Clinical Genetics - 1977

137 articles | Last updated: 2025-12-03 14:12:56
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Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Chromosomal anomalies in patients with retinoblastoma
Partial trisomy 22: A recognizable syndrome
Down syndrome and maternal age in Japan, 1950–1973
A diagnostic index for Down syndrome
Linking of medical records to form pedigrees
Announcement
An autosomal dominant midline cleft syndrome resembling familial holoprosencephaly
Genetic variance of erythrocyte parameters in adult male twins
Alpha‐I‐antitrypsin (Pi) phenotypes in Lyon, France: departure from Hardy‐Weinberg equilibrium
The deletion 9p syndrome. A 61‐year‐old man with deletion of short arm 9
Wolf‐Hirschhorn syndrome and balanced (4;10) translocation in the father
Distribution patterns of satellite associations in human lymphocytes relative to age and sex
A t(5p‐;21q+) translocation in a family with Down syndrome
Linkage analysis with misclassification at one locus
Mydriasis and heredity* Aymara; Mestizo; non-Aymara
Hereditary cholinesterase deficiency: A report of a family with two rare genotypes
Studies on the metabolic defect in Broad‐ß disease (hyperlipoproteinaemia type III)
Major karyotypic abnormality in a child born to a woman with untreated malignant melanoma
Bloom's syndrome. V. Surveillance for cancer in affected families
On the classification of the acrocephalosyndactyly syndromes
The Stickler syndrome (Hereditary arthro‐ophthalmopathy)
The foetus in Duchenne muscular dystrophy: Muscle growth in tissue culture
Apparently balanced de novo translocations in patients with abnormal phenotypes
Interchromosomal effects in man
Medical Geneticist
The origin of the rapidly adhering cells found in amniotic fluids from foetuses with neural tube defects
Genetic study of hyperlipoproteinaemia types IV and V
Ascertainment in the sequential sampling of pedigrees
Trisomy 9 syndrome
Trisomy 8 syndrome
7q deletion syndrome (7q32→7qter)
Phenotypic correlations in patients with ring chromosome 22
High incidence of spinal muscular atrophy type I (Werdnig ‐ Hoffmann disease) in the Karaite community in Israel
Diagnosis, Treatment and Prevention of Genetic Disease
MRC/DHSS Phenylketonuria Register
Erratum
Congenital malformation of the feet with low body height
Short stature, craniofacial dysmorphism and dento‐skeletal abnormalities in a large kindred
Cytogenetic study of 10 cases of infectious mononucleosis
Further delineation of the supernumerary chromosome in the Cat‐Eye Syndrome
Agenesis of the corpus callosum, infantile spasms, spastic quadriplegia, microcephaly and severe mental retardation in three siblings
α‐L‐Fucosidase of human skin fibroblasts and amniotic fluid cells in tissue culture
Y Y syndrome in French security settings
Answer to Drs. Noël & Bénézech
International Symposium of Genetic Diseases among Ashkenazi Jews Ashkenazi Jews
Translocation Y/5 resulting in Cri du Chat syndrome
Partial deletion of long arm of chromosome 11: del (11) (q23)
Cystinuria and mental deficiency
Cystic fibrosis: Studies with the oyster ciliary assay
Trisomy 4p: five new observations and overview
Chylothorax in two mongoloid infants mongoloid
Central nervous system arteriovenous malformations in multiple generations of a family with hereditary hemorrhagic telangiectasia
Sclerosteosis — An autosomal recessive disorder Afrikaner; Afrikaner kindreds; Afrikaner people
Universal permanent alopecia, psychomotor epilepsy, pyorrhea and mental subnormality
Selective hypoaldosteronism in Iranian Jews: An autosomal recessive trait Iranian Jews / Jewish families from Iran
A new estimate of the achondroplasia mutation rate
Partial 7q trisomy
Serum pancreatic isoamylases in the diagnosis of cystic fibrosis heterozygotes: A non‐valuable test
Translocation 9q/13q resulting in duplication (trisomy 9pter→9q22) and deficiency (monosomy 13pter→13q12)
Infantile polymyoclonus: Its occurrence in second cousins
Linkage studies on the Marinesco‐Sjøgren syndrome and hypergonadotropic hypogonadism
Trisomy 9p syndrome and XYY syndrome in siblings
Sex‐linked chondrodysplasia punctata?
Announcements
Two XX males in one family and additional observations bearing on the etiology of XX males
Morphology of the placenta in fetal I‐cell disease
Adrenoleukodystrophy (Siemerling‐Creutzfeldt disease): Heterozygote with two clonal fibroblast populations
Down syndrome due to partial trisomy 21q
46, X,X‐X terminal rearrangement /<b>45</b>, X mosaicism in a child with short stature
X‐linked skeletal dysplasia with mental retardation
Heterozygote detection in phenylketonuria
A case of double trisomy in a liveborn infant: 48, XXY, + 13
Congenital dislocation of the hip joint in Northern Sweden: Neonatal diagnosis and need for orthopaedic treatment
Menkes Kinky Hair Syndrome: Is it a treatable disorder?
Familial occurrence of histiocytosis Swedish geographical isolate
Ganglioside G<sub>M2</sub> N‐acetyl‐ß‐D‐gafactosaminidase and asialo G<sub>M2</sub> (G<sub>A2</sub>) N‐acetyl‐ß‐D‐galactosaminidase; studies in human skin fibroblasts
A case report of a presumptive +i(18p) associated with serum IgA deficiency
The distribution of ancestral secondary cases in Parkinson's disease
Genetic heterogeneity of hypoxanthine‐phosphoribosyl transferase in human fibroblasts of 3 families*
Partial trisomies of chromosome 21 in man. Two new observations due to translocations 19;21 and 4;21
Dermatoglyphics in Cri du Chat syndrome
The 9p‐ deletion syndrome A patient with a 45,XX,‐9,‐15, + t(9/15) constitution due to maternal 3:l meiotic disjunction
Heritability of “sinking” pre‐beta lipoprotein level: a twin study
Two cases of Down syndrome with unusual <i>de novo</i> translocation*
Non‐fluorescent Y chromosome in a male infant with Turner's symptoms and XO/XY mosaicism
Chromosome polymorphisms in karyotypes from amniotic fluid cell cultures
Variable X‐linked recessive hypopituitarism with evidence of gonadotropin deficiency in two pre‐pubertal males
Apparently balanced <i>de novo</i> translocations in patients with abnormal phenotypes: Report of 6 cases
Low serum dopamine‐β‐hydroxylase activity in the dysequilibrium syndrome
DNA cytophotometry in pre‐natal cytogenetic diagnosis
Prenatal diagnosis of Meckel syndrome: alpha‐feto protein and beta‐trace protein in amniotic fluid
The incidence of Duchenne muscular dystrophy in the South East of Scotland
Trisomy 9 mosaicism
Etiology of facial clefting
Longer Y chromosome in criminals: A reappraisal
Announcement
Mild and severe Hunter syndrome (MPS II) within the same sibships
Heredity of idiopathic haemochromatosis: A study of 106 families
A complex mosaic with D/E translocation tdic(15;18) (p12;p11) in an oligospermic male with apparently total infertility
No evidence for a correlation between behaviour and the size of the Y chromosome Norwegian males
Pachyonychia congenita and steatocystoma multiplex
Unusual association of Saethre‐Chotzen syndrome and congenital adrenal hyperplasia
Colton blood groups: indication of linkage with the Kidd (Jk) system as support for assignment to chromosome 7 Danish families
Prenatal diagnosis of dysplastic kidney disease*
Announcements
Penetrance and expressivity of the gene responsible for the Gardner syndrome
Probable dominant inheritance in Blount's disease
Normal rate of sister chromatid exchange in Down syndrome
Gonadal dysgenesis with 45,X/46,X,dic(Yp) mosaicism
Somatic segregation and Fanconi anemia
X‐linked aqueductal stenosis
Aglossia‐adactylia syndrome (special emphasis on the inheritance pattern)
Facio‐cardio‐renal syndrome: a newly delineated recessive disorder
Acid‐soluble glycoproteins in amniotic fluid and cystic fibrosis of the foetus
Interaction of isolated Lp(a) lipoprotein with calcium ions and glycosaminoglycans <i>in vitro</i>
An unusual case of prenatal diagnosis in twin pregnancy
Tricho‐dento‐osseous syndrome: A scanning electron microscopic analysis
Dermatoglyphic patterns in trisomy 8 syndrome*
Familial occurrence of chromosome variant 17ph+
Bloom's syndrome in two Dutch families Dutch
Male with 45, X karyotype
Insertional translocation into the X chromosome of a 46, XY male
A problem for genetic counselling — split hand deformity
A family with syndactyly type II (synpolydactyly)
C‐bands in seven cases of accessory small chromosomes
Meiotic consequences of an intrachromosomal insertion of chromosome No. 1: a family pedigree
Trisomy 18qter and trisomy mapping of chromosome 18
A chromosome No. 2 abnormality in a child with a few congenital defects*
Amniocentesis in prenatal diagnosis A controlled series of 78 cases
Partial Trisomy 17
Cystic fibrosis: Evidence for a genetic compound from a family study in cell culture
46,XY, t(3;22)(p2;q13) resuIting in partial trisomy for the short arm of chromosome 3
Announcement
Heterogeneity in maple syrup urine disease: Aspects of cofactor requirement and complementation in cultured fibroblasts
The acrocephalosyndactyly syndromes: A metacarpophalangeal pattern profile analysis
Dominant ichthyosis vulgaris
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