and Caucasian descent
Transcervical cells and the prenatal diagnosis of haemoglobin (Hb) mutations
Cloned mice raise possibility of human cloning
A second gene for myotonic dystrophy
Lower extremity counterpart of the Poland syndrome
<i>TGFA</i>: exon–intron structure and evaluation as a candidate gene for Alström syndrome
Mutation in the factor V gene associated with inferior vena cava thrombosis in newborns
Genetic investigation of patients with hypercholesterolemia type IIa
Fetal gene therapy confers stable gene expression, germline and widespread somatic cell transfection
Genetic landmarks through philately – porphyria and its effect on world history
Mutations associated with very late‐onset metachromatic leukodystrophy
Correspondence
Mutations in the <i>endothelin‐receptor B</i> gene in Hirschsprung disease in Sweden
Identification of a common N540K mutation in 8/18 Taiwanese hypochondroplasia patients: further evidence for genetic heterogeneity
HotSpots
Multi‐organellar disorders of pigmentation: tied up in traffic
FISH and PCR analysis of the presence of Y‐chromosome sequences in a patient with Xq‐isochromosome and testicular tissue
Infantile sialic acid storage disease: report of the first case in South America
HotSpots: The <i>Fat</i> gene
HotSpots: Catch 22
40 years of the annual ‘Bar Harbor Course’ (1960–1999): a pictorial history
Genetic landmarks through philately – hereditary breast cancer 1
Further evidence from two families that craniofrontonasal dysplasia maps to Xp22
HotSpots
High frequency of tissue‐specific mosaicism in Turner syndrome patients
A locus for autosomal recessive achromatopsia on human chromosome 8q Irish ancestry
HotSpots ‐ Insufficient death: autoimmune lymphoproliferative syndrome
HotSpots ‐ Cutting it close: new insights into presenilin‐1 function
Timing is everything: especially with loss of tumor suppressor genes
Detection of a novel germline mutation in the von Hippel–Lindau tumour‐suppressor gene by fluorescence‐labelled base excision sequence scanning (F‐BESS)
Long‐term survival and normal cognitive development in infantile phosphofructokinase‐1 deficiency
Interstitial 4p deletion in a child with an Angelman syndrome‐like phenotype
A SHOXing new kind of inheritance
Perinatal hypophosphatasia: diagnosis and detection of heterozygote carriers within the family
Mexican geneticists’ views of ethical issues in genetics testing and screening. Are eugenic principles involved? Mexican; Chinese
A half cryptic derivative der(18)t(5;18)pat identified by M‐FISH and subtelomere probes: clinical findings and review of subtelomeric rearrangements
Hopes pinned on microarray technology to defeat TB
Antibody therapy for Alzheimer's disease
Mosaicism for a small marker chromosome resulting from a familial Robertsonian translocation (21;22)
Unmasking mutations: functional genetic testing
Relation of mathematical ability to psychosis in Iceland
Proximal myotonic myopathy: clinical and molecular investigation of a Norwegian family with PROMM
Prenatal diagnosis of peroxisome biogenesis disorders by means of immunofluorescence staining of cultured chorionic villous cells
To be or not to be an aggregate
Thalassemia carrier screening and prenatal diagnosis among the British Columbia (Canada) population of Chinese descent Chinese; Asian population
Nevoid basal cell carcinoma syndrome. Clinical findings in 37 Italian affected individuals Italian; African–Americans; Italian population
Missense mutations in phosphomannomutase 2 gene in two Japanese families with carbohydrate‐deficient glycoprotein syndrome type 1 Japanese
Impact of ApoE4 allele on total cholesterol levels of children in northern Spain
SMN: understanding a complex protein complex and its role in disease
Muddy waters: looking beyond the disease‐causing mutation, DNA mutations at second sites influence phenotype
High frequency of <i>de novo</i> deletions in Mexican Duchenne and Becker muscular dystrophy patients. Implications for genetic counseling
Chromosome 11q13 and atopic asthma
Clinical, biochemical, and molecular characterization of patients with glutathione synthetase deficiency
A <i>de novo</i> complex chromosomal rearrangement with nine breakpoints characterised by FISH in a boy with mild mental retardation, developmental delay, short stature and microcephaly
Association between CAG repeat number in the androgen receptor and male infertility in a Belgian study
Three common CFTR mutations should be included in a neonatal screening programme for cystic fibrosis in Sweden
Human renin gene <i>Bgl</i>I dimorphism associated with hypertension in two independent populations a genetically homogeneous ethnic population
Perceptions of the outcome of orthopedic surgery in patients with chondrodysplasias
Prevalence of human leukocyte antigen DQA1 and DQB1 alleles in Kuwaiti Arab children with type 1 diabetes mellitus Kuwaiti Arab; 'similar ethnic background'; 'Kuwaiti general population'
Neural stem cells – a versatile tool for cell replacement and gene therapy in the central nervous system
Beginning of a molecular era in hearing and deafness
A brief review of cryptic duplications of 21q as an emerging cause of Down syndrome: practical considerations for accurate detection
A microdeletion syndrome due to a 3‐Mb deletion on 19q13.2 – Diamond–Blackfan anemia associated with macrocephaly, hypotonia, and psychomotor retardation
Screening for FMR1 mutations among the mentally retarded: prevalence of the fragile X syndrome in Spain
HotSpots ‐ An unusual ataxia
Correspondence
Molecular mechanisms controlling lung morphogenesis
Pattern of central nervous system anomalies in a population with a high rate of consanguineous marriages
Family physicians’ perspectives on genetics and the human genome project
FISH analysis with locus‐specific probes in sperm from two translocation carrier men
Kenny–Caffey syndrome: an Arab variant?
Beginning of a molecular era in hearing and deafness
Additive effect of three noradrenergic genes (<i>ADRA2A</i>, <i>ADRA2C</i>, <i>DBH</i>) on attention‐deficit hyperactivity disorder and learning disabilities in Tourette syndrome subjects
Biology of presenilins as causative molecules for Alzheimer disease
A common truncation variant of lipoprotein lipase (Ser447X) confers protection against coronary heart disease: the Framingham Offspring Study
Epidemiology of dystrophinopathies in North‐West Tuscany: a molecular genetics‐based revisitation
Homozygosity for a novel DTDST mutation in a child with a ‘broad bone‐platyspondylic’ variant of diastrophic dysplasia
Infantile spasms in a patient with partial duplication of chromosome 2p
High frequency of type 1 GM1 gangliosidosis in southern Brazil
Association of pre‐eclampsia with common coding sequence variations in the lipoprotein lipase gene
Two common mutations (D9N, N291S) in lipoprotein lipase: a cumulative analysis of their influence on plasma lipids and lipoproteins in men and women
‘New’ manifestations of BOR syndrome
The malformed kidney: disruption of glomerular and tubular development
Association between polymorphism of the cholecystokinin gene and idiopathic Parkinson's disease
Evaluation of the facioscapulohumeral muscular dystrophy (FSHD1) phenotype in correlation to the concurrence of 4q35 and 10q26 fragments
Deletion of chromosome 4p detected by FISH in a girl with normal high resolution karyotype
Obituary
HotSpots
Genetic landmarks through philately – a brief history of diabetes mellitus
A proven case of materno‐foetal transfusion determined by cytogenetic and DNA analysis
Ethics and genetics: Advanced European bioethics course
Possible interaction of genotypes at cystathionine β‐synthase and methylenetetrahydrofolate reductase (MTHFR) in neural tube defects
Definition of the smallest pathological CAG expansion in <i>SCA7</i>
Growing up without sulfate
Neural stem cells – a versatile tool for cell replacement and gene therapy in the central nervous system
Genetic landmarks through philately – hemophilia
Diversity in expression of glucose‐6‐phosphate dehydrogenase deficiency in females Mediterranean; African
Tricho‐dento‐osseous syndrome and amelogenesis imperfecta with taurodontism are genetically distinct conditions
Glaucoma genetics, present and future
Clinical characteristics of Angelman syndrome patients with a non‐IC‐deleted imprinting mutation
Tetrasomy 21pter‐q22.11: molecular, cytogenetic, and clinical findings
Characterisation, phenotypic manifestations and X‐inactivation pattern in 14 patients with X‐autosome translocations
The vitamin D receptor <i>Fok</i>I start codon polymorphism and bone mineral density in osteoporotic postmenopausal French women French women
Clinical teratology: identifying teratogenic risks in humans
Tissue‐specific methylation differences in a fragile X premutation carrier
Cloning of translocation breakpoints associated with Shwachman syndrome and identification of a candidate gene
Genetic landmarks through philately – Kabuki theater and Kabuki syndrome
Inheritance of two different alleles of the low‐density lipoprotein (LDL)‐receptor gene carrying the recurrent Pro664Leu mutation in a patient with homozygous familial hypercholesterolaemia Uses 'Asian', 'English origin', 'ethnic origin', 'out-bred populations', 'UK'.
Genetic landmarks through philately – Henry Louis ‘Lou’ Gehrig and amyotrophic lateral sclerosis
Antibody deficiency, growth retardation, spondyloepiphyseal dysplasia and retinal dystrophy: a novel syndrome
Linkage disequilibrium mapping of the Nova Scotia variant of Niemann–Pick disease Acadians; Atlantic Canada; settlers; founder effect; relatively isolated areas
Pure trisomy 10p involving an isochromosome 10p
Angelman syndrome with uniparental disomy due to paternal meiosis II nondisjunction
Ebstein's anomaly associated with trisomy 9p
Professor Sarah Bundey 1936–1998
An individual with a healthy phenotype in spite of a pathogenic LDL receptor mutation (C240F)
High prevalence in the Greek population of the 35delG mutation in the connexin 26 gene causing prelingual deafness Greek population
Three novel small deletion mutations of the LDL receptor gene in Korean patients with familial hypercholesterolemia
Genetic aspects of population policy
Title
British Human Genetics Conference
A Thank you to Reviewers
Founder mutations in the LDL receptor gene contribute significantly to the familial hypercholesterolemia phenotype in the indigenous South African population of mixed ancestry originating from European, Indian and Jewish populations; Caucasoid admixture
How do carriers of hemophilia and their spouses experience prenatal diagnosis by chorionic villus sampling?