American Journal of Medical Genetics Part A - 2005

628 articles | Last updated: 2025-12-03 14:12:55
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6
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Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
Dwarfs in ancient Egypt
A novel <i>MSH2</i> germline mutation in homozygous state in two brothers with colorectal cancers diagnosed at the age of 11 and 12 years
<i>HRAS</i> mutations in Costello syndrome: Detection of constitutional activating mutations in codon 12 and 13 and loss of wild‐type allele in malignancy
Recent milestones in achondroplasia research
Complexity in genetic diseases: How patients inform the science by ignoring the dogma
A tribute to our teacher, Dr. Judith Hall: A child with the trait of the Earl of Shrewsbury
Illustration of genetic syndromes in the nursery
Glycine encephalopathy (nonketotic hyperglycinemia): Comments and speculations
Cystic adenomatoid malformation of the lung: Review of genetics, prenatal diagnosis, and in utero treatment
Clinical variation of Aarskog syndrome in a large family with 2189delA in the FGD1 gene
Echocardiographic findings in classical and hypermobile Ehlers–Danlos syndromes
Meckel on developmental pathology
Trisomy 16p: A longitudinal profile and photo essay
Fetal alcohol spectrum disorders in Finland: Clinical delineation of 77 older children and adolescents Finnish
Bosma arhinia microphthalmia syndrome
Festschrift reflection
Triplication of 8p22–8p23 in a patient with features similar to Kabuki syndrome
Introduction to Judith Hall Festschrift
Familial complex 3q;10q rearrangement unraveled by subtelomeric FISH analysis
Mitochondrial mutation in a child with distal arthrogryposis
Novel splicing mutation in the <i>NEMO</i> (<i>IKK‐gamma</i>) gene with severe immunodeficiency and heterogeneity of X‐chromosome inactivation
Breakpoint mapping in a case of mosaicism with partial monosomy 9p23 → pter and partial trisomy 1q41 → qter suggests neo‐telomere formation in stabilizing the deleted chromosome
Origin of the prevalent <i>SFTPB</i> indel g.1549C &gt; GAA (121ins2) mutation causing surfactant protein B (SP‐B) deficiency Western‐European chromosomes; ancestors from a region of Northwestern Europe populated by Frankish/S
A large interstitial deletion of 17p13.1p11.2 involving the Smith–Magenis chromosome region in a girl with multiple congenital anomalies
Investigation of confined placental mosaicism (CPM) at multiple sites in post‐delivery placentas derived through intracytoplasmic sperm injection (ICSI)
Adverse reproductive outcomes among pregnancies of aunts and (spouses of) uncles in Irish families with neural tube defects Irish
Findings from aCGH in patients with congenital diaphragmatic hernia (CDH): A possible locus for Fryns syndrome
A 46,X,inv(Y) young woman with gonadal dysgenesis and gonadoblastoma: Cytogenetics, molecular, and methylation studies
Overrepresentation of small supernumerary marker chromosomes (sSMC) from chromosome 6 origin in cases with multiple sSMC
Severe hypocalcemia due to a de novo mutation in the fifth transmembrane domain of the calcium‐sensing receptor
Patau syndrome with a long survival (146 months): A clinical report and review of literature
Molecular pathology of Shprintzen–Goldberg syndrome
Nevo syndrome with an <i>NSD1</i> deletion: A variant of Sotos syndrome? Japanese
Isolated 6q terminal deletions: An emerging new syndrome
<i>HRAS</i> mutation analysis in Costello syndrome: Genotype and phenotype correlation European (total 40) patients; Japanese, Italian, North American
A male baboon <i>(Papio hamadryas</i>) with a mosaic 43,XXY/42,XY karyotype
An intelligent person's guide to genetics. By Adrian Woolfson. London, Duckworth Overlook, 2004. 240 p.
Unusual cerebrotendinous xanthomatosis with fronto‐temporal dementia phenotype
A family with Duane anomaly and distal limb abnormalities: A further family with the arthrogryposis‐ophthalmoplegia syndrome
An Xq22.3 duplication detected by comparative genomic hybridization microarray (<i>Array‐CGH</i>) defines a new locus (<i>FGS5</i>) for FG syndrome
Array‐based comparative genomic hybridization analysis of recurrent chromosome 15q rearrangements
Co‐existing point mutations of mitochondrial DNA in a patient with a heart abnormality and Pearson syndrome‐like symptoms
Changes in hair morphology of mucopolysaccharidosis I patients treated with recombinant human α‐<scp>L</scp>‐iduronidase (laronidase, Aldurazyme)
Iridic and retinal coloboma associated with prenatal methimazole exposure
Fetal type IV glycogen storage disease: Clinical, enzymatic, and genetic data of a pure muscular form with variable and early antenatal manifestations in the same family
Distal arthrogryposis type 2A may be associated with juvenile glaucoma
Reply to letter to the editor by Lowry et al.: An epidemiological analysis of CHARGE syndrome: Preliminary results from a Canadian study [Issekutz et al., 2005]
Neurofibromatosis von Recklinghausen type I phenotype and early onset of cancers in siblings compound heterozygous for mutations in <i>MSH6</i>
Promotor genotype of the platelet‐derived growth factor receptor‐α gene shows population stratification but not association with spina bifida meningomyelocele European Caucasian descent
Majewski osteodysplastic primordial dwarfism type II (MOPD II) complicated by stroke: Clinical report and review of cerebral vascular anomalies
Systemic lupus erythematosus and other autoimmune disorders in children with Noonan syndrome
<i>CRELD1</i> and <i>GATA4</i> gene analysis in patients with nonsyndromic atrioventricular canal defects
Investigation of patients with mental retardation and dysmorphic features using comparative genomic hybridization and subtelomeric multiplex ligation dependent probe amplication
Epidemiology of hemimegalencephaly: A case series and review
Ebstein anomaly and duplication of the distal arm of chromosome 15: Report of two patients
Molecular cytogenetic characterization of a familial der(1)del(1)(p36.33)dup(1)(p36.33p36.22) with variable phenotype
Myhre syndrome in a female with previously undescribed symptoms: Further delineation of the phenotype
RE: An epidemiological analysis of CHARGE syndrome: Preliminary results from a Canadian study [Issekutz et al., 2005]
Perlman syndrome: Clinical report and nine‐year follow‐up
A paternally derived inverted duplication of distal 14q with a terminal 14q deletion
Report of a third family with Oliver syndrome
Severe bilateral panlobular emphysema and pulmonary arterial hypoplasia: Unusual manifestations of Menkes disease
Wilms tumor in an 11‐year‐old with hemihyperplasia
Mos 46,XX,r(18).ish r(18)(18ptel−,18qtel−)/46,XX.ish del(18)(18ptel−): An example for successive ring chromosome formation
Response to Kosaki et al. “Molecular pathology of Shprintzen–Goldberg syndrome”
Costello syndrome and hyperinsulinemic hypoglycemia
No detectable genomic aberrations by BAC array CGH in Kabuki make‐up syndrome patients
A patient with monosomy 1p36, atypical features and phenotypic similarities with Cantu syndrome
Submicroscopic deletions and duplications in individuals with intellectual disability detected by array‐CGH
Sequence variations in <i>AGTR2</i> are unlikely to be associated with X‐linked mental retardation
Cardiovascular malformations in Fryns syndrome: Is there a pathogenic role for neural crest cells?
A novel <i>DFNA9</i> mutation in the vWFA2 domain of <i>COCH</i> alters a conserved cysteine residue and intrachain disulfide bond formation resulting in progressive hearing loss and site‐specific ves
Turner syndrome: Four challenges across the lifespan
Case reports of oculofaciocardiodental syndrome with unusual dental findings (Am J Med Genet 136A: 275–277, 2005)
Analysis of the planar cell polarity gene <i>Vangl2</i> and its co‐expressed paralog <i>Vangl1</i> in neural tube defect patients (Am J Med Genet 136A: 90–92, 2005)
Adult phenotype in Costello syndrome (Am J Med Genet 136A: 128–135, 2005)
<i>Parkin</i> mutation analysis in clinic patients with early‐onset Parkinson's disease (Am J Med Genet 129A: 44–50, 2004)
Connexin 26 variants and auditory neuropathy/dys‐synchrony among children in schools for the deaf
Familial vertebral segmentation defects, Sprengel anomaly, and omovertebral bone with variable expressivity
Skeletal changes in epidermal nevus syndrome: Does focal bone disease harbor clues concerning pathogenesis?
Du Pan syndrome phenotype caused by heterozygous pathogenic mutations in <i>CDMP1</i> gene Polish family
A 72‐year‐old Danish puzzle resolved—comparative analysis of phenotypes in families with different‐sized <i>HOXD13</i> polyalanine expansions
Hypertrichosis in patients with <i>SURF1</i> mutations
A girl with partial trisomy 12q24.31 inherited from her father and a possible novel syndrome transmitted from her mother
Founder SVA retrotransposal insertion in Fukuyama‐type congenital muscular dystrophy and its origin in Japanese and Northeast Asian populations
Severe infantile Marfan syndrome versus neonatal Marfan syndrome
Detection of cryptic chromosome aberrations in a patient with a balanced t(1;9)(p34.2;p24) by array‐based comparative genomic hybridization
Molecular cytogenetic characterization of an insertional translocation, ins(6;7)(p25;q33q34): Deletion/duplication of 7q33‐34 and clinical correlations
Correct usage of “loss of imprinting”
Kallmann syndrome in a 47,XXX patient
A novel mutation in the <i>MSX2</i> gene in a family with foramina parietalia permagna (FPP)
Letter to the editor: Novel <i>GJA1</i> mutation in oculodentodigital dysplasia
Cleidocranial dysplasia: Molecular genetic analysis and phenotypic‐based description of a Middle European patient group Middle European
Sensorineural hearing loss in children and adults with Williams syndrome
Familial gigantism caused by an <i>NSD1</i> mutation
Medial temporal lobe dysgenesis in hypochondroplasia
A novel 17 bp deletion in the <i>PHOX2B</i> gene causes congenital central hypoventilation syndrome with total aganglionosis of the small and large intestine
Homozygosity for a gross partial gene deletion of the C‐terminal end of ATP7B in a Wilson patient with hepatic and no neurological manifestations
Histopathology and fibrillin‐1 distribution in severe early onset Marfan syndrome
Response to Fukuzawa et al. correspondence “Correct Usage of Loss Imprinting”
New approach for the refinement of the location of the X‐chromosome breakpoint in a previously described female patient with choroideremia carrying a X;4 translocation
Genetic heterogeneity of deafness phenotypes linked to DFNA4
Asplenia in ATR‐X syndrome: A second report
Further delineation of the phenotype maps for partial trisomy 16q24 and Jacobsen syndrome by a subtle familial translocation t(11;16)(q24.2;q24.1)
XK‐aprosencephaly and related entities
Clinical features of 78 adults with 22q11 deletion syndrome
Interstitial deletion of chromosome 12q: Genotype–phenotype correlation of two patients utilizing array comparative genomic hybridization
A new and a reclassified ICF patient without mutations in <i>DNMT3B</i> and its interacting proteins SUMO‐1 and UBC9 (Am J Med Genet 136A: 31–37, 2005)
Meiotic exchange event within the stalk region of an inverted chromosome 22 results in a recombinant chromosome with duplication of the distal long arm
A syndrome characterized by contractures and pterygia of upper body associated with umbilical hernia, short stature, and distinctive face in an Arabic family Moslem Arabic family; Arabic family
XX sex reversal, palmoplantar keratoderma, and predisposition to squamous cell carcinoma: Genetic analysis in one family Sicilian
Novel phenotype of craniosynostosis and ocular anterior chamber dysgenesis with a fibroblast growth factor receptor 2 mutation
A new locus for nonsyndromic deafness <i>DFNB51</i> maps to chromosome 11p13‐p12
Precision and error of three‐dimensional phenotypic measures acquired from 3dMD photogrammetric images
Partial trisomy 4q and preaxial limb defects
Ehlers–Danlos syndrome type VIB with characteristic facies, decreased curvatures of the spinal column, and joint contractures in two unrelated girls
Transitory hypogammaglobulinemia of infancy in FG syndrome
Detection of low level sex chromosome mosaicism in Ullrich–Turner syndrome patients
On being a medical geneticist
Intrachromosomal insertion mimicking a pericentric inversion: Molecular cytogenetic characterization of a three break rearrangement of chromosome 20
Prenatal magnetic resonance imaging in Gomez‐Lopez‐Hernandez syndrome and review of the literature
Genome‐wide SNP arrays as a diagnostic tool: Clinical description, genetic mapping, and molecular characterization of Salla disease in an Old Order Mennonite population Old Order Mennonite; Mennonite population; reference to Finland (common cause in Finland)
Facial and physical features of Aicardi syndrome: Infants to teenagers
A case of C3 deficiency with a novel homozygous two‐base deletion in the <i>C3</i> gene
Pharmacogenetics of psychotropic drugs. By Bernard Lerer, editor. Cambridge University Press, Cambridge, New York, Port Melbourne, Madrid, Capetown, 2002
Optic atrophy and sensorineural hearing loss in a family caused by an R445H <i>OPA1</i> mutation
Delineation of the clinical phenotype associated with <i>OPHN1</i> mutations based on the clinical and neuropsychological evaluation of three families
Clinical and molecular studies on two further families with Simpson‐Golabi‐Behmel syndrome
Chromosome 11‐q24 region in Tourette syndrome: Association and linkage disequilibrium study in the French Canadian population French Canadian population
Ring chromosome 9 [r(9)(p24q34)]: A report of two cases
A male with two idic(Y)(q12) chromosomes: A distinct phenotype resembling the XXXY/XXXXY syndrome
Complete trisomy 1q with mosaic Y;1 translocation: A recurrent aneuploidy presenting diagnostic dilemmas
Segmental and full paternal isodisomy for chromosome 14 in three patients: Narrowing the critical region and implication for the clinical features Japanese
FISH‐mapping of telomeric 14q32 deletions: Search for the cause of seizures
Klippel‐Feil anomaly in a boy and Dubowitz syndrome with vertebral fusion in his brother: A new variant of Dubowitz syndrome?
Vessels' morphology in <i>SMAD4</i> and <i>BMPR1A</i>‐related juvenile polyposis
Adults with VATER association: Long‐term prognosis
Triploid mosaicism in a 45,X/69,XXY infant
Trisomy 17p10‐p12 due to mosaic supernumerary marker chromosome: Delineation of molecular breakpoints and clinical phenotype, and comparison to other proximal 17p segmental duplications
X‐linked adrenoleukodystrophy with partial deletion of <i>ALD</i> due to fusion with the neighbor gene, <i>PLXNB3</i>
Autosomal recessive Oliver–McFarlane syndrome: Retinitis pigmentosa, short stature (GH deficiency), trichomegaly, and hair anomalies or CPD syndrome (chorioretinopathy‐pituitary dysfunction)
Molecular study of <i>WISP3</i> in nine families originating from the Middle‐East and presenting with progressive pseudorheumatoid dysplasia: Identification of two novel mutations, and description of Middle‐East; Lebanon; Syria; Palestinian Bedouin descent
Cosegregation of the G7444A mutation in the mitochondrial COI/tRNA<sup>Ser(UCN)</sup> genes with the 12S rRNA A1555G mutation in a Chinese family with aminoglycoside‐induced and nonsyndromic hearing l Chinese
Stickler syndrome: Clinical characteristics and diagnostic criteria
The Cyclopes in Odysseus' <i>Apologos</i>
<i>SOX2</i> mutation causes anophthalmia, hearing loss, and brain anomalies
Screening for new <i>MTHFR</i> polymorphisms and NTD risk Irish; ethnically homogeneous Irish; African-American; American-Caucasian; Irish population
Can parents adjust to the idea that their child is at risk for a sudden death?: Psychological impact of risk for long QT syndrome
Cryptic duplication and deletion of 9q34.3 → qter in a family with a t(9;22)(q34.3;p11.2)
No evidence for triallelic inheritance ofMKKS/BBS loci in Amish Mckusick-Kaufman syndrome
Acro‐dermato‐ungual‐lacrimal‐tooth (ADULT) syndrome: Report of a child with phenotypic overlap with ulnar‐mammary syndrome and a new mutation in <i>TP63</i>
A family with X‐linked anophthalmia: Exclusion of <i>SOX3</i> as a candidate gene
Auriculo‐condylar syndrome is associated with highly variable ear and mandibular defects in multiple kindreds
DiGeorge anomaly in a patient with isochromosome 18p born to a diabetic mother
Detection of an unexpected subtelomeric 15q26.2 → qter deletion in a little girl: Clinical and cytogenetic studies
Trisomy 10 mosaicism and maternal uniparental disomy 10 in a liveborn infant with severe congenital malformations
Absent pulmonary valve with intact ventricular septum and patent ductus arteriosus: A specific cardiac phenotype associated with deletion 18q syndrome
Mosaicism of proximal 15q duplication/deletion resulting in Prader–Willi syndrome with normal methylation
Non-skewed X-inactivation may cause mental retardation in a female carrier of X-linked α-thalassemia/mental retardation syndrome (ATR-X): X-inactivation study of nine female carriers of ATR-X
Bifurcation of the femur with tibial agenesis and additional anomalies
Precocious sister chromatid separation (PSCS) in Cornelia de Lange syndrome
Risks of human conotruncal heart defects associated with 32 single nucleotide polymorphisms of selected cardiovascular disease-related genes
Germline mosaicism of a novel <i>UBE3A</i> mutation in Angelman syndrome
Missense mutations in <i>N</i>‐acetylglucosamine‐1‐phosphotransferase α/β subunit gene in a patient with mucolipidosis III and a mild clinical phenotype
Michels syndrome, Carnevale syndrome, OSA syndrome, and Malpuech syndrome: Variable expression of a single disorder (3MC syndrome)?
Acrofacial dysostosis (AFD) with preaxial limb hypoplasia (Nager AFD) and club foot diagnosed in a fetus from 1812 in the anatomical collections at the University of Halle, Germany
Demonstration of two novelLAMB2 mutations in the original Pierson syndrome family reported 42 years ago
Recognition of Smith-Lemli-Opitz syndrome (RSH) in the fetus: Utility of ultrasonography and biochemical analysis in pregnancies with low maternal serum estriol
Variation in IRF6 contributes to nonsyndromic cleft lip and palate
Chromosome 1q42 deletion and agenesis of the corpus callosum
A new case of 2q duplication supports either a locus for orofacial clefting between markers D2S1897 and D2S2023 or a locus for cleft palate only on chromosome 2q13‐q21
A novel in-frame deletion in ARX is associated with lissencephaly with absent corpus callosum and hypoplastic genitalia
Identification and study of Utah pseudo‐isolate populations—prospects for gene identification dating back to its European founders
A novel missense mutation in a C2 domain ofOTOF results in autosomal recessive auditory neuropathy
Duplication of Xq26.2-q27.1, includingSOX3, in a mother and daughter with short stature and dyslalia
A new syndrome of congenital generalized osteosclerosis and bilateral polymicrogyria
X‐chromosome inactivation and telomere size in newborns resulting from intracytoplasmic sperm injection
Juvenile onset Huntington disease resulting from a very large maternal expansion
The natural history of severe anemia in cartilage-hair hypoplasia
Probable identity-by-descent for a mutation in the Dyggve-Melchior-Clausen/Smith-McCort dysplasia (Dymeclin) gene among patients from Guam, Chile, Argentina, and Spain
Infants with Bochdalek diaphragmatic hernia: Sibling precurrence and monozygotic twin discordance in a hospital‐based malformation surveillance program
Novel amino acid substitution in the Y‐position of collagen type II causes spondyloepimetaphyseal dysplasia congenita Polish population
An MCA/MR syndrome with hypocholesterolemia due to familial hypobetalipoproteinemia: Report of a second patient with Nguyen syndrome
Schmid type of metaphyseal chondrodysplasia and <i>COL10A1</i> mutations—findings in 10 patients
A patient with mutations in DNA Ligase IV: Clinical features and overlap with Nijmegen breakage syndrome
Growth deficiency, facial anomalies, and brachydactyly (Frías syndrome): A second family
Recurrence of Mowat–Wilson syndrome in siblings with the same proven mutation
Meier‐Gorlin (ear‐patella‐short stature) syndrome: Growth hormone deficiency and previously unrecognized findings
Book review
Familial visceral neuropathy: A defined entity?
High prevalence of the <i>W24X</i> mutation in the gene encoding connexin‐26 (<i>GJB2</i>) in Spanish Romani (gypsies) with autosomal recessive non‐syndromic hearing loss Spanish Romani (gypsies); gypsies; ethnic groups; Spanish regions (Andalusia and Catalonia)
Clefting, amniotic bands, and polydactyly: A distinct phenotype that supports an intrinsic mechanism for amniotic band sequence
Analysis ofRPS19 in patients with cartilage-hair hypoplasia and severe anemia: Preliminary results
Is there an increased birth defect risk to children born to offspring of first cousin parents?
Trisomy 20q13 → 20qter in a girl with multiple congenital malformations and a recombinant chromosome 20 inherited from a paternal inversion (20)(p13q13.1): Clinical report and review of the trisomy 20
Book review
Brachydactylic multiple delta phalanges plus syndrome
The outcome of diagnostic studies on the etiology of mental retardation: Considerations on the classification of the causes
Pigmentary mosaicism following the lines of Blaschko in a girl with a double aneuploidy mosaicism: (47,XX,+7/45,X)
Book review
Gracile bones, periostal appositions, hypomineralization of the cranial vault, and mental retardation in brothers: Milder variant of osteocraniostenosis or new syndrome?
Marshall–Smith syndrome: Natural history and evidence of an osteochondrodysplasia with connective tissue abnormalities
Fetus with interstitial del(5)(p13.1p14.2) diagnosed postnatally with Cornelia de Lange syndrome
Mutation analysis of the <i>HDAC 1</i>, <i>2</i>, <i>8</i> and <i>CDKL5</i> genes in Rett syndrome patients without mutations in <i>MECP2</i>
Ring chromosome 4 in a patient with early onset type 2 diabetes, deafness, and developmental delay
Geneticists' views on science policy formation and public outreach
Patient with a non‐mosaic isodicentric Yp and mild developmental delay
A patient with mosaic partial trisomy 18 resulting from dicentric chromosome breakage
Chromosome rearrangements in Cornelia de Lange syndrome (CdLS): Report of a der(3)t(3;12)(p25.3;p13.3) in two half sibs with features of CdLS and review of reported CdLS cases with chromosome rearrang
Arthrogryposis multiplex with deafness, inguinal hernias, and early death: A family report of a probably autosomal recessive trait
Schizencephaly: Heterogeneous etiologies in a population of 4 million California births
Microphthalmia with linear skin defects (MLS) syndrome: Clinical, cytogenetic, and molecular characterization of 11 cases
Characterization of a familial balanced rec(13) in a child with mild MR and his half‐sibling with two structurally rearranged chromosomes 13
Congenital palmar polyonychia with postaxial limb defects may be the same as the ulnar–mammary syndrome
Reply to letter to the editor by Crow: “Probable new syndrome in a Mexican family with congenital palmar polyonychia and postaxial limb defects”
Male‐to‐male transmission in Laurin–Sandrow syndrome and exclusion of <i>RARB</i> and <i>RARG</i>
Familial recurrence of heart defects in subjects with congenitally corrected transposition of the great arteries
Analysis of <i>NF1</i> transcriptional regulatory elements
Book Review
Revertant mosaicism and retrotransposons: Another explanation of “natural gene therapy”
The <i>GJB2</i> mutation R75Q can cause nonsyndromic hearing loss DFNA3 or hereditary palmoplantar keratoderma with deafness
Microcephaly is not mandatory for the diagnosis of mosaic variegated aneuploidy syndrome
Book review
Molecular and phenotypic characterization of ring chromosome 22
Cost comparison of genetic and clinical screening in families with hereditary hemorrhagic telangiectasia
A mitochondrial tRNA aspartate mutation causing isolated mitochondrial myopathy
Craniosynostosis and ectopia lentis in a propositus whose parents are cousins (Am J Med Genet (Early View))
Inappropriate tall stature and renal ectopy in a male patient with X‐linked congenital adrenal hypoplasia due to a novel missense mutation in the <i>DAX‐1</i> gene
Increased occurrence of cleft lip in glycogen storage disease type II (GSDII): Exclusion of a contiguous gene syndrome in two patients by presence of intragenic mutations (<i>Am J Med Genet</i> 85: 5–
Factors related to the development of communication in CHARGE syndrome (Am J Med Genet 133A:282–290)
Interstitial deletion in 3q in a patient with blepharophimosis‐ptosis‐epicanthus inversus syndrome (BPES) and microcephaly, mild mental retardation and growth delay: Clinical report and review of the
Unilateral radio‐ulnar synostosis associated with hypotonia, developmental delay, and facial dysmorphism
Should chromosome breakage studies be performed in patients with VACTERL association? European genotype–phenotype correlation study for FA
Cryptic unbalanced translocation t(17;18)(p13.2;q22.3) identified by subtelomeric FISH and defined by array‐based comparative genomic hybridization in a patient with mental retardation and dysmorphic
Cystathionine beta-synthase c.844ins68 gene variant and non-syndromic cleft lip and palate
Inheritance pattern of Beckwith–Wiedemann syndrome is heterogeneous in 291 families with an affected proband
Cardiofaciocutaneous syndrome (CFC) with congenital peripheral neuropathy and nonorganic malnutrition: An autopsy study
Epidemiologic characteristics of anophthalmia and bilateral microphthalmia among 2.5 million births in California, 1989–1997
Growth hormone benefits children with 18q deletions
Microdeletion in the <i>SHOX</i> 3′ region associated with skeletal phenotypes of Langer mesomelic dysplasia in a 45,X/46,X,r(X) infant and Leri–Weill dyschondrosteosis in her 46,XX mother: Implicatio Japanese
Plantar lipomatosis, unusual facies, and developmental delay: Confirmation of Pierpont syndrome
Unusual mixed gonadal dysgenesis associated with Müllerian duct persistence, polygonadia, and a 45,X/46,X,idic(Y)(p) karyotype
Pallister-Hall syndrome: Unreported skeletal features of a<i>GLI3</i>mutation
Molecular cytogenetic characterization of a de novo supernumerary ring chromosome 7 resulting in partial trisomy, tetrasomy, and hexasomy in a child with dysmorphic signs, congenital heart defect, and
Initial cancer genetic counseling consultation: Change in counselees' cognitions and anxiety, and association with addressing their needs and preferences
Multiple aneuploidy recurrence
Sigmoid diverticulitis in patients with Williams–Beuren syndrome: Relatively high prevalence and high complication rate in young adults with the syndrome
Long term follow‐up of developmental delay in a child with prenatally‐diagnosed trisomy 20 mosaicism
Clinical and molecular characterization of the first adult congenital disorder of glycosylation (CDG) type Ic patient
Exclusion of <i>WNT4</i> as a major gene in Rokitansky‐Küster‐Hauser anomaly
A report of three patients with an interstitial deletion of chromosome 15q24
Structural central nervous system (CNS) anomalies in Kabuki syndrome
Fine mapping of autosomal dominant nonsyndromic hearing impairment <i>DFNA21</i> to chromosome 6p24.1‐22.3
22q11.2 duplication syndrome: Two new familial cases with some overlapping features with DiGeorge/velocardiofacial syndromes
Re: Distal arthrogryposis in two sisters born to different fathers [Hwu et al. 2004. Am J Med Genet 125A:100-101.]
Tetralogy of fallot in a patient with developmental coxa vara/spondylometaphyseal dysplasia-corner fracture type (DCV/SMD-CF) expanding the variability
Re: Polymicrogyria versus pachygyria in 22q11 microdeletion
Craniosynostosis: Another feature of the 22q11.2 deletion syndrome
Trisomy of the short arm of chromosome 5 due to a de novo inversion and duplication (5)(p15.3 p13.3)
Speech-language characteristics of children with Sotos syndrome
X-linked dominant chondrodysplasia with platyspondyly, distinctive brachydactyly, hydrocephaly, and microphthalmia
550delA mutation in the calpain 3 (CAPN3) gene: DMD/BMD, SMA, or LGMD2A—clinically misdiagnosed cases
Editorial: Perspectives on craniosynostosis
Sex-specific chromosome instability in early human development
Diaphanospondylodysostosis (DSD): Confirmation of a recessive disorder with abnormal vertebral ossification and nephroblastomatosis
Arachnoidal cyst, orofacial dysplasia, poor motor control, and severe language delay
Another case of Varadi-Papp Syndrome with a molar tooth sign
Genetics and women in science
Book review
Book review
Behavioral aspects of Angelman syndrome: A case control study (Am J Med Genet 132A: 8–12)
AGG interspersion patterns in the CGG repeat of the <i>FMR1</i> gene and linked DXS548/FRAXAC1 haplotypes in Brazilian populations
Inverted duplication of 15q with terminal deletion in a multiple malformed newborn with intrauterine growth failure and lethal phenotype
Pachygyria and polymicrogyria in 22q11 deletion syndrome
Gonadal mosaicism in severe Pallister–Hall syndrome (Am J Med Genet 124A: 296–302 (2004)
Hypothelia, syndactyly, and ear malformation—A variant of the scalp–ear–nipple syndrome?: Case report and review of the literature (<i>Am J Med Genet</i> 134A: 220–222 (2005))
<i>AJMG</i> reviewers 2004
A retrospective family study of childhood medulloblastoma (Am J Med Genet 134A(4): 399–403)
Midline raphé, sternal cleft, and other midline abnormalities: A new dominant syndrome? (Am J Med Genet 135A:9–12)
Holoprosencephaly with microphthalmia, hypoplastic ears, vertebral segmentation defects, and congenital heart defects
A newly recognized syndrome of cutis aplasia, lipomatous footpads, microcephaly, hypotelorism, and, variably, single maxillary central incisor, and holoprosencephaly
van den Ende-Gupta syndrome of blepharophimosis, arachnodactyly, and congenital contractures
Trichomegaly in two sisters with synophrys in the older sibling
Case reports of oculofaciocardiodental syndrome with unusual dental findings
Trisomy 3q25.1-qter and monosomy 8p23.1-pter in a patient: Cytogenetic and molecular analysis with delineation of the phenotype
Three cases with de novo 6q imbalance and variable prenatal phenotype
Uniparental disomy (UPD) other than 15: Phenotypes and bibliography updated
Spondylo-mega-epiphyseal dysplasia with prominent upper limb mesomelia, punctate calcifications, and deafness
G59S mutation in theGJB2 (connexin 26) gene in a patient with Bart-Pumphrey syndrome
A new and a reclassified ICF patient without mutations in <i>DNMT3B</i> and its interacting proteins SUMO‐1 and UBC9
Total truncation of the molybdopterin/dimerization domains of SUOX protein in an Arab family with isolated sulfite oxidase deficiency Arab
Analysis of the planar cell polarity gene <i>Vangl2</i> and its co‐expressed paralogue <i>Vangl1</i> in neural tube defect patients
Clinical and molecular characterization of two adults with autosomal recessive Robinow syndrome
DHCR7 mutations in Brazilian Smith-Lemli-Opitz syndrome patients
The new Wolf–Hirschhorn syndrome critical region (WHSCR‐2): A description of a second case
Characterization of six marker chromosomes by comparative genomic hybridization
Is Dandy-Walker malformation associated with “distal 13q deletion syndrome”? Findings in a fetus supporting previous observations
Neurofibromatosis-Noonan syndrome: Molecular evidence of the concurrence of both disorders in a patient
New case of contiguous gene syndrome at chromosome 8p11.2p12
Mutation spectrum in Jewish cystic fibrosis patients in Israel: Implication to carrier screening Jewish
Variations of theCFTR gene in the Hanoi-Vietnamese
CDG‐IL: An infant with a novel mutation in the<i>ALG9</i>gene and additional phenotypic features
Dentatorubral‐pallidoluysian atrophy in three generations, with clinical courses from nearly asymptomatic elderly to severe juvenile, in an Australian family of Macedonian descent Macedonian descent / Macedonian origin
Seven letters to the editor reporting new findings in patients with holoprosencephaly
SHH Ile111Asp in alobar holoprosencephaly in a proposita, whose mother had only a solitary median maxillary incisor
Atypical interhemispheric fusion with a cebocephalic-like functional single nostril nose and a novelSHH mutation
Cerebro-oculo-nasal syndrome, a disorder with some manifestations suggestive of the holoprosencephalic spectrum: New case and imaging review of previous cases
CNS findings in three cases of septo-optic dysplasia, including one with semilobar holoprosencephaly
Central nervous system malformations in oral‐facial‐digital syndrome, type 1
Newly recognized overgrowth syndrome with macrosomia, macrocrania, hyperostosis of the cranial vault, mental deficiency, seizures, poor motor control, and orofacial dyspraxia
Association of Adams-Oliver syndrome with pulmonary arterio-venous malformation in the same family: A further support to the vascular hypothesis
Mutation in the von Willebrand factor-A domain is not a prerequisite for theMATN3 mutation in multiple epiphyseal dysplasia
Single median maxillary central incisor, hypophyseal tumor, andSHH mutation
Prenatal diagnosis of FRA10A: A case report and literature review
Prenatal death in Smith-Lemli-Opitz/RSH syndrome
Human Genome Epidemiology: A scientific foundation for using genetic information to improve health and prevent disease
Development of an audit tool for genetic services
Minor malformations characteristic of the retinoic acid embryopathy and other birth outcomes in children of women exposed to topical tretinoin during early pregnancy
Intrachromosomal triplication for the distal part of chromosome 15q
The adult phenotype in Costello syndrome
Reported multivitamin consumption and the occurrence of multiple congenital anomalies
Malformations of the axial skeleton in the museum Vrolik: II: Craniosynostoses and suture-related conditions
A new observation of acro‐cardio‐facial syndrome substantiates interindividual clinical variability
Folate‐related genes and omphalocele
Hyperthrophic cardiomyopathy and the <i>PTPN11</i> gene
Distinct phenotype associated with a cryptic subtelomeric deletion of 19p13.3‐pter
Cause of sudden, unexpected death of Prader–Willi syndrome patients with or without growth hormone treatment
Molecular characterization of del(8)(p23.1p23.1) in a case of congenital diaphragmatic hernia
Identification of an alternative 5′‐untranslated exon and new polymorphisms of angiotensin‐converting enzyme 2 gene: Lack of association with SARS in the Vietnamese population
Application of a comprehensive protocol for the identification of Gaucher disease in Brazil
Detection of genomic rearrangements by DHPLC: A prospective study of 90 patients with inherited peripheral neuropathies associated with <i>17p11.2</i> rearrangements
A novel filamin A D203Y mutation in a female patient with otopalatodigital type 1 syndrome and extremely skewed X chromosome inactivation
Cerebellar vermis aplasia: Patient report and exclusion of the candidate genes <i>EN2</i> and <i>ZIC1</i>
Generalized arterial calcification of infancy: Different clinical courses in two affected siblings
Risks for severe mental retardation occurring in isolation and with other developmental disabilities Blacks; Asians
Update: PGD and Holt‐Oram syndrome
Hair whorls and handedness: Informative phenotypic markers in nonsyndromic cleft lip with or without cleft palate (NS CL/P) cases and their unaffected relatives
Mosaicism for an <i>FMR1</i> gene deletion in a fragile X female
Prenatal diagnosis of chromosome 4 mosaicism: Prognostic role of cytogenetic, molecular, and ultrasound/MRI characterization
Maladaptive behaviors and risk factors among the genetic subtypes of Prader–Willi syndrome
Terminal deletion of 6p results in a recognizable phenotype
<i>PTPN11</i> mutations play a minor role in isolated congenital heart disease
Investigation of <i>UBE3A</i> and <i>MECP2</i> in Angelman syndrome (AS) and patients with features of AS (Am J Med Genet 125A: 167–172)
Xq chromosome duplication in males: Clinical, cytogenetic and array CGH characterization of a new case and review
Reply to “Statin Drugs and Congenital Anomalies” by Gibb and Scialli
Complex chromosome rearrangement and recombinant balanced translocation in a mother and a daughter with the same phenotypic abnormalities
Polymorphisms in DNA repair genes as risk factors for spina bifida and orofacial clefts
Reply to Ruiter et al.: A possible example of acrofacial dysostosis type Kennedy–Teebi
Prenatal mucolipidosis type II (I‐cell disease) can present as Pacman dysplasia
Distinguishing Pacman dysplasia from mucolipidosis II: Comment on Saul et al. [2005]
Genetic regulation of osteoarthritis: A QTL regulating cranial and caudal acetabular osteophyte formation in the hip joint of the dog (<i>Canis familiaris</i>)
Mayer–Rokitansky–Küster–Hauser anomaly and its associated malformations
The external ear: More attention to detail may aid syndrome diagnosis and contribute answers to embryological questions
Sensorineural deafness, abnormal genitalia, synostosis of metacarpals and metatarsals 4 and 5, and mental retardation: Description of a second patient and exclusion of <i>HOXD13</i>
Tumor risk in Beckwith–Wiedemann syndrome: A review and meta‐analysis
Autosomal dominant inheritance of spondyloenchondrodysplasia
OEIS complex with del(3)(q12.2q13.2)
<i>EMX2</i>‐independent familial schizencephaly: Clinical and genetic analyses Turkish
Eponymous Jacobsen syndrome: Mapping the breakpoints of the original family suggests an association between the distal 1.1 Mb of chromosome 21 and osteoporosis in Down syndrome
Are the betaine‐homocysteine methyltransferase (<i>BHMT</i> and <i>BHMT2</i>) genes risk factors for spina bifida and orofacial clefts?
Polymicrogyria versus pachygyria in 22q11 microdeletion
Novel mutation in <i>DGUOK</i> in hepatocerebral mitochondrial DNA depletion syndrome associated with cystathioninuria old colony Mennonite families
No evidence of paternal transmission of fragile X syndrome
Response to letter: “No evidence of paternal transmission of fragile X syndrome” by Doris and Peter Steinbach
Essential versus complex autism: Definition of fundamental prognostic subtypes
Cerebral, cerebellar, and colobomatous anomalies in three related males: Sex‐linked inheritance in a newly recognized syndrome with features overlapping with Joubert syndrome
Immune abnormalities are a frequent manifestation of Kabuki syndrome
Omphalocele, advanced maternal age, and fetal morbidity outcomes
Del(18)(q12.2q21.1) caused by a paternal sister chromatid rearrangement in a developmentally delayed girl
Cockayne syndrome: The developing phenotype
Tel Hashomer camptodactyly syndrome: 12‐year follow‐up of a Hungarian patient and review Hungarian
Reply to correspondence to the editor by de Wit et al.—“Re: Polymicrogyria versus pachygyria in 22q11 deletion”
Autosomal recessive omodysplasia: Early prenatal diagnosis and a possible clue to the gene location
Maternal uniparental disomy 14 in a 15‐year‐old boy with normal karyotype and no evidence of precocious puberty
Shprintzen–Goldberg syndrome: Fourteen new patients and a clinical analysis mainly German individuals
Association of migraine‐like headaches with Schimke immuno‐osseous dysplasia
A new <i>DAX1</i> gene mutation associated with congenital adrenal hypoplasia and hypogonadotropic hypogonadism
Unilateral acheiria and fatal primary pulmonary hypertension in a girl with incontinentia pigmenti
Array comparative genomic hybridization analysis of a familial duplication of chromosome 13q: A recognizable syndrome
Living with a hereditary disease: Persons with muscular dystrophy and their next of kin
Higher frequency of uncommon 1.5–2 Mb deletions found in familial cases of 22q11.2 deletion syndrome
FXTAS, SCA10, and SCA17 in American patients with movement disorders
Unstable Robertsonian translocations der(13;15)(q10;q10): Heritable chromosome fission without phenotypic effect in two kindreds
Relationship between polymorphisms in genes involved in homocysteine metabolism and maternal risk for Down syndrome in Brazil
Another case of interstitial del(12) involving the proposed cardio‐facio‐cutaneous candidate region
Long‐term follow‐up in a patient with metatropic dysplasia
Floating‐Harbor syndrome complicated by tethered cord: A new association and potential contribution from growth hormone therapy
Gonadoblastoma in Turner syndrome and Y‐chromosome‐derived material
Syndromes and Epistemology I: Autistic spectrum disorders
Identification of high frequency of Y chromosome deletions in patients with sex chromosome mosaicism and correlation with the clinical phenotype and Y‐chromosome instability
Schimke‐immuno‐osseous dysplasia: New mutation with weak genotype–phenotype correlation in siblings
Studies of reduced folate carrier 1 (<i>RFC1</i>) A80G and 5,10‐methylenetetrahydrofolate reductase (<i>MTHFR</i>) C677T polymorphisms with neural tube and orofacial cleft defects
Sequence of abnormal dendritic spine development in primary somatosensory cortex of a mouse model of the fragile X mental retardation syndrome
Oncogenomics: Molecular approaches to cancer edited by Charles and David Duggan. Wiley‐Liss, Hoboken, NJ, 2004.
Hypoparathyroidism–retardation–dysmorphism (HRD) syndrome in triplets
Novel autosomal recessive progressive hyperpigmentation syndrome Iraqui origin
Other tumors in Sotos syndrome
Reduction of birth prevalence rates of neural tube defects after folic acid fortification in Chile
Sex and congenital malformations: An international perspective
Adams–Oliver syndrome and hepatoportal sclerosis: Occasional association or common mechanism?
Cystic fibrosis carriers have higher neonatal immunoreactive trypsinogen values than non‐carriers
<i>GJB2</i> (connexin 26) mutations are not a major cause of hearing loss in the Indonesian population Indonesian population; other populations
Monozygotic twins concordant for blood karyotype, but phenotypically discordant: A case of “mosaic chimerism”
Congenital anomaly of cervical vertebrae is a major complication of Rubinstein–Taybi syndrome
Autopsy findings of a 37‐year‐old man with a complex mosaic karyotype involving del(18p), monosomy 13, and trisomy 20
Spectrum of malformations of the hindbrain (cerebellum, pons, and medulla) in a cohort of children with high rate of parental consanguinity
Use of the glycophorin A somatic mutation assay for rapid, unambiguous identification of Fanconi anemia homozygotes regardless of <i>GPA</i> genotype
Clinical report of a pure subtelomeric 1qter deletion in a boy with mental retardation and multiple anomalies adds further evidence for a specific phenotype
Facial characteristics are not distinctive features for the acrofacial dysostosis syndrome type Kennedy–Teebi
Book review
Theodore Francis Thurmon III, M.D. (October 20, 1937–January 3, 2005)
Molecular characterization of a 14q deletion in a boy with features of Holt–Oram syndrome
Subtelomere deletions and translocations are frequently familial
A novel <i>MGP</i> mutation in a consanguineous family: Review of the clinical and molecular characteristics of Keutel syndrome Arab
Physician exposure to and attitudes toward advertisements for genetic tests for inherited cancer susceptibility
An unusual reciprocal translocation detected by subtelomeric FISH: Interstitial and not terminal
Phenotypes with <i>GATA4</i> or <i>NKX2.5</i> mutations in familial atrial septal defect
Statin drugs and congenital anomalies
Familial variable expression of dilated cardiomyopathy in Alström syndrome: A report of four sibs
Craniofacial defects of blastogenesis: Duplication of pituitary with cleft palate and orophgaryngeal tumors
Split hand malformation, hypospadias, microphthalmia, distinctive face and short stature in two brothers suggest a new syndrome
Midline raphé, sternal cleft, and other midline abnormalities: A new dominant syndrome?
Attention‐deficit/hyperactivity disorder (ADHD) and variable clinical expression of Aarskog–Scott syndrome due to a novel <i>FGD1</i> gene mutation (R408Q)
Familial recurrence rates and genetic models of multiple sclerosis
<i>SOX2</i> anophthalmia syndrome
Autosomal dominant microtia and ocular coloboma: New syndrome or an extension of the oculo‐auriculo‐vertebral spectrum?
Mental retardation in a boy with anterior cervical hypertrichosis
Inappropriate tall stature and renal ectopy in a male patient with X‐linked congenital adrenal hypoplasia due to a novel missense mutation in the <i>DAX‐1</i> gene
Progressive external ophthalmoplegia: A new family with tremor and peripheral neuropathy
Fryns syndrome with osteochondrodysplasia
Functional disomy of Xp: Prenatal findings and postnatal outcome
Tenascin‐X deficiency in autosomal recessive Ehlers–Danlos syndrome
A girl with inverted triplication of chromosome 3q25.3 → q29 and multiple congenital anomalies consistent with 3q duplication syndrome
Malpuech syndrome: Three patients and a review
Somatic and gonadal mosaicism in Hutchinson–Gilford progeria
Acrofacial dysostosis type Rodríguez
Barth syndrome: <i>TAZ</i> gene mutations, mRNAs, and evolution
Cardiovascular genetics clinics
Renpenning syndrome comes into focus
Significance of bifid epiglottis
Holoprosencephaly and limb reduction defects: A consideration of Steinfeld syndrome and related conditions
Response to the letter to “MTHTR 677C‐T polymorphism is not excluded as maternal risk for Down syndrome among Turkish women”
Prevalence of nonsyndromic oral clefts in Texas: 1995–1999
Vascular abnormalities in the fingers of patients affected with hereditary hemorrhagic telangiectasia (HHT) as assessed by color doppler sonography
Early development of occipital horns in a classical Menkes patient (Am J Med Genet 130A: 211–213)
Congenital diaphragmatic hernia in WAGR syndrome
A provisionally unique syndrome of macrosomia, bone overgrowth, macrocephaly, and tall stature
Skewed X‐inactivation in carriers establishes linkage in an X‐linked deafness‐mental retardation syndrome (Am J Med Genet 131A: 209–212)
Three patients with hallucal polydactyly and WAGR syndrome, including discordant expression of Wilms tumor in MZ twins
Autosomal recessive mesoaxial synostotic syndactyly with phalangeal reduction maps to chromosome 17p13.3 Pakistani; Turkish; distinct ethnic backgrounds
RE: ?Risk calculations: Still essential in the molecular age,? AJMG 129A:215?217
Response to Devriendt et al. ?Pulmonary atresia/ventricular septal defect associated with facial port-wine stain and retinal vascular abnormality?
Double trisomy (Am J Med Genet 124A: 96?98)
The 22q11.2 deletion in African‐American patients: An underdiagnosed population? African‐American
Fibular aplasia, tibial campomelia, and oligosyndactyly in a male newborn infant: A case report and review of the literature
Gastric juvenile polyposis associated with germline SMAD4 mutation
Rapid array‐based genomic characterization of a subtle structural abnormality: A patient with psychosis and der(18)t(5;18)(p14.1;p11.23)
Differentiating campomelic dysplasia from Cumming syndrome
Retrospective family study of childhood medulloblastoma
Mutational analysis of the<i>TCOF1</i>gene in 11 Japanese patients with Treacher Collins Syndrome and mechanism of mutagenesis
Karyotype/phenotype correlations in duplication 4q: Evidence for a critical region within 4q27‐28 for preaxial defects
Reconstructing the behaviors of extinct species: An excursion into comparative paleoneurology
Down syndrome and comorbid autism‐spectrum disorder: Characterization using the aberrant behavior checklist
Mutation analysis of the <i>NSD1</i> gene in a group of 59 patients with congenital overgrowth Japanese, nonJapanese
Unrelated patients with a rearrangement of chromosome 2 causing duplication of 2p23 and deletion of 2q37
Elevated fibroblast growth factor‐23 in hypophosphatemic linear nevus sebaceous syndrome
Addressing the “petty tyranny” of IRBs
Bilateral preaxial polydactyly in a WAGR syndrome patient
Unusual phenotype with progressive vertebral fusion in a girl with an apparently balanced t(10;20)(p11;p13) translocation
Duplication of chromosome 4q: Renal pathology of two siblings
Baller?Gerold syndrome after fetal exposure to sodium valproate
Place of preimplantation diagnosis in genetic practice
Malformations of the axial skeleton in <i>Museum Vrolik</i> I: Homeotic transformations and numerical anomalies
Agenesis of tibia with bifid femur, congenital heart disease, and cleft lip with cleft palate or tracheoesophageal fistula: Possible variants of Gollop‐Wolfgang complex
An interstitial deletion of chromosome 7 at band q21: A case report and review
A QF-PCR system to detect chromosome 13 aneuploidy from as few as ten cells
Recombination in a male carrier of two reciprocal translocations involving chromosomes 14, 14′, 15, and 21 leading to balanced and unbalanced rearrangements in offspring
Isolated ectrodactyly caused by a heterozygous missense mutation in the transactivation domain of TP63
Association of deletion 22 and trisomy 21: A likely random association in patients with conotruncal heart defects
Myhre's syndrome in a girl with normal intelligence
Amish brittle hair syndrome gene maps to 7p14.1
Improved molecular diagnosis of dystrophinopathies in an unselected clinical cohort
Is multicenter collaborative research in clinical genetics dead and, if so, what killed it?
Use of targeted array‐based CGH for the clinical diagnosis of chromosomal imbalance: Is less more?
Mosaic tetrasomy 14pter‐q13 due to a supernumerary isodicentric derivate of proximal chromosome 14q
New findings in craniofacial dyssynostosis
Re: Microcephalic osteodysplastic primordial dwarfism with severe microdontia and skin anomalies [Kantaputra et al. 2004. Am J Med Genet 130A:181–190]
Response to: Microcephalic osteodysplastic primordial dwarfism with severe microdontia and skin anomalies by Dr. Judith Hall
Four novel <i>NIPBL</i> mutations in Japanese patients with Cornelia de Lange syndrome Japanese
<i>SOX2</i> anophthalmia syndrome
Carpal and tarsal synostoses and transverse reduction defects of the toes in two brothers heterozygous for a double de novo <i>NOGGIN</i> mutation
Hypothelia, syndactyly, and ear malformation?a variant of the scalp-ear-nipple syndrome?: Case report and review of the literature
Recurrence of Fabry disease as a result of paternal germline mosaicism for α-galactosidase a gene mutation
Autosomal dominant inheritance of left ventricular outflow tract obstruction
High incidence of malformation syndromes in a series of 1,073 children with cancer
Genotypic and phenotypic characterization of Noonan syndrome: New data and review of the literature
Factors associated with preterm delivery in mothers of children with Beckwith-Wiedemann syndrome: A case cohort study from the BWS registry
Craniosynostosis and ectopia lentis in a propositus whose parents are cousins
Equal proportion of adult male and female homozygous for the 677C ? T mutation in the methylenetetrahydrofolate reductase polymorphism
Escobar variant with pursed mouth, creased tongue, ophthalmologic features, and scoliosis in 6 children from Oman
Epidemiology of double aneuploidies involving chromosome 21 and the sex chromosomes
Prenatal diagnosis of trisomy 1q21-qter: Case report and review of literature
Detailed clinical description of four patients with 1.3 and 2.1 Mb chromosome imbalances derived from a familial t(12;17)(q24.33;q25.3)
Subtelomeric deletions of chromosome 6p: Molecular and cytogenetic characterization of three new cases with phenotypic overlap with Ritscher?Schinzel (3C) syndrome
Accuracy and precision in Bayesian analysis
Sex and congenital malformations: An international perspective
Identification of a novel mutation in theL-ferritin IRE leading to hereditary hyperferritinemia-cataract syndrome
Evidence based medicine in inborn errors of metabolism: Is there any and how to find it
Sudden infant death syndrome not caused by Norwegian Jervell and Lange‐Nielsen mutations
Partial trisomy 2q: Report of a patient with dup (2)(q33.1q35)
Frequency of incidental intracranial aneurysms in neurofibromatosis type 1
Characterization of the symptoms associated with dural ectasia in the Marfan patient
Scoliosis in CHARGE: A prospective survey and two case reports
Deletion of both <i>MTM1</i> and <i>MTMR1</i> genes in a boy with myotubular myopathy
Chromosome 18 aberrations and epilepsy: A review
Genetic counseling for<i>BRCA1</i>/<i>2</i>: A randomized controlled trial of two strategies to facilitate the education and counseling process
A kindred withMYH-associated polyposis and pilomatricomas
Trisomy 20 mosaicism caused by a maternal meiosis II error is associated with normal intellect but multiple congenital anomalies
<i>GC79</i>/<i>TRPS1</i> and tumorigenesis in humans
Homozygosity for a non-pseudogene complex glucocerebrosidase allele as cause of an atypical neuronopathic form of Gaucher disease
Threshold effect of urinary glycosaminoglycans and the walk test as indicators of disease progression in a survey of subjects with Mucopolysaccharidosis VI (Maroteaux-Lamy syndrome)
Cri du chat syndrome and complex karyotype in a patient with infantile spasms, hypsarrhythmia, nonketotic hyperglycinemia, and heterotopia
Inheritance analysis of congenital left ventricular outflow tract obstruction malformations: Segregation, multiplex relative risk, and heritability
Interstitial deletion 8q11.2‐q13 with congenital anomalies of CHARGE association
Behavioral profiles and symptoms of autism in CHARGE syndrome: Preliminary Canadian epidemiological data
Reducing challenging behaviors and fostering efficient learning of children with CHARGE syndrome
Cerebellar hypoplasia?endosteal sclerosis: A long term follow-up
Book review
Repetitive behaviors in CHARGE syndrome: Differential diagnosis and treatment options
CHARGE syndrome: Developmental and behavioral data
Psychological benefit of diagnostic certainty for mothers of children with disabilities: Lessons from Down syndrome
Interstitial deletion 11(p11.12p11.2) and analphoid marker formation results in inherited Potocki–Shaffer syndrome
Trisomy 15q25.2‐qter in an autistic child: Genotype–phenotype correlations
Isolated elevated sweat chloride concentrations in the presence of the rare mutation S1455X: An extremely mild form of <i>CFTR</i> dysfunction
DLX3 mutation associated with autosomal dominant amelogenesis imperfecta with taurodontism
Craniofacial features in osteogenesis imperfecta: A cephalometric study
Lateral meningocele syndrome: Vertical transmission and expansion of the phenotype
Mosaic monosomy of a neocentric ring chromosome maps brachyphalangy and growth hormone deficiency to 13q31.1‐13q32.3
Nevo syndrome is allelic to the kyphoscoliotic type of the Ehlers–Danlos syndrome (EDS VIA)
Supernumerary ring chromosome 20 in a mother and her child
CHARGE syndrome “behaviors”: Challenges or adaptations?
Updated diagnostic criteria for CHARGE syndrome: A proposal
A dominantly inherited spondylometaphyseal dysplasia with “corner fractures” and congenital scoliosis
Familial neurocardiogenic (vasovagal) syncope
<i>GJB2</i> mutations: Passage through Iran mirrors the south‐to‐north European gradient; supports a founder effect in southeastern Europe
A chicken consultation with ramifications
8.5 Mb deletion at distal 5p in a male ascertained for azoospermia
Monozygotic twins concordant for Crouzon syndrome
Valproate embryopathy: Clinical and cognitive profile in 5 siblings
Factors related to the development of communication in CHARGE syndrome
Congenital intrahepatic portosystemic venous shunt: An unusual feature in LEOPARD syndrome and in neurofibromatosis type 1
Familial recurrence of nonsyndromic congenital heart defects in first degree relatives of patients with deletion 22q11.2
A novel mutation in theDIA1 gene in a patient with methemoglobinemia type II
New type of twin spot
Novel contributions to the Asian CFTR mutation spectrum: Genotype and phenotype in Thai patients with cystic fibrosis
Guanidinoacetate methyltransferase deficiency identified in adults and a child with mental retardation
LIT1 andH19 methylation defects in isolated hemihyperplasia
Axenfeld-Rieger malformation and distinctive facial features: Clues to a recognizable 6p25 microdeletion syndrome
Novelc-KIT germline mutation in a family with gastrointestinal stromal tumors and cutaneous hyperpigmentation
A novel 9 bp deletion in the filamin a gene causes an otopalatodigital-spectrum disorder with a variable, intermediate phenotype
Behavioral features of CHARGE syndrome: Parents' perspectives of three children with CHARGE syndrome
Clinical evidence of decreased olfaction in Bardet-Biedl syndrome caused by a deletion in the<i>BBS4</i>Gene
Maternal inheritance in cyclic vomiting syndrome
ZFPM2/FOG2 andHEY2 genes analysis in nonsyndromic tricuspid atresia
Dominant negative mutations in the C-propeptide of COL2A1 cause platyspondylic lethal skeletal dysplasia, torrance type, and define a novel subfamily within the type 2 collagenopathies
Clinical and molecular characterization of a Chinese patient with auditory neuropathy associated with mitochondrial 12S rRNA T1095C mutation
Mutations inPOMT1 are found in a minority of patients with Walker-Warburg syndrome
Large deletion involving the 5?-UTR in the spastin gene caused mild phenotype of autosomal dominant hereditary spastic paraplegia
Autistic‐like behavior in CHARGE syndrome
An adult Sanfilippo type A patient with homozygous mutation R206P in the sulfamidase gene
A novel GJA1 mutation causes oculodentodigital dysplasia without syndactyly
Mapping of hereditary trichilemmal cyst<i>(TRICY1)</i>to chromosome 3p24-p21.2 and exclusion of β-<i>CATENIN</i>and<i>MLH1</i>
Mapping of a novel autosomal recessive nonsyndromic deafness locus (DFNB46) to chromosome 18p11.32-p11.31
Myopathy and phosphorylase kinase deficiency caused by a mutation in thePHKA1 gene
Subtelomeric rearrangements as neutral genomic polymorphisms
A patient with isochromosome 18q, radial-thumb aplasia, thrombocytopenia, and an unbalanced 10;18 chromosome translocation
Neonatal paroxysmal trismus and camptodactyly: The Crisponi syndrome
Behavior in CHARGE syndrome: Introduction to the special topic
Behavioral features of CHARGE syndrome (Hall–Hittner syndrome) comparison with Down syndrome, Prader–Willi syndrome, and Williams syndrome
Changing demographics of advanced maternal age (AMA) and the impact on the predicted incidence of Down syndrome in the United States: Implications for prenatal screening and genetic counseling
An epidemiological analysis of CHARGE syndrome: Preliminary results from a Canadian study
Clinical and genetic epidemiology of Bardet-Biedl syndrome in Newfoundland: A 22-year prospective, population-based, cohort study
Prevalence of theFMR1 mutation in Taiwan assessed by large-scale screening of newborn boys and analysis of DXS548-FRAXAC1 haplotype
Can specific deficits in executive functioning explain the behavioral characteristics of CHARGE syndrome: A case study
Speculations on the pathogenesis of CHARGE syndrome
Myocardial storage of chondroitin sulfate-containing moieties in Costello syndrome patients with severe hypertrophic cardiomyopathy
Simultaneous occurrence of neurofibromatosis type 1 and tuberous sclerosis in a young girl
Scott Rogers on dinosaur behavior, in: The Annals of Morphology
CHARGE syndrome from birth to adulthood: An individual reported on from 0 to 33 years
Book review
Some twin spots may not be twins
α-thalassemia/mental retardation syndrome in a 45,X male
De novo duplication of the short arm of chromosome 12: dup(12)(p13.1p13.3)
A woman with 46,XX,dup(16)(p13.11 p13.3) and the ATR-X phenotype
A splicing mutation in the ?/? GlcNAc-1-phosphotransferase gene results in an adult onset form of mucolipidosis III associated with sensory neuropathy and cardiomyopathy
A novel autosomal recessive nonsyndromic hearing impairment locus (DFNB42) maps to chromosome 3q13.31-q22.3
Adaptive behavior in children with CHARGE syndrome
Genomic and transcription studies as diagnostic tools for a prenatal detection of X-linked dilated cardiomyopathy due to a dystrophin gene mutation
Supernumerary der(1) marker chromosome derived from a ring chromosome 1 which has retained the original centromere and euchromatin from 1q21.1 ? q21.3 with substantial loss of 1q12 heterochromatin in
Joubert syndrome is not a cause of classical autism
Williams–Beuren syndrome and West “syndrome:” Causal association or contiguous gene deletion syndrome?
Intrafamilial phenotypic variability of osteopetrosis due to chloride channel 7 (CLCN7) mutations
Three patients with terminal deletions within the subtelomeric region of chromosome 9q
Further case report of a child with a 9q34 deletion and a review of the reported cases
<i>GJB2</i> mutations in keratitis‐ichthyosis‐deafness syndrome including its fatal form
CHARGE association in Sweden: Malformations and functional deficits Swedish
Anomalies of the kidney and urinary tract are common in de Lange syndrome
Critique of ?sibpair studies implicate chromosome 18 in essential hypertension? by S. Rutherford, M.P. Johnson, and L.R. Griffiths.Am J Med Genet 126A:241-247 (2004)
A new autosomal recessive oto-facial syndrome with midline malformations
Double-layered patella in multiple epiphyseal dysplasia is not exclusive toDTDST mutation
Truncus arteriosus and isochromosome 8q
CHARGE syndrome: 2005
Rare proximal interstitial deletion of chromosome 4q, del(4)(q13.2q21.22): New case and comparison with the literature
Mosaic trisomy 4: Long-term outcome on the first reported liveborn
MTHFD1 R653Q polymorphism is a maternal genetic risk factor for severe abruptio placentae
Phenotypic expression of genotype-phenotype correlation in cystic fibrosis patients carrying the 852del22 mutation
Neonatal toxicity and transient neurodevelopmental deficits following prenatal exposure to lithium: Another clinical report and a review of the literature
Marinesco–Sjögren syndrome in a male with mild dysmorphism
Idiopathic talipes equinovarus (ITEV) (clubfeet) in Texas
NKX2.5 and congenital heart defects: A population-based study
BRCA1/2 testing in hereditary breast and ovarian cancer families II: Impact on relationships
Critique of ?sibpair studies implicate chromosome 18 in essential hypertension? by S. Rutherford, M.P. Johnson, and L.R. Griffiths. 2004. Am J Med Genet 126A:241-247
14q32.3 deletion syndrome with autism
Preimplantation diagnosis for homeobox gene<i>HLXB9</i>mutation causing Currarino syndrome
A patient with a ring chromosome 2 and microdeletion of 2q detected using FISH: Further support for ?ring chromosome 2 syndrome?
The genetics of tethered cord syndrome
Bindewald syndrome: Tetralogy of Fallot, large ears, severe growth and mental retardation
Genetics of tethered cord ?syndrome?: The FG syndrome