American Journal of Medical Genetics Part A - 2002

156 articles | Last updated: 2025-12-03 14:12:55
Caucasian
3
White
1
European
2
Other
8
Article Title Cauc. White Euro. Other Phrases Used
T A T A T A T A
14q(22) deletion in a familial case of anophthalmia with polydactyly
Margareta Mikkelsen European Society of Human Genetics (ESHG); Danish, Danes, Denmark, German, Munich
Medial temporal lobe dysgenesis in Muenke syndrome and hypochondroplasia
Attitudes and distress levels in women at risk to carry a <i>BRCA1/BRCA2</i> gene mutation who decline genetic testing
Association study of autistic disorder and chromosome 16p
Methylenetetrahydrofolate reductase (MTHFR): incidence of mutations C677T and A1298C in Brazilian population and its correlation with plasma homocysteine levels in spina bifida
Twin brothers with MIDAS syndrome and XX karyotype
A Japanese girl with mental retardation, severe microretrognathia, and brachydactyly: Another case of the Gurrieri syndrome
Aural atresia and microtia in Kabuki syndrome
Homozygous inactivation of <i>NF1</i> gene in a patient with familial NF1 and disseminated neuroblastoma
Detection of point mutation in dystrophin gene reveals somatic and germline mosaicism in the mother of a patient with Duchenne muscular dystrophy
van den Ende–Gupta syndrome of blepharophimosis, arachnodactyly, and congenital contractures: Clinical delineation and recurrence in brothers Hispanic
Ten years follow up of a boy with a complex chromosomal rearrangement: Going from a &gt; 5 to 15‐breakpoint CCR
Interstitial deletion of the short arm of chromosome 1: Attempt to establish a clinical phenotype (46,XX,del (1)(p22p32))
Poland anomaly—report of an unusual family
Y chromosomal polysomy: A unique case of 49,XYYYY in amniotic fluid cells
Effects of<i>MECP2</i>mutation type, location and X‐inactivation in modulating Rett syndrome phenotype
Relationship of deficits of <i>FMR1</i> gene specific protein with physical phenotype of fragile X males and females in pedigrees: A new perspective
Another explanation for familial Cornelia de Lange syndrome
Prenatal diagnosis of a trisomy 7/maternal uniparental heterodisomy 7 mosaic fetus
Leukodystrophy associated with oligodontia in a large inbred family: Fortuitous association or new entity?
X‐chromosome inactivation (XCI) patterns in placental tissues of a paternally derived bal t(X;20) case
Complex chromosomal rearrangement and associated counseling issues in a family with Pelizaeus‐Merzbacher disease
Novel missense mutations and a 288‐bp exonic insertion in <i>PAX9</i> in families with autosomal dominant hypodontia
Bilateral Poland anomaly: Does it exist?
Syndromic form of X‐linked mental retardation with marked hypotonia in early life, severe mental handicap, and difficult adult behavior maps to Xp22
Prenatal diagnosis of mosaic tetrasomy 10p associated with megacisterna magna, echogenic focus of left ventricle, umbilical cord cysts and distal arthrogryposis
Novel perforin mutation in a patient with hemophagocytic lymphohistiocytosis and CD45 abnormal splicing
Familial MCA/MR syndrome due to inherited submicroscopic translocation t(18;21)(q22.1q21.3) with breakpoint at the Down syndrome critical region
FISH and cytogenetic characterization of a terminal chromosome 1q deletion: Clinical case report and phenotypic implications
Prenatal diagnosis of isolated femoral bent bone skeletal dysplasia: Problems in differential diagnosis and genetic counseling
September 11, 3 PM
Generalized skeletal dysplasia in mother and daughter with 22q11 deletion syndrome
Screening for cryptic chromosomal abnormalities in patients with mental retardation and dysmorphic facial features using telomere fish probes
Clinical and genetic aspects of trigonocephaly: A study of 25 cases
Sperm segregation patterns by fluorescence in situ hybridization studies of a 46,XY,t(2;6) heterozygote giving rise to a rare triploid product of conception with a 69,XXY,t(2;6)(p12;q24)der(6)t(2;6)(p
A supernumerary chromosome 20, identified by FISH, in a male with azoospermia—cause or coincidence?
<i>FOXL2</i>‐mutations in blepharophimosis‐ptosis—epicanthus inversus syndrome (BPES); challenges for genetic counseling in female patients
New case of “Apple‐Peel” intestinal atresia and ocular anomalies with mosaic variegated aneuploidy
Routine cytogenetic and FISH studies for 17p11/15q11 duplications and subtelomeric rearrangement studies in children with autism spectrum disorders
Molecular characterization of a 12q22‐q24 deletion associated with congenital deafness: Confirmation and refinement of the DFNA25 locus
Mutation analysis of the MECP2 gene in patients with Rett syndrome
High risk of malignancy in mosaic variegated aneuploidy syndrome
Exclusion of the <i>SALL1</i> gene as a cause of branchio‐oculo‐facial syndrome
CHARGE association and secondary hypoadrenalism
Teebi hypertelorism syndrome: Additional cases
Broad phenotypic spectrum caused by an identical heterozygous <i>CDMP‐1</i> mutation in three unrelated families
Spondyloepimetaphyseal dysplasia with joint laxity leptodactylic form: Clinical course and phenotypic variations in four patients
Early use of clinical <i>BRCA1/2</i> testing: Associations with race and breast cancer risk
Oligoyric microcephaly in a child with Williams syndrome
Somatic instability of the androgen receptor CAG repeat in a normal female
An unusual family with brachydactyly
New syndrome with generalized lipodystrophy and a distinctive facial appearance: Confirmation of Keppen‐Lubinski syndrome?
X‐linked recessive chondrodysplasia punctata: Spectrum of arylsulfatase E gene mutations and expanded clinical variability
Aural atresia, microtia, complex heart defect, and hearing loss syndrome: Additional case
Clinical paper and statistics
Recombinants of intrachromosomal transposition of subtelomeres in chromosomes 1 and 2: A cause of minute terminal chromosomal imbalances
Cryptic t(1;12)(q44;p13.3) translocation in a previously described syndrome with polymicrogyria, segregating as an apparently X‐linked trait
Bilateral microphthalmia with cyst, facial clefts, and limb anomalies: A new syndrome with features of Waardenburg syndrome, cerebro‐oculo‐nasal syndrome, and craniotelencephalic dysplasia
Fetology: Diagnosis and Management of the Fetal Patient, by D.W. Bianchi, T.M. Crombleholme, and M.E. D'Alton
Overgrowth Syndromes, Oxford Monographs on Medical Genetics, No. 43, by M.M. Cohen, Jr., G. Neri, and R. Weksberg
Pachygyria and polymicrogyria in 22q11 deletion syndrome
Biological and environmental contributions to adaptive behavior in fragile X syndrome
Prenatal diagnosis of a rare chromosomal instability syndrome: Variegated aneuploidy related to premature centromere division (PCD)
De novo interstitial tandem duplication of chromosome 20p12.1p13
Chromosomal fragility in patients with triple A syndrome
De novo mutation in the gene encoding connexin‐26 (<i>GJB2</i>) in a sporadic case of keratitis‐ichthyosis‐deafness (KID) syndrome
Female carriers of fragile X premutations have no increased risk for additional diseases other than premature ovarian failure
Extended phenotype of pontocerebellar hypoplasia with infantile spinal muscular atrophy
Autopsy on a case of Roberts syndrome reported in 1672: The earliest description?
Exclusion of <i>RNX</i> as a major gene in congenital central hypoventilation syndrome (CCHS, Ondine's curse)
The prevalence and manifestations of hereditary hemorrhagic telangiectasia in the Afro‐Caribbean population of the Netherlands Antilles: A family screening Afro‐Caribbean population; people of African descent
CFC syndrome
Cardio‐facio‐cutaneous syndrome phenotype and del(12q)
Editor's note: Regarding correspondence on CFC syndrome and interstitial 12q deletions
Parental consanguinity and congenital heart malformations in a developing country
Patient with Sotos syndrome, Wolff‐Parkinson‐White pattern on electrocardiogram, and two right‐sided accessory bypass tracts
Unknown diagnosis in two male cousins with facial abnormalities, optic atrophy, abnormal EEG, and severe psychomotor retardation
Patient with terminal duplication 3q and terminal deletion 5q: comparison with the 3q duplication syndrome and distal 5q deletion syndrome
Gaucher disease associated with parkinsonism: Four further case reports
Lack of association between <i>ZIC2</i> and <i>ZIC3</i> genes and the risk of neural tube defects (NTDs) in hispanic populations hispanic populations
An Introduction to Genetic Engineering, 2nd Edition, by Desmond S.T. Nicholl
Speech characteristics in the Kabuki syndrome
Parents' and children's attitudes toward the enrollment of minors in genetic susceptibility research: Implications for informed consent
An angel with Down syndrome in a sixteenth century Flemish Nativity painting one of the earliest European representations of Down syndrome
Double supernumerary isodicentric chromosomes derived from 15 resulting in partial hexasomy
Comment on Elejalde syndrome and relationship with Griscelli syndrome
Hypomelanosis, immunity, central nervous system: No more “and”, not the end
15‐Month‐old infant with failure to thrive, hepatomegaly, increased liver enzymes, hypoproteinemia, and seizures
Apparent encephalocele in twin fetus papyraceus with twin‐reversal arterial perfusion
Griscelli syndrome without hemophagocytosis in an eleven‐year‐old girl: Expanding the phenotypic spectrum of <i>Rab27A</i> mutations in humans Arabic origin
Hirschsprung disease, mental retardation, characteristic facial features, and mutation in the gene <i>ZFHX1B</i> (<i>SIP1</i>): Confirmation of the Mowat‐Wilson syndrome
Familial lateral semicircular canal malformation with external and middle ear abnormalities
Donepezil for the treatment of language deficits in adults with Down syndrome: A preliminary 24‐week open trial
Mosaicism in a patient with Down syndrome reveals post‐fertilization formation of a robertsonian translocation and isochromosome
Scimitar vein anomaly with multiple cardiac malformations, craniofacial, and central nervous system abnormalities in a brother and sister: Familial scimitar anomaly or new syndrome? Italian parents
Further delineation of the Toriello‐Carey syndrome: A report of two siblings
Poor outcome in Down syndrome fetuses with cardiac anomalies or growth retardation
Chromosome 22q11.2 deletion and phenotypic features in 30 patients with conotruncal heart defects Turkish
Unique case of deletion and duplication in the long arm of the Y chromosome in an individual with ambiguous genitalia
Genetic testing for hereditary colorectal cancer in children: Long‐term psychological effects
Novel CNS syndrome and ectodermal dysplasia
The Genetics and Biology of Sex Determination (Novartis Foundation Symposia #244), edited by Derek Chadwick and Jamie Goode
Concurrence of fragile X syndrome and 47, XYY in an individual with a Prader‐Willi‐like phenotype
Risk perception of participants in a family‐based genetic screening program on familial hypercholesterolemia
Postnatal growth failure, microcephaly, mental retardation, cataracts, large joint contractures, osteoporosis, cortical dysplasia, and cerebellar atrophy
18q‐ syndrome and ectodermal dysplasia syndrome: Description of a child and his family
Del 22Q11.2 and hemophagocytic lymphohistiocytosis: A non‐random association
Trisomy 8 mosaicism: Selective growth advantage of normal cells vs. growth disadvantage of trisomy 8 cells
Child with overgrowth, pigmentary streaks, polydactyly, and intestinal lymphangiectasia: Macrocephaly–cutis marmorata telangiectatica congenita syndrome or new disorder?
Documentation of anomalies not previously described in Fryns syndrome
Invited comment on Arnold et al., “Documentation of anomalies not previously described in Fryns syndrome”
Cardio‐facio‐cutaneous syndrome: First presentation in a 52‐year‐old woman
Lack of association between Y chromosome haplogroups and male infertility in Japanese men Japanese
Clinical and genetic heterogeneity in frontometaphyseal dysplasia: Severe progressive scoliosis in two families
Hereditary gingival fibromatosis (HGF) with hypertrichosis is unlinked to the HGF1 and HGF2 loci
Editor's note
Thermodynamic determination of β‐hexosaminidase isoenzymes in mononuclear and polymorphonuclear leukocyte populations
Distinctive spondylometaphyseal dysplasia in two siblings
Novel mutation in sonic hedgehog in non‐syndromic colobomatous microphthalmia
Muellerian aplasia associated with ring chromosome 8p12q12 mosaicism
Biochemical characterization of two (C300F, P425T) arylsulfatase a missense mutations
Prevalence of mitral valve prolapse in Stickler syndrome
Endogenous hydrogen sulfide overproduction in Down syndrome
Molecular, biochemical, and phenotypic analysis of a hemizygous male with a severe atypical phenotype for X‐linked dominant Conradi‐Hunermann‐Happle syndrome and a mutation in <i>EBP</i>
Interrupted aortic arch in a child with trisomy 5q31.1q35.1 due to a maternal (20;5) balanced insertion
What do ratings of cancer‐specific distress mean among women at high risk of breast and ovarian cancer?
True hermaphroditism with ambiguous genitalia due to a complicated mosaic karyotype: Clinical features, cytogenetic findings, and literature review
Hypertrichosis terminalis, gingival hyperplasia, and a characteristic face: A new distinct entity
Two new cases of analphoid marker chromosomes
Atypical progeroid syndrome: An unknown helicase gene defect?
Lack of association between eNOS gene polymorphisms and ischemic heart disease in the Spanish population
X‐linked dominant chondrodysplasia punctata (CDPX2) caused by single gene mosaicism in a male
A clinical perspective of cystic fibrosis and new genetic findings: Relationship of CFTR mutations to genotype–phenotype manifestations
Gaucher disease: In vivo evidence for allele dose leading to neuronopathic and nonneuronopathic phenotypes
Congenital myopathy, recurrent secretory diarrhea, bullous eruption of skin, microcephaly, and deafness: A new genetic syndrome?
Recurrence of complex camptopolydactyly in a sibling suggestive of autosomal recessive mode of inheritance
De novo dup(X)(q22.3q26) in a girl with evidence that functional disomy of X material is the cause of her abnormal phenotype
Humeroradial synostosis, ulnar aplasia and oligodactyly, with contralateral amelia, in a child with prenatal cocaine exposure
TGFβ/Smad signaling system and its pathologic correlates
Mesomelic and rhizomelic short stature: The phenotype of combined Leri‐Weill dyschondrosteosis and achondroplasia or hypochondroplasia
Is immunosuppression therapy in renal allograft recipients teratogenic? A single‐center experience
46,XY gonadal dysgenesis: Evidence for autosomal dominant transmission in a large kindred
First patient with trisomy 21 accompanied by an additional der(4)(:p11 → q11:) plus partial uniparental disomy 4p15‐16
Velocardiofacial syndrome in an unexplained XX male
Incidence of Smith‐Lemli‐Opitz syndrome in Ontario, Canada
Hemifacial myohyperplasia: An additional case
Down syndrome before down: A postscript
Communication with close and distant relatives in the context of genetic testing for hereditary breast and ovarian cancer in cancer patients
Further delineation of Wittwer syndrome and refinement of the mapping region
Mild phenotype in a 15‐year‐old boy with Pallister–Killian syndrome
Molecular cytogenetic analysis of a constitutional de novo interstitial deletion of chromosome 12p in a boy with developmental delay and congenital anomalies
45,X/46,XY mosaicism and fragile X syndrome
Reply to correspondence from Martínez‐Frías et al.—“Incidence of Smith‐Lemli‐Opitz syndrome in Ontario, Canada”
A distinct neurocognitive phenotype in female fragile‐X premutation carriers assessed with visual attention tasks
Two sibs with brachyolmia type Hobaek: Five year follow‐up through puberty