Clinical Genetics - 1997

185 articles | Last updated: 2025-12-03 14:12:56
Caucasian
5
White
3
European
3
Other
26
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Announcements
Association of angiotensin II type 1 receptor gene polymorphism with essential hypertension
Interstitial deletion of long arm of chromosome no. 5 with growth hormone deficiency‐an emerging syndrome?
A Cys634Gly substitution of the <i>RET</i> proto‐oncogene in a family with recurrence of multiple endocrine neoplasia type 2A and cutaneous lichen amyloidosis
Genetic epidemiology of Duchenne and Becker muscular dystrophy in Slovenia
A tetranucleotide repeat polymorphism within the human elastin gene (ELNi1)
Condensed chromatin enhancement in the phytohemagglutinin‐stimulated lymphocyte interphase nuclei of two xeroderma pigmentosum patients and artificial chromatin condensation of healthy cell nuclei by
Chromosome 21 and platelets: a gene dosage effect?
Microcephaly and intracranial calcification: two new cases
Delineation of a ring chromosome 16 by the FISH‐technique: a case report with review
Announcements
Analysis of the (CAG)n repeat causing Huntington's disease in a Mexican population Mexican population
The cholesteryl ester transfer protein (CETP) locus as a candidate gene in abdominal aortic aneurysm
A novel V415A mutation in exon 9 of the low density lipoprotein receptor gene causing familial hypercholesterolemia
Analysis of 65 Turkish patients with congenital aplastic anemia (Fanconi anemia and non‐Fanconi anemia): Hacettepe experience
Pearson marrow pancreas syndrome: a molecular study and clinical management
APO E Polymorphism in Spanish and Moroccan populations Northern European populations; South‐European populations; Spanish and Moroccan populations; Basque individual
Brachydactyly in a child with duplication‐deficiency subsequent to t(15;20)(q25.2;p12.2)mat. Candidate regions on one or both chromosomes?
Malignant hyperthermia susceptibility, an autosomal dominant disorder? Swedish
Association of the renin gene polymorphism with essential hypertension in a Chinese population Chinese population
Recurrent brachial plexus neuropathy in a family with subtle dysmorphic features‐a case of hereditary neuralgic amyotrophy
Moving towards a syndrome: a review of 20 cases and a new case of non‐mosaic tetrasomy 9p with long‐term survival
Cardio‐facio‐cutaneous (CFC) syndrome — a distinct entity? Report of three patients demonstrating the diagnostic difficulties in delineation of CFC syndrome
Interstitial deletion 2(p11.2p13): a rare chromosomal abnormality
A T &gt; C transition causing a Leu &gt; Pro substitution in a conserved region of the arylsulfatase A gene in a late infantile metachromatic leukodystrophy patient
A DNA polymorphism at the angiotensin II type 1 receptor (AT1R) locus and myocardial infarction
Apolipoprotein E polymorphism in the Greek population "Greek population"; "Chinese population"
Lipoprotein(a) in plasma, arterial wall, and thrombus from patients with aortic aneurysm
Studies on effects of Lp(a) lipoprotein on gene expression in endothelial cells <i>in vitro</i>
Analysis of the mechanism of lipoprotein(a) assembly
The lysine‐binding function of Lp(a)
LDL‐unbound apolipoprotein(a) and carotid atherosclerosis in hemodialysis patients
Schizophrenia genetics at the millennium: cautious optimism
“Reduction” of CGG trinucleotide expansion from mother to offspring in seven fragile‐X families
Interaction of the cholesteryl ester transfer protein I405V polymorphism with alcohol consumption in smoking and non‐smoking healthy men, and the effect on plasma HDL cholesterol and apoAI concentrati Icelandic
Association analysis of CA repeat polymorphism of the endothelial nitric oxide synthase gene with essential hypertension in Japanese Japanese
Are common mutations of cystathionine β‐synthase involved in the aetiology of neural tube defects?
Short Report on DNA Marker at Candidate Locus
Mutation of <i>RET</i> codon 768 is associated with the FMTC phenotype
Centromeric alphoid DNA heteromorphisms of chromosome 21 revealed by FISH‐technique
Congenital cutis laxa and lysyl oxidase deficiency
Prenatal diagnosis of a <i>de novo</i> trisomy 6q22.2→6qter and monosomy lpter→1p36.3. Case report with a 2‐year follow‐up and a brief review of other prenatal cases of partial trisomy 6q
A new case of oculocerebral hypopigmentation syndrome (Cross syndrome) with additional findings
Möbius‐like syndrome associated with a 1;2 chromosome translocation
Detection of <i>SRY</i> in 45, X/47, XYY mosaicism leading to phenotypic female
Mspl identifies a biallelic polymorphism in the promoter region of the α<sub>2A</sub>‐adrenergic receptor gene
A highly polymorphic (CA) repeat sequence in the human lysyl oxidase‐like gene
Two novel mutations in a Canadian family with aspartylglucosaminuria and early outcome post bone marrow transplantation Finnish population; non-Finnish cases
Evaluation of an aspartame loading test for the detection of heterozygotes for classical phenylketonuria
Submicroscopic deletion in chromosome 22q11 in trizygous triplet siblings and their father Clinical variability of 22q11 deletion
Reciprocal translocation 4; 11 with both adjacent‐1 segregants viable within a family
Case Report: Prenatal diagnosis of mosaic tetrasomy 21q confirmed by fluorescence <i>in situ</i> hybridization
Vocal cord paralysis and cystic kidney disease in Hajdu‐Cheney syndrome
Marinesco‐Sjögren syndrome associated with acute mveloblastic leukemia
MN blood group affects response of serum LDL cholesterol level to a low fat diet
The prevalence of Usher syndrome and other retinal dystrophy‐hearing impairment associations
Molecular and clinical studies of three cases of female pseudohermaphroditism with caudal dysplasia suggest multiple etiologies
Polydactyly and fetal hydantoin syndrome: an additional component of the syndrome?
A patient with Edwards syndrome caused by a rare pseudodicentric chromosome 18 of paternal origin
A polymorphism in intron 6 of the CYP17 gene
Apolipoproteins B and E, and angiotensin I‐converting enzyme (ACE) genetic polymorphisms in Italian women with coronary artery disease (CAD) and their relationships with plasma lipid and apolipoprotei Italian women; population of Rome; Central and Southern Italy
Association analysis of TG repeat polymorphism of the neuronal nitric oxide synthase gene with essential hypertension Japanese subjects
A dinucleotide repeat and a Hae III polymorphism in the human nicotinic acetylcholine receptor alpha‐subunit gene (CHRNA1)
A study of the cognitive and psychological profile in 16 children with congenital or juvenile myotonic dystrophy
X‐linked severe mental retardation and a progressive neurological disorder in a Belgian family: clinical and genetic studies
Factor V Leiden (R506Q) and risk of venous thromboembolism: a case‐control study based on the Spanish population Spanish population; Spanish thrombophilic patients; populations worldwide
Oculocerebrocutaneous syndrome: report of three additional cases and aetiological considerations
Is the frequency of Robinow syndrome relatively high in Turkey? Four more case reports Turkish; Turkey
Del (X)(p21.2) in a mother and two daughters with variable ovarian function
Detection of 100% of the CFTR mutations in 63 CF families from Tyrol Hutterite brethren; Tyrolian; Bavaria; Middle-and Northern Germany; Styria; Northern Italy; Southern
Prenatal growth retardation associated with microcephaly, microphthalmos/iris coloboma and other congenital malformations in three siblings
Erratum
Discordance between malignant hyperthermia susceptibility and RYR1 mutation C1840T in two Scandinavian MH families exhibiting this mutation Scandinavian
Genetic analysis of adult‐onset cataract in a city‐based ophthalmic hospital
Mosaicism for a small supernumerary ring X chromosome in a dysmorphic, growth‐retarded male: mos47,XXY/48,XXY, + r(X)
Variant euchromatic band within 16q12.1
Lp(a) lipoprotein is a major risk factor for cardiovascular disease: pathogenic mechanisms and clinical significance Black; Swedish
Symmetry of neurological signs in Pakistani patients with probable inherited spastic cerebral palsy
The role of the apolipoprotein E polymorphism in the prediction of coronary artery disease age of onset
Genetic variation of the angiotensin‐converting enzyme gene: increased frequency of the insertion allele in Koreans Koreans; Samoan; Yanomami; 'ethnic' (as in 'ethnic importance')
An autosomal recessive adducted thumb‐club foot syndrome observed in Turkish cousins Turkish
Two mosaic‐YY males carrying asymmetric Y chromosomes
Paracentric inversion of chromosome 9 with schizoaffective disorder
Congenital intractable diarrhea of infancy in Iraqi Jews Iraqi Jewish origin; Jews of Iraqi origin; ethnic groups
Clinical variability of tetrasomy 12p
SSCP variants within the α4 subunit of the neuronal nicotinic acetylcholine receptor gene
Dandy‐Walker malformation and postaxial Polydactyly: nosological comments
Genetic mapping using fluorescent quantification of allele frequencies in pooled DNA loaded by solid support
Carrier screening for cystic fibrosis in primary care: evaluation of a project in South Wales The South Wales Cystic Fibrosis Carrier Screening Research Team
Prenatal growth retardation, microphthalmos/iris coloboma, cloudy cornea, urogenital anomalies and microcephaly. A possible new sublethal syndrome
A study of possible deleterious effects of consanguinity
Identification of a point mutation (G727T) in the glucose‐6‐phosphatase gene in Japanese patients with glycogen storage disease type 1a, and carrier screening in healthy volunteers Japanese
Supernumerary marker chromosomes (SMCs) in Turner syndrome are mostly derived from the Y chromosome
A novel point mutation (Pro84 ← Ser) of the low density lipoprotein receptor gene in a family with moderate hypercholesterolemia Finns
Clinical manifestation of a severe neonatal progeroid syndrome
<i>De novo</i> duplication of 12pter → p12.1: clinical and cytogenetic diagnosis confirmed by chromosome painting
Multiple epiphyseal dysplasia and pseudoachondroplasia due to novel mutations in the calmodulin‐like repeats of cartilage oligomeric matrix protein
Case Report: Two newborns with chromosome 4 imbalances: deletion 4q33 → q35 and ring r (4) (pterq35.2‐qter)
Ohdo syndrome: report on a Brazilian girl with additional findings
Detection of an EcoRI restriction fragment length polymorphism in the gene encoding the human TBP associated factor II 30 (TAF<sub>II</sub>30)
Linkage studies exclude the AT‐V gene(s) from the translocation breakpoints in an AT‐V patient
Molecular studies of an X;Y translocation chromosome in a woman with deletion of the pseudoautosomal region but normal height
Female pseudohermaphroditism due to classical 21‐hydroxylase deficiency in a girl with Turner syndrome
Two new polymorphisms in the BRCA 1 gene
Extending the overlap of three congenital overgrowth syndromes
Photoanthropometric study of craniofacial traits in individuals with Williams syndrome
On the many faces of Leber hereditary optic neuropathy
Codon 89 polymorphism of the human 5α‐steroid reductase type 2 gene
Three cases of trisomy 13 mosaicism and a review of the literature
Polycystic kidney disease, biliary dysgenesis in a patient with Larsen's syndrome
A case of Carpenter syndrome diagnosed in a 20‐week‐old fetus with postmortem examination
A case of mosaic trisomy 2 diagnosed at amniocentesis in an abnormal fetus and confirmed in multiple fetal tissues
Identification of the parental origin of polysomy in two 49,XXXXY cases
A novel mutation M‐21V in exon 1 of the low density lipoprotein receptor gene causing familial hypercholesterolemia
Scintigraphic evaluation of Tc‐99m‐low‐density lipoprotein (LDL) distribution in patients with Gaucher disease
Detection of dystrophin deletion carriers using FISH analysis
Oto‐facio‐osseous‐gonadal syndrome: a new form of syndromic deafness?
Ethics and Genetics: Advanced European Bioethics Course. Nijmegen (The Netherlands), November 20–22, 1997
Analyses of mutations in the human renal kallikrein (hKLKl) gene and their possible relevance to blood pressure regulation and risk of myocardial infarction
Combined partial trisomy 3p/monosomy 5p resulting in sonographic abnormalities
Earlier finishing of Xp21.2 subband replication of the inactive X chromosome in Rett syndrome girl but not in her 47,XXX mother
Partial trisomy 6p from a <i>de novo</i> translocation (6; 18) with variable mosaicism in different tissues
Consanguineous marriage and its clinical consequences in migrants to Australia Eastern Mediterranean; Asia and Africa; migrants
Familial inv(X)(p22q22): ovarian dysgenesis in two sisters with del Xq and fertility in one male carrier
Recurrent omphalocele with partial trisomy 3q and partial monosomy 11q
Applicability of a checklist for clinical screening of the fragile X syndrome
<i>Pst</i>l‐polymorphism in the human bactericidal permeability increasing protein (BPI) gene
Words of Thanks
Greig cephalopolysyndactyly syndrome: altered phenotype of a microdeletion syndrome due to the presence of a cytogenetic abnormality
Preface
Lp(a) lipoprotein level predicts survival and major coronary events in the Scandinavian Simvastatin Survival Study Scandinavian
High‐degree sequence conservation in LPA kringle IV‐type 2 exons and introns
Reporter gene analysis of four DNasel hypersensitive sites in the plasminogen/apolipoprotein(a) intergenic region
Metabolism of Lp(a): assembly and excretion
Vascular accumulation of Lp(a): <i>in vivo</i> analysis of the role of lysine‐binding sites using recombinant adenovirus
Lipoprotein(a): identification of subjects with a superbinding capacity for fibrinogen
Apolipoprotein E type ε4 allele, heritability and age at onset in twins with Alzheimer disease and vascular dementia
Spectrum of CFTR mutations in Argentine cystic fibrosis patients South European population
Oculopharyngeal muscular dystrophy (OPMD)‐report and genetic studies of an Australian kindred German descent; French Canadian population
<i>De novo</i> duplication of 7pter→p21.2 and deletion of 9pter→p23.5: clinical and cytogenetic diagnosis
Chromosome deletion 17pl 1.2 (Smith‐Magenis syndrome) in seven new patients, four of whom had been referred for fragile‐X investigation
Short Report on DNA Marker at Candidate Locus
Short Report on DNA Marker at Candidate Locus
A novel polymorphism (1121 C/T) in intron 3 of the human apolipoprotein A‐l gene
Deletion polymorphism in the angiotensin‐converting enzyme gene is not associated with hypertension in a Gulf Arab population
Short Communication: Little phenotypic variability in three CF sibs compound heterozygous for the 621 + 1G ← T and the 711 + 1G ← T mutations
The atherogenic lipoprotein phenotype is not caused by a mutation in the coding region of the low density lipoprotein receptor gene
Case Report: Corroboration of the lower extremity counterpart of the Poland sequence
Prenatal detection of double aneuploidy trisomy 10/monosomy X in a liveborn twin with exclusively monosomy X in blood
Complex chromosome rearrangement involving chromosomes 1, 4 and 16 revealed by fluorescence <i>in situ</i> hybridization
Terminal 2q deletion‐a recognizable syndrome
High prevalence of a novel mutation in the exon 4 of the low‐density lipoprotein receptor gene causing familial hypercholesterolemia in Belgium
Two novel missense mutations in the ATP‐binding domain of the adrenoleukodystrophy gene: immunoblotting and immunocytological study of two patients
Lissencephaly associated with cerebellar hypoplasia and myoclonic epilepsy in a Bedouin kindred: a new syndrome? Bedouin kindred
CpG hotspot mutations at the LDL receptor locus are a frequent cause of familial hypercholesterolemia among South African Indians South African Indians; Indian families
Geographic distribution of French‐Canadian low‐density lipoprotein receptor gene mutations in the Province of Quebec French-Canadians
Incomplete penetrance and expressivity skewing in hereditary multiple exostoses
A new multiple malformation syndrome of Müllerian dysgenesis and conductive hearing loss with facial hypoplasia, bilateral forearm deformity, brachydactyly, spinal stenosis and scoliosis
Benign familial microcytic thrombocytosis with autosomal dominant transmission
Essential hyperhidrosis in Turner syndrome
China's genetic services providers' attitudes towards several ethical issues: a cross‐cultural survey
GAPO syndrome: first Egyptian case with ultrastructural changes in the gingiva
Mild phenotypic manifestations of terminal deletion of the long arm of chromosome 4: clinical description of a new patient
Developmental aspects in apple peel intestinal atresia — ocular anomalies — microcephaly syndrome
Expand Long PCR for fragile X mutation detection
Differences in the prevalence of a TaqI RFLP in the 3‘ flanking region of the α<sub>1</sub>‐proteinase inhibitor gene between asthmatic and non‐asthmatic black and white South Africans
Influence of APOH protein polymorphism on apoH levels in normal and diabetic subjects
A case of <i>de novo</i> interstitial deletion of chromosome 5(q33q34)
An additional case of craniodigital syndrome: variable expression of the Filippi syndrome?
Rhombencephalosynapsis with facial anomalies and probable autosomal recessive inheritance: a case report
Turner syndrome in a mother and daughter: r(X) and fertility
A bi‐allelic tetranucleotide repeat in the promoter of the human inducible nitric oxide synthase gene
Intragenic tetranucleotide repeat polymorphism at the human histidase (HAL) locus
Osteopathia striata with cranial sclerosis: highly variable phenotypic expression within a family
Scalp defect, absence of nipples, ear anomalies, renal hypoplasia: another case of Finlay‐Marks syndrome
A Pvull polymorphism detected by a cDNA clone of the gene encoding the human spasmolytic protein (SML1 gene), one of three members of the trefoil peptide gene family clustered on chromosome 21q22.3
Cardiovascular risk factors in people with different genotypes in the insertion/deletion (I/D) polymorphism at the locus for angiotensin I‐converting enzyme (ACE)
Case Report: Partial trisomy of 15q due to inserted inverted duplication
Review: Epidemiology of Lp(a) lipoprotein: its role in atherosclerotic/thrombotic disease
Apolipoprotein(a) is a human vascular endothelial cell agonist: studies on the induction in endothelial cells of monocyte chemotactic factor activity
Biogenesis of Lp(a) in transgenic mouse hepatocytes
Plasma concentrations of Lp(a) lipoprotein and TGF‐β<sub>1</sub> are altered in preeclampsia
High plasma levels of apo(a) fragments in Caucasians and African‐Americans with end‐stage renal disease: implications for plasma Lp(a) assay
Standardization of Lp(a) measurements
The genetics of alcoholism: 1997