Clinical Genetics - 1984

205 articles | Last updated: 2025-12-03 14:12:56
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Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Measuring the genetic contribution of a single locus to a multilocus disease
Triploidy, partial mole and dispermy. An investigation of 12 cases
Ethical and social aspects of risk predictions
Chromosomal constitution of infertile men
ESHG Symposium: Cancer and Genetics in 1984 Essen, 1–3 June, 1984
Polymorphism of the human Y chromosome: the evaluation of the correlation between the DNA content and the size of the heterochromatin and euchromatin*
In vitro reversal of fragile‐X expression by exogenous thymidine
Marker chromosomes in parents to children with Down's syndrome
The syndromic status of sclerosteosis and van Buchem disease The Afrikaners have Dutch antecedants; Afrikaner community of South Africa; Afrikaners
Mucopolysaccharidosis III B: hybridization studies on fibroblasts from a mild case and fibroblasts from severe patients
Dermal changes in Ehlers‐Danlos syndrome
Alpha‐1‐antitrypsin types and rheumatoid arthritis
Renal agenesis as a diagnostic feature of the crypthophthalmos‐syndactyly syndrome
Asymmetric skeletal anomalies in siblings
Linkage of plasma α‐L‐fucosidase (FUCA2) and the plasminogen (PLG) system European populations
Cluster of acute infantile spinal muscular atrophy (Werdnig‐Hoffmann disease) in a limited area of Reunion Island European population of the island
Trisomy 9 (pter → q1 to q3): the phenotype as an objective aid to karyotypic interpretation
Duplication in the proximal portion of the long arm of chromosome 15, in a girl without phenotypic features of the Prader‐Willi syndrome
Mental retardation, short stature, minor skeletal anomalies, craniofacial dysmorphism and macrodontia in two sisters and their mother
Spontaneous abortions and facial clefts
Germinal Mosaicism
Craniofrontonasal dysplasia: Genetic heterogeneity?
Reduced plasma concentrations of total, low density lipoprotein and high density lipoprotein cholesterol in patients with Gaucher type I disease
Fragile 22q13 segregating in a family
Combined sialidase (neuraminidase) and β‐galactosidase deficiency. Clinical, morphological and enzymological observations in a patient Japanese origin
A young girl with ring(18) mosaicism: cytogenetic studies and PEP A mapping
Date of conception and prevention of neural tube defects French Canadian population; ethnic groups identity
A new syndrome with camptodactyly, joint contractures, facial anomalies, and skeletal defects: a case report and review of syndromes with camptodactyly Sephardic Jewish
Del 11p/aniridia complex. Report of three patients and review of 37 observations from the literature
Confirmation of F13A assignment and sequence information concerning F13A‐HLA‐GLO Danish
Diagnosing of chromosome abnormalities in Denmark
Oculocutaneous albinism and anterior chambre cleavage malformations
Autosomal dominant lamellar ichthyosis: a new skin disorder*
Maternal translocation t(13:18)(q34:q11) and Edwar's syndrome in a fetus: 47, XY, t(13:18)(q34:q11) + 18
Birth intervals in oral cleft families
Comment on “Partial trisomy 11q…”, report by De France et al. (1984)
Encephalo‐oculo‐cutaneous dysplasia
Corrections
Isochromosome 18q with karyotype 46, XX, i(18q). Cytogenetics and pathology
Fetal mortality in sibships of cases with neural tube defects
Infantile Refsum's disease (phytanic acid storage disease): a variant of Zellweger's syndrome?
Two fertile Turner women in a family
Clinical delineation of proximal and distal partial 13q trisomy
Low density lipoprotein receptors in cultured skin fibroblasts from psoriasis patients
Anomalous cerebral venous drainage in Aarskog syndrome
London School of Hygiene and Tropical Medicine Diploma in Human and Clinical Genetics
Fetal mortality in oral cleft families (<i>V):</i> studies of sporadic vs familial and pure vs syndromic clefts
Autosomal recessive inheritance of juvenile periodontitis: test of a hypothesis
Severe limb malformations in 4p deletion
Analysis of human sperm chromosome complements from a male heterozygous for a reciprocal translocation t(11;22)(q23;q11)
Isolated asternia: an independent entity
Smith‐Lemli‐Opitz syndrome in two 46,XY infants with female external genitalia
The Williams syndrome: objective definition and diagnosis
Differential diagnosis of the Williams and the Noonan syndromes
Orbital cyst in addition to congenital cerebral and focal dermal malformations: a new entity
Fragile sites and chromosome breakpoints in constitutional rearrangements II. Spontaneous abortions, stillbirths and newborns
Ankylosing spondylitis is part of a multifactorial syndrome: hereditary multifocal relapsing inflammation (HEMRI)
Cholesterol ester storage disease in an adult presenting with sea‐blue histiocytosis
Familial partial monosomy 5p and trisomy 5q; three cases due to paternal pericentric inversion 5 (p151q333)
Distal trisomy 14q syndrome; a case report
THIRD NORDIC CONFERENCE Pepsinogen and gastric cancer
Autosomal recesslve ichthyosis in Norway: II. Sjøgren‐Larsson‐like ichthyosis without CNS or eye involvement
Prader‐Willi syndrome in a child with a balanced (X;15) de novo translocation
Alpers' disease
Endocrine Genetics and Genetics of Growth
Further delineation of the Cohen syndrome; report on chorioretinal dystrophy, leukopenia and consanguinity
Causes of variation in birth weight: A study of offspring of twins
Grebe chondrodysplasia and brachydactyly in a family
46, X, i(Xq)/45, X mosaicism with gonadal dysgenesis associated with 21p‐
Robertsonian Translocation and Prader‐Willi syndrome
Bloom's syndrome XI. Progress report for 1983
Absent tibiae, triphalangeal thumbs and polydactyly: description of a family and prenatal diagnosis
A new psychomotor retardation syndrome with peculiar facies and marfan‐oid habitus
The NEU‐COFS (cerebro‐oculo‐facio‐skeletal) syndrome: report of a case
Clinical and Genetic Aspects of Fanconi's Anaemia Abstracts from Workshop at Free University
Letters to the Editors
Letters to the Editors
The use of structured scenarios in genetic counselling
Trisomy 7 and Potter syndrome
Interstitial deletion of chromosome 1 (q23–25). Report of a case
Alternative explanations for recurrent achondroplasia in siblings of normal parents
Fourth International Conference on Environmental Mutagens
Chromosome maps of man and mouse II
The Nance‐Horan syndrome: a rare X‐linked ocular‐dental trait with expression in heterozygous females
Aneuploidy in recurrent spontaneous aborters: the tendency to parental nondisjunction
Agonadism with positive H‐Y antigen
Selection against genetic defects in semen donors
Genetics of site specific colon cancer: a family study Indian Sikh family
Prader‐Willi syndrome in Black females Black females
Chromosome studies on normal males in 16 families with the marker X chromosome
Controlled comparison of plasma and serum for cystic fibrosis protein
Pi phenotypes in patients with ankylosing spondylitis, acute anterior uveitis, psoriasis and chronic prostatitis Norwegian
Genital anomaly and cardiomyopathy: a new syndrome
Duplication in chromosome 15q in a boy with the Prader‐Willi syndrome; further cytogenetic confusion
Sensorineural deafness and peripheral neuropathy
Parental determinants of birth weight
α‐L‐iduronidase deficiency in mucopolysaccharidosis type I against a radio‐labelled sulfated disaccharide substrate derived from dermatan sulfate
ATPase activity of erythrocyte membrane in patients with trisomy 21 (Down's syndrome)
Long arm deletions of the X chromosome and their symptoms: a new case (bp q24) and a short review of the literature
Klinefelter syndrome and two fragile X chromosomes
Non‐progressive psychomotor retardation in a child with severe deficiency of arylsulphatase A activity
Familial 5p‐ syndrome
A supernumerary microchromosome in amniotic cell cultures and talipes equinovarus in a live born female
Epinephrine‐induced platelet aggregation. A twin study**
Abnormal chromosome in Prader‐Willi syndrome
Alpha‐mannosidosis: analysis of urinary oligosaccharides with high performance liquid chromatography and diagnosis of a case with unusually mild presentation
Problems of detecting mosaicism in skin. A case of trisomy 8 mosaicism illustrating the advantages of <i>in situ</i> tissue culture
Partial trisomy 11q due to paternal t(11q;18p); further delineation of the clinical picture
Fetal mortality in oral cleft families (VII): birth intervals
Arteriohepatic dysplasia: phenotypic features and family studies
Dermatoglyphic features in Prader‐Willi syndrome with respect to chromosomal findings
Deletion of the long arm of chromosome 11 [46, XX, deI(11)(q24.1 → qter)]
Clinical consequences of heterozygosity for autosomal‐recessive diseases*,**
Chromosome fragility in Alzheimer's disease
The development of four unselected 47,XYY boys
Myotonic dystrophy and autosomal balanced translocation t(2; 20) (p21; q11)
Abnormal B.A.E.P. in a family with Moebius syndrome: evidence for supranuclear lesion
Craniofrontonasal dysplasia ‐ a distinct entity with lethality in the male?
Nager's acrofacial dysostosis with thumb duplication: report of a case
A 5p;22q reciprocal translocation with a high risk for segregation of unbalanced offspring
First trimester biopsies of chorionic villi for prenatal diagnosis: experience of two laboratories
Four cases of the prenatal diagnosis of trisomy 20 mosaicism with a follow up investigation
Prometaphase chromosome and immunological studies in different derivatives of balanced t(8;14)(p231;q323)
Meningocele in a boy with trisomy 13
“Blind” versus direct vision technique for fetal skin sampling in cases for prenatal diagnosis
Familial balanced insertion (5;10) and monosomy and trisomy (10) (q24.2→q25.3)
The level of 6‐phosphogluconate dehydrogenase (6‐PGD) activity in a patient with a 1p terminal deletion suggests that the gene locus is not distal to sub‐band p36.3 on chromosome 1
Cytogenetics of ring chromosome 7
Mohr syndrome variant or Joubert‐Boltshauser syndrome?
The Human Gene Map 15 November 1983
Familial minor neurodevelopmental disorders
Familial Wolf's syndrome with a hidden 4p deletion by translocation of an 8p segment. Unbalanced inheritance from a maternal translocation (4;8)(p15.3;p22). Case report, review and risk estimates
Five generations of t(4;8)(q35;q13) leading to a case of partial 8q trisomy with consideration of potential pregnancy outcomes from translocation carriers
Control of homozygous β‐thalassemia by carrier screening and antenatal diagnosis in Sardinians
Familial pericentric inversion (14)(p11;q24) with a rec dup(q) in one offspring
Manifestations and natural history of idiopathic hemihypertrophy: a review of eleven cases
Male to male transmission of the G syndrome
The impact of large Y chromosome on pregnancy, foetus and birth
Detection of the fragile X chromosome and other fragile sites
Usefulness of 4‐methylumbelliferyl‐6‐ sulfo‐2‐acetamido‐2‐deoxy‐β‐D‐glucopyranoside for the diagnosis of GM2 gangliosidoses in leukocytes
Fetal mortality in oral cleft families (IX): factors relating to the occurrence of sporadic clefts
Early clinical signs in Coffin‐Lowry syndrome
X‐linked recessive microencephaly, microphthalmia with corneal opacities, spastic quadriplegia, hypospadias and cryptorchidism
The fragile X syndrome: A study of 83 families
Familial occurrence of azoospermia and extreme oligozoospermia
Interstitial deletion of the long arm of chromosome 6 [del(6)(q16q22)]: case report and review of the literature
Weyers acrodental dysostosis in a family
Reply to Dr. Hoo
Mechanisms that cause Craniofacial and Oral Birth Defects
Frequency of abnormal karyotypes in relation to the ascertainment method in females referred for suspected sex chromosome abnormality
Ehlers‐Danlos syndrome type IV D: an autosomal recessive disorder
Reduced fertility in women with X chromosome abnormality
Cytogenetic and clinical findings in ten 45, X/46, XY patients*
Duplication or insertion in 15q11–13 associated with mental retardation ‐short stature and obesity ‐ Prader‐Willi or Cohen syndrome?
Partial Trisomy 9q resulting from a familial translocation t(9;16)(q32;q24)
Ocular, cerebral and cutaneous malformations: confirmation of an association
Fragile sites and chromosome breakpoints in constitutional rearrangements I. Amniocentesis
Oro‐facio‐digital syndromes I and II: radiological methods for diagnosis and the clinical variations
Analysis of a familial 15p + polymorphism: exclusion of Y/15 translocation
Occurrences of methylmalonic aciduria and Hartnup disorder in the same family
FamiIial vascuIar malformations Report of 25 members of one family
Papers presented at The Third Nordic Conference of Medical Genetics Helsinki, Finland, 17–19 February 1984
Two cases of 11p13 interstitial deletion and unusual clinical features
Semi‐lethal bone dysplasia in three sibs: a new genetic disorder
Diagnostic transcervical chorionic biopsles in first trimester pregnancies
The Occurrence of “Finnish” hereditary diseases in the other Nordic countries
Basement membrane proteins in human amniotic fluid
Scoliosis and retinal changes in a G syndrome carrier
Lchthyosis vulgaris with hypogenitalism and hypogonadism: evidence for different genotypes by lipoprotein electrophoresis and steroid sulfatase testing*
The Schinzel syndrome in a mother and daughter
A Weaver‐like syndrome in a Japanese boy mongoloid slanting of the palpebral fissures
The psychological profile of the fragile X syndrome
Diagnostic considerations in arthrogry‐posis syndromes in South Africa
Autosomal recessive inheritance of Charcot‐Marie‐Tooth disease associated with sensorineural deafness Indian
Ring chromosome 10 syndrome: case report and the possibility of clinical diagnosis
Is the Pi<sup>F</sup> allele of α<sub>1</sub>‐antitrypsin as‐sociated with pulmonary disease?
Partial ornithine transcarbamylase deficiency associated with recurrent hyperammonemia, lethargy and depressed sensorium
Partial sweat gland aplasia in incontinentia pigmenti Bloch‐Sulzberger
Fetoscopy in prenatal diagnosis of the Majewski and the Saldino‐Noonan types of the Short Rib‐Polydactyly syndromes
Mentally retarded siblings with congenital heart defect, peculiar facies and cryptorchidism in the male: possible McDonough syndrome with coincidental (X; 20) translocation
Mandibuloacral dysplasia: a rare progeroid syndrome Two brothers confirm autosomal recessive inheritance
Mosaic tetrasomy 21 in a male child
Monosomy X associated with fra(17p12) and 22p‐
Further evidence for a significant effect of fetal genes on variation in birth weight
Chorionic villi sampling under direct vision
The manifestations and natural history of spondylo‐epi‐metaphyseal dysplasia with joint laxity Afrikans‐speaking community of South Africa
Endocrine and genetic characterization of cousins with male pseudohermaphroditism: evidence that the Lubs pheno‐type can result from a mutation that alters the structure of the androgen receptor
The Coffin‐Siris syndrome: Report of a family and further delineation
The gene for apolipoprotein C‐ll is closely linked to the gene for apolipoprotein E on chromosome 19
Amniotic fluid analysis in prenatal diagnosis of neural tube defects: a comparison between six biochemical tests supplementary to the measurement of amniotic fluid alpha‐fetoprotein
Two sibs with bilateral diaphragmatic defect
New anomalies found in the 11q‐ syndrome
Cytogenetics of Prader‐Willi Syndrome
The inheritance of constitutive and facultative skin colour
Atypical gonadal dysgenesis: the role of Yq in determining phenotype and malignancy risk
Preaxial polydactyly type 4: variability in a large kindred
Polymorphism at the Apoprotein‐E locus in relation to risk of coronary disease
Medical Genetics: 1984. May 10–12, 1984, in Washington, DC
Interstitial deletion of band q12 of chromosome 5
Familial porencephaly
Hydrops fetalis: a new aspect of trisomy 18
Hereditary lymphedema: a new combination of symptoms not fitting into present classifications
Rocker bottom feet
Unexpected findings at prenatal diagnosis
Experience with transabdominal fine needle biopsy from chorionic villi in the first trimester: an alternative to amniocentesis