Clinical Genetics - 1986

222 articles | Last updated: 2025-12-03 14:12:56
Caucasian
2
White
1
European
2
Other
12
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Germinal mosaicism in Apert syndrome
Osteoporosis‐pseudoglioma syndrome
Genetic screening for artificial insemination by donor (AID)
Fetal mortality in sibships of cases with neural tube defects
Use of Y chromosome specific probes to detect low level sex chromosome mosaicism
DNA probes for linkage analysis of X linked diseases: Localisation of the disease locus for anhidrotic ectodermal dysplasia
Studies on fragile X‐mental retardation by the use of DNA probes
Cystic fibrosis ‐ a search for the basic defect
RFLP studies in families with Duchenne muscular dystrophy
The most profoundly retarded children in the county of Aarhus II. Etiologic and pathogenetic aspects
Chromosome abnormalities in mesenchymal neoplasms
Genetic effects in offspring of cancer patients
Restriction enzyme analysis of human HLA‐linked C4‐genes in the Finnish population Finnish population
High‐resolution banding: a study of 85 patients with mental retardation
Xp21/autosome translocations
Third International Conference on Chorionic Villus Sampling and Early Prenatal Diagnosis
Number of “high genes” involved in determining the activity of paraoxonase Danish family material
Structure, origin and effects of a supernumerary marker chromosome 15
Partial deletion of the short arm of chromosome 3: further delineation of the 3p25 ‐ 3pter syndrome
Cerebroside‐β‐glucosidase activity in Gaucher brain
Trisomy 4 due to nondisjunction during maternal meiosis II
Unusual pedigree patterns in seven families with spinal muscular atrophy; further evidence for the allelic model hypothesis
Growth curves for height in Noonan syndrome
Genetic modelling in schizophrenia according to HLA typing
Discoid lupus erythematosus‐like skin lesions in a patient with autosomal recessive chronic granulomatous disease
Skeletal maturation in the XY female syndrome
The fetal pathology of the XXXXY‐syndrome
Chromosomal mosaicism and maternal cell contamination in chorionic villi cultures
Distal 11q monosomy. The typical 11q monosomy syndrome is due to deletion of subband 11q24.1
Klinefelter's syndrome in Sardinia Sardinian
Pyknoachondrogenesis: An association of skeletal defects resembling achondrogenesis with generalized bone sclerosis. A new condition?
In defence of partial trisomy
Fragile X; experience of a laboratory
Tapeto‐retinal degeneration in four Norwegian counties I
Iris (Lisch) nodules in neurofibromatosis
Inheritance of atrioventricular conduction time in Tokelau Islanders Polynesians; Tokelau Islanders; racial groups
Inherited Xp21 deletion in a boy with complex glycerol kinase deficiency syndrome
Genetic control over fragile X chromosome expression
α<sub>1</sub>‐antitiypsin deficiency and the flaccid lung syndrome
Proximal duplications of chromosome 15: clinical dilemmas
High resolution pattern of an inverted duplication (15)
Osteoporosis‐pseudoglioma syndrome and the ocular form of osteogenesis imperfecta
27th Annual Short Course in Medical and Experimental Genetics
Chorion in culture
Cytogenetic heterogeneity of translocations associated with Duchenne muscular dystrophy
Evidence for preferential involvement of chromosome bands 6p21 and 13q14 in amniotic fluid cell balanced translocation pseudomosaicism
Long term survival of a patient with the cerebro‐hepato‐renal (Zellweger) syndrome
Determination of the acetylator phenotype in a Turkish population Turkish population
ERRATUM
The Borjeson‐Fbrssman‐Lehmann syndrome
The McCune‐Albright syndrome: a lethal gene surviving by mosaicism
Heterogeneity of Morquio disease
Multiple congenital anomalies in a child born after prenatal diagnosis of trisomy 20mosaicism
Announcements
Mental retardation in a North Swedish isolate North Swedish
P<scp>etros</scp> T<scp>sipouras</scp><sup>4</sup>
The problem of isolated cases of Huntington's disease in South Wales 1974–1984
The CHARGE syndrome
Coexistent pseudohypoparathyroidism and D brachydactyly in a family
Asymmetric crying facies with microcephaly and mental retardation. An autosomal dominant syndrome with variable expressivity
Use of a biotinylated DNA probe specific for the human Y chromosome for rapid antenatal sex determination
Evaluation of urinary cells in acid cholesteryl ester hydrolase deficiency
Unspecific reactions of HLA‐B antisera on fibroblasts from patients and carriers of Duchenne muscular dystrophy
Prometaphase chromosome analysis as a routine diagnostic technique
Accumulation and defective β‐oxidation of very long chain fatty acids in Zellweger's syndrome, adrenoleukodystrophy and Refsum's disease variants
Cryptophthalmos ‐ syndactyly syndrome without cryptophthalmos
Infantile type of sialic acid storage disease with sialuria Austrian ancestry
Detection and exclusion of carriers of ornithine transcarbamylase deficiency by RFLP analysis
Arthrogryposis and <b>46,</b>XY, t(1;16) chromosome constitution
Mapping status of cystic fibrosis
A computerised register for Huntington's chorea in Denmark
Single abnormal cells may be interpreted as pseudomosaicism or mosaicism
Genetic counselling of Duchenne muscular dystrophy families based on analysis of flanking DNA markers
Reciprocal effects of apolipoprotein E alleles (ε2 AND ε4) on plasma lipid levels in normolipidemic subjects
The Grant Syndrome: Persistent Wormian bones, blue sclerae, mandibular hypoplasia, shallow glenoid fossae and campomelia ‐ an autosomal dominant trait
A family with craniofrontonasal dysplasia, and fragile site 12q13 segregating independently
Partial deletion of the short arm of chromosome 3
On the origin of extra isochromosomes
ERRATUM
Adult polycystic liver and kidney diseases are separate entities
Relative reliability of three different discriminant analysis methods for detecting PKU gene carriers
Partial trisomy 3p syndrome
Normal female carrier and affected male half‐sibs with t (X;5) (q13;p15)
Comments on methods and results in: Sherman et al., “Segregation analysis of balanced pericentric inversions in pedigree data”
Heterochromatinization of human X‐ chromosomes: classification of replication profile
Autosomal dominant lamellar ichthyosis
Peculiar face, deafness, cleft palate, male pseudohermaphroditism, and growth and psychomotor retardation; a new autosomal recessive syndrome?
International Conference on Reproduction and Human Cancer Bethesda, Maryland, May 11–13, 1987
Dermatoglyphics in Congenital Adrenal Hyperplasia (CAH)
Pepsinogen A polymorphism in gastric mucosa and urine, with special reference to patients with gastric cancer
A recent survey of consanguineous marriages in Japan
High‐resolution cytogenetic studies in patients with Prader‐Willi syndrome
Analysis of fragile X‐mental retardation families using flanking polymorphic DNA probes Swedish families
Inbreeding and schizophrenia
Recombination aneusomy of chromosome 5 associated with multiple severe congenital malformations
A study into possible deviation from the Hardy‐Weinberg equilibrium by the alleles of the hypervariable sequence in the region of the human insulin gene
The arylsulphatases of chorionic villi: potential problems in the first‐trimester diagnosis of metachromatic leucodystrophy and Maroteaux‐Lamy disease
A genetic‐diagnostic survey in an institutionalized population of 173 severely mentally retarded patients
Tapeto‐retinal degeneration in four Norwegian counties II
Calvarial hyperostosis: a benign X‐linked recessive disorder
Neuronal Ceroid Lipofuscinosis (NCL) or Batten Disease International Registry
Number of loci responsible for the inheritance of high and low activity of paraoxonase Danish
Familial transmission of a non‐Robertsonian translocation dicentric
Clinical and genetic studies of muscular dystrophy in young girls
An infant with thanatophoric dwarfism surviving 169 days
Isolated congenital bowed long bones
Pierre Robin anomaly with an accessory metacarpal of the index fingers
Thymus deficiency in an infant with a chromosome t(18;22)(q12.2;p11.2)pat rearrangement
Names in genetics: ban on partial trisomy, tetrasomy and monosomy
Announcement
Congenital heart disease in supernumerary der(22), t(11;22) syndrome
Deleted ring chromosome 22 in a mentally retarded boy
Absent tibiae, triphalangeal thumbs, Polydactyly and non‐penetrance
Dominantly inherited craniodiaphyseal dysplasia: A new craniotubular dysplasia
A postaxial Polydactyly and progressive myopia syndrome of autosomal dominant origin
Triplication, Partial Tetrasomy or Tetramere?
Concerning the article “Gonadoblastoma and Y chromosome fluorescence”. Clin. Genet. 29, 311–316 (1986)
Ring 21 chromosome: the mild end of the phenotypic spectrum
Neurodevelopmental and psychological aspects in a child with 49XYYYY karyotype
An evaluation of maternal cell contamination in cultures of chorionic villi for the prenatal diagnosis of chromosome abnormalities
DNA polymorphism at the apolipoprotein B locus is associated with lipoprotein level
Response to Stene's comments on the segregation of balanced pericentric inversions
A simplified method for observing and recording dermatoglyphic patterns, including counting sweat pores
Linkage of transcobalamin II (TC2) to the P blood group system and assignment to chromosome 22
Linkage between the loci for cystic fibrosis and paraoxonase
Whole‐arm t (X;17) (Xp17q;Xq17p) and gonadal dysgenesis
Tricho‐rhino‐phalangeal syndrome without exostoses, with an interstitial deletion of 8q23
De novo del(4) (p15.32) with incomplete expression of the Wolf‐Hirschhorn syndrome
Heterozygote expression in Grebe Chondrodysplasia
Typing of families with classical phenylketonuria using three alleles of the Hindlll linked restriction fragment polymorphism, detectable with a phenylalanine hydroxylase cDNA probe
First trimester chorionic villi sampling and direct chromosome preparations
Craniofrontonasal dysplasia: clinical and genetic analysis
Usher syndrome in four Norwegian counties Norwegian ("four Norwegian counties")
High resolution chromosome results in retinoblastoma families
Increased levels of apo‐transcobalamins I and II in amniotic fluid from pregnant women with previous neural tube defect offspring
The Johanson‐Blizzard syndrome: report of a new case with special reference to the dentition and review of the literature
Autosomal dominant onychodystrophy and anonychia with type B brachydactyly and ectrodactyly
Familial supernumerary non‐satellited microchromosome
Frequency of rare fragile sites among mentally subnormal schoolchildren
First trimester diagnosis of Pompe's disease (glycogenosis type II) with normal outcome: assay of acid α‐glucosidase in chorionic villous biopsy using antibodies
Effect of sibship position on reproductive behavior of couples after the birth of a genetically handicapped child
The Cowden syndrome: a clinical and genetic study in 21 patients
Copper‐measurement in a muscle‐biopsy. A possible method for postmortem diagnosis of Menkes disease
On the nosology of the Cornelia de Lange and Coffin‐Siris syndromes
Guidelines for the diagnosis of fragile X
A simple technique for recording and counting sweat pores on the dermal ridges
A de novo translocation in a family with a balanced reciprocal chromosomal translocation
A family with congenital suprabulbar paresis (Worster‐Drought syndrome)
X‐linked short stature with skin pigmentation: evidence for heterogeneity of the Russell‐Silver syndrome
Osteoporosis‐pseudoglioma or osteogenesis imperfecta?
Psychosocial adjustment of adult women with Turner syndrome
The spectrum of clinical features in CHARGE syndrome
Gonadoblastoma and Y‐chromosome fluorescence
Trichodermodysplasia with dental alterations: an apparently new genetic ectodermal dysplasia of the trichoodonto‐onychial subgroup
Spastic paresis, glaucoma and mental retardation ‐ a probable autosomal recessive syndrome?
A racial difference in apolipoprotein E allele frequencies between the Japanese and Caucasian populations
Ehlers‐Danlos features with progeroid facies and mild mental retardation
Weill‐Marchesani syndrome in mother and son
Client reactions to genetic counseling: self‐reports of influence
Trisomy (18q) and tetrasomy (18p) resulting from isochromosome formation
Indication against genetic localisation of the human transcobalamin II gene (TC2) on chromosome 16
The effect of consanguineous marriages on reproductive wastage
235 cases of prenatal 1st trimester cytogenetic diagnosis based on transabdominal CVS
Characterization of neoplasia‐associated chromosome abnormalities by Southern blot analysis
The prognostic implication of cytogenetic findings in non‐Hodgkin lymphomas
Early diagnosis of Mb. Recklinghausen
Polymorphism of type I collagen genes in the Finnish population
Mutagenic effect of amniotic fluid from smoking women at term
Linkage studies in choroideremia
Clinical use of DNA markers (RFLP) in genetic counselling and prenatal diagnosis of haemophilia A and B
Cockayne syndrome, early‐onset type: clinical and cytogenetic findings
The fragile X chromosome: prenatal diagnosis
Effect of genetic factors on the variation in plasma concentration of antithrombin III: A twin study
DNA polymorphisms around the apo Al gene in normal and hyperlipidaemic individuals selected for a twin study Norwegian population; UK individuals
Segregation analysis of brown oculocutaneous albinism
Critical segment for 9p deletion syndrome
7th International Congress of Human Genetics – Satellite Workshop
The Human Gene Map 15 April 1986: The Morbid Anatomy of the Human Genome
Dermatoglyphic peculiarities in families with X‐linked mental retardation and fragile site Xq27: a collaborative study
Autosomal whole arm translocations in man
Paternal non‐disjunction in a 46, XY/ 47, XXY individual with a fragile 17p12 in the mother
An unusual variant chromosome 9 due to disturbance of normal chromatin condensation at band p12?
Prenatal diagnosis and pathoanatomy of iniencephaly
Segregation analysis of balanced pericentric inversions in pedigree data
A syndrome with intracranial calcification and microcephaly in two sibs, resembling intrauterine infection
Deletion of chromosome 11 (p11p13) in a patient with Beckwith‐Wiedemann syndrome
δ‐aminolevulinic acid dehydrase (porphobilinogen synthase) in two families with inherited enzyme deficiency
St. Helena familial genu valgum
An asymmetric type of chondrodysplasia in an adult male
Oto‐Palato‐Digital syndrome in four generations of a larqe family
Congenital cutis laxa
Mutation of the Duchenne muscular dystrophy gene associated with meiotic recombination
Announcements
Minimal pigment: a new type of oculocutaneous albinism
Detection and localization of an extra HLA locus in a karyotypically normal male by chromosomal in situ hybridization Black
A variant of the “DIDMOAD” syndrome: (Diabetes Insipidus, Diabetes Mellitus, Optic Atrophy and Deafness)
A new skeletal dysplasia syndrome with rhizomelia of the humeri and other malformations Arab family
Mosaicism for ring and isopseudodicentric chromosome 13
Genetics of Skin Diseases, ESDR‐Symposium Oslo
Determination of cholinesterase and acetylcholinesterase in amniotic fluid
Usefulness of a registry of congenital malformations for genetic counseling and prenatal diagnosis
Homozygosity for a Y/22 chromosome translocation: t(Y;22) (q12;p12/13)
DA/DAPI pattern of marker chromosome: cytogenetics of cat eye syndrome
Population cytogenetics of autosomal fragile sites
Cytogenetic analysis in 100 spontaneous abortions in North‐East Scotland
Sanfilippo disease in Greece Greek ethnic community of Turkey
Congenital cutis laxa with retardation of growth and motor development: a recessive disorder of connective tissue with male lethality
Cerebral gigantism with hydronephrosis: a case report
Pericentric inversion 16 in man ‐ a second case
Ocular osteogenesis imperfecta
Cardiovascular manifestations in Fabry's disease
Measurement of body fat in Turner syndrome
Incidence of trisomy 18 in Sweden in 1981–1982: Clustering in a small region
A new chromosome instability disorder
Diagnostic applications of H‐Y serology: H‐Y negative phenotype in cells from 45, X/ 46, XY fetus with testes
Full expression of Hunter's disease in a female with an X‐chromosome deletion leading to non‐random inactivation
The acrocallosal syndrome in sisters
Multiple sulphatase deficiency presenting at birth
Exencephaly in human fetuses
Osteogenesis imperfecta or Osteoporosis‐pseudoglioma syndrome
Case report: partial trisomy 20q (20q13.13→qter)
Cryptophthalmos‐syndactyly syndrome without cryptophthalmos